Ne èlé ŋku ɖe viwòa ŋu la, ɖe nèse le ɖokuiwò me kpɔ be eƒe ŋkuwo mele ye kpɔm tẽ o, abe ɖe wole du dzi le afisia kple afima ko ene, alo abe ɖe womate ŋu anɔ teƒe ɖeka tututu o enea? Ðe nèsena le ɖokuiwò me ɣeaɖewoɣi be meléa ŋku ɖe fefenu sue aɖe ŋu nyuie o, ɖeko wòƒoa saŋku ɖe eŋua? Enye nusi sɔ ŋutɔ be vidada alo vifofo nase vɔvɔ̃ kple dzimaɖitsitsi geɖe ne wokpɔ nu siawo tɔgbe. Egbea míele nu ƒom tso nɔnɔme aɖe si ate ŋu ahe dzesi siawo vɛ eye wònɔa anyi le vidzidzi me ŋu . Woyɔa esia be ‘Optic Nerve Hypoplasia’.
Nukae nye ‘Ŋku ƒe Lãmetsiŋusẽ ƒe Hypoplasia’?
Kpuie ko la, Optic Nerve Hypoplasia nye dɔléle si wodzina. Nusi dzɔna le afisiae nye be ŋku ƒe lãmeka si tsɔa gbedasiwo yia míaƒe ŋkuwo kple ahɔhɔ̃a dome la metsina nyuie o alo ele sue. Bu eŋu abe fotoɖemɔ̃ eve ene. Woɖoa nusi fotoɖemɔ̃a kpɔna ɖe ahɔhɔ̃a abe nɔnɔmetatawo ene to ŋku ƒe lãmeka dzi. Eyata ne lãmeka sia metsi nyuie o la, nusi ŋkua kpɔna la meyia ahɔhɔ̃a me nyuie o. Esia ate ŋu ahe ŋku ƒe kuxi vovovowo vɛ, abe ŋku ƒe tsatsam ene .
Menye ŋku ƒe lãmeka dzi koe nɔnɔme sia gblẽa nu le o. Ɣeaɖewoɣi la, ate ŋu akpɔ ŋusẽ ɖe ɖevia ƒe ahɔhɔ̃ ƒe akpa bubuwo ƒe tsitsi hã dzi, vevietɔ:
- Ahɔhɔ̃ ƒe titina ƒe dɔmawɔmawɔ nyuie: Ahɔhɔ̃a ƒe akpa siwo ma nutome eveawo dome, abe septum pellucidum kple corpus callosum ene, mate ŋu atsi nyuie o. Ɣeaɖewoɣi la, ɖewohĩ nusiawo mava do goe kura o. Esiawo le vevie na kadodo le ahɔhɔ̃a ƒe akpa aɖewo dome.
- Pituitary Gland Hypoplasia: Ðewohĩ èse Pituitary Gland ŋkɔ kpɔ. Enɔa ahɔhɔ̃a ƒe gɔme, le Hypothalamus te. Lãmetsi sue sia kpɔa míaƒe ŋutilã ƒe dɔ vevi geɖe dzi, vevietɔ lãmetsiŋusẽ ƒe dɔwɔwɔ . Eyata ne lãkusi sia metsi nyuie o la, ɖewohĩ mawɔ lãmetsi siwo ŋutilã hiã o, alo ate ŋu awɔ nu ʋɛ aɖewo ko.
Ɣeaɖewoɣi la, wogayɔa nɔnɔme sia be `(Optic Nerve Hypoplasia)` alo `(Septo-Optic Dysplasia - SOD)` alo `(de Morsier Syndrome)`. Esia le alea elabena abe alesi numekukuwo ɖee fia ene la, amesiame kloe si ŋu `(SOD)` le la ƒe ŋku ƒe lãmeka ƒe tsitsi si ŋu wògblẽ nu le. Ke hã, amesiwo ŋu `(ONH)` le (i.e. le 5% kple 10%) ƒe alafa memamã sue aɖe koe ahɔhɔ̃a ƒe titina akpawo ƒe tsitsi gblẽa nu le (le kpɔɖeŋu me, `(Septum Pellucidum)`).
