Ingabe ingane yakho ithola amaqhubu angavamile emzimbeni wayo? Lokhu kungaba uphawu lwe-Complex Lymphatic Anomalies (CLA)!

Ngezinye izikhathi siyesaba kakhulu uma sibona izinguquko ezincane emizimbeni yezingane zethu, akunjalo? Ikakhulukazi uma singazi kahle ukuthi ziyini lezo zinto. Namuhla sizokhuluma ngesimo esingavamile kodwa esibaluleke kakhulu okufanele sisiqaphele. Lokhu kubizwa ngokuthi yi-Complex Lymphatic Anomalies , noma (CLA) ngamafuphi. Abanye abantu babesibiza nangokuthi (Lymphangiomatosis) ngaphambili. Ngakho-ke ungase uzwe womabili la magama.

Okokuqala, ake sibone, yini i-Complex Lymphatic Anomalies (CLA)?

Kalula nje, i-Complex Lymphatic Anomalies (CLA) iyisimo esingavamile kodwa esingase sivele lapho ingane iba nezimila ezingengozini ezibizwa ngokuthi ama-lymphatic malformations noma ama-lymphangiomas ohlelweni lwe-lymphatic lwengane. Lezi zimila zingakhula zibe amathambo engane, izicubu ezixhumeneyo, nezinye izitho zomzimba, okubangela umonakalo.

Cabanga nje, noma ngabe ingane yethu inalesi simo lapho izalwa, isikhathi esiningi izimpawu ziqala ukuvela lapho isikhulile kancane, mhlawumbe eminyakeni embalwa kamuva. Yingakho ngezinye izikhathi sekwephuze kakhulu ukukubona lokhu.

Ngakho-ke, luyini lolu hlelo lwe-lymphatic?

Kulungile, manje cishe uyazibuza ukuthi luyini uhlelo lwe-lymphatic. Kalula nje, luyisistimu yokuzivikela emangalisayo emzimbeni wethu. Lufana namasosha ezweni lakithi. Lolu hlelo lwe-lymphatic lusiza umzimba wethu ukuvimbela izifo futhi ulwe nazo uma zinjalo. Luyingxenye ebalulekile yesistimu yethu yokuzivikela.

Uhlelo lwe-lymphatic lwakhiwe yinethiwekhi yamapayipi amancane abizwa ngokuthi imithambo ye-lymphatic, ama-gland afana nama-lymph node, kanye nezitho ezifana ne-spleen. Le mithambo ye-lymphatic ifana namapayipi amancane. Iqoqa uketshezi lwe-lymph ezicutshini zomzimba, iluhlunge, iluhlanze, bese ilubuyisela egazini. Akuyona yini umsebenzi omangalisayo lona?

Kunezinhlobo ezimbili ze-CLA: ezihlukanisiwe kanye nezihlelekile.

Ama-Complex Lymphatic Anomalies angahlukaniswa ngezinhlobo ezimbili eziyinhloko:

1. Ama-CLA Ahlukanisiwe: Lokhu kwenzeka lapho izimila zigcinwa endaweni eyodwa yomzimba wengane. Isibonelo, zingathinta kuphela umgodi wesifuba. Kulesi simo, amaphaphu nezicubu ezithambile zesifuba (i-mediastinum) kuthinteka kakhulu.

2. Ama-CLA ajwayelekile: Kulesi simo, lawa mathumba angavela ezindaweni eziningi emzimbeni wengane, njengamathambo, isifuba kanye nesisu.

Ngale ndlela, izimpawu kanye nokwelashwa kungahluka kuye ngendawo ethintekile.

Yiziphi izinhlobo eziyinhloko ze-Complex Lymphatic Anomalies (CLA)?

Kunezinhlobo ezine eziyinhloko ze-CLA. Nakuba uhlobo ngalunye lunezinye zezimpawu ezifanayo, ziyizimo ezihlukile. Futhi izinguquko zezakhi zofuzo ezibangela zona nazo zihlukile.

