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He cyst anei kou i loko o kou iwi kuamoʻo? (Syringomyelia) E aʻo kākou e pili ana i ia mea.

He cyst anei kou i loko o kou iwi kuamoʻo? (Syringomyelia) E aʻo kākou e pili ana i ia mea.

Ke ʻeha nei ʻoe i ke kua i kekahi manawa, ka mae ʻana o kou mau lima, a i ʻole ka paʻakikī i ka hele ʻana? Manaʻo kekahi poʻe he mau mea maʻamau kēia, akā ma hope o kēia mau hōʻailona aia paha kahi maʻi koʻikoʻi. I kēia lā e kamaʻilio mākou e pili ana i kahi maʻi laha ʻole e hoʻopilikia ana i ko mākou kaula iwi kuamoʻo. ʻO ia hoʻi ʻo syringomyelia .

He aha ka Syringomyelia?

I ka ʻōlelo maʻalahi, ʻo Syringomyelia kahi kūlana kahi e hana ʻia ai kahi ʻeke piha i ka wai (i kapa ʻia he syrinx) i loko o kou iwi kuamoʻo . E noʻonoʻo e pili ana, holo ke kaula kuamoʻo ma kou iwi kuamoʻo. Ua like kēia kaula kuamoʻo me kahi 'ʻelele' e lawe ana i nā leka mai kou lolo a i ke koena o kou kino, a mai kou kino hoʻi i kou lolo. No laila, hiki i kēia 'syrinx' ke nui a lōʻihi i ka hala ʻana o ka manawa. He aha ka mea e hana ʻia ke hana ʻia kēlā? Hoʻomaka ka hōʻino ʻia o ke kaula kuamoʻo. ʻUmi ʻia a hōʻino ʻia nā olonā nerve e lawe ana i kēlā mau leka.

He aha kēia wai?

ʻO ka wai i loko o kēia cyst ua kapa ʻia ʻo Cerebrospinal Fluid (CSF) . ʻO kēia wai, i kapa ʻia ʻo CSF, e hoʻopuni maʻamau i ko mākou lolo a me ke kaula spinal e pale iā lākou. Ua like ia me nā mea hoʻokuʻu haʻalulu i loko o ke kaʻa. ʻAʻole wale ia, akā ua piha pū nā lua i loko o ko mākou lolo (i kapa ʻia ʻo Ventricles) me kēia CSF. Hoʻopili ʻia kēia mau lua i kahi kahawai liʻiliʻi (Central Canal) e holo ana ma ke kaula spinal.

No laila, inā loaʻa iā ʻoe ʻo `(Syringomyelia)`, ʻo ka mea e hana ʻia, ʻo ia ka hōʻiliʻili ʻana o kēia wai `(CSF)` i loko o ka ʻiʻo o ke kaula kuamoʻo, e hoʻonui ana i kēlā kahawai waena `(Central Canal)` a hana i kahi `(Syrinx)`. ʻO ka hapa nui o ka manawa, hana ʻia kahi `(Syrinx)` i ka wā ʻaʻole e hana maʻamau ka `(CSF)` kahe a puni ke kaula kuamoʻo a i ʻole a puni ka ʻaoʻao haʻahaʻa o ka lolo (`(Brain Stem)`), ʻo ia hoʻi, aia kekahi mea e ālai ana i kēlā kahe. Inā pili kēia `(Syrinx)` i ka `(Brain Stem)`, ua kapa ʻia kēlā ʻano `(Syringobulbia)`.

ʻO ka Syringomyelia pinepine e hoʻopilikia i nā ʻāpana o luna o ke kaula spinal, ʻo ia hoʻi, nā ʻāpana cervical a me thoracic.

ʻO wai ka mea e loaʻa pinepine ai kēia maʻi? Pehea ka maʻamau?