Aleke gbegbee nɔnɔme sia bɔe?
Le akɔntabubu siwo le dukɔwo abe United States ene me nu la, ɖevi ɖeka le 10,000 ɖesiaɖe meWogblɔ be nɔnɔme sia `(Optic Nerve Hypoplasia)` ateŋu adze ame abe 100,000 ene dzi. Azɔ hã, wode dzesii be nɔnɔme siae nye nu vevitɔ si gbɔ ɖevi siwo mexɔ ƒe 3 haɖe o ƒe ŋkuwo megakpɔa nu nyuie o. Ðevi mawo tɔgbe le Sri Lanka hã.
Ðe Optic Nerve Hypoplasia nye dɔléle sesẽ aɖea?
Ẽ, esia nye nɔnɔme sesẽ aɖe, eye ate ŋu anye nu sesẽ ɣeaɖewoɣi. Gake nusiwo wògblẽna le ame ŋu la toa vovo tso ame ɖeka gbɔ yi bubu gbɔ. Ðevi aɖewo ate ŋu akpɔ kuxi gã aɖe. Azɔ hã, ne dɔlékuiwutikea gblẽ la, ate ŋu ado kplamatse ŋutilãa ƒe lãmetsiŋusẽ ƒe dɔwɔwɔ. Kuxi aɖewo siwo do ƒome kple lãmetsiŋusẽ ate ŋu ade ame ƒe agbe afɔku me gɔ̃ hã. Eyata ne èsusu be dzesi siawo le viwò ŋu, alo ne ède dzesi tɔtrɔ aɖewo le woƒe nuwɔna me la, ele vevie ŋutɔ be nàyi ɖɔkta gbɔ enumake, vevietɔ ɖeviwo alo ŋkudɔdala.
Nukae nye Optic Nerve Hypoplasia ƒe dzesiwo?
Dzesi siwo wokpɔna le nɔnɔme sia me ate ŋu adze ŋku ɖeka ko alo ŋku evea siaa dzi.
Dzesi siwo woate ŋu akpɔ siwo do ƒome kple ŋkuwo:
- Nukpɔkpɔ ƒe dɔmawɔmawɔ nyuie: Esia ate ŋu atso nukpɔkpɔ ƒe ɖiɖi vie dzi va ɖo ŋku ƒe nukpɔkpɔ keŋkeŋ (Nukpɔkpɔ ƒe kuxi sesẽ alo Ŋkuagbã).
- Nystagmus: Ŋkuwo ƒe ʋuʋu kabakaba atraɖii tso axa ɖeka yi axa ɖeka alo yi dzi kple anyime, abe gaƒoɖokui ƒe asi evelia ene, gake kabakaba wu.
- Strabismus (ŋku siwo wotso) alo Esotropia (ŋku siwo mefia mɔ ɖeka o): Ŋku ɖeka ate ŋu akpɔ ŋgɔ tẽ evɔ ŋku evelia ate ŋu atrɔ ɖe mɔ si to vovo na ema nu.
- Esesẽna be wò susu nanɔ nu ŋu: Ne wobia tso amea si be wòalé ŋku ɖe nane, abe fefenu ene ŋu la, ate ŋu anye be mate ŋu alé ŋku ɖe eŋu nyuie o.
Dzesi siwo ate ŋu ado mo ɖa le ahɔhɔ̃a ƒe tsitsi ƒe nɔnɔme siwo mesɔ o ta:
- Susu ƒe Ŋgɔyiyi ƒe Kuxiwo (`(Susu ƒe Nuwɔametɔnyenye)`): Nuwo abe nusɔsrɔ̃ ƒe kuxiwo, susu ƒe ŋutetewo ƒe tsitsi le mɔ si sɔ ɖe ƒexɔxɔ nu o.
- Alɔ̃madɔmadɔ: Ame ƒe tagbɔ buna zi ɖeka eye wòʋuʋuna.
