Loaʻa iā ʻoe kēia mau hōʻailona ʻē? E aʻo kākou e pili ana i ka maʻi ʻo Behçet ma nā ʻōlelo maʻalahi!

Ua lohe paha ʻoe i ka maʻi ʻo Behçet? He mea ʻē paha ke kani ʻana o ka inoa. Akā, he ʻano paʻakikī maoli nō ia, akā hiki ke hoʻokele ʻia e hiki ke hoʻopilikia i nā ʻāpana like ʻole o ko kākou kino. No laila, e kamaʻilio kākou e pili ana i ia mea i kēia lā, me ka maʻalahi loa, e like me ke kamaʻilio ʻana me kahi hoaaloha.

He aha ka maʻi o Behçet?

I ka ʻōlelo maʻalahi, ʻo ka maʻi ʻo Behçet kahi mumū mau o nā kīʻaha koko i loko o ko kākou kino. Ua kapa pū nā kauka iā ia he "vasculitis." He ʻano kēia e pehu ai nā kīʻaha koko, ʻulaʻula, a ʻeha. Hiki iā ia ke hoʻopilikia i nā kīʻaha koko nui (nā artery) a me nā kīʻaha koko liʻiliʻi (nā veins). I kekahi manawa ua kapa ʻia kēia maʻi ʻo "Silk Road disease" no ka mea he mea maʻamau ia ma nā wahi ma ke Alanui Silk i ka mōʻaukala.

ʻO wai ka mea i ʻoi aku ka paʻakikī o ka loaʻa ʻana o kēia maʻi?

Hiki i ka maʻi ʻo Behçet ke hoʻopilikia i kekahi ma ka honua. Eia nō naʻe, ʻoi aku ka maʻamau ma kekahi mau ʻāina. No ka laʻana, ʻoi aku ka maʻamau ma ka ʻākau o Turkey, nā ʻāina a puni ke Kai Mediterranean, ka Hikina Waena a me ʻAsia Hikina. ʻAʻole ia he mea maʻamau ma nā ʻāina e like me ʻAmelika Hui Pū ʻIa. Hoʻomaka pinepine nā hōʻailona e ʻike ʻia ma waena o 20 a me 30 mau makahiki. Eia nō naʻe, hiki ke loaʻa i kēlā me kēia makahiki. ʻOiai ua manaʻo mua ʻia e hoʻopilikia like i nā kāne a me nā wahine, ua hōʻike kekahi mau noiʻi he ʻoi aku ka nui o ka loaʻa ʻana o kēia maʻi i nā kāne .

He aha nā hōʻailona o kēia maʻi? Pehea ko mākou manaʻo?

ʻO kēia ka mea nui loa. Hiki ke ʻokoʻa nā hōʻailona o ka maʻi Behçet mai kēlā kanaka a kēia kanaka. ʻO ke ʻano kēia, ʻaʻole like paha nā hōʻailona āu e loaʻa ai me ko kekahi kanaka ʻē aʻe. Akā aia kekahi mau hōʻailona koʻikoʻi i maʻamau.

ʻEha waha

ʻO kēia ka hōʻailona mua a ka poʻe he nui e ʻike ai . Ua like ia me nā ʻeha ʻōpū a mākou e loaʻa mau ai i loko o ko mākou waha, akā ʻoi aku ka nui, ʻoi aku ka pinepine, a ʻoi aku ka ʻeha . Hiki i kekahi poʻe ke loaʻa i kēia mau ʻeha waha ma mua o ka ʻike ʻia ʻana o nā hōʻailona ʻē aʻe. Hiki iā lākou ke ʻike ʻia ma nā lehelehe, ke alelo, a ma loko o nā papālina.

E noʻonoʻo, loaʻa mau iā ʻoe nā ʻeha waha, ʻeha loa lākou ʻaʻole hiki iā ʻoe ke ʻai a inu paha, a ma hope o ka lawe ʻana i ka lāʻau lapaʻau, hoʻi hou mai lākou i kekahi mau lā ma hope. He kūlana ia e like me ia.

Nā ʻeha o ka ʻōpū

E like me nā ʻeha waha, hiki ke loaʻa nā ʻeha ʻōpū. Hiki i kēia ke ʻeha. Hiki iā lākou ke loaʻa ma ka scrotum i nā kāne a me ka vulva i nā wahine. Eia naʻe, ʻaʻole lākou i maʻamau e like me nā ʻeha waha.

ʻO ka mumū o ka maka

ʻO ka mumū o nā maka kekahi hōʻailona koʻikoʻi o kēia maʻi. Hiki i kēia ke hana i ka ʻulaʻula, ka ʻeha, ka ʻike maka pohihihi, ka ʻike ʻana i ka mālamalama, a me nā maka waimaka . Inā ʻaʻole mālama pono ʻia, hiki iā ia ke alakaʻi i ka nalowale loa o ka ʻike.Aia kahi manawa kūpono. Aia nā hōʻike e hōʻike ana he mea maʻamau kēia ʻano hōʻino maka ma nā ʻāina e like me ka Hikina Waena a me Iapana.

