Ingabe ingane yakho encane ngezinye izikhathi yenza ngendlela exakile, sengathi ihleka imizuzwana embalwa nje? Noma ingabe ibonisa izimpawu zokuthomba ngaphambi kwesikhathi? Kuyaqondakala ukuzizwa wesaba kancane uma ubona lezi zinto. Namuhla sizokhuluma ngesimo sobuchopho esingadala lezi zimpawu, okuyinto engavamile, kodwa kubalulekile ukuqaphela.

Ngakho-ke iyini le hamartoma ye-hypothalamic?

Kalula nje, i-Hypothalamic Hamartoma (HH) iyisimila esikhula ku-hypothalamus, ingxenye yobuchopho etholakala ngaphakathi ebuchosheni . Kodwa-ke, ayisona isimila somdlavuza, okusho ukuthi ayinawo amangqamuzana omdlavuza (angenawo umdlavuza) . I-hypothalamus iyisakhiwo esincane esilingana ne-alimondi. Kodwa idlala indima ebaluleke kakhulu emzimbeni wethu. Isebenza njengomxhumanisi phakathi kwesistimu yethu ye-endocrine kanye nesistimu yezinzwa , isiza ukugcina i-homeostasis (ibhalansi) emzimbeni.

Cabanga ngale ndlela, i-hypothalamus ifana nephaneli yokulawula emzimbeni wethu. Ilawula lezi zinto:

• Ukushaya kwegazi
• Izinga lokushisa lomzimba
• Ingcindezi nokucindezeleka esikuzwayo
• Indlala nokoma
• Ukukhishwa kwama-hormone kusuka ku-pituitary gland
• Imijikelezo yokulala nokuvuka

Lesi simila, esibizwa ngokuthi i-hypothalamic hematoma , siqala ukwakheka ngenkathi umntwana esesesibelethweni (`isibeletho siyakhula') . Bese sikhula kancane kancane njengoba ubuchopho bukhula. Ingxenye engcono kakhulu ukuthi asisabalali kwezinye izingxenye zobuchopho noma kwezinye izingxenye zomzimba . Ngokuvamile, kuba nesimila esisodwa kuphela, kodwa akuvamile ukuba kube neziningana. Kunezindlela zokwelapha ezinhle zokulawula izimpawu zalesi simo.

Ngakho-ke yiziphi izimpawu zalesi simo se-hypothalamic hematoma (HH)?

Izimpawu zalesi simo zingahluka kumuntu nomuntu, kodwa kunezimpawu ezimbalwa eziyinhloko ezingabonakala:

• Ukuthomba kwangaphambi kwesikhathi
• Ukuquleka
• Izimpawu ze-neurological

Kuyini 'Ukuthomba Kwangaphambi Kokukhulelwa'?

Okwenzekayo ukuthi ubuchopho bethu buqala ukukhulula ama-hormone ocansi ngaphambi kwesikhathi sawo. Ngokuvamile , amantombazane angabonisa lezi zimpawu ngaphambi kweminyaka engu-8 kanye nabafana ngaphambi kweminyaka engu-9 .

Izimpawu ezingase zibonwe amantombazane :

• Ukuthuthukiswa kwebele
• Ukukhula kwezinwele emakhwapheni nasezindaweni zangasese
• Ukuqala kokuya esikhathini
• Induna

Izimpawu abafana abangase bazibone:

• Ukujula kwezwi
• Ukukhula kwezinwele ebusweni, emakhwapheni nasezindaweni zangasese
• Ukwandiswa kwe-scrotum nama-testicles
• Induna

Cabanga ukuthi kumelwe ukuba kubuhlungu kangakanani kuwe nendodakazi yakho lapho beqala ukubonisa lezi zinguquko kusenesikhathi kunabangane babo. Ngakho-ke uma ubona into efana nale, kungcono ukubona udokotela ngokushesha okukhulu.

Ake sifunde nangokuxhuzula.

Kuvamile futhi ukuthi ukuquleka kwesifo sokuwa kwenzeke ngalesi simo. Esinye sezifo ezivame kakhulu 'ukuquleka kwe-gelastic' . Lokhu kuwukuhleka okungazelelwe, okungalawuleki ngaphandle kwesizathu esibonakalayo . Kubangelwa ukungajwayelekile emsebenzini kagesi ebuchosheni. Lokhu kungahlala imizuzwana embalwa, kodwa kungenzeka izikhathi eziningana ngosuku, noma ezimweni ezimbi kakhulu, izikhathi eziningana ngehora.

