Ua makaʻu paha ʻoe i ka ʻike ʻana i kāu keiki liʻiliʻi e loaʻa ana nā palapū polū-poni ma ko lākou kino, ʻoi aku hoʻi ko lākou mau wāwae? A i ʻole, ma ke ʻano he kanaka makua, ua ʻike anei ʻoe i nā kiko ʻulaʻula liʻiliʻi ma kou ʻili a ʻike i kou ʻāʻī e kahe ana ke koko i kou palaki ʻana i kou mau niho? He mea maʻamau ka makaʻu ke ʻike ʻoe i nā mea e like me kēia. Akā i ka hapa nui o ka manawa, ʻo ke kumu he ʻano i kapa ʻia ʻo ITP. No laila i kēia lā, e kamaʻilio kākou e pili ana i ke ʻano o ITP, no ke aha e hana ai, he mea weliweli anei ia, a me ka mea e hana ai e pili ana i ia mea, me he mea lā e kamaʻilio ana ʻoe me kahi hoaaloha.
He aha wale nō ka ITP?
ʻOiai paha he lōʻihi iki kēia inoa, he maʻalahi loa kona manaʻo. E wehewehe kākou.
- Idiopathic : ʻO ke ʻano maʻalahi loa o kēia, ʻo ia ka "ʻaʻohe kumu i ʻike ʻia."
- Thrombocytopenic: ʻO ke ʻano kēia, aia ka emi ʻana o ka helu o nā cell i loko o ko mākou koko i kapa ʻia ʻo 'thrombocytes'. Kāhea pinepine mākou i kēia mau thrombocytes 'platelets' .
- Purpura: Pili kēia i nā palapū poni i hoʻokumu ʻia e ke kahe ʻana o ke koko ma lalo o ka ʻili.
I ka ʻōlelo maʻalahi, ʻo ITP kahi kūlana e kū mai ana i ka wā e hana hewa ai ka ʻōnaehana pale ponoʻī o ko mākou kino, e luku ana i nā platelets, he mea nui no ke kāpili ʻana o ke koko, a e hoʻemi ana i ka helu o nā platelets.
E noʻonoʻo i kēia ʻano: ke loaʻa iā mākou kahi ʻoki a ʻeha paha ma kekahi wahi o ko mākou kino, wikiwiki kēia mau mea hana liʻiliʻi i kapa ʻia ʻo platelets e hoʻōki i ke kahe ʻana o ke koko a hoʻopili iā ia ma kahi e like me ka 'plaster' e pani ai i ka lua. I ka ITP, ʻo ka mea e hana ʻia, ʻo ia ka manaʻo o ko mākou ikaika pale ponoʻī (ʻōnaehana pale) he mau ʻenemi kēia mau mea hana liʻiliʻi (platelets) a hoʻouka a luku iā lākou. A laila emi ka helu o nā platelets i loko o ke koko. ʻO ia ke kumu ʻaʻole e hoʻōki ke kahe ʻana o ke koko i kahi ʻeha liʻiliʻi, a hana ʻia nā palapū.
ʻElua ʻano o ITP - ʻokoʻa ke ʻano o kona hōʻike ʻana i nā keiki a me nā mākua!
He ʻokoʻa loa ke ʻano o ka ulu ʻana o ka ITP i nā keiki a me nā pākeke. He mea nui e hoʻomaopopo i kēia ʻokoʻa.
| ʻAno | ITP koʻikoʻi i nā keiki | ITP Mau Loa i nā Mākua |
|---|---|---|
| Makahiki maʻamau loa | He mea maʻamau ia i nā keiki ʻōpio ma waena o nā makahiki 2-6. | Hoʻopilikia pinepine ia i ka poʻe ʻōpio a me ka poʻe waena (20-50 mau makahiki). ʻOi aku ka maʻamau i nā wahine. |
| Kumu | Hiki ke hana pinepine ia i 1-4 mau pule ma hope o kahi maʻi viral , e like me ke anu a i ʻole ka chickenpox. | ʻAʻole pinepine hiki ke loaʻa ke kumu kikoʻī (idiopathic). Hiki ke pili pū me nā maʻi ʻē aʻe (e.g. lupus). |
| Ka lōʻihi o ka maʻi | He manawa pōkole kēia (ʻoi) a hoʻoholo pinepine ʻia ma lalo o 6 mau mahina. | He maʻi mau kēia. ʻOi aku ka lōʻihi o ia ma mua o 6 mau mahina, i kekahi manawa i ke ola holoʻokoʻa. |
| ʻO ke ʻano o ka ho'ōla ʻana | ʻOi aku ma mua o 80% o nā keiki e ho'ōla koke ʻia me ka ʻole o ka lāʻau lapaʻau. | He mea kākaʻikahi ka ho'ōla koke ʻana, a pono pinepine ka lāʻau lapaʻau e kaohi i nā hōʻailona. |
He aha nā hōʻailona nui o kēia maʻi?
ʻO ka helu platelet haʻahaʻa e hoʻonui i ka pilikia o ke kahe koko, no laila e ʻike paha ʻoe i nā hōʻailona e like me:
- ʻEha maʻalahi (Purpura): ʻOiai me kahi ʻeha liʻiliʻi, i kekahi manawa ʻike ʻia nā ʻeha poni a polū paha ma ke kino.
