Ake sifunde ngomuthi wokugomela i-Fosdenopterin (umuthi wokuntuleka kwe-Molybdenum Cofactor)

Ukuletha umntwana osanda kuzalwa ekhaya kuyintokozo emndenini. Kodwa ngezinye izikhathi, ezinye izingane zingazalwa zinezimo zofuzo ezingavamile kakhulu. Kuvamile ngathi ukuzizwa sesaba kakhulu futhi sikhathazekile lapho sizwa ngalezi zinto. Kodwa namuhla, ngenxa yokuthi isayensi yezokwelapha isithuthuke kakhulu, manje kunezixazululo zezifo eziningi ezazingenakwelashwa ngaphambili. Namuhla, sizokhuluma ngomuthi okhethekile onikezwayo wesimo esingavamile kangaka. Lowo umuthi wokugomela i-Fosdenopterin.

Iyini le Fosdenopterin? Yenzani?

Kalula nje, i-Fosdenopterin (igama lomkhiqizo: i-Nulibry) umuthi osetshenziselwa ukwelapha isimo esingavamile kakhulu sezakhi zofuzo esibizwa ngokuthi i-Molybdenum cofactor deficiency (MoCD) . Kulungile, manje ake sibone ukuthi iyini i-MoCD. Cabanga ukuthi umzimba wethu ufana nefektri enkulu. Ukuze le fektri yenze konke kahle, idinga abasebenzi abancane abahlukene ababizwa ngama-enzyme. Ukuze le enzyme isebenze kahle, idinga enye ingxenye encane eyisizayo. Siyibiza ngokuthi i-cofactor. I-Molybdenum cofactor ingenye yomsizi obalulekile. Umuntu one-MoCD unesici sezakhi zofuzo emzimbeni wakhe esivimbela ekwenzeni le Molybdenum cofactor. Ngemuva kwalokho, ngenxa yalomsizi, amanye ama-enzyme awasebenzi. Ngenxa yalokho, ubuthi obuyingozi emzimbeni buqala ukuqongelela emzimbeni. Lawa ma-toxin, ikakhulukazi lawo abangela umonakalo obulalayo ebuchosheni, yilokho okwenzekayo ku-MoCD. Yilapho umuthi obizwa ngokuthi i-Fosdenopterin ungena khona. Lokho okwenziwa yilo muthi ukunikeza i-Molybdenum cofactor umzimba ongakwazi ukuyikhiqiza ngaphandle. Kufana nokuletha isisebenzi esilahlekile efektri. Bese lawo ma-enzyme angasebenzi aqala ukusebenza futhi, ukuqongelela kobuthi kuyaphela, futhi umonakalo ebuchosheni uyancishiswa.

Izinto okufanele uzitshele udokotela wakho ngaphambi kokuthatha imithi

Ngaphambi kokunikeza wena noma ingane yakho lo muthi, kubaluleke kakhulu ukuxoxa ngolwazi oluthile nodokotela wakho. Ngoba impumelelo nokuphepha kokwelashwa kuncike kulolo lwazi. Nazi ezinye izinto okufanele uqiniseke ukuthi uyazikhuluma:

• Ukungezwani komzimba : Sitshele uma une -allergies ku-Fosdenopterin noma kunoma yimuphi omunye umuthi, ukudla, udayi, noma izithasiselo.
• Ukukhulelwa : Uma ukhulelwe, uzama ukukhulelwa, noma usola ukuthi ukhulelwe, kufanele nakanjani utshele udokotela wakho.
• Uma ungumama oncelisayo: Uma ungumama oncelisayo, yazisa udokotela ngalokhu futhi.

Uma usitshela lolu lwazi ngokwethembeka futhi ungalufihli, kuzosiza kakhulu ithimba lezokwelapha ukukunikeza ukwelashwa okufanele nokuphephile kakhulu.

Uyisebenzisa kanjani le mithi?

I-Fosdenopterin iwumjovo ojovwa emthanjeni. Ngokuvamile unikezwa yithimba lezokwelapha esibhedlela noma emtholampilo. Kodwa-ke, kwezinye izimo, unganikezwa ngaphandle kwesibhedlela, ekhaya. Uma lokhu kwenzeka, awunalutho okufanele ukhathazeke ngalo. Ithimba lezokwelapha lizokuqeqesha ngokuphelele ukuthi ungalungiselela kanjani futhi unikeze lo muthi ngendlela efanele.

• Landela imiyalelo ngqo: Kubaluleke kakhulu ukuphuza umuthi njengoba nje udokotela wakho ekutshela, ngesikhathi esifanele, nsuku zonke. Qhubeka uwuthatha kuze kube yilapho ithimba lakho lezokwelapha likutshela ukuthi uyeke.
• Izinaliti nezinaliti ezisetshenzisiwe: Leli iphuzu elibaluleke kakhulu. Ungalokothi uphonse izinaliti nezinaliti ezisetshenzisiwe emgqonyeni kadoti. Kukhona isitsha esikhethekile sazo (isitsha sokuhlaba). Uma ungenaso, ungacela udokotela wakho noma ithimba lezokwelapha ukuthi akunike sona. Lokhu kuzokuvikela wena, umndeni wakho, kanye nendawo ezungezile.
• Imiyalelo Yokusebenzisa: Funda IMIYALELO YOKUSEBENZISA eza nalo muthi ngokucophelela. Uma unemibuzo mayelana nokuqukethwe, cela ithimba lakho lezokwelapha ukuthi likuchazele.