Esikhathini esiningi, lolu hlobo lwesifo sokuwa luqala ingane ingakafiki ngisho nonyaka owodwa ubudala . Kodwa-ke, ngemva kweminyaka eyi-10, ukuvama kwalokhu kungabonakala kuncipha.

Ngaphezu kwalesi sifo sokuwa esibangelwa yi-gelatinous, kunezinye izinhlobo zesifo sokuwa:

• Ukuquleka kwe-Atonic: Kulokhu, kuba nokulahlekelwa okungazelelwe kokulawula imisipha, futhi ungase uquleke, njengokungathi othile ukucindezele.
• Ukuquleka kwe-Dacrystal: Lokhu ukukhala okungazelelwe, okungalawuleki. Lokhu kwenzeka ngaphandle kwesizathu esibonakalayo.
• Ukuquleka kwe-Tonic-clonic: Yilokhu abantu abaningi abakwaziyo ngokuthi "ukuqina." Kuba khona ukulahlekelwa ukwazi, bese umzimba uqhaqhazela futhi unyakaze ngokungalawuleki.

Ziyini izimpawu ze-neurological?

Lesi simo, esibizwa ngokuthi i-hypothalamic hematoma (HH), singathinta nokuziphatha kwengane yakho, imizwa yayo, kanye nokusebenza kwengqondo . Lokhu kusho ukuthi:

• Isifo sokungakwazi ukunaka/sokungasebenzi kahle (ADHD)
• Ukuphazamiseka kokuziphatha
• Ukukhubazeka kwengqondo
• Ukushintshashintsha kwemizwa, ukuhlala ngendlela efanayo ngezikhathi ezahlukene ('Ukuphazamiseka kwemizwa')
• Isifo sokungavumelani nokuphikisa (isifo sokungavumelani nokuphikisa)
• Ukuziphatha okusabelayo (isibonelo, ukuthukuthela ngokushesha, ukuba nolaka)
• Izinkinga ngenkumbulo yesikhashana

Njengabazali, sikhathazeka kakhulu lapho ingane ibonisa eyodwa noma ngaphezulu yalezi zimpawu. Kodwa kubalulekile ukukhumbula ukuthi kunezindlela zokwelapha ezinconywa ngodokotela zazo zonke lezi zimpawu.

Yiziphi izinhlobo eziyinhloko ze-hypothalamic hematoma (HH)?

Kunezinhlobo ezimbili eziyinhloko ze-hematoma ye-hypothalamic, ezihlukaniswe ngokwendawo yesimila kanye nezimpawu ezisibangelayo :

1. I-Intrahypothalamic lesion: Kulesi simo, isimila sitholakala eduze kwangemuva kwe-hypothalamus yakho. Lokhu kuphazamisa ukusebenza kukagesi kobuchopho, okungabangela ukuquleka kanye nokuziphatha okungajwayelekile.

2. Isilonda se-Parahypothalamic (Isilonda esithambile - `Isilonda se-Parahypothalamic`):Kulesi simo, isimila sitholakala eduze kwengaphambili le-hypothalamus. Lolu hlobo luvame ukuhlotshaniswa nokuthomba kwasekuqaleni.

Nokho, ngezinye izikhathi zombili lezi zinhlobo zingaba khona kumuntu oyedwa ngesikhathi esisodwa.

Kungani le hematoma ye-hypothalamic (HH) yakheka? Iyini imbangela?

Eqinisweni, ochwepheshe abasazi kahle ukuthi yini ebangela i-HH. Futhi ayikho indlela yokuyivimbela. Esikhathini esiningi, lesi simo senzeka 'ngokungahleliwe.' Lokho kusho ukuthi asihambi emindenini . Ngakho amathuba okuthi usithole njengefa aphansi kakhulu.

Kodwa-ke, ucwaningo lwamuva nje luthole uhlobo oluthile lwesakhi sofuzo esibizwa ngokuthi i-GLI3 ezicutshini zesimila ezivela ezimila ezikhishwe. Ezinye izinhlobo zezakhi zofuzo nazo zitholakale kulezi zimila ezikhishwe. Ucwaningo olwengeziwe luyaqhubeka ngalezi zakhi zofuzo.

