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Ingabe uhlangabezana nokugcwala kwamafutha ezingxenyeni ezahlukene zomzimba wakho? Ake sifunde nge-Lipodystrophy!

Ingabe uhlangabezana nokugcwala kwamafutha ezingxenyeni ezahlukene zomzimba wakho? Ake sifunde nge-Lipodystrophy!

Wake wabona, noma wabhekana nokulahlekelwa amafutha ngokuzumayo kwezinye izindawo zomzimba wakho, noma ukwanda kwamafutha okungafuneki kwezinye izindawo? Lokhu ngezinye izikhathi kungaba yinto engenakwenzeka. Namuhla sizokhuluma ngalesi simo. Ngokwezokwelapha, lokhu kubizwa ngokuthi i-Lipodystrophy . Ungakhathazeki, yize igama lingase lizwakale lingavamile, ake sixoxe ngakho kalula.

Kuyini i-Lipodystrophy?

Kalula nje, i-Lipodystrophy ukulahleka okuphelele noma okuyingxenye kwezicubu zamafutha, lokho esivame ukukubiza ngokuthi “amafutha,” kwezinye izindawo, noma ukunqwabelana kwamafutha okungavamile ezindaweni ezahlukene zomzimba.

Zicabange uncipha isisindo ezindaweni ezithile zomzimba wakho, njengezingalo nemilenze yakho, kuyilapho uthola amafutha amaningi ezindaweni ezifana nobuso bakho nentamo. Yilokhu okwenzekayo ku-Lipodystrophy. Kunezinhlobo ezahlukene zalesi simo, ezinye zazo ezingezofuzo (okungukuthi, into esizalwa nayo), kanti ezinye zikhula kamuva ngenxa yezinye izimo zezokwelapha. Uhlobo ngalunye luthinta abantu ngendlela ehlukile futhi lunezimpawu ezahlukene.

Kungani amafutha (izicubu zamafutha) ebaluleke kangaka emzimbeni wethu?

Manje ungase ucabange, "Uma unamafutha amancane, kungcono." Kodwa empeleni, izicubu zamafutha zenza imisebenzi eminingi ebalulekile emizimbeni yethu. Bheka:

  • Ukugcinwa kwamandla: Kukulezi zicubu ezinamafutha lapho amakhalori engeziwe esiwathola ekudleni esikudlayo agcinwa khona njengamandla.
  • Ukuvikela: Kuhlinzeka ngesivikelo esifana nomcamelo ezithweni ezahlukahlukene zomzimba wethu.
  • Ukugcina ukufudumala: Kugcina ukushisa komzimba futhi kusivikele emakhazeni endawo ezungezile.
  • Ukukhishwa kwama-hormone: Ama-hormone amaningana abalulekile, njenge -leptin, akhiqizwa futhi akhishwe egazini.
  • Ukulawula ukuvuvukala: Kuphinde kusize ukulawula ukuvuvukala emzimbeni.

Ngakho-ke, uma lesi zicubu zamafutha zilahleka noma zibekwe ngendlela engavamile ngenxa ye-lipodystrophy, akugcini nje ngokushintsha ukubukeka kwethu, kodwa nemisebenzi ebalulekile ye-metabolic emzimbeni nayo iyaphazamiseka. Abantu abaningi abane-lipodystrophy basengozini yokuthola izifo ezifana nesifo sikashukela kanye nokuba namazinga e-cholesterol egazini angajwayelekile.

Ingabe zikhona izinhlobo ze-lipodystrophy?

Yebo, i-Lipodystrophy ingahlukaniswa ngezinhlobo ezimbili eziyinhloko: izakhi zofuzo kanye ne-acquired.

Izinhlobo ze-Lipodystrophy yezakhi zofuzo

Lezi zizuzwe njengefa, okungukuthi, izinhlobo ezenzeka ngenxa yokuguquka kwezakhi zofuzo.

  • I-Congenital Generalized Lipodystrophy (CGL): Lesi yi -Berardinelli-Seip syndrome.Yaziwa nangokuthi. Lesi yisimo esingavamile kakhulu. Kulokhu, amafutha omzimba acishe alahleke ngokuphelele noma kakhulu. Lokhu kubangelwa yisici sofuzo esikhona lapho kuzalwa. Lesi simo ngokuvamile singatholakala phakathi nonyaka wokuqala wokuphila.
  • I-Familial Partial Lipodystrophy (FPLD): Lesi futhi yisimo esibangelwa izakhi zofuzo. Kodwa-ke, sivame ukutholakala kamuva ekuphileni. Kulesi simo, ingane ilahlekelwa amafutha ikakhulukazi emilenzeni nasezingalweni, futhi iqoqa amafutha amaningi ebusweni nasentanyeni.

Izinhlobo ze-Acquired Lipodystrophy

Lezi yizinhlobo ezivela ngemva kokuzalwa kwethu kanye nangesikhathi sokuphila kwethu ngezizathu ezahlukene.

  • I-Acquired Generalized Lipodystrophy (AGL): Eyaziwa nangokuthi i-Lawrence syndrome , lesi simo sibangela ukulahleka kwamafutha, ngokuvamile ebusweni, entanyeni, ezingalweni nasemilenzeni. Lokhu kulahlekelwa kwamafutha kungenzeka ngokushesha, emavikini ambalwa, noma kancane kancane ezinyangeni noma eminyakeni. Ngokuvamile kuqala ebuntwaneni noma ebusheni, kodwa kungenzeka kunoma yimuphi ubudala. Kunezimbangela eziningana ezingaba khona ze-AGL.
  • I-Acquired Partial Lipodystrophy (APL): Eyaziwa nangokuthi i-Barraquer-Simons syndrome , lesi simo sibangela ukulahlekelwa kancane kancane kwamafutha ebusweni, entanyeni, ezingalweni nasesifubeni ngesikhathi sobuntwana. Abanye abantu bangase babe namafutha amaningi ezindaweni ezifana nesisu, imilenze, nezinqe. I-APL ivame ukuhlotshaniswa nezimo zokuzivikela komzimba .
  • I-lipodystrophy (LD-HIV) ebangelwa ukwelashwa nge-antiretroviral esebenzayo kakhulu (HAART): Lolu hlobo lwe-lipodystrophy lwenzeka kubantu abangenwe yigciwane le-human immunodeficiency virus (HIV) ngemuva kokuthola ukwelashwa nge-antiretroviral esebenzayo kakhulu (HAART) okuhlanganisa ne-HIV-1 protease inhibitors . Ukwenzeka kwalesi simo kuncike ekuqineni nasekudeni kwesikhathi sokwelashwa. Abantu abane-LD-HIV bavame ukulahlekelwa amafutha kancane kancane ezingalweni zabo, emilenzeni nasebusweni. Abanye abantu bangase bathole amafutha amaningi ebusweni babo, entanyeni, emhlane ongaphezulu, nasesinqeni.
  • I-Localized Lipodystrophy: Lokhu kwenzeka lapho amafutha elahleka endaweni encane yomzimba kuphela. Isibonelo, lesi simo singavela uma imithi (njenge-insulin) ifakwa endaweni efanayo ngokuphindaphindiwe. Ibukeka njenge-dimple encane, kodwa isikhumba esiphezu kwayo ngokuvamile asithinteki.

Ingabe i-Lipodystrophy ne-Lipoatrophy ziyinto efanayo?