Nā pilikia ʻili

He mea maʻamau nō hoʻi nā pilikia ʻili. I kekahi manawa, hiki ke ʻike ʻia nā pehu e like me ka pimple a me nā nodules ʻulaʻula (erythema nodosum). He ʻeha kēia mau puʻupuʻu ke hoʻopā aku. I kekahi manawa, hiki ke ulu aʻe nā ʻeha ʻili. He ʻili wale kekahi o kēia mau mea, aʻo kekahi he hohonu. ʻO kekahi hiʻohiʻona ʻē aʻe, inā ua ʻōpala ʻia a hou ʻia paha ka ʻili, e ʻulaʻula ka wahi a e ʻike ʻia kahi pehu liʻiliʻi i loko o kekahi mau lā . Ua kapa nā kauka i kēia he "hoʻāʻo pathergy maikaʻi."

ʻEha hui

He mea maʻamau nō hoʻi ka ʻeha o nā hono i waena o kēia mau maʻi. Hoʻopilikia ia i nā kuʻekuʻe wāwae, nā kuli, nā kuʻekuʻe lima, a me nā pūhaka . Hiki i nā hono ke pehu, ʻulaʻula, a ʻeha ke pā. Eia nō naʻe, ʻaʻole ia e hōʻeha mau loa i nā hono.

Ka mumū o nā aa

Hiki i ka mumū i loko o nā kīʻaha koko ke hana i nā ʻūpā koko, nā ālai ʻana , a i ʻole ka ālai piha ʻana o nā kīʻaha koko. Hiki i kēia ke hoʻopilikia i nā aa koko ma luna, kokoke i ka ʻili, a me nā aa koko hohonu, aia ma loko o ke kino. I kekahi manawa, hiki ke hoʻopilikia ʻia ka aa koko nui loa i loko o ko mākou kino, ʻo ia ka vena cava, hiki ke alakaʻi i nā pilikia olakino koʻikoʻi. Hoʻokumu ʻia kēia mau pilikia kīʻaha koko e ka mumū, ʻaʻole e kahi kīnā i loko o ka ʻōnaehana hoʻopaʻa koko.

Ke komo ʻana o ka lolo

I kekahi manawa hiki i kēia maʻi ke hoʻopilikia i ka lolo. ʻO ke kikoʻī, nā membrane e uhi ana i ka lolo (meninges). A laila ʻike ʻia nā hōʻailona e like me ke kuni, ka ʻeha poʻo nui, ka ʻoʻoleʻa o ka ʻāʻī, ka paʻakikī o ka hoʻonohonoho ʻana i ka neʻe ʻana i ka wā e hele ai . I kekahi manawa , hiki ke loaʻa kahi hahau . ʻO kēia ka wā e ālai ʻia ai a pohā paha kekahi kīʻaha koko i loko o ka lolo.

Nā hiʻohiʻona o ke ala Gastrointestinal (GI)

Hiki nō hoʻi ke loaʻa nā pilikia i loko o ka ʻōnaehana hoʻoheheʻe ʻana, ʻo ia hoʻi, i loko o nā ʻōpū. Hiki paha iā ʻoe ke ʻike i nā mea e like me ka ʻōpū ʻeha a me ke koko i loko o ka ʻōpala . ʻO kēia no ka mea he mau ʻeha ma ka waha a me ka ʻāpana genital, a me nā ʻeha i loko o nā ʻōpū. He mea weliweli iki kēia mau ʻeha i loko o nā ʻōpū, no ka mea hiki iā lākou ke hoʻoulu i ke kahe koko mai nā ʻōpū a i ʻole ka haki ʻana.

Nā hopena ma nā ʻōpū ʻē aʻe

ʻOiai he mea kakaikahi loa, hiki i ka maʻi ke hoʻopilikia i nā ʻōpū ʻē aʻe, e like me nā māmā, nā puʻupaʻa, a me nā kīʻaha koko nui (aorta).

No ke aha i loaʻa ai ka maʻi ʻo Behçet? He aha ke kumu?

