Ingabe ngezinye izikhathi uzizwa ukhathele, uphelelwa umoya, noma unemilenze evuvukele? Sivame ukukhohlwa ngalezi zimpawu, sicabanga ukuthi ziwukukhathala okuvamile noma into eyenzekayo uma sisebenza kanzima. Kodwa ngezinye izikhathi, ngemuva kwalezi zimpawu, kungase kube nesifo senhliziyo esingavamile futhi esingajwayelekile. Leso ngesinye sezifo esizokhuluma ngazo namuhla, okungukuthi i-Restrictive Cardiomyopathy (RCM) . Ungakhathazeki, sizokhuluma ngalokhu kalula nangendlela ongayiqonda.
Kalula nje, kuyini i-Restrictive Cardiomyopathy?
Leli gama lingase lizwakale liyinkimbinkimbi kancane, kodwa ake silichaze kalula futhi siliqonde.
Inhliziyo yethu iyisitho esimangalisayo. Inezindawo ezine eziyinhloko. Amakamelo amabili aphezulu abizwa ngokuthi i-atria , kanti amakamelo amabili amakhulu, aqinile phansi abizwa ngokuthi ama-ventricle . Amakamelo amabili aphansi enza umsebenzi oyinhloko wokupompa igazi emizimbeni yethu yonke. Ukuze lo msebenzi usebenze kahle, imisipha emagumbini idinga ukwelulwa ngokuqinile, igcwaliswe ngegazi, bese ifinyezwa ngamandla ukuze igazi liqhubekele phambili.
Cabanga ngebhola elisha sha lerabha. Liguquguquka kangakanani? Yileyo ndlela amaseli enhliziyo enempilo okufanele abe ngayo. Kufanele avuvuke kahle lapho igazi lingena, athathe igazi, bese lifinyela kahle lapho kudingeka likhishwe.
Esifweni esibizwa ngokuthi i-Restrictive Cardiomyopathy , izindonga zemisipha zala maseli ziyaqina . Njengerabha endala, eyomiswe yilanga. Ngenxa yalokhu kuqina, amaseli awakwazi ukwelula kahle futhi agcwale igazi. Lokhu kusho ukuthi awakwazi ukwamukela igazi elanele eliza enhliziyweni. Lapho inani legazi eliza enhliziyweni lehla, inani legazi elimpontshelwa emzimbeni nalo liyancipha. Lena yinkinga eyisisekelo yalesi sifo.
Lesi sifo singeseqembu lezifo zemisipha yenhliziyo ezibizwa ngokuthi i-Cardiomyopathy . Kodwa-ke, sibhekwa njengohlobo olungavamile kakhulu phakathi kwazo. Cishe u-5% wabo bonke abaguli be-Cardiomyopathy abahlushwa yilesi simo.
Lesi sifo sikwenza uzizwe kanjani? (Izimpawu)
Ezigabeni zokuqala zalesi sifo, ungase ungabi nazimpawu. Kodwa ngokuhamba kwesikhathi, njengoba ukunikezwa kwegazi enhliziyweni kuncipha, izimpawu zokwehluleka kwenhliziyo ziqala ukuvela. Lezi zingase zivele eyodwa ngesikhathi noma eziningana ngesikhathi esisodwa.
Ake sibone ukuthi ziyini lezo zimpawu kuthebula elingezansi.
| Isibonakaliso | Incazelo elula |
|---|---|
| Ubunzima bokuphefumula (i-Dyspnea) | Ungase uzizwe uphelelwa umoya, ikakhulukazi lapho wenza umsebenzi olula, uhamba, noma ulele phansi. Lokhu kungabangelwa uketshezi oluqongelelana emaphashini lapho inhliziyo ingakwazi ukupompa igazi kahle. |
| Ukuvuvukala kwemilenze, amaqakala, nezinyawo (i-Edema) | Ngenxa yobuthakathaka bokusebenza kwenhliziyo ukupompa, uketshezi luqala ukuqongelela ezingxenyeni ezingezansi zomzimba. Lungabangela nokuvuvukala. |
| Ukukhathala okukhulu nokukhathala | Inani legazi elihlinzeka izitho zomzimba ngomoya-mpilo nezakhamzimba ezizidingayo liyancipha, ngakho uhlala uzizwa ukhathele futhi ungakwazi ukwenza lutho. |
| Ukushaya kwenhliziyo | Ungase uzizwe sengathi ukushaya kwenhliziyo yakho kuyakhuphuka ngokuzumayo, isifuba sakho siyashaya, noma awusakwazi ukushaya. |
| Isiyezi noma Ukuquleka | Lesi simo singabangelwa ukwehla kokunikezwa kwegazi ebuchosheni, ikakhulukazi uma usukuma ngokuzumayo. |
| Ubuhlungu besifuba | Ukuqina kwesifuba noma ubuhlungu kungase kwenzeke ngesikhathi sokuzivocavoca noma sokuphumula. |
Into ebalulekile ukuthi lezi zimpawu zingabonakala nakwezinye izimo eziningi zezokwelapha. Ngakho-ke uma unesinye noma ngaphezulu salezi, into engcono kakhulu ongayenza ukungesabi bese ubona udokotela ukuze akunike iseluleko.