ʻO ka maʻi Syringomyelia ka mea i ʻike pinepine ʻia i nā kānaka ma waena o 20 a me 50 mau makahiki. Eia nō naʻe, hiki ke loaʻa i nā keiki a me ka poʻe ʻelemakule. Eia nō naʻe, he maʻi kakaikahi loa ia. Hoʻopilikia ia ma kahi o 8 o 100,000 mau kānaka. ʻO ia ke kuleana no kahi o 5% o nā hihia o ka paraplegia, ʻo ia ke ʻano i palaho ai nā wāwae a me ke kino haʻahaʻa.

He aha nā hōʻailona o Syringomyelia?

ʻO ka maʻamau, e ulu mālie nā hōʻailona, ​​a hiki ke ʻoi aku ka ʻino i nā makahiki.Hiki i kekahi poʻe ke loaʻa kahi `(Syrinx)` liʻiliʻi a hele no ka manawa lōʻihi me ka ʻole o nā hōʻailona. ʻOkoʻa nō hoʻi nā hōʻailona, ​​ma muli o kahi o ka `(Syrinx)` i loko o ka iwi kuamoʻo, pehea kona nui, a pehea kona lōʻihi. Hiki ke ʻike ʻia nā hōʻailona ma kekahi ʻaoʻao o ke kino a i ʻole ma nā ʻaoʻao ʻelua. ʻOiai he liʻiliʻi loa paha kekahi poʻe, hiki i kekahi ke hoʻopilikia nui ʻia.

ʻO nā hōʻailona maʻamau e ʻike ʻia:

  • ʻEha poʻo .
  • ʻO ka ʻeha e hele ana i lalo ma nā lima, i lalo o ka ʻāʻī, i lalo o ke kua, a i ʻole i lalo o nā wāwae (Radiculopathy).
  • Ka nāwaliwali holomua a me ka nawaliwali o nā ʻiʻo ma nā lima a me/a i ʻole nā ​​​​wāwae (Muscle Atrophy).
  • ʻO ka ʻūmiʻi a i ʻole ka paʻa ʻana o nā ʻiʻo o ke kua, nā poʻohiwi, ka ʻāʻī, nā lima, a i ʻole nā ​​​​wāwae.
  • Ka nalowale o ka ʻike i ka ʻeha a i ʻole ka mahana , ʻoi aku hoʻi ma nā lima.
  • ʻO ka maneʻo a i ʻole ke ʻāʻī ʻana ma nā lima a me/a i ʻole nā ​​wāwae.
  • Nā pilikia me ke kaulike a me ka paʻakikī i ka hele wāwae.
  • Ka nalowale ʻana o ke kaohi ʻana i ka ʻōpū a me ka mimi.
  • Nā pilikia e pili ana i ka hana moekolohe.

Ma waho aʻe o kēia mau hōʻailona, ​​​​aia kekahi mau hōʻailona e pili nui ana i nā keiki ʻōpio:

  • ʻO ke skoliosis.
  • Ka hele wāwae.

ʻO ka mea nui loa, inā loaʻa iā ʻoe a i ʻole kāu keiki kekahi o kēia mau hōʻailona, ​​​​pono ʻoe e ʻike i ke kauka i ka wā hikiwawe loa.

No ke aha e ulu ai ʻo Syringomyelia? He aha nā kumu?

ʻO kaʻoiaʻiʻo, ʻaʻole i ʻike pono nā kānaka ʻepekema i ke kumu nui o ka syrinx. Akā, ʻo ka hapa nui o nā kumumanaʻo e hōʻike ana ʻo ke kumu nui he ālai ʻia a i ʻole he pilikia me ke kahe ʻana o ka wai cerebrospinal (CSF) a mākou i kamaʻilio ai ma mua.

Hiki ke hoʻokaʻawale ʻia nā kumu o syringomyelia i ʻelua mau ʻāpana nui: congenital (ʻo ia hoʻi ke ola i ka wā hānau) a loaʻa (ʻo ia hoʻi ka ulu ʻana ma hope o ke ola) .

