He mea kupaianaha ke ʻano o ka ulu ʻana o nā ʻōpū o kahi pēpē i loko o ka ʻōpū o ka makuahine, ʻeā? I loko o kēia kaʻina hana paʻakikī, hiki ke hana ʻia nā loli liʻiliʻi i kekahi manawa. ʻO 'Horseshoe Kidney' kekahi ʻano maʻi kakaikahi e kū mai ana i ka wā hānau. E hopohopo paha ʻoe ke lohe ʻoe i kēia inoa. Akā, mai hopohopo, e kamaʻilio mākou e pili ana i nā mea āpau me ka maʻalahi a me ka maopopo.
I ka ʻōlelo maʻalahi, he aha kēia Lio Holo Lio?
He mea maʻalahi loa kēia. ʻO ka maʻamau, loaʻa iā kākou ʻelua mau puʻupaʻa i loko o ko kākou kino. Aia lākou ma luna pono o ka pūhaka, ma nā ʻaoʻao ʻelua o ke kuamoʻo. Akā i loko o ke kūlana i kapa ʻia ʻo 'Horseshoe Kidney', hui pū nā wēlau haʻahaʻa o kēia mau puʻupaʻa ʻelua i ka wā e ulu ana ke pēpē i loko o ka ʻōpū, e hana ana i ke ʻano 'U', a i ʻole he lio. Ua kapa ʻia kēia ma ke ʻano lapaʻau ʻo Renal Fusion . Hana pinepine kēia ma waena o nā pule 7 a me 9 o ka hāpai ʻana.
ʻAʻole maʻamau loa kēia ʻano. Hoʻopilikia ia ma kahi o 1 i loko o kēlā me kēia 500 pēpē i hānau ʻia. ʻOi aku ka maʻamau o ia i nā keikikāne ma mua o nā kaikamahine. ʻO ka mea maikaʻi loa, ʻo ka hapa nui o nā keiki me kēia ʻano ʻaʻole lākou e loaʻa i nā pilikia olakino koʻikoʻi.
Eia nō naʻe, ma kahi o ka hapakolu o nā keiki me kēia ʻano pili o ka puʻupaʻa e loaʻa paha nā pilikia ʻē aʻe me ka puʻuwai, nā kīʻaha koko, ka ʻōnaehana nerve, ka ʻōnaehana mimi, ka ʻōnaehana hoʻoheheʻe, a i ʻole ka ʻōnaehana iwi. ʻOiai ʻaʻohe lāʻau lapaʻau no ka Horseshoe Kidney, hiki i kāu kauka ke mālama i nā pilikia ʻē aʻe e pili ana a kōkua i kāu keiki e ola i ke ola olakino.
He aha nā hōʻailona o kēia maʻi?
ʻO ka mea kupanaha, ʻaʻole i loaʻa i kahi hapakolu o nā keiki kekahi mau hōʻailona. Eia nō naʻe, hiki i kekahi mau keiki ke loaʻa i kekahi mau pilikia. Ua papa inoa ka papa ma lalo nei i kekahi o nā pilikia maʻamau a me kā lākou mau hōʻailona.
| Pilikia paha | Nā hōʻailona i ʻike pinepine ʻia |
|---|---|
| ʻO ka maʻi ʻaʻai mimi (UTI) |
|
| Nā Pōhaku Puʻupaʻa | |
| Pehu ʻana o nā puʻupaʻa (Hydronephrosis) (Ka piha ʻana o ka mimi a me ka pehu ʻana o nā puʻupaʻa ma muli o ke ālai ʻia ʻana o ke kahe ʻana o ka mimi) |
Nā pilikia olakino ʻē aʻe e hiki ke hana me ka Horseshoe Kidney
Ma waho aʻe o nā mea i ʻōlelo ʻia ma luna nei, aia kekahi mau pilikia olakino ʻē aʻe.
- ʻO ka puʻupuʻu Wilms: He puʻupuʻu maʻi kanesa e hiki ke hana i nā puʻupaʻa o nā keiki ʻōpio.
- ʻO ka maʻi puʻupaʻa polycystic: Ke hoʻokumu ʻia ʻana o nā cysts he nui ʻaʻole cancerous i loko o nā puʻupaʻa.
- Ka maʻi ʻaʻai puʻupaʻa: Aia kahi pilikia o kēia i ka wā makua.
- Hydrocephalus: Hōʻiliʻili ʻana o ka wai i loko o ka lolo.
- Spina bifida: ʻO ia ke ʻano i ulu pono ʻole ai kekahi ʻāpana o ka iwi kuamoʻo.
Mai hopohopo i kēia papa inoa. ʻAʻole kēia manaʻo e loaʻa i nā kānaka a pau kēia mau mea a pau. ʻO ia hoʻi, aia kahi manawa e loaʻa ai iā lākou. No laila he mea nui e noho ma lalo o ka nānā ʻana a ke kauka.
No ke aha lā kēia e hana nei? He aha ke kumu?
ʻAʻole ʻike ʻia ke kumu kikoʻī o kēia, akā manaʻoʻiʻo nā loea lapaʻau he pilikia paha ia i loko o nā genes o ke keiki.
ʻO nā keiki me nā kūlana hoʻoilina ma lalo nei e pilikia nui ana i ka loaʻa ʻana o ka Horseshoe Kidney.