Dzesi siwo do ƒome kple lãmetsiŋusẽ siwo ate ŋu ado mo ɖa le lãkusi ƒe tsitsi si dzi ɖe kpɔtɔ ta:
Esia le vevie ŋutɔ, elabena lãmetsiŋusẽwo kpɔa ŋusẽ ɖe nu geɖe dzi le míaƒe ŋutilã me.
- Ŋutilã ƒe dɔwɔwɔ dzi ɖuɖu sesẽ: Le kpɔɖeŋu me, dɔ kple tsikɔwuame dzi ɖuɖu ƒe ŋutete manɔamesi, alɔ̃dɔdɔ ƒe kuxiwo, ŋutilã ƒe dzoxɔxɔ dzi kpɔkpɔ nyuie ƒe ŋutete manɔamesi.
- Dɔléle ƒe ʋuʋu: Kɔkɔme ƒe anyimanɔmanɔ si sɔ ɖe ƒexɔxɔ nu, eye wòva nɔa kpuie wu ɖevi bubuwo sã.
- Hypothyroidism: Esia hã gblẽa nu le ŋutilãa ƒe dɔwɔwɔ geɖe ŋu.
- Ƒewuiwo ƒe heheɖemegbe.
- Sukli ƒe agbɔsɔsɔ si le ʋu me (Hypoglycemia): Esia ate ŋu anye afɔku.
- Nɔnɔme si le abe suklidɔ ene gake medo ƒome kple sukli o, si naa aɖuɖɔtoe kple tsikɔwuame fũ (`(Diabetes Insipidus)`).
- Jaundice: Ŋutilã kple ŋku ƒe ɣie, vevietɔ le vidzĩ siwo wodzi yeyee gome.
Tsɔe be viwònyɔnuvi suea le agbagba dzem be yealé ŋku ɖe fefenu aɖe ŋu, gake edze abe eƒe ŋkuwo megale ŋku lém ɖe nu ŋu nyuie o ene, alo ɖeko wòle ʋuʋum. Alo eɖea aɖuɖɔ ɣesiaɣi, edzena abe vuvɔ le wɔwɔm ene, eye mano notsi nyuie o. Ne èkpɔ nane si le abe esia ene la, ehiã be nàyi ɖɔkta gbɔ enumake.
Ðe Optic Nerve Hypoplasia ate ŋu ana ame nazu ŋkuagbãtɔ keŋkeŋa?
Le go aɖewo me la, ẽ. Nɔnɔme sia ate ŋu ana ame nakpɔ nu vevie alo ana ame nakpɔ ŋku keŋkeŋ gɔ̃ hã . Le go bubu me la, nukpɔkpɔ ƒe kuxi sue aɖe koe nɔa ɖevi aɖewo ŋu. Ɣeaɖewoɣi ne ɖevia le tsitsim la, dzesi siawo dometɔ aɖewo (abe nystagmus ene) ate ŋu aɖe akpɔtɔ. Wò ɖɔkta ate ŋu agblɔ alesi tututu nɔnɔme sia akpɔ ŋusẽ ɖe viwòa dzii na wò.
Nukawo gbɔe nɔnɔme sia tso?
Numekulawo meka ɖe nusi tututu hea Optic Nerve Hypoplasia vɛ dzi haɖe o. Gake wosusu be nutoa me kple domenyiŋusẽfianu ƒe ƒuƒoƒo gbɔe wòtso. Le kpɔɖeŋu me, ate ŋu anye be nɔnɔmea do ƒome kple fugboe ƒe ahanono ƒe dɔléle (FAS), si tsoa vidadaa ƒe ahanono le fufɔɣi gbɔ.
Togbɔ be womate ŋu ake ɖe domenyiŋusẽfianu si gbɔ wòtso ŋu ɣesiaɣi o hã la, le go aɖewo me la, domenyiŋusẽfianu ƒe tɔtrɔ (`(Mutations)`) ate ŋu akpɔ ŋusẽ ɖe esia dzi. Wonyia domenyiŋusẽfianu ƒe tɔtrɔ siawo ƒe dome abe `(Autosomal Recessive)`, si fia be ne ɖevia xɔ domenyiŋusẽfianu sia si wotrɔ tso vidadaa kple fofoa siaa gbɔ ko hafi ɖevia ate ŋu axɔ nɔnɔme sia. Domenyiŋusẽfianu siwo ate ŋu akpɔ gome le eme dometɔ aɖewoe nye:
- `(HESX1)`
- `(SOX2)`
- `(SOX3)`
- `(OTX2)`
- `(PROKR2)`
- Domenyiŋusẽfianu bubu siwo womede dzesii haɖe o.