I-Lipodystrophy yigama elijwayelekile lokusatshalaliswa kwamafutha okungavamile. Liphinde lihlobane ne -Lipoatrophy , okusho ukulahlekelwa amafutha. Abanye ososayensi nodokotela basebenzisa womabili la magama ukuchaza isimo esifanayo. Kalula nje, i-Lipoatrophy iyi-subset ye-Lipodystrophy.

Ubani othinteka kakhulu yilesi simo? Sivame kangakanani?

Izinhlobo eziningi ze-lipodystrophy ziqala ebuntwaneni, kodwa izinhlobo ezitholakalayo zingakhula nakubantu abadala.

Ngaphandle kwe -HAART-induced lipodystrophy (LD-HIV) , ezinye izinhlobo ze-acquired lipodystrophy zivame ukubathinta abesifazane. Ngenxa yokuthi ukutheleleka nge-HIV kuvame kakhulu kwabesilisa, i-LD-HIV ivame kakhulu nakwabesilisa.

Ngokuvamile, i-lipodystrophy ayivamile kakhulu . Kodwa-ke, izinhlobo ze-lipodystrophy ezitholakalayo (ukuphila konke) ziya ngokuya zivamile ngenxa yemiphumela emibi yemithi ethile.

I-lipodystrophy ithinta kanjani umzimba wami?

Uhlobo ngalunye lwe-lipodystrophy luthinta umzimba ngendlela ehlukile, kodwa kunezici ezimbili eziyinhloko ezivamile: ukulahlekelwa kwezicubu zamafutha kanye nokuntuleka kwe-hormone leptin .

Umphumela wokulahlekelwa yizicubu zamafutha emzimbeni

Izicubu zethu zamafutha zakhiwe ngamaseli abizwa ngokuthi ama-adipocytes . Iseli ngalinye lama-adipocyte liqukethe cishe amaconsi e-lipid angu-90%. Lawa ma-adipocytes agcina amafutha (ama-triglycerides). Uma lawa maseli amafutha onakele ngenxa ye-lipodystrophy, awakwazi ukugcina amafutha kahle.

Kwezinye izimo ze-Lipodystrophy, la mafutha alahlekile abekwa ngendlela engafanele kwezinye izicubu zomzimba wethu, isibonelo, esibindini, kuma-pancreas, noma ezicutshini zemisipha. Lokhu kungaholela ezinkingeni zempilo ezifana nalezi:

  • Isifo sesibindi esinamafutha / i-hepatic steatosis
  • Ukumelana ne-insulin kanye namazinga aphezulu e-insulin egazini (hyperinsulinemia)
  • Isifo Sikashukela (i-Diabetes Mellitus)
  • Amazinga aphezulu e-triglycerides egazini (i-hypertriglyceridemia)
  • I-Pancreatitis
  • I-Metabolic syndrome
  • Isifo semithambo ye-coronary

Kodwa khumbula, akubona bonke abantu abane-lipodystrophy abazoba nalezi zimo. Abanye bangaba nezinhlobo ezithambile, kanti abanye bangaba nezinhlobo ezimbi kakhulu.

Imiphumela Yokuntuleka Kwe-Leptin Emzimbeni

Njengoba abantu abane-lipodystrophy belahlekelwa izicubu zamafutha, balahlekelwa nama-hormone athile, ikakhulukazi i-hormone i-leptin .

I-Leptin iyi-hormone ekhiqizwa yizicubu zethu zamafutha. Isisiza ukuthi silondoloze isisindo somzimba esijwayelekile isikhathi eside. Uyazi ukuthi kanjani? Ngokusenza sizizwe sanelisekile futhi silawule indlala yethu. Ososayensi basacwaninga nge-leptin. Bakholelwa ukuthi i-leptin ithinta i-metabolism yethu, umsebenzi wesistimu ye-endocrine , kanye nomsebenzi wesistimu yokuzivikela komzimba .

Abantu abane-lipodystrophy bangase babe namazinga e-leptin aphansi, okungaholela ekulambeni ngokweqile, ukumelana ne-insulin, kanye nezinye izinkinga zempilo.

Ziyini izimpawu ze-lipodystrophy?

Ngenxa yokuthi kunezinhlobo eziningi ze-lipodystrophy, izimpawu nazo ziyahlukahluka kakhulu.

Uphawu oluvame kakhulu ukulahleka kwamafutha okusobala nokuqhubekayo kwezinye izindawo zomzimba, kuyilapho ngesikhathi esifanayo, ukunqwabelana kwamafutha okungavamile noma okungafunwa kwezinye izindawo zomzimba.

Isibonelo, abantu abane -acquired partial lipodystrophy (APL) balahlekelwa kancane kancane amafutha ebusweni, entanyeni, ezingalweni nasesifubeni ngesikhathi besebancane. Abanye abantu abane-APL bangase bathole amafutha amaningi ezindaweni ezifana nesisu, imilenze, kanye nezinqe.

Kuye ngohlobo lwe-lipodystrophy onalo kanye nobudala bakho, ungase ungaboni noma yiziphi izinkinga ezinkulu zempilo iminyaka eminingi. Kodwa-ke, izinhlobo eziningi ze-lipodystrophy zibangela i-cholesterol ephezulu egazini, ama-triglycerides, kanye namazinga kashukela (glucose). Udokotela wakho angakubona lokhu ngokuhlolwa kwegazi okuvamile, njengephaneli ye-lipid kanye nephaneli ye-metabolic eyisisekelo .

Ezinye izinhlobo ze-lipodystrophy, ikakhulukazi i-partial lipodystrophy, zingaba nzima ukuzixilonga. Ngakho-ke, kubalulekile ukubona udokotela uma wena noma ingane yakho nithola izimpawu ezintsha noma uma uphawu olukhona luba lubi kakhulu, kungakhathaliseki ukuthi imbangela iyini.

Ziyini izimbangela ze-lipodystrophy?

Izimbangela ze-lipodystrophy ziyahlukahluka kuye ngokuthi ngabe ibangelwa ufuzo noma itholwe.

Izimbangela ze-Lipodystrophy yezakhi zofuzo

Izinhlobo ze-lipodystrophy zofuzo – okungukuthi i-congenital generalized lipodystrophy (CGL) kanye ne-familial partial lipodystrophy (FPLD) – zibangelwa izinguquko ezithile zofuzo .

Ukuguquka kwezakhi zofuzo kuwushintsho ochungechungeni lwethu lwe-DNA. Uchungechunge lwethu lwe-DNA yilona olunikeza amangqamuzana ethu ulwazi aludingayo ukuze enze imisebenzi yawo. Ngakho-ke, uma ingxenye yalolu chungechunge lwe-DNA ingaphelele noma yonakele, singase sibe nezimpawu zesifo sofuzo.