• I-Generalized Lymphatic Anomaly (GLA):Lesi simo sivame ukuthinta izingxenye ezahlukene zomzimba wengane. Isibonelo, la mathumba angavela emathanjeni, e-spleen, esibindini, emaphashini, nasezicutshini ezithambile zesifuba (mediastinum).
• I-Kaposiform Lymphangiomatosis (KLA): Lolu uhlobo lwe-CLA olubi kakhulu nolusakazeka ngokushesha. Ku-KLA, imithambo ye-lymphatic ethwala uketshezi lwe-lymph emzimbeni wengane iyakhula. Lokhu kubangela ukuthi ihlasele futhi yonakalise izitho, amathambo, nezicubu ezizungezile.
• I-Central Conduction Lymphatic Anomaly (CCLA): Izingane ezine-CCLA nazo zinemithambo ye-lymph ekhulisiwe. Kodwa-ke, ku-CCLA, le mithambo ekhulisiwe itholakala kakhulu emzimbeni. Lokhu kungathinta uhlelo lokugaya ukudla futhi kuvimbele ingane ekukhipheni kahle uketshezi lwe-lymph emzimbeni.
• Isifo sikaGorham-Stout (GSD): Saziwa nangokuthi isifo sikaGorham, lesi simo sibangela ukuba amathambo amaningi ancibilike ngenxa yokwakheka kwemithambo ye-lymphatic ngaphakathi kwamathambo. Sibizwa nangokuthi "isifo samathambo esinyamalalayo." Singathinta noma yiliphi ithambo. Kodwa-ke, izingane ezine-GSD zivame ukulahlekelwa amathambo ezimbanjeni, ekhanda, entanyeni, nasemgogodleni wesibeletho.

Sivame kangakanani lesi simo se-CLA?

Ama-Complex Lymphatic Anomalies empeleni ayivelakancane kakhulu . Ngenxa yokuthi awavamile kangako, ngezinye izikhathi kungaba nzima ngodokotela ukuwaxilonga ngokunembile. Ngakho-ke, uma unezimpawu, kubaluleke kakhulu ukubona uchwepheshe ngokushesha okukhulu.

Yini ebangela le CLA?

Odokotela nabacwaningi basazama ukuthola ukuthi yini ebangela i-CLA. Kodwa-ke, ucwaningo lwamuva lubonisa ukuthi lesi simo singabangelwa kokubili ukuguquka kwezakhi zofuzo okuzuzwa njengefa okudluliselwa kubazali kuya ezinganeni, kanye nokuguquka kwezakhi zofuzo ezenzeka ngemva kokuzalwa. Lokhu kusho ukuthi kuhlobene nofuzo.

Ubani osengozini yokuthola i-CLA?

Ama-Complex Lymphatic Anomalies angathinta noma ubani. Ngokukhethekile, izimpawu zalesi simo zivame ukuvela ebuntwaneni noma ebusheni. Ngakho-ke, noma ngabe lesi simo sikhona ekuzalweni, kungathatha isikhathi ukuthi izimpawu zibonakale.

Ngakho-ke, yiziphi izimpawu ze-CLA?

Izimpawu zingahluka kuye ngengane enalesi sifo. Futhi, izimpawu ziyahlukahluka kuye ngokuthi yisiphi isitho somzimba esithintekile nokuthi sibi kangakanani. Esikhathini esiningi, lesi sifo siqhubeka kancane. Ngakho-ke, singase singazinaki kakhulu ezinye zezimpawu, noma singase sicabange ukuthi zibangelwa esinye isifo.

Uma uhlelo lokuphefumula lwengane yakho luthintekile:

Ngalesi sikhathi, kungase kuvele izimpawu ezifana ne-asthma.

• Ukukhwehlela okuqhubekayo.
• Ubunzima bokuphefumula (ukuphelelwa umoya).
• Ukuphefumula ( umsindo wokukhala kwekhwela ) lapho uphefumula.

Uma uhlelo lwamathambo lwengane yakho luthintekile:

• Ubuhlungu emathanjeni noma emalungeni.
• Ngisho nokuwa okuncane kungabangela ukuphuka .
• Ukuba ndikindiki ezithweni.
• Ubuhlungu noma ubuthakathaka obubangelwa ukucindezelwa kwemizwa .