Nukawoe nye nusiwo ate ŋu ana Optic Nerve Hypoplasia nadzɔ?
Afɔku aɖewo li siwo ate ŋu ahe nɔnɔme sia vɛ. Esiawo nye nusiwo gblẽa nu le vidadaa ŋu zi geɖe le fufɔɣi:
- Dada ƒe ƒe si mede ƒe 19 o.
- Fufɔfɔ zi gbãtɔ.
- Ame aɖe le ƒomea me (ƒome si wodzi) la xɔ nɔnɔme sia kpɔ.
Ne èle ƒome gɔme dzem alo nèle mɔ kpɔm na vi bubu la, ele vevie ŋutɔ be nàyi atikewɔƒe siwo kpɔa vidzidzi do ŋgɔ na vidzidzi edziedzi. Esia akpe ɖe ŋuwò be mia kple viwò si le dɔ me na mi siaa mianɔ lãmesẽ me.
Nukawoe nye nɔnɔme sia ƒe kuxiwo?
Kuxi siwo dona tso ŋku ƒe lãmekawo ƒe dɔmawɔmawɔ nyuie me la toa vovo le ahɔhɔ̃a ƒe akpa si ŋu wògblẽ nu le nu. Kuxi aɖewo ate ŋu anye:
- Ŋutete manɔanyi be wòaɖu ŋutilã ƒe dzoxɔxɔ dzi.
- Dɔwuame kple tsikɔwuame si gbɔ eme (`(Hyperphagia)`) eye le esia ta lolo akpa (`(Obesity)`).
- Nuɖuɖu ƒe dzodzro ƒe bu alo gbegbe be yemaɖu nu (`(Hypophagia)`).
- Alɔ̃dɔdɔ kple nyɔnyrɔ̃ ƒe tsatsam ƒe masɔmasɔ.
- Tsitsi ƒe megbetsitsi: Esia fia be lãmekawo ƒe dɔwɔwɔ ƒe ŋutete (abe azɔlizɔzɔ kple ʋuʋudedi ene) kple kadodomɔnu (abe kadodomɔnu ene) ƒe megbetsitsi.
- Autism Spectrum Disorder (ASD) ƒe dɔléle si nye Autism ƒe Dɔléle.
Kuxi siawo dometɔ aɖewo, vevietɔ kuxi siwo le ŋutilã ƒe dzoxɔxɔ dzi kpɔkpɔ kple nuɖuɖu nana me, ate ŋu ade ame ƒe agbe afɔku me le go aɖewo me, eyata ele be woakpɔ nyuie ŋutɔ.
Aleke wowɔna dea dzesi Optic Nerve Hypoplasia?
Zi geɖe la, ŋkudɔdalae dea dzesi nɔnɔme sia le ŋkudodokpɔ kple dodokpɔ bubuwo megbe. Zi geɖe la, esia ƒe dzesi gbãtɔe nye ŋku ƒe ʋuʋu si mesɔ o. Woate ŋu akpɔ dzesi sia le vidzĩ ƒe dzidzi ƒe ɣleti ʋɛ gbãtɔwo me. Gake ɣeaɖewoɣi la, ate ŋu adzɔ be madze ƒã o vaseɖe esime ɖevia ɖo suku alo ɖevi.
ONH ate ŋu adzɔ ɖeɖeko, si fia be mekpɔa ŋusẽ ɖe ahɔhɔ̃a ƒe akpa bubuwo dzi o. Alo, tsɔ kpe ɖe ŋku ƒe lãmeka ŋu la, woate ŋu akpɔe be tsitsimekuxi ɖeka alo esi wu nenema le ahɔhɔ̃a ƒe titina kple lãkusi si me ʋu sina tona me.
