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Da farko, bari mu gani, me yasa zubar jini baya tsayawa a cikin jinin haila?
A taƙaice, akwai sunadarai na musamman waɗanda ke taimaka wa jini ya yi gudawa. Muna kiran waɗannan " masu samar da jini ." Kamar yadda ake buƙatar turmi don haɗa tubali yayin gina bango, waɗannan ma'adanai suna da mahimmanci don dakatar da zubar jini. Mutumin da ke fama da cutar hemophilia yana da ƙarancin ɗaya daga cikin waɗannan ma'adanai masu samar da jini.- Mutane masu fama da cutar hemophilia A ba su da wani sinadari mai suna Factor VIII.
- Mutane masu fama da cutar hemophilia B ba su da wani sinadari mai suna Factor IX.
To menene wannan sabon maganin da ake kira Qfitlia (fitusiran)?
Wannan magani ne da ke aiki ta wata hanya mai ban mamaki. Mun yi magana a baya game da gaskiyar cewa jini yana buƙatar wani abu da ake kira thrombin don ya yi gudawa. A cikin jikinmu, akwai wani furotin da ke sarrafa samar da wannan thrombin, wato, yana dakatar da samar da ƙarin thrombin. Ana kiransa antithrombin .Ka yi tunanin haka. Kana da sinadarin hada jini (thrombin) a jikinka wanda ke taimakawa wajen zubar jini. Amma akwai wani abu (antithrombin) wanda ke sarrafa shi kuma yana hana shi aiki. A cikin hemophilia, samar da sinadarin da ke taimakawa (thrombin) da farko yana da ƙasa. Don haka lokacin da sinadarin da ke hana (antithrombin) ya yi aiki yadda ya kamata, toshewar jini yana raguwa sosai. Abin da Qfitlia ke yi shi ne rage adadin antithrombin da ke hana shi. Sannan, adadin thrombin da jikinka ke samarwa a zahiri yana barin shi ya yi aiki yadda ya kamata ba tare da an hana shi ba. Wannan yana nufin yana amfani da tsarin jiki don ƙarfafa zubar jini, maimakon ba ka sinadarin hada jini da ka rasa. Wannan shine maganin farko da ke rage thrombin da za a yi amfani da shi wajen magance hemophilia.Bari mu ƙara bayani game da bambancin da ke tsakanin waɗannan hanyoyin magani guda biyu.
Za ka iya fahimtar wannan bambanci cikin sauƙi daga teburin da ke ƙasa.| Halaye | Maganin Gargajiya (Sauya Ma'auni) | Maganin fitusiran (Qfitlia) |
|---|---|---|
| Aiki | Ana bayar da sinadarin clotting factor da ya rasa a jiki a waje. | Yana rage antithrombin, wanda ke hana zubar jini, kuma yana bawa jiki damar amfani da ƙarin sinadarin thrombin nasa. |
| Yadda ake bayarwa | Sau da yawa ta hanyar jijiya. | A ƙarƙashin fata (ƙasa da fata). |
| Mita | Yana iya zama dole sau da yawa a mako. | Sau ɗaya a wata ko kuma bayan kowane wata biyu (sau 6-12 a shekara). |
| Ga waɗanda ke da masu hana | Maganin al'ada na al'ada ba ya aiki, kuma ana buƙatar wasu magunguna na musamman (maganin da ke wucewa). | Ana iya amfani da wannan maganin cikin nasara ga mutanen da ke da maganin hana ƙwayoyin cuta (antibodies a kan abubuwan). |
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Check Availability →Shin wannan maganin ya dace da ni kuma ta yaya zan yi amfani da shi?
Idan kana da hemophilia A ko B kuma kana da shekaru sama da 12, likitanka zai iya la'akari da ko wannan maganin ya dace da kai. Abu mafi mahimmanci shine ana iya amfani da shi ga mutanen da suka sami magungunan hana haihuwa (juriya) ga maganin da ya gabata. Duk da haka, kafin fara wannan maganin, likitanka zai yi gwaje-gwajen jini da yawa. 1. Matsayin antithrombin: Wannan yana auna adadin antithrombin da ke cikin jininka. Ana ƙayyade adadin Qfitlia bisa ga wannan ƙimar. 2. Aikin hanta: Ana sa ido kan hanta kafin da kuma lokacin magani. Ana ba da wannan maganin a matsayin allura a ƙarƙashin fata (a ƙarƙashin fata). Wannan yana nufin cewa ba a ba shi cikin jijiya ba. Kai ko mai kula da kai za ka iya ba ka a gida bayan horo. Ana ba da shi a fatar ciki, cinya, ko bayan hannun sama. Ya kamata ka guji wuraren da ke da raunuka ko yankewa. Idan kana shan wasu magungunan hemophilia, ƙila ka buƙaci dakatar ko canza waɗannan jiyya bayan fara Qfitlia. Likitanka zai yi maka bayani a sarari. Kada ka daina shan magungunan da kake amfani da su a yanzu ko kuma ka daina shan Qfitlia ba tare da shawarar likita ba. Yin hakan na iya ƙara haɗarin zubar jini.Ya kamata mu kuma san illolin da ke tattare da hakan? Ta yaya za mu iya hana su?
Kamar kowace magani, Qfitlia na iya samun wasu illoli. Yana da muhimmanci a san su kuma a ɗauki matakai don hana su.- Kumburin Jini : Saboda wannan maganin yana ƙarfafa zubar jini, yana da matuƙar wuya a sami kumburin jini da ba a so a cikin jijiyoyin. Likitanka zai ƙayyade adadin da ya dace don matakin antithrombin ɗinka don rage wannan haɗarin.
- Karin enzymes na hanta: Wasu mutane na iya samun karin enzymes na hanta. Shi ya sa likitoci ke yawan lura da yanayin hanta ta hanyar gwajin jini .
- Duwatsun Gallstone da Kumburin Gallbladder: Idan kwatsam ka fuskanci alamun kamar ciwon ciki mai tsanani, tashin zuciya, da amai , sanar da likitanka nan da nan.
- Kamuwa da cuta: Akwai ƙaramin haɗarin kamuwa da cuta a wurin allurar. Saboda haka, yana da mahimmanci a koyaushe a yi allurar tsafta kuma kamar yadda likitanka ya umarta. Kyakkyawan ayyukan tsafta, kamar wanke hannu akai-akai, suma suna da mahimmanci.
Saƙon Ɗauka Gida
- Qfitlia (fitusiran) sabuwar hanyar magance hemophilia A da B ce wadda ke aiki ta wata hanya daban.
- Wannan yana aiki ta hanyar rage adadin antithrombin, wanda ke hana zubar jini, maimakon ba wa jiki ƙarancin zubar jini a waje.
- Wannan maganin allura ce a ƙarƙashin fata, ba a cikin jijiya ba, kuma yawanci ana ba da shi ba kasafai ba, kamar sau ɗaya a wata ko bayan wata biyu.
- Likitan ku zai tantance ko wannan maganin ya dace da ku bayan gwaje-gwajen jini da yawa.
- Domin gujewa illa, yana da mahimmanci a yi gwajin jini (musamman aikin antithrombin da hanta) akai-akai kamar yadda likitanka ya umarta.
- A guji dakatar da maganin Qfitlia ba tare da shawarar likita ba saboda kowane dalili.
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