Uma uhlelo lokugaya ukudla lwengane yakho luthintekile:

• Ukuvuvukala kwesisu kanye nobuhlungu besisu .
• Ukuntuleka kwegazi kanye nokukhathala okuqhubekayo.
• Uhudo.
• Ukudla akunambitheki.
• Isicanucanu nokuhlanza.
• Ukwehlisa isisindo ngaphandle kwesizathu.

Uma uhlelo lomchamo lwengane yakho luthintekile:

• Igazi emchameni (i-hematuria).
• Ubuhlungu besifuba.
• Umfutho wegazi ophezulu ezinganeni.

Uma ingane yakho inesinye noma ngaphezulu salezi zimpawu, sicela ufune iseluleko sezokwelapha. Lezi akuzona izimpawu eziqondene ngqo ne-CLA, kodwa kubalulekile ukuhlolwa.

Odokotela bakuthola kanjani lesi simo se-CLA?

Ngenxa yokuthi i-CLA iyisimo esingavamile futhi izimpawu ziyahlukahluka, ngezinye izikhathi kungaba nzima ngodokotela ukuthola isimo esiqondile. Njengoba ivame ukuthinta amaphaphu namathambo ezingane, udokotela wengane yakho angase acele ukuhlolwa okufana nalokhu:

• I-Bronchoscopy: Ukuhlola ukutheleleka noma ezinye izinkinga emigudwini yomoya.
• Ukuhlolwa kokusebenza kwamaphaphu: Kala ukuthi amaphaphu akho asebenza kahle kangakanani.
• I-MRI yomzimba wonke: Ukuhlola izinto ezifana nezitho ezithintekile, izilonda zamathambo, noma uketshezi esiswini.
• Ama-X-ray: Ukuhlola amathambo abonakala esolisayo noma alimele ku-MRI. Ama-X-ray esifubeni angabheka nokukhubazeka emaphashini.

Ngezinye izikhathi odokotela bathatha isampula encane yama-lymph node kanye nezicubu (i-biopsy) bese beyihlola ngaphansi kwe-microscope. Nakuba lokhu kuhlolwa kungaxilonga i-CLA ngokuqinisekile, ngezinye izikhathi kungabangela izinkinga, njengokuqoqwa koketshezi lwe-lymph oluzungeze amaphaphu (i-chylothorax). Ngenxa yalokhu, odokotela bavame ukuthembela ekuhlolweni okungangenisi kakhulu ukuze benze ukuxilongwa.

Iphathwa kanjani i-CLA?

Ngenxa yokuthi i-CLA ingathinta izindawo eziningi zomzimba wengane, odokotela basebenzisana, okungukuthi, basebenzisa indlela ehlukahlukene yokuhlela ukwelashwa okufanele ingane. Lapho welapha i-CLA, ukugxila okuyinhloko ukulawula izimpawu zengane. Ukuze wenze lokhu, ungenza izinto ezinjengalezi:

• Ukufakelwa kwamathambo: Ukulimala kwamathambo ezimweni ezifana ne-GSD.
• Ukudla okunamaphrotheni amaningi noma ukudla okunomsoco ngemithambo yegazi (ukudla okunomsoco okuphelele noma i-TPN).
• Ukwelashwa nge-Sclerotherapy: Ukunciphisa noma ukuvala izimila noma imithambo ye-lymph.
• Ukuhlinzwa: Ukususa izimila noma ukufaka amapayipi amancane (ama-shunt) ukuze kube lula ukuhamba koketshezi lwe-lymph.
• Ukwelashwa ngemisebe noma ngamakhemikhali: Ukunciphisa izimila ezingezona umdlavuza (lezi zisetshenziswa kuphela ezimweni ezinzima kakhulu nezisongela ukuphila).

Muva nje, izindlela zokwelapha eziqondiwe eziqondise ekuguqulweni kwezakhi zofuzo ezibangela lesi simo nazo zisetshenzisiwe. Lezi zindlela zokwelapha ziboniswe futhi zisebenza kahle njengokwelashwa kokuqala kwe-CLA.

Ingabe i-Complex Lymphatic Anomalies (CLA) ingavinjelwa?

Ngeshwa, cha . I-CLA iyenzeka ngesikhathi sokukhulelwa, futhi imbangela eqondile ayaziwa. Ngakho-ke, akukho lutho obungakwenza ukuvimbela ingane yakho ukuthi ingakhuli nalesi simo.