Enye into ukuthi kungase kube nokuxhumana phakathi kwale hematoma ye-hypothalamic kanye nesimo sofuzo esibizwa ngokuthi i-Pallister-Hall syndrome (PHS) . Lesi simo se-PHS sibangelwa uhlobo lofuzo. Singabangela ukukhubazeka ekukhuleni kwezandla, izinyawo, i-larynx (ibhokisi lezwi), kanye ne-anus.

Yiziphi izinto ezibangela lesi simo?

Lesi simo singathinta noma ubani. Sivame kakhulu kwabesilisa . I-HH ithinta kakhulu izingane kanye nabantu abadala abasebasha. Kodwa-ke, kwezinye izimo, lesi simo singase singabonwa kuze kube yilapho izimpawu zibonakala lapho umuntu esemdala.

Yiziphi izinkinga ezingaba khona ze-hypothalamic hematoma (HH)?

Ukuthomba ngaphambi kwesikhathi kungathinta impilo yengane engokomzimba nengokwengqondo , ikakhulukazi lapho imizimba yayo ishintsha ngokushesha kunezinye izingane ezingontanga yayo. Isibonelo, bangase babe nobude obufushane . Ngaphezu kwalokho, ingane ingase ingakwazi ukuqonda lezi zinguquko kahle. Lokhu kungathinta ukuzethemba kwayo kanye nenhlalakahle yayo engokomzwelo. Ithimba lezokwelapha lengane yakho lingasiza ekuphatheni noma yiziphi izinkinga ezingase zivele.

Lesi simo se-hypothalamic hematoma (HH) sitholakala kanjani?

Udokotela wakho angenza izivivinyo eziningana zezithombe ukuqinisekisa isimo se-HH.

• Ukuskena kwe-MRI (MRI - Magnetic Resonance Imaging): Lokhu kungathatha izithombe ezicacile nezinemininingwane yobuchopho bakho. Izingane ezincane zingadinga ukunikezwa umuthi wokudambisa ukuze zihlale zinganyakazi ngesikhathi se-MRI. Lokhu kungenxa yokuthi uma zihamba, izithombe zingase zingacaci. Cabanga ngakho njengesithombe esithathwayo futhi uma zihamba, izithombe zizoba zingacaci.

• Ukuhlolwa kwe-EEG (`EEG - Electroencephalogram`): Uma unesifo sokuwa, udokotela wakho angase futhi akuyalele ukuhlolwa kwe-EEG. Lokhu kwenzelwa ukuqapha umsebenzi kagesi ebuchosheni bakho . Njenge-ECG yenhliziyo yethu, lokhu kuhlola umsebenzi wobuchopho.

• Ukuhlolwa kwemizwa: Lokhu kulinganisa ubukhulu bezinkinga zengqondo, njengokucabanga, ukufunda, kanye nenkumbulo . Udokotela wakho angase futhi enze ukuhlolwa kwegazi ukuhlola amazinga ama-hormone. Lokhu kuhlolwa kungasiza ekuhleleni ukwelashwa.

Ngezinye izikhathi, i-HH ingaba nzima ukuyixilonga ngoba izimpawu zayo zingafana nezezinye izimo zezinzwa .

Kulungile, pho yiziphi izindlela zokwelapha lokhu?

Izindaba ezinhle ukuthi kunezindlela zokwelapha lesi simo, i-hypothalamic hematoma (HH). Kunezindlela ezimbili zokwelapha eziyinhloko:

• Imithi yokulawula ukuthomba ngaphambi kwesikhathi: Lokhu kusebenzisa uhlobo lwemithi ebizwa ngokuthi 'ama-agonist e-Gonadotropin-releasing hormone' . Le mithi isebenza ngokulawula ukukhishwa kwama-hormone ngaphambi kwesikhathi, njengoba kushiwo ngaphambili.
• Ukuhlinzwa ukulawula ukuquleka kwesifo sokuwa: Ake sixoxe ngalokhu ngemininingwane ethe xaxa.

Ngaphezu kwalokho, udokotela wengane yakho angase ancome ukwesekwa kwezemfundo esikoleni, ukwelashwa, noma eminye imithi yezinkinga zemizwa, ukuziphatha, kanye nezengqondo.

Yikuphi ukuhlinzwa okwenziwayo kwe-hypothalamic hematoma (HH)?