  • Izimbangela ze-congenital generalized lipodystrophy (CGL): Izinhlobo ze-CGL 1 kuya ku-4 zibangelwa izinguquko ezakhiweni ze- AGPAT2, BSCL2, CAV1 , kanye ne -CAVIN1 . Lezi zakhi zofuzo zibalulekile ekukhuleni nasekusebenzeni kwamaseli okugcina amafutha (ama-adipocyte) ezicutshini zethu zamafutha. Ukuguqulwa kwezakhi zofuzo kulezi zakhi zofuzo kuthinta isakhiwo kanye nomsebenzi wama-adipocyte. Ingane ene-CGL izuza lezi zinguquko ezakhiweni zezakhi zofuzo kubazali bayo. Ngisho noma bobabili abazali benekhophi eyodwa yezakhi zofuzo eziguquliwe, ngokuvamile azibonisi izimpawu.
  • Izimbangela ze-Familial Partial Lipodystrophy (FPLD): Ukuguquka kwezakhi zofuzo eziningana kungabangela i-FPLD. Okuvame kakhulu yi -LMNA.Uguquko ku-gene ebizwa ngokuthi i-LMNA. I-gene ye-LMNA kanye nezinye izakhi zofuzo ezihilelekile ku-FPLD ziyala ama-adipocyte ukuthi agcine amafutha futhi enze amaprotheni ahlukahlukene abalulekile ekugcineni amafutha. Uma kwenzeka ushintsho kunoma yiliphi lala ma-gene, ukukhula, isakhiwo, noma umsebenzi wama-adipocyte kuthinteka kabi. Amacala amaningi e-FPLD azuzwa njengefa ngendlela elawulwa yi-autosomal . Lokhu kusho ukuthi ukuba nekhophi eyodwa yezakhi zofuzo eziguquliwe kuseli ngalinye kwanele ukubangela lesi sifo. Ngezinye izikhathi, umuntu one-FPLD uzuza i-mutation komunye wabazali bakhe abathintekile. Kwezinye izimo, zibangelwa izinguquko ezintsha, ezingahleliwe ku-gene, futhi zingavela ngisho noma kungekho muntu emndenini oke waba nalesi sifo ngaphambili.

Izimbangela ze-Acquired Lipodystrophy

I-lipodystrophy etholakala ngokungemthetho ingabangelwa imithi, ukusabela kwe-autoimmune , noma izimbangela ezingavamile . Nakuba kungekho sisekelo esiqondile sezakhi zofuzo se-lipodystrophy etholakala ngokungemthetho, abanye abacwaningi bakholelwa ukuthi abanye abantu bangase babe nesifo sofuzo sokuthuthukisa i-lipodystrophy etholakala ngokungemthetho.

  • Izimbangela ze-Acquired Generalized Lipodystrophy (AGL): I-AGL ingavela ngemva kokutheleleka noma ngemva kwesifo sesimiso somzimba sokuzivikela. Izifo eziye zahlotshaniswa ne-AGL zifaka:
  • I-Chickenpox (i-Chickenpox / i-varicella)
  • Isimungumungwane
  • Ukukhwehlela okubi (i-pertussis)
  • I-Diphtheria
  • Inyumoniya
  • I-Osteomyelitis
  • I-Mononucleosis (i-Mononucleosis / i-mono)

Akuqiniseki ukuthi uzoba ne-AGL ngoba nje unalezi zifo.

Izimo zokuzivikela komzimba ezihambisana ne-AGL zifaka:

  • I-autoimmune thyroiditis
  • I-hepatitis yokuzivikela komzimba
  • I-dermatomyositis yezingane
  • Isifo samathambo esibizwa ngokuthi i-rheumatoid arthritis
  • Isifo sikaSjogren
  • I-autoimmune hemolytic anemia

Uma unalezi zifo zesimiso somzimba sokuzivikela, akunakushiwo ukuthi nakanjani uzoba ne-AGL.

Ezimweni eziningi, imbangela ye-AGL ayikwazi ukutholakala (idiopathic).

  • Izimbangela Zokutholakala Kwe-Partial Lipodystrophy (APL): Ososayensi bakholelwa ukuthi i-APL ibangelwa ukuthi amasosha omzimba ethu abhubhisa ngephutha amaseli amafutha. Abantu abangaphezu kuka-80% abane-APL bane-Complement 3 egazini labo.Kukhona izinga eliphansi leprotheyini ebizwa ngokuthi i-complement factor. Le phrotheyini ivame ukuba yingxenye yempendulo yesimiso sethu somzimba sokuzivikela. Abantu abane-APL bavame ukuba ne-autoantibody ebizwa ngokuthi i-complement 3-nephritic factor egazini labo. I-autoantibody iyiprotheyini esesimisweni somzimba sokuzivikela ehlasela futhi yonakalise izicubu ezinempilo ngephutha.
  • Izimbangela ze-lipodystrophy ebangelwa ukwelashwa nge-antiretroviral (HAART) esebenzayo kakhulu (LD-HIV): Ososayensi abakaqiniseki ukuthi kungani i-HAART, equkethe i-HIV-1 protease inhibitors, ibangela i-lipodystrophy.

Izindaba ezinhle ukuthi abantu abaningi abaqala ukwelashwa nge-HIV manje akudingeki bakhathazeke kakhulu nge-lipodystrophy, njengoba imithi emisha ye-HIV yenza lesi simo singabi sengozini enkulu.

Wazi kanjani ukuthi une-lipodystrophy?

Uma unezimpawu ze-lipodystrophy, udokotela wakho uzokwenza ukuhlolwa ngokomzimba, abuze ngomlando wakho wezokwelapha kanye nomlando wezokwelapha womndeni, bese eyala ukuhlolwa okuthile ukuqinisekisa ukuxilongwa nokubona ukuthi zikhona yini ezinye izimbangela zezimpawu zakho.

Yiziphi izivivinyo ezisetshenziswa ukuxilonga i-lipodystrophy?

Udokotela wakho angase akucele ukuthi uhlolwe kaningana ukuze kutholakale i-lipodystrophy kanye/noma ukuze abone ukuthi zikhona yini ezinye izimbangela zezimpawu zakho. Lokhu kufaka phakathi:

  • Iskena se-MRI yomzimba wonke (i-Magnetic Resonance Imaging): I-MRI isebenzisa i-magnet enkulu, amaza omsakazo, kanye nekhompyutha ukwenza izithombe ezinemininingwane yezitho zomzimba nezinye izakhiwo emzimbeni wakho. Udokotela wakho angase akuyalele lokhu kuhlolwa ukuhlola ukwakheka nokusabalala kwamafutha emzimbeni wakho.
  • Iphaneli Ephelele Ye-Metabolic: Lokhu ukuhlolwa kwegazi okulinganisa izinto ezingu-14 ezahlukene egazini lakho. Kuhlinzeka ngolwazi olubalulekile mayelana nokulinganisela kwamakhemikhali emzimbeni wakho kanye ne-metabolism. Udokotela uzobheka ngqo amazinga kashukela egazini lakho (i-glucose) kanye nama-enzyme esibindi .
  • Iphaneli Ye-Lipid: Lokhu futhi ukuhlolwa kwegazi. Kukala inani lama-molecule amafutha abizwa ngokuthi ama-lipid egazini lakho. Lokhu kuhlolwa kuvame ukufaka izilinganiso ezine ze-cholesterol kanye nesilinganiso se-triglyceride. I-Lipodystrophy ivame ukubangela amazinga e-cholesterol angajwayelekile.
  • Ukuhlolwa kwe-Leptin: Lokhu kulinganisa izinga le-leptin egazini lakho. Uma une-lipodystrophy futhi amazinga akho e-leptin ephansi kunokuvamile, lokhu kungakunikeza umbono wokuthi umzimba wakho uzosabela kanjani ekwelashweni kokufaka esikhundleni se-leptin.
  • Ukuhlolwa Kwezakhi Zofuzo: Uma udokotela wakho esola ukuthi une-Lipodystrophy ezuzwe njengefa (eyezakhi zofuzo), angase ancome ukuhlolwa kwezakhi zofuzo ukuqinisekisa ukuxilongwa.
  • Ukuhlolwa kwezinso:Lokhu kuhilela ukususa isampula yezicubu zezinso ngokuhlinzwa bese uyihlola ngaphansi kwesibonakhulu. Udokotela wakho angase akucele lokhu kuhlolwa ukuze abone ukuthi izinso zakho zithintekile yini yi-lipodystrophy.