Yiziphi izinkinga ezingaba khona ze-CLA?

I-CLA ingabeka ingane yakho engozini yalokhu okulandelayo:

• Ama-Ascites: Ukuqongelela koketshezi esiswini.
• Ukuphuka kwamathambo.
• I-Chylothorax kanye ne-Chylopericardium: Iqoqo loketshezi olufana nobisi (chyle) oluqukethe uketshezi lwe-lymph kanye namafutha olwelwesini olumboza amaphaphu (pleura) noma isikhwama esizungeze inhliziyo (pericardium).
• Amaphaphu awile/i-pneumothorax.
• Ukwehluleka kwesibindi.
• Ukukhubazeka.
• Ukuphuma kwegazi kwe-pericardial.
• Ukuvuvukala kwe-pleural kanye ne-cardiogenic pulmonary edema.

Ezinye zalezi zinkinga zingaba zimbi kakhulu, ngakho-ke kubalulekile ukuqaphela izimpawu nokulandela imiyalelo kadokotela wakho.

Liyini ikusasa lomuntu one-CLA?

Akukho ukwelashwa kwe-Complex Lymphatic Anomalies (CLA). Ikusasa lengane yakho lincike ekutheni yiziphi izinhlelo zomzimba ezithintekile nokuthi izimpawu zimbi kangakanani.

Ukuphuma kwegazi emithanjeni yegazi kuyimbangela ehamba phambili yokufa phakathi kwabantu abane-CLA. Kodwa-ke, ngokwelashwa nokuphathwa okufanele, ingane ingasizwa ukuba iphile impilo evamile.

Kufanele ngimbone nini udokotela?

Uma ingane yakho inanoma yiziphi zalezi zimpawu, xhumana nodokotela ngokushesha:

• Ubuhlungu esiswini noma emathunjini.
• Uma kukhona igazi emchameni.
• Ukukhwehlela okuqhubekayo, ukuphefumula kanzima, noma ubunzima bokuphefumula.
• Ukucasuka okungachazeki, ukukhathala, noma ukwehlisa isisindo.

Uma unanoma yikuphi kwalokhu, sicela ubonane nodokotela ngokushesha.

Yini okufanele ngiyibuze udokotela?

Ungase ufune ukubuza udokotela wengane yakho imibuzo efana nale:

• Yiziphi izingxenye zomzimba wengane yami ezithinte lesi simo?
• Yiziphi izindlela zokwelapha ezitholakalayo enganeni yami?
• Ingabe ingane yami idinga ukuhlinzwa?
• Ingabe kufanele ngiqaphele izimpawu zezinkinga?

Kubaluleke kakhulu ukubuza le mibuzo nokuqonda kahle isimo.

Ekugcineni, kufanele ngithi...

Uma uthola ukuthi ingane yakho ine-CLA (lymphangiomatosis), kuyinto evamile ukuzizwa wesaba futhi ukhathazekile ngokuthi kuzoyithinta kanjani impilo nekusasa layo. Iningi lethu kungenzeka ukuthi alikaze lizwe ngalesi sifo ngaphambili. Futhi akukho lutho obungakwenza ukuze usivimbele.

Isinyathelo sokuqala sokusiza ingane yakho ukuba nolwazi oluphelele ngalesi sifo, izimpawu zaso, kanye nokwelashwa kwaso. Bona udokotela ochwepheshe bezifo zesistimu ye-lymphatic. Bangaphendula imibuzo yakho futhi banikeze ukunakekelwa okukhethekile kwezokwelapha ingane yakho ekudingayo.

Nakuba kungekho ikhambi le-CLA, ukwelashwa okufanele kanye nokuphathwa kungasiza ingane yakho iphile impilo ejabulisayo nenempilo. Ngakho-ke, hlala uqinile futhi wenze konke okusemandleni akho ngengane yakho.

` Izinkinga Eziyinkimbinkimbi Ze-Lymphatic, I-Lymphangiomatosis, Izifo Zesistimu Ye-Lymphatic, Izimila Zobuntwana, I-Osteomalacia, Izimpawu Ze-Pulmonary, Izifo Ezingavamile Zezingane