Ukuze kulawulwe ukuquleka, udokotela angase ancome ukuhlinzwa kwesifo sokuwa noma enye inqubo yokususa noma ukubhubhisa i-hematoma. Imithi yokuvimbela ukuquleka ngokuvamile ayisebenzi ekuqulekeni kwe-gelastic . Kodwa-ke, ingasiza ekulawuleni ezinye izinhlobo zokuquleka.

Manje ake sibone ukuthi ziyini lezi zinhlobo zokuhlinzwa:

• Ukuhlinzwa Kommese We-Gamma: Empeleni lolu uhlobo lokuhlinzwa, kodwa uhlobo lokwelashwa ngemisebe okwenziwa ngaphandle kokusikwa kwesikhumba . Ngokukhethekile, lusebenzisa imisebe enamandla yamandla ukubhubhisa isimila.
• Ukususwa kwesimila (ukuhlinzwa kokususwa): Kulokhu, udokotela ohlinzayo ususa isimila ngokuvula ugebhezi (i-craniotomy) noma ngokwenza imbobo encane egebhezini bese efaka ithuluzi elincane elibizwa ngokuthi i-endoscope ngalo.
• Ukususwa kwe-laser ye-stereotactic: Lokhu akuhlaseli kakhulu.Indlela. Isimila sibhujiswa ukukhanya kwe-laser okuthunyelwa ngekhebula le-fiber optic.
• I-Stereotactic thermoablation: Lolu futhi uhlobo lokwelashwa kwe-ablation. Lusebenzisa ukushisa ukwelapha i-hematoma . Udokotela ohlinzayo ufaka ama-probe amancane ngekhanda endaweni lapho kukhona khona isimila. Ama-probe abe esefudunyezwa kusetshenziswa amaza omsakazo ukuze abhubhise izicubu zesimila.

Nakuba lezi zinqubo zokuhlinzwa zingase zizwakale ziyinkimbinkimbi kancane, odokotela bazochaza konke ngokuningiliziwe.

Iyini iphrojekthi yokululama kulesi simo?

Ezimweni eziningi , isibikezelo (noma umbono) we-hypothalamic hematoma (HH) sihle , njengoba kunezindlela zokwelapha ezisebenzayo zokulawula izimpawu.

Ukuhlinzwa kunganciphisa ukuvama kanye nobukhali bokuxhuzula. Abanye abantu bahlala bengenaso nhlobo isithuthwane ngemva kokuhlinzwa . Kwezinye izimo, uma i-hematoma ingasuswa ngokuphephile nangokuphelele, lesi simo singase selapheke. Kodwa-ke, kunengozi yokuthi isithuthwane sibuye.

Njengoba kushiwo ngaphambili, ukujova njalo ngenyanga kwemithi evimbela ukukhishwa kwamahomoni athile kungasiza ekulawuleni izimpawu zokuthomba ngaphambi kwesikhathi. Lapho ingane yakho ifinyelela eminyakeni lapho ukuthomba kuvame ukwenzeka khona, udokotela angayekisa le mithi. Iningi lezingane nentsha lizodlula ekuthombeni nasekukhuleni ngokocansi njengoba kulindelekile ngalesi sikhathi .

Kuye ngesimo sengane yakho, udokotela wayo angakunikeza ulwazi olungcono kakhulu.

Kuthiwani ngesilinganiso sokusinda?

Ikhono lokuphila nalesi simo ('isikhathi sokuphila') lingahluka kumuntu nomuntu. Kuncike ezintweni eziningana:

• Usayizi kanye nohlobo lwesimila se-hematoma
• Ukuthi ukuquleka kwesifo sokuwa kukhulu kangakanani futhi kuvame kangakanani
• Iphumelela kangakanani le ndlela yokwelapha?

Udokotela wakho uzokuchazela lokhu ngemva kokucabangela zonke lezi zici.

Kodwa-ke, kunengozi yokufa okungazelelwe kwesifo sokuwa (i-SUDEP) ngale hematoma engaphansi kwe-hypothalamic. Ngakho-ke, udokotela wakho uzokusiza ukuthi uzigcine uphephile futhi adale uhlelo lokwelashwa lokulawula ukuquleka kwakho kwesifo sokuwa.

Uma ingane yami inalezi zimpawu, kufanele ngimbone nini udokotela?