Be ɖɔktaa naɖo kpe dɔlélea dzi la, ate ŋu abia be woado nɔnɔmetatawo kpɔ, abe MRI (Magnetic Resonance Imaging) scan alo CT scan (Computed Tomography scan) ene. Scan siawo kpena ɖe ɖɔktaa ŋu wòkpɔa alesi viwò ƒe ahɔhɔ̃ le tsitsime nyuie wu.
Tsɔ kpe ɖe eŋu la, woate ŋu awɔ ʋudodokpɔ geɖe. Wowɔa esiawo be woatsɔ aɖe nɔnɔme bubu siwo me dzesi mawo tɔgbe le la ɖa. Le kpɔɖeŋu me, woate ŋu alé ŋku ɖe serum cortisol kple tsitsimeŋusẽ ƒe agbɔsɔsɔ ŋu. Esiawo ate ŋu anye esiwo mesɔ o le ONH me.
Ðe woate ŋu ada Optic Nerve Hypoplasiaa?
Nublanuitɔe la, fifia la, womekpɔ atike aɖeke na dɔléle sia o. Esi wònye dɔléle si wodzina ta la, womate ŋu atrɔe alo agbugbɔe aɖo eteƒe o.
Eyata aleke nèwɔa nu ɖe esia ŋui?
Dɔdamɔnua ƒe taɖodzinue nye be woaɖu ɖevia ƒe dzesiwo dzi eye woana gbɔdzɔe wo. Esia ate ŋu ato vovo tso ame ɖeka gbɔ yi bubu gbɔ. Dɔdamɔnu vevitɔwoe nye:
- Nukpɔkpɔ ƒe Dɔdamɔnu:Mɔ̃ siwo kpena ɖe nukpɔkpɔ ƒe kuxiwo ŋu, abe ŋkumeɖobolo tɔxɛwo kple ŋkumeɖonu siwo lolona (`nu siwo mekpɔa nu nyuie o`) zazã atsɔ akpe ɖe ɖevia ŋu wòawɔ gbesiagbedɔwo.
- Lãmetsiŋusẽ ɖɔliɖɔli ƒe Atikewɔwɔ: Ne lãmetsiŋusẽ ƒe gbɔdzɔgbɔdzɔ le ame ŋu le kuxi siwo le lãkusi si me ʋu sina tona ŋu ta la, wonaa lãmetsiŋusẽwo le gota. Atike tɔxɛwo li na esia.
- Lãmesẽfefewɔwɔ, Dɔwɔƒe ƒe Dɔdamɔnu, kple/alo Nuƒoƒo ƒe Dɔdamɔnu: Atikewɔmɔnu siawo kpena ɖe ɖevi ƒe ŋutilã ƒe tsitsi, ŋutete be wòawɔ gbesiagbedɔwo le eɖokui si, kple nuƒoƒo ƒe ŋutete ŋu.
Ðɔktaa akpɔ atikewɔwɔ ƒomevi si nyo na viwòa eye wòawɔ atikewɔwɔ ƒe ɖoɖo si sɔ ɖe enu. Le viwòa ƒe dzesi bubuwo nu la, ate ŋu ahiã be woawɔ atike tɔxɛ bubuwo.
Ne ehiã be nàna atike viwòa la, bia wò ɖɔkta nyuie tso ɣeyiɣi si nàna atikeawo, agbɔsɔsɔme si nànae, alesi nànae, kple eƒe nugbegblẽ le ame ŋu siwo ŋu wòle be nànya.
Aleke ɖevia ƒe etsɔme anɔ le nɔnɔme sia me?
Nusiwo Optic Nerve Hypoplasia gblẽna le ame ŋu la toa vovo ŋutɔ tso ame ɖeka gbɔ yi bubu gbɔ. Woate ŋu akpɔ dzesi aɖewo le vidzĩme, gake bubuwo ate ŋu adze le ɖevime alo ƒewuiwo me. Nya nyuiae nye be nɔnɔme sia mewɔa ŋgɔyiyi o. Esia fia be nɔnɔmea megagblẽna ɖe edzi le ɣeyiɣi aɖe megbe o . Dzesi aɖewo, abe nystagmus ene, ate ŋu anyo ɖe edzi gɔ̃ hã ne ame tsi.