Nā kumu hānau

Hoʻopili pinepine ʻia ʻo Syringomyelia me kahi maʻi i kapa ʻia ʻo Chiari Malformation Type 1. ʻO kēia ka manawa e puka ai ka ʻaoʻao haʻahaʻa o kā mākou cerebellum i loko o ka foramen magnum, kahi lua ma ke kumu o ke poʻo. ʻO ka maʻamau, hele ke kaula spinal ma o kēia lua. Ke ālai nei kēia pilikia kūkulu i ke kahe maʻamau o ka wai cerebrospinal (CSF).

I ka manawa pinepine, ʻo kēia "Chiari Malformation" kahi mea i loaʻa i ka wā hānau. Eia nō naʻe, ʻaʻole paha e loaʻa i kekahi poʻe me ka "Chiari Malformation Type I" kekahi mau hōʻailona, ​​a i ʻole ʻaʻole paha lākou e loaʻa nā hōʻailona a hiki i ko lākou wā ʻōpiopio a ʻelemakule paha.

ʻO nā kumu hānau ʻē aʻe:

  • Myelomeningocele: Ua kapa ʻia hoʻi ʻo Open Spina Bifida, he kīnā hānau kēia. ʻO kēia kahi e pani pono ʻole ai ke kaula spinal a me ke kahawai spinal ma mua o ka hānau ʻana. He ʻano kīnā neural tube (NTD) kēia.
  • ʻO ka maʻi kaula i hoʻopaʻa ʻia:He maʻi neurological laha ʻole nō hoʻi kēia. ʻO ka mea e hana ʻia ma ʻaneʻi, ʻo ia ka hoʻopili ʻia ʻana o ke kaula spinal i nā ʻiʻo a puni ka iwi kuamoʻo (ʻo ia ka mea i kapa ʻia ʻo ke kaula hoʻopaʻa ʻia). Hoʻopili pinepine ʻia kēia me ka "Spina Bifida" a me ka "Scoliosis".

Nā Kumu i Loaʻa

ʻO nā kumu e kōkua ai i ka ulu ʻana o "Syringomyelia" ma hope o ke ola:

  • Nā ʻeha o ke kaula kuamoʻo: ʻO kēia ʻano syringomyelia i kekahi manawa i kapa ʻia ʻo post-traumatic syringomyelia. Hiki ke hana i nā mahina a i ʻole nā ​​​​makahiki ma hope o ka ʻeha mua. Hoʻokumu pinepine ʻia e ka ʻiʻo ʻeha e ālai ana i ke kahe o ka CSF.
  • Nā Puʻupuʻu o ke kaula kuamoʻo: ʻO nā puʻupuʻu, ʻoiai ʻo hemangioblastomas a me ependymomas, hiki ke ālai i ke kahe o ka wai cerebrospinal (CSF), e hana ana i ka syringomyelia.
  • ʻAraknoiditis: ʻO ka membrane arachnoid kekahi o nā membrane e hoʻopuni a pale i ke kaula spinal. Inā lilo kēia membrane i mumū (pehu), hiki iā ia ke hana i ka syringomyelia. Hiki ke hana ʻia kēia e nā maʻi e like me ka sarcoidosis, transverse myelitis, a me ka multiple sclerosis (MS).
  • Meningitis: ʻO ka meningitis kahi maʻi o nā membrane pale (meninges) e hoʻopuni ana i ka lolo a me ke kaula spinal. Hiki i kēia ke hana i ka syringomyelia.

I kekahi manawa, hiki ke ulu aʻe ka syringomyelia me ke kumu ʻole. Ua kapa ʻia kēia he idiopathic syringomyelia .

Pehea e ʻike pono ai i kēia maʻi?

I mea e ʻike pono ai inā loaʻa iā ʻoe ʻo `(Syringomyelia)`, e lawe mua kāu kauka i kāu mōʻaukala olakino a laila e hana i kahi hoʻokolokolo kino. E nānā pono ʻo ia i ka hana aʻalolo. Hiki iā ia ke kuhikuhi iā ʻoe i kahi `(Neurologist)` - he kauka loea i nā maʻi o ka lolo a me ka ʻōnaehana nerve.