Uma unenkinga ngengane yakho, uyayazi kangcono . Ngakho-ke ungangabazi ukubona udokotela, noma ngabe kuyinto encane nje. Qaphela kakhulu lezi zimpawu:

• Izimo zesifo sokuwa (ukuhleka, ukugxumagxuma, ukuwa)
• Ukuthomba ngaphambi kwesikhathi (isib., ukukhula kwezinwele kusenesikhathi, ukujula kwezwi)
• Izinguquko ekunakeni, ekukhumbuleni, noma ekhonweni lokufunda
• Izinguquko zokuziphatha (isib., ukuthukuthela ngezinto ezincane, ukucasuka)
• Ukungalingani kwama-hormone (isb., ukoma ngokweqile, izinguquko ekufiseni ukudla, ukushintshashintsha kwemizwelo okukhulu)

Uma ingane yami ine-hypothalamic hematoma (HH), yimiphi imibuzo okufanele ngiyibuze udokotela?

Uma usuthole ukuthi ingane yakho ine-HH, ungabuza udokotela imibuzo efana nale:

• Hlobo luni lokwelashwa olunconywayo?
• Kungenzeka kangakanani ukuthi kuzodingeka elashwe noma ahlinzwe kaningi?
• Iyini imiphumela emibi yokwelashwa?
• Lokhu kwelashwa kuzothinta kanjani inqubo yansuku zonke yengane yami, umsebenzi wesikole, kanye nemisebenzi evamile?

Kuvamile ukuzizwa wesaba futhi ushaqekile uma utshelwa ukuthi unesimila sobuchopho, uma unesifo sokuwa, noma uma ubhekana nezinguquko emzimbeni wakho ngaphambi kokuba uguge. Kodwa ingxenye engcono kakhulu ukuthi kunezindlela zokwelapha ezisebenzayo zokuphatha izimpawu ze-hypothalamic hematoma . Kuzodingeka uhlale uthintana nethimba lakho lezokwelapha. Bazoqinisekisa ukuthi izimpawu zakho aziphazamisi impilo yakho yomzimba noma yengqondo. Ukuhlinzwa kunganciphisa ukuvama nobukhali bezimpawu zakho, ngakho-ke khuluma nodokotela wakho mayelana nokuthi ungumuntu ofanele yini.

Ngakho-ke, yiziphi izinto ezibaluleke kakhulu okufanele uzikhumbule kulokho esikhulume ngakho? (Umyalezo Wokuya Ekhaya)

I-Hypothalamic hematoma (HH) iyigama elithusayo kancane, kodwa kubaluleke kakhulu ukuliqaphela.

Khumbula, lokhu akuwona umdlavuza. Futhi lesi yisimo esenzeka lapho kuzalwa umntwana.

• Izici eziyinhloko: Ukuthomba ngaphambi kwesikhathi, izinhlobo ezahlukene zokuxhuzula (ikakhulukazi 'ukuxhuzula kwe-Gelastic'), kanye nezinkinga zokuziphatha/zokufunda yizona eziyinhloko.
• Imbangela eqondile ayaziwa: Esikhathini esiningi, lokhu kwenzeka ngokungahleliwe. Akuvamile ukuthi kube yifa.
• Kunezindlela zokwelapha ezinhle: Kunezindlela zokwelapha ezisebenzayo, njengemithi kanye nokuhlinzwa, ukulawula izimpawu, ikakhulukazi zesifo sokuwa kanye nokuthomba ngaphambi kwesikhathi.
• Ukuqashelwa kusenesikhathi kubalulekile: Uma usola ukuthi ingane yakho inayo noma iyiphi yalezi zimpawu, bheka udokotela ngokushesha. Uma ukwelashwa kuqala ngokushesha, umphumela uba ngcono.
• Awuwedwa: Lokhu kungaba nzima ngokomzwelo kuwe nakumntanakho. Ukusekelwa odokotela, abeluleki nomndeni kubaluleke kakhulu.

Ngiyethemba ukuthi lolu lwazi luzokusiza. Kungakhathaliseki ukuthi kwenzekani, kungcono ukukhuluma nodokotela futhi uthole iseluleko ngaphandle kokwesaba.

I- Hypothalamic hematoma, isimila sobuchopho, ukuthomba kwengane, isifo sokuwa, isifo sokuwa esibangelwa yi-gelatinous, izinkinga zamahomoni, ukuhlinzwa kobuchopho