- ʻO ka maʻi Turner: Hoʻopilikia wale kēia maʻi i nā kaikamahine a hoʻoulu i ke kino pōkole a me nā pilikia me nā ovaries.
- ʻO ka maʻi Edwards: ʻIke ʻia hoʻi ʻo "Trisomy 18", ʻo kēia maʻi ke kumu o ka ulu ʻole ʻana, ke kaumaha haʻahaʻa i ka wā hānau, a me kekahi mau pilikia olakino koʻikoʻi i loko o ka ʻōpū.
- ʻO Down syndrome: ʻIke ʻia hoʻi ʻo "Trisomy 21", hana ʻia kēia e kahi chromosome keu e hoʻoulu ai i ka lohi o ka noʻonoʻo a me ka ulu ʻana, a me nā pilikia olakino ʻē aʻe.
- ʻO ka maʻi Patau: Ua kapa ʻia kēia ʻo `(Trisomy 13)` a ke kumu o nā pilikia e like me ka lehelehe māwae a me ka palale, a me ka nāwaliwali o nā ʻiʻo.
Pehea e ʻike ai ke kauka i kēia? He aha ka lāʻau lapaʻau?
ʻAʻole ʻike pinepine ʻia kēia ʻano ma o nā scan prenatal. ʻOiai ua like nā hōʻailona o kēia ʻano me nā maʻi ʻē aʻe, he mea nui e ʻike i kāu kauka no ka ʻike pololei.
E nīnau kāu kauka iā ʻoe e pili ana i nā hōʻailona o kāu keiki a me ka mōʻaukala olakino, e nānā i kāu keiki, a laila e hana i kekahi mau hoʻokolohua e hōʻoia i ke kūlana pololei, e like me:
- Nā hoʻāʻo koko: E nānā i ke ʻano o ka hana ʻana o kou mau puʻupaʻa.
- Nā hoʻāʻo mimi: E nānā no nā maʻi a i ʻole nā pilikia ʻē aʻe.
- ʻO ke kani ʻana o nā puʻupaʻa: Hoʻohana i nā nalu kani e kiʻi i ke kiʻi o nā puʻupaʻa e nānā i nā pōhaku, nā ʻōpū, a i ʻole ke kanesa.
- Nā hoʻāʻo X-ray kūikawā: ʻO nā hoʻāʻo e like me `(Intravenous pyelogram - IVP)` a i ʻole `(Voiding cystourethrogram - VCUG)` e nānā pehea e holo ai ka mimi i loko o ke kino.
- Radionuclide scan: Hoʻohana ʻia kahi mahele liʻiliʻi loa o kahi mea radioactive e ʻike ai i nā wahi pilikia.
- MRI a i ʻole CT scan: Hoʻohana ʻia kēia mau mea e kiʻi i nā kiʻi ʻoi aku ka maopopo.
I ka wā e pili ana i ka lāʻau lapaʻau, ʻaʻole hiki ke hoʻololi ʻia ka Horseshoe Kidney. Ke hui pū ʻia nā puʻupaʻa, e mau ana lākou pēlā. Eia nō naʻe, hiki ke mālama pono ʻia nā pilikia e kū mai ana mai ia mea. No ka laʻana, hiki ke hāʻawi ʻia nā antibiotics no ka maʻi urinary tract, a hiki ke hana ʻia ke ʻoki no nā pōhaku puʻupaʻa.
ʻO ka mea nui, inā ʻaʻohe hōʻailona o kāu keiki, ʻaʻole paha lākou e pono i kekahi lāʻau lapaʻau.
Nā mea ʻē aʻe āu e pono ai e ʻike ma ke ʻano he makua
Aia kēia mau puʻupaʻa ma lalo iki a ma mua o ke kino ma mua o ka maʻamau. No laila, ʻoi aku ka nui o ko lākou ʻeha ʻana i kahi ulia a hāʻule paha. No laila, e kamaʻilio me kāu kauka e pili ana i nā haʻuki pili. He mea nui loa e nīnau i kāu keiki i nā hana palekana nona e hana ai.
He manaʻo maikaʻi nō hoʻi e hoʻokomo kāu keiki i kahi kūpeʻe lima makaʻala lapaʻau.I loko o kahi pilikia, e kōkua ia i ka poʻe e mālama ana i ke keiki e ʻike koke i kēia kūlana a hāʻawi i ka lāʻau kūpono.
Leka Lawe-Home
- He maʻi ka puʻupaʻa lio i loaʻa i ka wā hānau. ʻAʻole ia he hewa o nā mākua.
- Nui nā keiki me kēia maʻi e ola maʻamau a olakino me ka ʻole o nā hōʻailona.
- Hiki ke mālama pono ʻia nā pilikia maʻamau e like me nā maʻi ʻaʻai mimi (UTI) a me nā pōhaku puʻupaʻa.
- He mea nui loa ka mālama mau ʻana i ka launa pū ʻana me ke kauka e nānā i ke olakino o ke keiki a e hana i nā hoʻokolohua lapaʻau i ka manawa kūpono.
- E nīnau i kāu kauka i nā haʻuki a me nā hana kūpono no kāu keiki, e noʻonoʻo ana i ka palekana.











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