Yini okufanele uyenze uma uphuthelwa umthamo?

Lokhu kuyahlukahluka kancane kuye ngokuthi umuthi utholakala kuphi.

• Uma uphuza imithi yakho esibhedlela noma emtholampilo: Uma ungakwazi ukuya esimisweni sakho esihleliwe, shayela ithimba lakho lezokwelapha ngokushesha okukhulu. Kubaluleke kakhulu ukungaphuthelwa yisimiso sakho esihleliwe.
• Uma uphuza umuthi wakho ekhaya: Uma uphuthelwa umthamo, thatha ngokushesha nje lapho ukhumbula. Kodwa uma uphuza umthamo wakho olandelayo, linda okungenani amahora ayisithupha ngaphambi kokuthi uthathe umthamo ophuthelwe. Ungalokothi uthathe umthamo ophindwe kabili noma umthamo owengeziwe. Uma ungaqiniseki, khuluma nethimba lakho lezempilo ukuze uthole iseluleko.

Yini okufanele uyenze uma uphuza ngokweqile?

Uma ucabanga ukuthi uthathe umuthi omningi kakhulu, shayela ngokushesha i-National Poisons Information Centre e-National Hospital eColombo, noma uye eMnyangweni Wezimo Eziphuthumayo (ETU) wesibhedlela esiseduze.

Izinto okufanele uziqaphele uma usebenzisa umuthi

• Eminye imithi: Lo muthi akulindelekile ukuthi uhlangane neminye imithi. Kodwa-ke, kuphephile ukutshela udokotela wakho ngayo yonke eminye imithi oyithathayo (kufaka phakathi amavithamini , amakhambi, kanye nezithasiselo). Futhi, tshela udokotela wakho uma ubhema noma uphuza utshwala .
• Zivikele elangeni: Lokhu kubaluleke kakhulu. Isikhumba sakho singase sibe nomuzwa omkhulu elangeni ngenkathi uthatha lo muthi. Ngakho-ke, gwema ukuphuma elangeni ngangokunokwenzeka. Uma kufanele uphume, gqoka izingubo ezimboza isikhumba sakho kahle futhi usebenzise umuthi omuhle wokuvikela ilanga. Ungasebenzisi izibani zelanga noma imibhede yokushiswa kwelanga.
• Ukuhlolwa okuvamile: Qiniseka ukuthi uya kudokotela wakho. Kufanele uhlole njalo ukuthi ukwelashwa kwakho kuhamba kanjani. Uma izimpawu zakho zingathuthuki noma zibonakala ziba zimbi kakhulu, yazisa ithimba lakho lezokwelapha.

Yimiphi imiphumela emibi engaba khona yalo muthi?

Njenganoma yimuphi umuthi, i-Fosdenopterin ingabangela eminye imiphumela emibi. Kodwa-ke, akuwona wonke umuntu oyitholayo. Eminye yale miphumela iyingozi, kanti eminye ivamile. Into ebaluleke kakhulu ukuqaphela. Lolu hlu aluhlanganisi yonke imiphumela emibi engaba khona. Uma uhlangabezana nanoma yiziphi izimpawu ezingavamile, khuluma nodokotela wakho ukuze uthole iseluleko sezokwelapha.

Ungawugcina kanjani umuthi?

Kubaluleke kakhulu ukugcina lo muthi ngendlela efanele. Uma ugcinwe ngendlela engafanele, umuthi ungase ulahlekelwe ukusebenza kwawo.

• Gcina kude nezingane: Gcina kude nezingane nezilwane ezifuywayo.
• Amabhodlela angavulwanga: Lawa kufanele agcinwe efrijini ezingeni lokushisa eliphakathi kuka--25 no--10 degrees Celsius . Gcina ebhokisini lokuqala kuze kube yilapho uyisebenzisa. Vikela futhi ekukhanyeni. Susa ebhokisini cishe imizuzu engama-30 ngaphambi kokusebenzisa.
• Ngemva kokuxuba: Ngemva kokuxuba umuthi, ungagcinwa ekamelweni lokushisa noma efrijini ezingeni lokushisa eliphakathi kwama-degree Celsius angu-2 no-8 . Kodwa-ke, kumele usetshenziswe zingakapheli amahora angu-4 ukuxuba .
• Imithi ephelelwe yisikhathi: Lahla imithi ephelelwe yisikhathi.

Cela ithimba lakho lezokwelapha iseluleko sendlela yokulahla ngokuphephile imithi engasetshenziswanga nephelelwe yisikhathi. I-Fosdenopterin, i-Nulibry, ukuntuleka kwe-Molybdenum cofactor, i-MoCD, izifo zofuzo, izifo zobuntwana, umuthi wokugomela, imiphumela emibi, imithi, i-Sri Lanka