Kungani lokhu kwenzeka? (Izizathu)
Ngokuvamile, i-Restrictive Cardiomyopathy ivela njengomphumela ongemuhle wesinye isimo sezokwelapha. Okusho ukuthi, esinye isifo silimaza imisipha yenhliziyo futhi sibangele ukuthi iqine. Ngezinye izikhathi, akukho sizathu esithile esingatholakala.
Lezi ezinye zezizathu eziyinhloko:
- I-Amyloidosis: Lokhu kwenzeka lapho iphrotheni engajwayelekile ekhiqizwa ngumzimba (i-amyloid) ifakwa ezithweni ezahlukene zomzimba, okuhlanganisa nenhliziyo. Uma le phrotheni ifakwa enhliziyweni, izindonga zemisipha yenhliziyo ziba lukhuni futhi ziqine.
- I-Sarcoidosis: Lesi yisimo lapho kwakheka khona izigaxa ezincane zamangqamuzana okuvuvukala (ama-granuloma) ezingxenyeni ezahlukene zomzimba. Uma lokhu kwakheka enhliziyweni, kungalimaza imisipha yenhliziyo futhi kubangele ukuqina.
- I-Hemochromatosis: Lesi yisimo lapho umzimba uqoqa insimbi eningi kakhulu, enganqwabelana ezithweni ezifana nenhliziyo. Lokhu kungalimaza nenhliziyo.
- Izifo zezicubu ezixhumeneyo: Izimo ezifana ne-scleroderma zingabangela nokuba imisipha yenhliziyo iqine.
- Ezinye izindlela zokwelapha umdlavuza: Eminye imithi yokulwa nomdlavuza (i-chemotherapy) kanye nokwelashwa ngemisebe nakho kungabangela umonakalo emisipheni yenhliziyo njengomphumela ongemuhle.
Udokotela ukuthola kanjani lokhu?
Uma utshela udokotela wakho ngezimpawu zakho, into yokuqala azokwenza ukukuhlola ngokucophelela. Bazolalela inhliziyo yakho, balinganise umfutho wegazi lakho, futhi bahlole ukuthi imilenze yakho ivuvukele yini.
Ngemuva kwalokho, kunconywa ukuhlolwa okuningana ukuqinisekisa ukuxilongwa okuqondile nokuthola ukuthi yini ebangele lokho.
| Ukuhlolwa | Yini elindelekile kulokhu? |
|---|---|
| I-Echocardiogram | Lesi isivivinyo esibaluleke kakhulu. Kufana nokuskena kwenhliziyo nge-ultrasound. Kungabona ngokucacile ukuthi amagumbi enhliziyo agcwele igazi kahle nokuthi izindonga zawo zijiyile noma ziqinile. |
| Ukuhlolwa kwegazi nomchamo | Lokhu kungasiza ekutholeni imbangela. Isibonelo, ukuhlolwa kwegazi kungasetshenziswa ukuhlola isimo esifana ne-hemochromatosis. |
| I-X-ray yesifuba, i-CT yenhliziyo, i-MRI yenhliziyo | Lezi zinhlobo zokuskena zinganikeza ulwazi olujulile mayelana nosayizi, ukuma, kanye nesakhiwo senhliziyo. |
| I-Biopsy ye-Myocardial | Kwezinye izimo, kuthathwa ingxenye encane kakhulu yomsipha wenhliziyo bese ihlolwa ngaphansi kwe-microscope. Lokhu kubaluleke kakhulu ukuqinisekisa imbangela eqondile, njenge-amyloidosis noma i-sarcoidosis. |
| Ezinye izivivinyo | Ukuhlolwa okufana ne-ECG (Electrocardiogram) kanye ne-Exercise Stress Test nakho kungenziwa uma kudingeka. |
Yiziphi izindlela zokwelapha lokhu?
Akukho ukwelashwa okuqondile kwe-Restrictive Cardiomyopathy. Kunezinhloso ezimbili eziyinhloko ekwelashweni:
1. Ukwelapha isifo esiyisisekelo esibangele lesi simo.
2. Lawula izimpawu ezikhona futhi wenze impilo ibe lula.
Ngokwesibonelo:
- Uma lesi simo sibangelwa yi -sarcoidosis , imithi efana ne -corticosteroids inganikezwa ngenxa yaso.
- Uma kungenxa ye -hemochromatosis (ukwanda kwensimbi), ukwelashwa okubizwa ngokuthi i-phlebotomy yokwelapha kwenziwa ukuze kususwe igazi ukuze kususwe insimbi eningi emzimbeni.