Yiziphi izindlela zokwelapha i-lipodystrophy?

Ukwelashwa nokuphathwa kwe-lipodystrophy kuncike ohlotsheni oluthile onalo, nokuthi unezinye izimo ezihlobene nalokho, njengesifo sikashukela noma amazinga e-cholesterol angajwayelekile.

Izindlela zokwelapha ezivame ukusetshenziswa zokulawula i-lipodystrophy yilezi:

  • Imithi yokufaka esikhundleni se-Leptin: Udokotela wakho angase akunikeze uhlobo lokwenziwa lwe-hormone i-leptin ebizwa ngokuthi i-metreleptin . Abantu abane-lipodystrophy bavame ukuba nokuntuleka kwe-leptin. Le hormone isiza ekulawuleni i-metabolism yomzimba futhi inganciphisa amazinga aphezulu e-cholesterol kanye ne-triglyceride.
  • Ukwelashwa kwesifo sikashukela kanye nokumelana ne-insulin: Uma unesifo sikashukela esibangelwa yi-lipodystrophy, udokotela wakho angase akunike imithi yomlomo efana ne -pioglitazone, i-metformin, i-sulfonylureas , noma i-thiazolidinediones ukuze uyelaphe. Abanye abantu abane-lipodystrophy kungadingeka bathathe i-insulin yokwenziwa ukuze belaphe isifo sikashukela sabo. Kungadingeka futhi uhlole amazinga kashukela egazini lakho njalo ekhaya nge-glucometer .
  • Ukulawula amazinga e-triglyceride kanye ne-cholesterol: Imithi ephuzwayo okukhulunywe ngayo ngaphambili esiza ekwelapheni isifo sikashukela ingasiza ekulawuleni amazinga e-cholesterol. Udokotela wakho angase futhi akunike ama-statin , njenge- rosuvastatin kanye ne-pravastatin . Abantu abanamazinga aphezulu e-triglyceride kungadingeka bathathe izithasiselo ze-fibric acid derivatives noma i-n-3 polyunsaturated fatty acids , njengalezo ezitholakala kumafutha enhlanzi.
  • Ukuhlinzwa kobuhle kanye nezinqubo: Abantu abane-lipodystrophy ezindaweni ezizwela kakhulu ubuhle, njengobuso, isifuba, kanye nezindawo zangasese, bangase bahlinzwe ubuhle ukuze bathuthukise ukubukeka kwabo kanye nokuzethemba. Odokotela abahlinzayo be-plastic bangase benze ukufakelwa kwezicubu zamafutha e-autologous, ukwakhiwa kabusha kobuso besebenzisa ama-free flaps, kanye ne-silicone noma ezinye izimila. Bangase futhi basebenzise amasu okususa amafutha noma ukuhlinzwa ukuze basuse ama-fat deposits angafuneki ezindaweni ezifana nesilevu noma ngemuva kwentamo (ngokuvamile okubizwa ngokuthi "i-buffalo hump" ).

Ososayensi basenokuningi okufanele bakufunde mayelana nendlela yokwelapha nokuphatha i-lipodystrophy. Njengoba bethola okwengeziwe mayelana nobunzima bezinqubo ze-metabolic, kungase kutholakale ezinye izindlela zokwelapha.

Ingabe i-lipodystrophy ingavinjelwa?

Ezimweni eziningi, i-Lipodystrophy ayikwazi ukuvinjelwa.

Izinhlobo ze-lipodystrophy zofuzo azinakuvinjelwa, njengoba ziwumphumela wokuguqulwa kwezakhi zofuzo okuzuzwe njengefa. Uma uhlela ukuba nezingane, qonda ingozi yokuba nengane enesifo sofuzo bese ukhuluma nodokotela wakho mayelana nokuhlolwa kwezakhi zofuzo.

I-lipodystrophy etholakala ngokutholakala ivame ukubangelwa ukutheleleka noma isifo sesimiso sokuzivikela komzimba. Nakuba ezinye izifo, njenge-chickenpox kanye nokukhwehlela okungapheli, zingavinjelwa ngokugonywa, ezinye izifo kanye nezifo zesimiso sokuzivikela komzimba ezihlobene ne-lipodystrophy etholakala ngokutholakala azikwazi ukuvinjelwa.

Iyini iphrojekthi ye-lipodystrophy?

Umbono we-lipodystrophy uncike kakhulu kuhlobo lwe-lipodystrophy onalo, nokuthi unezinye izimo noma izinkinga ezihlobene nazo, njengesifo sikashukela, izinkinga zesibindi noma zezinso.

Ukulungiswa kobuhle kwezindawo ezinamafutha aphansi kanye nezindawo ezinamafutha amaningi kusiza ukuthuthukisa ikhwalithi yokuphila kwabantu abane-lipodystrophy.

Uma wena noma ingane yakho nitholakala ninesifo se-lipodystrophy, khuluma nodokotela wakho ngalokho okufanele ukulindele nokuthi ungasiphatha kanjani kangcono lesi simo.

Kufanele ubonane nini nodokotela mayelana ne-lipodystrophy?

Uma ubona ukuthi wena noma ingane yakho iyancipha kakhulu ezindaweni ezithile, noma ukuthi amafutha ayanda ezindaweni ezithile, khuluma nodokotela wakho.

Uma wena noma ingane yakho nitholakala ninesifo i-Lipodystrophy, kufanele nihlangane nethimba lezokwelapha njalo ukuqinisekisa ukuthi ukwelashwa kwenu kusebenza kahle kuwe.

Okokugcina, izinto okufanele uzikhumbule

I-Lipodystrophy yisimo esingavamile kodwa esibucayi. Nakuba kungekho ikhambi, ezinye izindlela zokwelapha zingasiza ekulawuleni izimpawu zayo kanye nezimo ezihlobene nayo, njengesifo sikashukela kanye namazinga e-cholesterol angajwayelekile.

Ukwelashwa kuyahlukahluka kakhulu kumuntu nomuntu. Ngakho-ke, ithimba lakho lezokwelapha lizosebenzisana nawe ukudala uhlelo olukulungele kangcono. Ungesabi ukubuza udokotela wakho imibuzo. Bakhona ukukusiza. Lolu lwazi luzokusiza nakanjani uphile impilo enempilo!


i- lipodystrophy, izicubu zamafutha, i-leptin, izakhi zofuzo, ezitholwe, isifo sikashukela, i-cholesterol, i-triglyceride, i-HIV, izifo ze-metabolic

Frequently Asked Questions (FAQ)

Yiziphi izivivinyo ezisetshenziswa ukuxilonga i-lipodystrophy?

Udokotela wakho angase akucele ukuthi uhlolwe kaningana ukuze kutholakale i-lipodystrophy kanye/noma ukuze abone ukuthi zikhona yini ezinye izimbangela zezimpawu zakho. Lokhu kufaka phakathi:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Ingabe uhlangabezana nokugcwala kwamafutha ezingxenyeni ezahlukene zomzimba wakho? Ake sifunde nge-Lipodystrophy!