Ðevi siwo ŋu ONH le hiã be dzilawo, dɔnɔdzikpɔlawo, kple ɖɔktawo nalé ŋku ɖe wo ŋu ahalé be na wo ɣeyiɣi didi. Ele be woalé ŋku ɖe wo ŋu edziedzi be woakpɔ egbɔ be woƒe lãmesẽ nyo. Ele be woado ŋku kpɔ zi ɖeka ya teti le ƒea me eye woakpɔ eŋutinunyala bibi bubuwo ne ehiã.
Togbɔ be kuxi sesẽ siwo le ʋuka me ate ŋu ade ame ƒe agbe afɔku me hã la, nu nyuitɔ kekeake ate ŋu ado tso eme ne wokpɔ dɔlélea dze sii hedae kaba.
Ðe woate ŋu axe mɔ ɖe Optic Nerve Hypoplasia nua?
Fifia la, womenya mɔ aɖeke si dzi woato axe mɔ ɖe nɔnɔme sia nu o. Ne èle ɖoɖo wɔm be yeafɔ fu la, anyo be nàyi domenyiŋusẽfianu ŋuti aɖaŋuɖola alo dɔnɔdzikpɔla do ŋgɔ na vidzidzi gbɔ be nàsrɔ̃ nu geɖe tso afɔku siwo ate ŋu ado tso ŋuwò kple alesi nàwɔ anɔ lãmesẽ me ŋu.
Ɣekaɣie wòle be makpɔ ɖɔkta?
Ne viwòa ƒe ŋkuwo mele ŋku lém ɖe ŋuwò nyuie o, womeɖo wo ɖe ɖoɖo nu o, alo le ʋuʋum le mɔ si mebɔ o nu la, yi ɖɔkta gbɔ enumake. Azɔ hã, gblɔe na wò ɖɔkta ne viwòa mele tsitsime ƒe nu veviwo gbɔ ɖom (le kpɔɖeŋu me, ele tsatsam, le tsatsam, alo asiɖoɖo nusiwo sɔ gbɔ) siwo sɔ ɖe woƒe ƒexɔxɔ nu o.
Ne alɔ̃madɔmadɔ aɖe le viwòa ŋu la, ƒo ka na 911 enumake alo nàkplɔ wo ayi kɔdzi ƒe xɔ si me wowɔa dɔ kpata le si te ɖe ŋuwò.
Nya kawoe wòle be mabia ɖɔktaa?
Àte ŋu abia wò ɖɔkta nya siawo abe esiawo ene:
- Aleke mate ŋu akpe ɖe vinyea ŋu wòaɖu eƒe dzesiwo dzi?
- Nukae wòle be mawɔ ne mede dzesii be vinyea ƒe tsitsime ƒe nu vevi aɖewo to vovo?
- Ðe vinyea hiã ŋkumeɖobolo alo nu bubu siwo akpe ɖe eŋu wòakpɔ nua?
- Aleke nɔnɔme `(ONH)` akpɔ ŋusẽ ɖe vinye dzi ne edze suku gɔme?
- Zi nenie wòle be woado vinye ƒe ŋku kpɔ?
Mlɔeba la, nu siwo dzi wòle be woaɖo ŋkui
Abe dzila ene la, esɔ be nàse le ɖokuiwò me be yeƒe mo wɔ yaa eye vɔvɔ̃ ɖo ye ne viwò ƒe ŋkuwo le tsaglãla tsam eye womele ŋku lém ɖe ŋuwò nyuie o. Nɔnɔme aɖe si woyɔna be Optic Nerve Hypoplasia ate ŋu akpɔ ŋusẽ ɖe viwò ƒe ŋutete be wòakpɔ wò nyuie dzi. Ate ŋu akpɔ ŋusẽ ɖe ahɔhɔ̃a ƒe akpa bubu siwo kpena ɖe ame ŋu le dɔ veviwo abe lãmetsiŋusẽ ƒe dɔwɔwɔ kple ŋutilã ƒe tsitsi ene hã dzi.