- Manje sekukhona imithi emisha yezinhlobo ezithile ze -amyloidosis .
Ngaphezu kwalokho, udokotela wakho angancoma okulandelayo ukusiza ukuphatha izimpawu zokuhluleka kwenhliziyo:
- Ama-Diuretics: Lawa avame ukubizwa ngokuthi 'amaphilisi amanzi'. Asiza umzimba ukukhipha amanzi angaphezulu ngomchamo, okungasiza ekunciphiseni ukuvuvukala emilenzeni kanye nokuphelelwa umoya.
- Imithi yokulawula izinga lokushaya kwenhliziyo: Uma ukushaya kwenhliziyo yakho kungajwayelekile, imithi efana ne -beta-blockers noma i-calcium channel blockers inganikezwa ukuyilawula.
- Imithi yokucindezela kwegazi.
Ezinye iziguli ezinesifo esibi kakhulu zingadinga ukufakelwa inhliziyo . Odokotela batusa nokunakekelwa kokunciphisa ubuhlungu , okusiza isiguli sizizwe sikhululekile futhi kunciphise ukungakhululeki okubangelwa yizimpawu.
Sihlala kanjani siphilile kulesi simo?
Kuvamile ukuzizwa wesaba uma uthola ukuthi unalesi sifo. Kodwa-ke, ngokwelashwa okufanele kanye nezinguquko ezincane endleleni yakho yokuphila, unganciphisa umthwalo enhliziyweni yakho futhi uphile impilo engcono.
Izinguquko zendlela yokuphila
- Ukulawula usawoti: Nciphisa inani likasawoti owufaka ekudleni kwakho. Usawoti ungandisa ukugcinwa kwamanzi emzimbeni, okuholela ekuvuvukeni nasekuphefumuleni kanzima. Ukudla okusemathinini, amasoso athengwe esitolo, kanye namasoseji kugcwele usawoti.
- Ukudla okunempilo: Yidla imifino emisha, izithelo, nokudla okucebile nge-fiber. Nciphisa amafutha ezilwane, amaswidi, kanye nemikhiqizo kafulawa.
- Ukuzivocavoca: Buza udokotela wakho ukuthi hlobo luni lokuzivocavoca olukufanele. Ukuzivocavoca okunzima kungase kungafaneleki, kodwa ukuzivocavoca okulula njengokuhamba ngokuvamile kulungile.
- Nciphisa ukucindezeleka: Ukucindezeleka akukuhle enhliziyweni. Khulula ingqondo yakho ngezinto ezifana nokuzindla, ukuzivocavoca ngokuphefumula, kanye nokuzibandakanya entweni oyithandayo.
Khumbula njalo ukulandela imiyalelo kadokotela wakho ngqo. Thatha imithi yakho ngesikhathi. Uma unenkinga, ungesabi ukukhuluma nodokotela wakho.
Kunini lapho udinga ukubonana nodokotela ngokushesha?
Uma une-Restrictive Cardiomyopathy, kunezimpawu ezithile okufanele uziqaphele kakhulu. Lezi kungaba yisimo esiphuthumayo.
Uma uhlangabezana nanoma yiziphi izimpawu ezilandelayo, hamba uye eMnyangweni Wezimo Eziphuthumayo (ETU) wesibhedlela esiseduze ngokushesha:
- Ubuhlungu besifuba obukhulu noma obungazelelwe
- Ukuphefumula okuphuthumayo, okunzima
- Ukuquleka noma ukulahlekelwa ukwazi
Lokhu kungaba izimpawu zokucindezeleka okukhulu enhliziyweni, ngakho-ke ukufuna ukwelashwa ngaphandle kokuchitha isikhathi kungasindisa impilo.
Umlayezo Wokuya Nawe Ekhaya
- I-Restrictive Cardiomyopathy yisimo esingavamile lapho imisipha emakamelweni aphansi (amakamelo) enhliziyo iba lukhuni futhi ingakwazi ukugcwala igazi kahle.
- Ubunzima bokuphefumula, ukuvuvukala kwemilenze, ukukhathala okukhulu, kanye nokushaya kwenhliziyo okungajwayelekile kuphakathi kwezimpawu eziyinhloko.
- Imbangela yalesi sifo ivame ukuba esinye isimo sezokwelapha njenge-Amyloidosis noma i-Sarcoidosis.
- Ukwelashwa kuhloswe kakhulu ukulawula izimpawu ngenkathi kwelashwa imbangela.
- Ungaphila impilo enempilo ngokulandela ukudla okunosawoti omncane, ukuzivocavoca njengoba kunconywe udokotela wakho, kanye nokuphuza imithi oyinikezwe udokotela ngesikhathi.
- Uma uzwa ubuhlungu obukhulu esifubeni, ubunzima bokuphefumula, noma ukuquleka, hamba uye eMnyangweni Wezimo Eziphuthumayo (ETU) wesibhedlela ngokushesha.











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