Ingabe uhlangabezana nokugcwala kwamafutha ezingxenyeni ezahlukene zomzimba wakho? Ake sifunde nge-Lipodystrophy!

Wake wabona, noma wabhekana nokulahlekelwa amafutha ngokuzumayo kwezinye izindawo zomzimba wakho, noma ukwanda kwamafutha okungafuneki kwezinye izindawo? Lokhu ngezinye izikhathi kungaba yinto engenakwenzeka. Namuhla sizokhuluma ngalesi simo. Ngokwezokwelapha, lokhu kubizwa ngokuthi i-Lipodystrophy . Ungakhathazeki, yize igama lingase lizwakale lingavamile, ake sixoxe ngakho kalula.

Kuyini i-Lipodystrophy?

Kalula nje, i-Lipodystrophy ukulahleka okuphelele noma okuyingxenye kwezicubu zamafutha, lokho esivame ukukubiza ngokuthi “amafutha,” kwezinye izindawo, noma ukunqwabelana kwamafutha okungavamile ezindaweni ezahlukene zomzimba.

Zicabange uncipha isisindo ezindaweni ezithile zomzimba wakho, njengezingalo nemilenze yakho, kuyilapho uthola amafutha amaningi ezindaweni ezifana nobuso bakho nentamo. Yilokhu okwenzekayo ku-Lipodystrophy. Kunezinhlobo ezahlukene zalesi simo, ezinye zazo ezingezofuzo (okungukuthi, into esizalwa nayo), kanti ezinye zikhula kamuva ngenxa yezinye izimo zezokwelapha. Uhlobo ngalunye luthinta abantu ngendlela ehlukile futhi lunezimpawu ezahlukene.

Kungani amafutha (izicubu zamafutha) ebaluleke kangaka emzimbeni wethu?

Manje ungase ucabange, "Uma unamafutha amancane, kungcono." Kodwa empeleni, izicubu zamafutha zenza imisebenzi eminingi ebalulekile emizimbeni yethu. Bheka:

  • Ukugcinwa kwamandla: Kukulezi zicubu ezinamafutha lapho amakhalori engeziwe esiwathola ekudleni esikudlayo agcinwa khona njengamandla.
  • Ukuvikela: Kuhlinzeka ngesivikelo esifana nomcamelo ezithweni ezahlukahlukene zomzimba wethu.
  • Ukugcina ukufudumala: Kugcina ukushisa komzimba futhi kusivikele emakhazeni endawo ezungezile.
  • Ukukhishwa kwama-hormone: Ama-hormone amaningana abalulekile, njenge -leptin, akhiqizwa futhi akhishwe egazini.
  • Ukulawula ukuvuvukala: Kuphinde kusize ukulawula ukuvuvukala emzimbeni.

Ngakho-ke, uma lesi zicubu zamafutha zilahleka noma zibekwe ngendlela engavamile ngenxa ye-lipodystrophy, akugcini nje ngokushintsha ukubukeka kwethu, kodwa nemisebenzi ebalulekile ye-metabolic emzimbeni nayo iyaphazamiseka. Abantu abaningi abane-lipodystrophy basengozini yokuthola izifo ezifana nesifo sikashukela kanye nokuba namazinga e-cholesterol egazini angajwayelekile.

Ingabe zikhona izinhlobo ze-lipodystrophy?

Yebo, i-Lipodystrophy ingahlukaniswa ngezinhlobo ezimbili eziyinhloko: izakhi zofuzo kanye ne-acquired.

Izinhlobo ze-Lipodystrophy yezakhi zofuzo

Lezi zizuzwe njengefa, okungukuthi, izinhlobo ezenzeka ngenxa yokuguquka kwezakhi zofuzo.

  • I-Congenital Generalized Lipodystrophy (CGL): Lesi yi -Berardinelli-Seip syndrome.Yaziwa nangokuthi. Lesi yisimo esingavamile kakhulu. Kulokhu, amafutha omzimba acishe alahleke ngokuphelele noma kakhulu. Lokhu kubangelwa yisici sofuzo esikhona lapho kuzalwa. Lesi simo ngokuvamile singatholakala phakathi nonyaka wokuqala wokuphila.
  • I-Familial Partial Lipodystrophy (FPLD): Lesi futhi yisimo esibangelwa izakhi zofuzo. Kodwa-ke, sivame ukutholakala kamuva ekuphileni. Kulesi simo, ingane ilahlekelwa amafutha ikakhulukazi emilenzeni nasezingalweni, futhi iqoqa amafutha amaningi ebusweni nasentanyeni.

Izinhlobo ze-Acquired Lipodystrophy

Lezi yizinhlobo ezivela ngemva kokuzalwa kwethu kanye nangesikhathi sokuphila kwethu ngezizathu ezahlukene.

  • I-Acquired Generalized Lipodystrophy (AGL): Eyaziwa nangokuthi i-Lawrence syndrome , lesi simo sibangela ukulahleka kwamafutha, ngokuvamile ebusweni, entanyeni, ezingalweni nasemilenzeni. Lokhu kulahlekelwa kwamafutha kungenzeka ngokushesha, emavikini ambalwa, noma kancane kancane ezinyangeni noma eminyakeni. Ngokuvamile kuqala ebuntwaneni noma ebusheni, kodwa kungenzeka kunoma yimuphi ubudala. Kunezimbangela eziningana ezingaba khona ze-AGL.
  • I-Acquired Partial Lipodystrophy (APL): Eyaziwa nangokuthi i-Barraquer-Simons syndrome , lesi simo sibangela ukulahlekelwa kancane kancane kwamafutha ebusweni, entanyeni, ezingalweni nasesifubeni ngesikhathi sobuntwana. Abanye abantu bangase babe namafutha amaningi ezindaweni ezifana nesisu, imilenze, nezinqe. I-APL ivame ukuhlotshaniswa nezimo zokuzivikela komzimba .
  • I-lipodystrophy (LD-HIV) ebangelwa ukwelashwa nge-antiretroviral esebenzayo kakhulu (HAART): Lolu hlobo lwe-lipodystrophy lwenzeka kubantu abangenwe yigciwane le-human immunodeficiency virus (HIV) ngemuva kokuthola ukwelashwa nge-antiretroviral esebenzayo kakhulu (HAART) okuhlanganisa ne-HIV-1 protease inhibitors . Ukwenzeka kwalesi simo kuncike ekuqineni nasekudeni kwesikhathi sokwelashwa. Abantu abane-LD-HIV bavame ukulahlekelwa amafutha kancane kancane ezingalweni zabo, emilenzeni nasebusweni. Abanye abantu bangase bathole amafutha amaningi ebusweni babo, entanyeni, emhlane ongaphezulu, nasesinqeni.
  • I-Localized Lipodystrophy: Lokhu kwenzeka lapho amafutha elahleka endaweni encane yomzimba kuphela. Isibonelo, lesi simo singavela uma imithi (njenge-insulin) ifakwa endaweni efanayo ngokuphindaphindiwe. Ibukeka njenge-dimple encane, kodwa isikhumba esiphezu kwayo ngokuvamile asithinteki.

Ingabe i-Lipodystrophy ne-Lipoatrophy ziyinto efanayo?