Gake ɖo ŋku edzi be menye wò ɖeka koe o. Ðɔkta ate ŋu ado viwòa kpɔ, akpɔ dɔlélea, eye wòana atikewɔwɔ ƒe ɖoɖo si sɔ ɖe woƒe dzesi tɔxɛwo nu.
Enye nusi sɔ be ɖeviwo nahiã kpekpeɖeŋu vi aɖe le suku wu ɖevi bubuwo, vevietɔ ne wole ɣeyiɣi didi vie xɔm hafi wole tsitsim wu ame bubuwo. Ne ède dzesi dzesi aɖe si ɖea fu na viwò si le ŋusẽ kpɔm ɖe viwòa ƒe tsitsi alo eƒe tsitsi dzi la, mègahe ɖe megbe le egblɔ na wò ɖɔkta o. Viwò ƒe atikewɔlawo ƒe ƒuƒoƒo le klalo ɣesiaɣi be yewoaɖo nyabiase ɖesiaɖe si anɔ asiwò ŋu. Ne dzi le ƒowò la, àte ŋu ana beléle nyuitɔ kekeake si hiã viwòa.
👩🏽 ⚕️ Nyabiase bubuwo (FAQs)
💬 Ðe Optic Nerve Hypoplasia (ONH) nye ahɔhɔ̃medɔ si nana ame ƒe ŋku gbãa?
Esia nye nɔnɔme si me ŋku ƒe lãmeka si tsɔa nɔnɔmetatawo tso ŋkua gbɔ yia ahɔhɔ̃a me la metsina/gbɔdzɔna keŋkeŋ le vidzidzi me (esi wògakpɔtɔ le vidzidɔa me) o! Esia wɔnɛ be ɖevia megakpɔa nu nyuie o, eye ate ŋu agbã ŋku keŋkeŋ gɔ̃ hã. Esia nye domenyiŋusẽfianu ƒe kuxi si le ɖeviwo ŋu tso wo dziɣi ke.
💬 Eyata ɖe Septo-Optic Dysplasia (SOD) hã nye nu ɖeka?
SOD (De Morsier ƒe dɔléle) nye dɔléle si me afɔku le wu eye mebɔ o wu ONH. Le go sia me la, menye ɖeko ŋku ƒe lãmeka (ONH) ƒe tsitsi nyuie o, ke tsɔ kpe ɖe eŋu la, septum pellucidum ƒe wɔwɔme si mede blibo o le ahɔhɔ̃a titina, kple pituitary gland ƒe dɔmawɔmawɔ nyuie keŋkeŋ. Esia wɔnɛ be ɖevia megakpɔa nu nyuie o eye lãmetsiŋusẽ ƒe kuxi geɖe siwo ate ŋu ana wòatsi nyuie o la ɖea fu nɛ.
💬 Ðe woate ŋu ada gbe le ɖevi siawo ŋu to ŋkumeɖobolo dodo alo laser dɔwɔwɔ mea?
Esia nye ŋku ƒe lãmeka ƒe ‘tsitsi ƒe gbɔdzɔgbɔdzɔ’, eyata mɔ aɖeke meli si dzi woato agbugbɔ ŋkumekpɔkpɔ sia aɖo ŋkume to ŋkumeɖobolo dodo, laser zazã, alo amekoko aɖeke wɔwɔ le xexeame me o! (Enye nusi womate ŋu ada o). Gake atikewɔwɔ vevitɔ kekeakee nye be woana gotagome ‘lãmetsiŋusẽtike’ (Thyroid, Growth hormones) ɖevi siwo ƒe lãkusi (Pituitary) mewɔa dɔ o le SOD dɔléle ta, eye woana ɖevi ma natsi abe ɖevi si sɔ ene.
` ŋku ƒe lãmeka ƒe ʋuʋu, septo-optic dysplasia, ŋkuʋuʋu si wodzina, ŋku ƒe dɔmawɔmawɔ nyuie, pituitary gland, ɖeviwo ƒe tsitsi, nystagmus











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