ʻAʻole ʻike ʻia ke kumu kikoʻī o kēia maʻi . Ke noiʻi nei nā kānaka ʻepekema iā ia. ʻO kekahi manaʻo, he "maʻi autoimmune" paha ia. I ka ʻōlelo maʻalahi, ʻo ia hoʻi, ʻo kā mākou ʻōnaehana pale ponoʻī, ka ʻōnaehana e pale aku iā mākou mai ka maʻi, e hoʻouka hewa ana i kā mākou mau hunaola olakino ponoʻī.. ʻO kēia hoʻouka kaua ke kumu o nā kūlana mumū i ʻōlelo ʻia ma luna. ʻIke ʻia kekahi mau māka gene, e like me `(HLA-B5)` a me `(HLA-B51), i kekahi poʻe me kēia maʻi. Eia naʻe, ʻaʻole nā ​​​​mea āpau me kēia mau māka gene e hoʻomohala i ka maʻi ʻo Behçet. No laila, ʻaʻole hiki ke ʻōlelo ʻia ʻo nā genes wale nō ke kumu. Manaʻo pū nā kānaka noiʻi i loko o ka poʻe i loaʻa i kēia maʻi, aia kahi manaʻo e hiki mai kēia maʻi ma muli o kahi maʻi (bacteria a viral paha) . ʻO ke ʻano kēia e hiki i nā mea genetic a me ke kaiapuni ke hoʻopilikia iā ia.

ʻO wai ka mea i ʻoi aku ka pilikia o ka loaʻa ʻana o kēia maʻi?

ʻOi aku ka pilikia o kekahi poʻe i ka loaʻa ʻana o kēia maʻi ma mua o nā poʻe ʻē aʻe:

• ʻO ka poʻe e noho ana ma nā wahi i loaʻa pinepine ai kēia maʻi (e like me Turkey, Middle East).
• ʻO nā kānaka ma waena o 20 a me 40 mau makahiki .
• ʻO nā kānaka me kekahi mau genes kikoʻī (HLA-B5 a i ʻole HLA-B51)
• ʻO nā kāne (ʻoi aku ka nui o ka pilikia o nā kāne i ka loaʻa ʻana o kēia maʻi ma mua o nā wahine).

Pehea e ʻike pololei ʻia ai kēia maʻi? (Diagnosis)

ʻAʻohe hoʻokolohua hoʻokolohua hoʻokahi e ʻike ai i ka maʻi ʻo Behçet. Hoʻomaopopo nā kauka i ka maʻi ma muli o kāu mau hōʻailona. Ke ʻimi nui nei lākou i:

• Hoʻi pinepine ʻia (ʻoi aku ma mua o ʻekolu manawa i ka makahiki) o nā ʻeha waha .
• Eia kekahi, pono e loaʻa ma ka liʻiliʻi ʻelua o kēia mau ʻano :
• Nā ʻeha ma ka ʻāpana genital.
• Ka mumū o nā maka.
• Nā pilikia ʻili.
• He hoʻāʻo pathergy maikaʻi - ʻO ke ʻano kēia, e ʻike ʻia kahi ʻulaʻula, e like me ka pehu, i loko o kekahi mau lā ma hope o kahi ʻili i ʻō ʻia a i ʻole ka ʻili i ʻō ʻia. Hāʻawi kēia i kahi manaʻo o ka hana maikaʻi o ka ʻōnaehana pale.

I mea e ʻike pololei ai i kēia maʻi, pono e kāpae i nā maʻi ʻē aʻe e hoʻoulu ai i nā ʻeha waha e like me ka maʻi ʻo Behçet . No ka laʻana, ʻo `(systemic lupus)`, `(Crohn's disease)` (kahi maʻi mumū o nā ʻōpū), a me nā ʻano ʻē aʻe o `(vasculitis)`. Hiki i kāu kauka ke kauoha i nā hoʻāʻo koko e kōkua i ka kāpae ʻana i kēia mau maʻi ʻē aʻe.

He maʻi hoʻoilina anei kēia?

ʻAʻohe hōʻike maopopo e hōʻike ana he maʻi hoʻoilina ka maʻi ʻo Behçet . Loaʻa ka hapa nui o nā hihia ma ke ʻano ulia pōpilikia, me ka ʻole o ka mōʻaukala ʻohana. ʻOiai ua hōʻike ʻia kahi pakeneka liʻiliʻi loa o nā hihia i loko o kekahi mau lālā o ka ʻohana hoʻokahi, ʻaʻohe ʻano hoʻoilina maopopo.

He aha nā lāʻau lapaʻau no kēia? (Lāʻau lapaʻau)

ʻAʻohe lāʻau lapaʻau no kēia maʻi i kēia manawa . Eia nō naʻe, aia kekahi mau lāʻau lapaʻau e hiki ke kōkua i ka mālama ʻana i nā hōʻailona:

• ʻO nā Corticosteroids (e.g., prednisone): ʻO kēia nā lāʻau lapaʻau nui. Hoʻemi kēia mau lāʻau lapaʻau i ka mumū a me ka hana nui o ka ʻōnaehana pale.
• Colchicine (Colcrys®): Kōkua kēia i nā ʻeha waha, nā ʻeha ʻōpū, a i kekahi manawa ʻeha hui.
• ʻO nā lāʻau lapaʻau immunosuppressant ʻē aʻe : ʻO nā laʻana he methotrexate (Trexall®, Rasuvo®), azathioprine (Imuran®, Azasan®), cyclophosphamide (Cytoxan®, Neosar®), a me cyclosporine (Gengraf®, Neoral®, Sandimmune®). I nā hihia koʻikoʻi, hoʻohana pū ʻia nā anti-TNF (Tumor Necrosis Factor) biologics e like me infliximab (Remicade®), etanercept (Enbrel®), a me tocilizumab (Actemra®).