I-Lipodystrophy yigama elijwayelekile lokusatshalaliswa kwamafutha okungavamile. Liphinde lihlobane ne -Lipoatrophy , okusho ukulahlekelwa amafutha. Abanye ososayensi nodokotela basebenzisa womabili la magama ukuchaza isimo esifanayo. Kalula nje, i-Lipoatrophy iyi-subset ye-Lipodystrophy.

Ubani othinteka kakhulu yilesi simo? Sivame kangakanani?

Izinhlobo eziningi ze-lipodystrophy ziqala ebuntwaneni, kodwa izinhlobo ezitholakalayo zingakhula nakubantu abadala.

Ngaphandle kwe -HAART-induced lipodystrophy (LD-HIV) , ezinye izinhlobo ze-acquired lipodystrophy zivame ukubathinta abesifazane. Ngenxa yokuthi ukutheleleka nge-HIV kuvame kakhulu kwabesilisa, i-LD-HIV ivame kakhulu nakwabesilisa.

Ngokuvamile, i-lipodystrophy ayivamile kakhulu . Kodwa-ke, izinhlobo ze-lipodystrophy ezitholakalayo (ukuphila konke) ziya ngokuya zivamile ngenxa yemiphumela emibi yemithi ethile.

I-lipodystrophy ithinta kanjani umzimba wami?

Uhlobo ngalunye lwe-lipodystrophy luthinta umzimba ngendlela ehlukile, kodwa kunezici ezimbili eziyinhloko ezivamile: ukulahlekelwa kwezicubu zamafutha kanye nokuntuleka kwe-hormone leptin .

Umphumela wokulahlekelwa yizicubu zamafutha emzimbeni

Izicubu zethu zamafutha zakhiwe ngamaseli abizwa ngokuthi ama-adipocytes . Iseli ngalinye lama-adipocyte liqukethe cishe amaconsi e-lipid angu-90%. Lawa ma-adipocytes agcina amafutha (ama-triglycerides). Uma lawa maseli amafutha onakele ngenxa ye-lipodystrophy, awakwazi ukugcina amafutha kahle.

Kwezinye izimo ze-Lipodystrophy, la mafutha alahlekile abekwa ngendlela engafanele kwezinye izicubu zomzimba wethu, isibonelo, esibindini, kuma-pancreas, noma ezicutshini zemisipha. Lokhu kungaholela ezinkingeni zempilo ezifana nalezi:

  • Isifo sesibindi esinamafutha / i-hepatic steatosis
  • Ukumelana ne-insulin kanye namazinga aphezulu e-insulin egazini (hyperinsulinemia)
  • Isifo Sikashukela (i-Diabetes Mellitus)
  • Amazinga aphezulu e-triglycerides egazini (i-hypertriglyceridemia)
  • I-Pancreatitis
  • I-Metabolic syndrome
  • Isifo semithambo ye-coronary

Kodwa khumbula, akubona bonke abantu abane-lipodystrophy abazoba nalezi zimo. Abanye bangaba nezinhlobo ezithambile, kanti abanye bangaba nezinhlobo ezimbi kakhulu.

Imiphumela Yokuntuleka Kwe-Leptin Emzimbeni

Njengoba abantu abane-lipodystrophy belahlekelwa izicubu zamafutha, balahlekelwa nama-hormone athile, ikakhulukazi i-hormone i-leptin .

I-Leptin iyi-hormone ekhiqizwa yizicubu zethu zamafutha. Isisiza ukuthi silondoloze isisindo somzimba esijwayelekile isikhathi eside. Uyazi ukuthi kanjani? Ngokusenza sizizwe sanelisekile futhi silawule indlala yethu. Ososayensi basacwaninga nge-leptin. Bakholelwa ukuthi i-leptin ithinta i-metabolism yethu, umsebenzi wesistimu ye-endocrine , kanye nomsebenzi wesistimu yokuzivikela komzimba .

Abantu abane-lipodystrophy bangase babe namazinga e-leptin aphansi, okungaholela ekulambeni ngokweqile, ukumelana ne-insulin, kanye nezinye izinkinga zempilo.

Ziyini izimpawu ze-lipodystrophy?

Ngenxa yokuthi kunezinhlobo eziningi ze-lipodystrophy, izimpawu nazo ziyahlukahluka kakhulu.

Uphawu oluvame kakhulu ukulahleka kwamafutha okusobala nokuqhubekayo kwezinye izindawo zomzimba, kuyilapho ngesikhathi esifanayo, ukunqwabelana kwamafutha okungavamile noma okungafunwa kwezinye izindawo zomzimba.

Isibonelo, abantu abane -acquired partial lipodystrophy (APL) balahlekelwa kancane kancane amafutha ebusweni, entanyeni, ezingalweni nasesifubeni ngesikhathi besebancane. Abanye abantu abane-APL bangase bathole amafutha amaningi ezindaweni ezifana nesisu, imilenze, kanye nezinqe.

Kuye ngohlobo lwe-lipodystrophy onalo kanye nobudala bakho, ungase ungaboni noma yiziphi izinkinga ezinkulu zempilo iminyaka eminingi. Kodwa-ke, izinhlobo eziningi ze-lipodystrophy zibangela i-cholesterol ephezulu egazini, ama-triglycerides, kanye namazinga kashukela (glucose). Udokotela wakho angakubona lokhu ngokuhlolwa kwegazi okuvamile, njengephaneli ye-lipid kanye nephaneli ye-metabolic eyisisekelo .

Ezinye izinhlobo ze-lipodystrophy, ikakhulukazi i-partial lipodystrophy, zingaba nzima ukuzixilonga. Ngakho-ke, kubalulekile ukubona udokotela uma wena noma ingane yakho nithola izimpawu ezintsha noma uma uphawu olukhona luba lubi kakhulu, kungakhathaliseki ukuthi imbangela iyini.

Ziyini izimbangela ze-lipodystrophy?

Izimbangela ze-lipodystrophy ziyahlukahluka kuye ngokuthi ngabe ibangelwa ufuzo noma itholwe.

Izimbangela ze-Lipodystrophy yezakhi zofuzo

Izinhlobo ze-lipodystrophy zofuzo – okungukuthi i-congenital generalized lipodystrophy (CGL) kanye ne-familial partial lipodystrophy (FPLD) – zibangelwa izinguquko ezithile zofuzo .

Ukuguquka kwezakhi zofuzo kuwushintsho ochungechungeni lwethu lwe-DNA. Uchungechunge lwethu lwe-DNA yilona olunikeza amangqamuzana ethu ulwazi aludingayo ukuze enze imisebenzi yawo. Ngakho-ke, uma ingxenye yalolu chungechunge lwe-DNA ingaphelele noma yonakele, singase sibe nezimpawu zesifo sofuzo.