- Petechiae: E kuhikuhi i nā kiko ʻulaʻula a poni paha i hoʻokumu ʻia e nā kīʻaha koko liʻiliʻi ma lalo o ka ʻili. ʻIke pinepine ʻia kēia mau mea ma nā wāwae.
- Kokoke ka ihu.
- Ke kahe koko ʻana o nā ʻāʻī i ka wā e palaki ai i kou mau niho.
- Nā wā kaumaha i nā wahine.
- I kekahi manawa pinepine ʻole, hoʻokahe ʻia ke koko me ka ʻōpala a i ʻole ka mimi.
- ʻO ke kūlana kakaikahi loa akā ʻo ka mea weliweli loa: Ke kahe ʻana o ke koko i loko o ka lolo (Intracranial Hemorrhage). He mea kakaikahi loa kēia. Eia nō naʻe, inā loaʻa iā ʻoe nā hōʻailona e like me ke poʻo ʻeha nui, ka luaʻi ʻana, a me ka huikau , pono ʻoe e hele koke i ka Emergency Department (ETU) o ka haukapila.
He kūlana weliweli anei kēia? Pono anei kākou e makaʻu?
I pane pololei i kēia nīnau, ʻaʻole he maʻi weliweli ka ITP no ka hapa nui o nā kānaka, ʻoi aku hoʻi nā keiki.
Ma mua o 80% o nā keiki e ho'ōla loa mai ke kūlana i loko o kekahi mau mahina me ka ʻole o ka lāʻau lapaʻau. I nā keiki me ITP, nānā pinepine nā kauka i ke kūlana.
Eia nō naʻe, ʻokoʻa iki ka ITP mau loa i nā pākeke. No ka mea he lōʻihi kona mau ʻana, hiki iā ia ke hoʻopilikia i ke ʻano o ke ola. Eia nō naʻe, aia nā lāʻau lapaʻau i kēia lā e hiki ke hoʻomalu pono i kēia ʻano.
ʻO ka pilikia nui wale nō ma ʻaneʻi, ʻo ia ke kahe koko. Inā hāʻule ka helu platelet i kahi pae haʻahaʻa loa (e.g., emi ma lalo o 10,000), piʻi aʻe ka pilikia o ke kahe koko nui. He ʻoiaʻiʻo loa kēia no ka poʻe ma luna o 60 mau makahiki a me ka poʻe i loaʻa mua ke kahe koko. No laila he mea nui e ʻike i kāu kauka i ka wā e ʻike ai ʻoe i nā hōʻailona.
Pehea ʻoe e ʻike ai i kēia, e Kauka?
Ke ʻike ʻoe i ke kauka me kēia mau hōʻailona, ʻo ka mea mua āna e hana ai, ʻo ia ke nīnau iā ʻoe a me kāu keiki e pili ana i nā maʻi a i ʻole nā lāʻau lapaʻau āu e lawe nei. A laila, e nānā lākou i kou kino a nānā i nā palapū a i ʻole nā kiko ʻulaʻula.
ʻO ka hoʻokolohua koʻikoʻi aʻe ka helu koko piha (FBC) .
- Ma kēia hōʻike, hōʻike ka helu platelet i kahi waiwai haʻahaʻa loa .
- Eia nō naʻe, he mea maʻamau ka nui o nā hunaola koko ʻulaʻula a me nā hunaola koko keʻokeʻo.
He 'diagnosis of exclusion' ka ITP. ʻO ke ʻano kēia, ua ʻike ʻia ka ITP ma hope o ka hoʻopau ʻia ʻana o nā kumu ʻē aʻe o nā platelets haʻahaʻa (e like me ka dengue, leukemia, nā maʻi autoimmune ʻē aʻe, kekahi mau lāʻau lapaʻau). No kekahi mau maʻi ʻelemakule, hiki ke hana ʻia kahi hoʻāʻo iwi iwi e nānā inā lawa ka hana ʻana o ka iwi iwi i nā platelets.
Leka Lawe-Home
- ʻO ka ITP kahi kūlana kahi e hoʻopau ai kā mākou ʻōnaehana ponoʻī i nā platelet i loko o ke koko.
- ʻO nā hōʻailona nui ka ʻūhū ʻana, nā kiko ʻulaʻula ma ka ʻili, a me ke kahe ʻana o ke koko mai nā wahi like ʻole.
- He manawa pōkole wale nō ka ITP i nā keiki, hiki ke hana ma hope o ke kuni viral, a hoʻoholo wale ia me ka ʻole o ka lāʻau lapaʻau.
- Hiki i ka ITP i nā pākeke ke lilo i mea mau loa, akā hiki ke hoʻomalu ʻia.
- ʻOiai ʻo ke kahe koko ka pilikia nui o kēia maʻi, he mea kākaʻikahi loa nā pilikia koʻikoʻi e like me ke kahe koko i loko o ka lolo.
- Inā loaʻa iā ʻoe a i ʻole kāu keiki kēia mau hōʻailona, he mea nui loa ia ʻaʻole e hopohopo a e ʻike koke i kāu kauka no ka hōʻoia kūpono a me ka ʻōlelo aʻoaʻo.











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