He mea nui: Hiki i kēia mau lāʻau immunosuppressant ke hōʻemi i ka hiki o kou kino ke hakakā i nā maʻi, kahi e hoʻonui ai i kou pilikia o ka hoʻomohala ʻana i nā maʻi ʻē aʻe.

• ʻApemilast (Otezla®) : He papa waha kēia. Ua ʻae ʻia e mālama i nā ʻeha waha i ka poʻe me ka maʻi ʻo Behçet.

Ma muli o ke koʻikoʻi o kou kūlana, hiki i kāu kauka ke hoʻāʻo e kāohi i nā hōʻailona me nā mea e like me nā kulu maka, nā holoi waha, a me nā ʻaila ʻili ma mua o ka hoʻohana ʻana i kēia mau lāʻau.

He aha ke ʻano o ka manaʻolana e hiki iā ʻoe ke loaʻa i kou wā e ola nei me kēia maʻi?

He maʻi mau loa ʻo Behçet. ʻO ia hoʻi, ʻoiai ke mālama ʻia, hiki ke nalo a ʻike hou ʻia i kekahi manawa. He mea paʻakikī kēia ke ʻōlelo pololei i ka holomua o ka mālama ʻana. Pono nā maʻi he nui e kū i kēia mau hōʻailona i kekahi manawa i ko lākou ola. Eia nō naʻe, hiki i ka hapa nui o ka poʻe ke ola maʻamau a piha .

Pehea e hoʻokō pono ai i kēia maʻi?

Aia kekahi mau ala e kōkua ai i ka wā e noho ai me kēia maʻi:

• Kaulike ma waena o ka hoʻomaha a me ka hana : ʻO kahi papa hana hoʻoikaika kino mau e hoʻomaha ai i kou kino, e hōʻemi i ka ʻeha o nā hono a me nā wahi pilikia ʻē aʻe. Eia kekahi, ʻo ka hoʻomaha ʻana i ka wā e koʻikoʻi ai nā hōʻailona he mea maikaʻi ia no kou olakino noʻonoʻo a hiki ke hōʻemi i ka hopena o nā hōʻailona.
• ʻIke like a me ke kaiāulu : ʻO ia hoʻi ka loaʻa ʻana a me ke kamaʻilio ʻana me nā poʻe ʻē aʻe i loaʻa i ke ʻano like. Hiki ke paʻakikī kēia no ka mea he mea kakaikahi ke ʻano. Akā hiki i kāu kauka ke kōkua iā ʻoe e ʻimi i nā poʻe i loaʻa nā ʻike like.

Hiki i kēia maʻi ke make?

ʻO ka nui o ka make mai kēia maʻi ma kahi o 5%.ʻO nā kumu nui o ka make, ʻo ia ka perforation o ka ʻōpū, nā hahau ʻana, a me ka haki ʻana o nā aneurysms. ʻOiai ʻaʻole make pololei ka maʻi ʻo Behçet, hiki iā ia ke hana i nā ʻano pilikia olakino a me nā kūlana olakino ma ke kino holoʻokoʻa, he nui o ia mau mea he ʻeha. Eia nō naʻe, hiki ke hoʻokele pono i ka maʻi a ola i kahi ola maʻamau . ʻOi loa aku inā ʻoe e hoʻoikaika kino mau, hoʻomaha, a kamaʻilio me nā poʻe ʻē aʻe e hele nei i ka mea like.

ʻO ka hope, e hoʻomanaʻo i kēia mau mea!

Hiki i ka maʻi ʻo Behçet ke lilo i maʻi paʻakikī a ʻoluʻolu ʻole hoʻi. Akā e hoʻomanaʻo:

• He maʻi kēia e hiki ke mālama ʻia .
• Inā loaʻa iā ʻoe kēia mau hōʻailona, ​​e ʻimi koke i ke kōkua lapaʻau .
• Hiki iā ʻoe ke hoʻāʻo e ola i kahi ola maʻamau me ka mālama kūpono a me nā hoʻololi ʻana i ke ʻano o ka nohona.
• Mai ʻeha hoʻokahi, e hoʻopili me nā hui kākoʻo a i ʻole nā ​​​​maʻi ʻē aʻe .

Manaʻolana wau he mea pono kēia ʻike iā ʻoe. E ola kino!