  • Izimbangela ze-congenital generalized lipodystrophy (CGL): Izinhlobo ze-CGL 1 kuya ku-4 zibangelwa izinguquko ezakhiweni ze- AGPAT2, BSCL2, CAV1 , kanye ne -CAVIN1 . Lezi zakhi zofuzo zibalulekile ekukhuleni nasekusebenzeni kwamaseli okugcina amafutha (ama-adipocyte) ezicutshini zethu zamafutha. Ukuguqulwa kwezakhi zofuzo kulezi zakhi zofuzo kuthinta isakhiwo kanye nomsebenzi wama-adipocyte. Ingane ene-CGL izuza lezi zinguquko ezakhiweni zezakhi zofuzo kubazali bayo. Ngisho noma bobabili abazali benekhophi eyodwa yezakhi zofuzo eziguquliwe, ngokuvamile azibonisi izimpawu.
  • Izimbangela ze-Familial Partial Lipodystrophy (FPLD): Ukuguquka kwezakhi zofuzo eziningana kungabangela i-FPLD. Okuvame kakhulu yi -LMNA.Uguquko ku-gene ebizwa ngokuthi i-LMNA. I-gene ye-LMNA kanye nezinye izakhi zofuzo ezihilelekile ku-FPLD ziyala ama-adipocyte ukuthi agcine amafutha futhi enze amaprotheni ahlukahlukene abalulekile ekugcineni amafutha. Uma kwenzeka ushintsho kunoma yiliphi lala ma-gene, ukukhula, isakhiwo, noma umsebenzi wama-adipocyte kuthinteka kabi. Amacala amaningi e-FPLD azuzwa njengefa ngendlela elawulwa yi-autosomal . Lokhu kusho ukuthi ukuba nekhophi eyodwa yezakhi zofuzo eziguquliwe kuseli ngalinye kwanele ukubangela lesi sifo. Ngezinye izikhathi, umuntu one-FPLD uzuza i-mutation komunye wabazali bakhe abathintekile. Kwezinye izimo, zibangelwa izinguquko ezintsha, ezingahleliwe ku-gene, futhi zingavela ngisho noma kungekho muntu emndenini oke waba nalesi sifo ngaphambili.

Izimbangela ze-Acquired Lipodystrophy

I-lipodystrophy etholakala ngokungemthetho ingabangelwa imithi, ukusabela kwe-autoimmune , noma izimbangela ezingavamile . Nakuba kungekho sisekelo esiqondile sezakhi zofuzo se-lipodystrophy etholakala ngokungemthetho, abanye abacwaningi bakholelwa ukuthi abanye abantu bangase babe nesifo sofuzo sokuthuthukisa i-lipodystrophy etholakala ngokungemthetho.

  • Izimbangela ze-Acquired Generalized Lipodystrophy (AGL): I-AGL ingavela ngemva kokutheleleka noma ngemva kwesifo sesimiso somzimba sokuzivikela. Izifo eziye zahlotshaniswa ne-AGL zifaka:
  • I-Chickenpox (i-Chickenpox / i-varicella)
  • Isimungumungwane
  • Ukukhwehlela okubi (i-pertussis)
  • I-Diphtheria
  • Inyumoniya
  • I-Osteomyelitis
  • I-Mononucleosis (i-Mononucleosis / i-mono)

Akuqiniseki ukuthi uzoba ne-AGL ngoba nje unalezi zifo.

Izimo zokuzivikela komzimba ezihambisana ne-AGL zifaka:

  • I-autoimmune thyroiditis
  • I-hepatitis yokuzivikela komzimba
  • I-dermatomyositis yezingane
  • Isifo samathambo esibizwa ngokuthi i-rheumatoid arthritis
  • Isifo sikaSjogren
  • I-autoimmune hemolytic anemia

Uma unalezi zifo zesimiso somzimba sokuzivikela, akunakushiwo ukuthi nakanjani uzoba ne-AGL.

Ezimweni eziningi, imbangela ye-AGL ayikwazi ukutholakala (idiopathic).

  • Izimbangela Zokutholakala Kwe-Partial Lipodystrophy (APL): Ososayensi bakholelwa ukuthi i-APL ibangelwa ukuthi amasosha omzimba ethu abhubhisa ngephutha amaseli amafutha. Abantu abangaphezu kuka-80% abane-APL bane-Complement 3 egazini labo.Kukhona izinga eliphansi leprotheyini ebizwa ngokuthi i-complement factor. Le phrotheyini ivame ukuba yingxenye yempendulo yesimiso sethu somzimba sokuzivikela. Abantu abane-APL bavame ukuba ne-autoantibody ebizwa ngokuthi i-complement 3-nephritic factor egazini labo. I-autoantibody iyiprotheyini esesimisweni somzimba sokuzivikela ehlasela futhi yonakalise izicubu ezinempilo ngephutha.
  • Izimbangela ze-lipodystrophy ebangelwa ukwelashwa nge-antiretroviral (HAART) esebenzayo kakhulu (LD-HIV): Ososayensi abakaqiniseki ukuthi kungani i-HAART, equkethe i-HIV-1 protease inhibitors, ibangela i-lipodystrophy.

Izindaba ezinhle ukuthi abantu abaningi abaqala ukwelashwa nge-HIV manje akudingeki bakhathazeke kakhulu nge-lipodystrophy, njengoba imithi emisha ye-HIV yenza lesi simo singabi sengozini enkulu.

Wazi kanjani ukuthi une-lipodystrophy?

Uma unezimpawu ze-lipodystrophy, udokotela wakho uzokwenza ukuhlolwa ngokomzimba, abuze ngomlando wakho wezokwelapha kanye nomlando wezokwelapha womndeni, bese eyala ukuhlolwa okuthile ukuqinisekisa ukuxilongwa nokubona ukuthi zikhona yini ezinye izimbangela zezimpawu zakho.

Yiziphi izivivinyo ezisetshenziswa ukuxilonga i-lipodystrophy?

Udokotela wakho angase akucele ukuthi uhlolwe kaningana ukuze kutholakale i-lipodystrophy kanye/noma ukuze abone ukuthi zikhona yini ezinye izimbangela zezimpawu zakho. Lokhu kufaka phakathi:

  • Iskena se-MRI yomzimba wonke (i-Magnetic Resonance Imaging): I-MRI isebenzisa i-magnet enkulu, amaza omsakazo, kanye nekhompyutha ukwenza izithombe ezinemininingwane yezitho zomzimba nezinye izakhiwo emzimbeni wakho. Udokotela wakho angase akuyalele lokhu kuhlolwa ukuhlola ukwakheka nokusabalala kwamafutha emzimbeni wakho.
  • Iphaneli Ephelele Ye-Metabolic: Lokhu ukuhlolwa kwegazi okulinganisa izinto ezingu-14 ezahlukene egazini lakho. Kuhlinzeka ngolwazi olubalulekile mayelana nokulinganisela kwamakhemikhali emzimbeni wakho kanye ne-metabolism. Udokotela uzobheka ngqo amazinga kashukela egazini lakho (i-glucose) kanye nama-enzyme esibindi .
  • Iphaneli Ye-Lipid: Lokhu futhi ukuhlolwa kwegazi. Kukala inani lama-molecule amafutha abizwa ngokuthi ama-lipid egazini lakho. Lokhu kuhlolwa kuvame ukufaka izilinganiso ezine ze-cholesterol kanye nesilinganiso se-triglyceride. I-Lipodystrophy ivame ukubangela amazinga e-cholesterol angajwayelekile.
  • Ukuhlolwa kwe-Leptin: Lokhu kulinganisa izinga le-leptin egazini lakho. Uma une-lipodystrophy futhi amazinga akho e-leptin ephansi kunokuvamile, lokhu kungakunikeza umbono wokuthi umzimba wakho uzosabela kanjani ekwelashweni kokufaka esikhundleni se-leptin.
  • Ukuhlolwa Kwezakhi Zofuzo: Uma udokotela wakho esola ukuthi une-Lipodystrophy ezuzwe njengefa (eyezakhi zofuzo), angase ancome ukuhlolwa kwezakhi zofuzo ukuqinisekisa ukuxilongwa.
  • Ukuhlolwa kwezinso:Lokhu kuhilela ukususa isampula yezicubu zezinso ngokuhlinzwa bese uyihlola ngaphansi kwesibonakhulu. Udokotela wakho angase akucele lokhu kuhlolwa ukuze abone ukuthi izinso zakho zithintekile yini yi-lipodystrophy.

Yiziphi izindlela zokwelapha i-lipodystrophy?

Ukwelashwa nokuphathwa kwe-lipodystrophy kuncike ohlotsheni oluthile onalo, nokuthi unezinye izimo ezihlobene nalokho, njengesifo sikashukela noma amazinga e-cholesterol angajwayelekile.

Izindlela zokwelapha ezivame ukusetshenziswa zokulawula i-lipodystrophy yilezi:

  • Imithi yokufaka esikhundleni se-Leptin: Udokotela wakho angase akunikeze uhlobo lokwenziwa lwe-hormone i-leptin ebizwa ngokuthi i-metreleptin . Abantu abane-lipodystrophy bavame ukuba nokuntuleka kwe-leptin. Le hormone isiza ekulawuleni i-metabolism yomzimba futhi inganciphisa amazinga aphezulu e-cholesterol kanye ne-triglyceride.
  • Ukwelashwa kwesifo sikashukela kanye nokumelana ne-insulin: Uma unesifo sikashukela esibangelwa yi-lipodystrophy, udokotela wakho angase akunike imithi yomlomo efana ne -pioglitazone, i-metformin, i-sulfonylureas , noma i-thiazolidinediones ukuze uyelaphe. Abanye abantu abane-lipodystrophy kungadingeka bathathe i-insulin yokwenziwa ukuze belaphe isifo sikashukela sabo. Kungadingeka futhi uhlole amazinga kashukela egazini lakho njalo ekhaya nge-glucometer .
  • Ukulawula amazinga e-triglyceride kanye ne-cholesterol: Imithi ephuzwayo okukhulunywe ngayo ngaphambili esiza ekwelapheni isifo sikashukela ingasiza ekulawuleni amazinga e-cholesterol. Udokotela wakho angase futhi akunike ama-statin , njenge- rosuvastatin kanye ne-pravastatin . Abantu abanamazinga aphezulu e-triglyceride kungadingeka bathathe izithasiselo ze-fibric acid derivatives noma i-n-3 polyunsaturated fatty acids , njengalezo ezitholakala kumafutha enhlanzi.
  • Ukuhlinzwa kobuhle kanye nezinqubo: Abantu abane-lipodystrophy ezindaweni ezizwela kakhulu ubuhle, njengobuso, isifuba, kanye nezindawo zangasese, bangase bahlinzwe ubuhle ukuze bathuthukise ukubukeka kwabo kanye nokuzethemba. Odokotela abahlinzayo be-plastic bangase benze ukufakelwa kwezicubu zamafutha e-autologous, ukwakhiwa kabusha kobuso besebenzisa ama-free flaps, kanye ne-silicone noma ezinye izimila. Bangase futhi basebenzise amasu okususa amafutha noma ukuhlinzwa ukuze basuse ama-fat deposits angafuneki ezindaweni ezifana nesilevu noma ngemuva kwentamo (ngokuvamile okubizwa ngokuthi "i-buffalo hump" ).

Ososayensi basenokuningi okufanele bakufunde mayelana nendlela yokwelapha nokuphatha i-lipodystrophy. Njengoba bethola okwengeziwe mayelana nobunzima bezinqubo ze-metabolic, kungase kutholakale ezinye izindlela zokwelapha.

Ingabe i-lipodystrophy ingavinjelwa?

Ezimweni eziningi, i-Lipodystrophy ayikwazi ukuvinjelwa.

Izinhlobo ze-lipodystrophy zofuzo azinakuvinjelwa, njengoba ziwumphumela wokuguqulwa kwezakhi zofuzo okuzuzwe njengefa. Uma uhlela ukuba nezingane, qonda ingozi yokuba nengane enesifo sofuzo bese ukhuluma nodokotela wakho mayelana nokuhlolwa kwezakhi zofuzo.

I-lipodystrophy etholakala ngokutholakala ivame ukubangelwa ukutheleleka noma isifo sesimiso sokuzivikela komzimba. Nakuba ezinye izifo, njenge-chickenpox kanye nokukhwehlela okungapheli, zingavinjelwa ngokugonywa, ezinye izifo kanye nezifo zesimiso sokuzivikela komzimba ezihlobene ne-lipodystrophy etholakala ngokutholakala azikwazi ukuvinjelwa.

Iyini iphrojekthi ye-lipodystrophy?

Umbono we-lipodystrophy uncike kakhulu kuhlobo lwe-lipodystrophy onalo, nokuthi unezinye izimo noma izinkinga ezihlobene nazo, njengesifo sikashukela, izinkinga zesibindi noma zezinso.

Ukulungiswa kobuhle kwezindawo ezinamafutha aphansi kanye nezindawo ezinamafutha amaningi kusiza ukuthuthukisa ikhwalithi yokuphila kwabantu abane-lipodystrophy.

Uma wena noma ingane yakho nitholakala ninesifo se-lipodystrophy, khuluma nodokotela wakho ngalokho okufanele ukulindele nokuthi ungasiphatha kanjani kangcono lesi simo.

Kufanele ubonane nini nodokotela mayelana ne-lipodystrophy?

Uma ubona ukuthi wena noma ingane yakho iyancipha kakhulu ezindaweni ezithile, noma ukuthi amafutha ayanda ezindaweni ezithile, khuluma nodokotela wakho.

Uma wena noma ingane yakho nitholakala ninesifo i-Lipodystrophy, kufanele nihlangane nethimba lezokwelapha njalo ukuqinisekisa ukuthi ukwelashwa kwenu kusebenza kahle kuwe.

Okokugcina, izinto okufanele uzikhumbule

I-Lipodystrophy yisimo esingavamile kodwa esibucayi. Nakuba kungekho ikhambi, ezinye izindlela zokwelapha zingasiza ekulawuleni izimpawu zayo kanye nezimo ezihlobene nayo, njengesifo sikashukela kanye namazinga e-cholesterol angajwayelekile.

Ukwelashwa kuyahlukahluka kakhulu kumuntu nomuntu. Ngakho-ke, ithimba lakho lezokwelapha lizosebenzisana nawe ukudala uhlelo olukulungele kangcono. Ungesabi ukubuza udokotela wakho imibuzo. Bakhona ukukusiza. Lolu lwazi luzokusiza nakanjani uphile impilo enempilo!


i- lipodystrophy, izicubu zamafutha, i-leptin, izakhi zofuzo, ezitholwe, isifo sikashukela, i-cholesterol, i-triglyceride, i-HIV, izifo ze-metabolic

Frequently Asked Questions (FAQ)

Yiziphi izivivinyo ezisetshenziswa ukuxilonga i-lipodystrophy?

Udokotela wakho angase akucele ukuthi uhlolwe kaningana ukuze kutholakale i-lipodystrophy kanye/noma ukuze abone ukuthi zikhona yini ezinye izimbangela zezimpawu zakho. Lokhu kufaka phakathi:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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