ʻO ka mea aʻe, e noi ʻia ʻoe e hana i nā hoʻokolohua kiʻi e kiʻi i nā kiʻi o kou iwi kuamoʻo a i ʻole kou lolo. I kekahi manawa, hiki ke ʻike ʻia ka syringomyelia ma kahi hanana i ka wā e hana ana i kēia mau hoʻokolohua kiʻi no kekahi maʻi ʻē aʻe.

He aha nā hoʻokolohua e hana ʻia e ʻike ai i kēia maʻi?

Inā kānalua kāu kauka i ka syringomyelia, hiki iā ia ke kauoha i hoʻokahi a ʻoi aku paha o kēia mau hoʻokolohua:

  • MRI (Magnetic Resonance Imaging) Scan: ʻO ke ala hilinaʻi loa e ʻike ai i ka `(Syringomyelia)` he scan MRI.Hoʻohana kēia i kahi magnet nui a me kahi kamepiula e kiʻi i nā kiʻi kikoʻī o nā mea i loko o kou kino. Me kēia hoʻāʻo, hiki i kāu kauka ke ʻike inā he `(Syrinx)` kou i loko o kou iwi kuamoʻo, a inā paha he mea ʻē aʻe, e like me ka puʻupuʻu. Hiki i kahi `(MRI)` ke hōʻike maopopo i kahi o ka `(Syrinx)`, kona nui, a me ka mamao o kona laha ʻana.
  • MRI Dynamic: Hōʻike kēia ʻano MRI pehea e kahe ai ka wai cerebrospinal (CSF) a puni ke kaula spinal a i loko o ka syrinx. Pono paha kēia i kahi mea hoʻohālikelike (kahi wai kūikawā e hoʻomālamalama i nā kiʻi) e hoʻokomo ʻia i loko o kou aʻa.
  • Myelogram me ka CT scan: Inā ʻaʻole hiki iā ʻoe ke loaʻa i kahi MRI, ʻo ke koho aʻe he CT scan. ʻO ka myelogram kahi hoʻāʻo e hoʻohana ana i kahi dye kūikawā i kapa ʻia he dye contrast a me kahi CT scan (Computed Tomography) e ʻimi i nā pilikia ma ke kaula spinal.

He aha nā lāʻau lapaʻau no Syringomyelia?

ʻO ka mālama ʻana no ka syringomyelia e pili ana i ke koʻikoʻi o kāu mau hōʻailona a me ka wikiwiki o ko lākou holomua.

Inā ʻaʻohe hōʻailona , ​​ʻaʻole mālama pinepine nā kauka i ka `(Syringomyelia)`. Eia nō naʻe, ke ʻōlelo nei lākou e nānā pono ʻia ka `(Syrinx)` e kahi `(Neurologist)` a i ʻole `(Neurosurgeon)`. No ka mea, hiki ke ʻike ʻia a ʻoi aku paha ka ʻino o nā hōʻailona i ka hala ʻana o ka manawa. ʻO ka maʻamau, hoʻokomo pū kēia nānā ʻana i nā scan `(MRI)` a me nā hoʻokolohua neurological i kēlā me kēia manawa.

No ka poʻe me nā hōʻailona, ​​​​ʻo nā pahuhopu nui o ka mālama ʻana no Syringomyelia:

  • Inā hiki, e mālama i ke kumu nui o ka syrinx.
  • Ke kāohi nei i nā hōʻailona .
  • Hoʻihoʻi i ke kahe kūpono o ka wai cerebrospinal (CSF) a pale i ka hōʻino hou ʻana i ke kaula spinal.

Hana pinepine ʻia kekahi ʻano hana ʻoki kino e mālama i ke kumu kumu a hoʻōki i ka hōʻino hou ʻana i ke kaula iwi kuamoʻo. ʻO nā lāʻau lapaʻau maʻamau e kāohi i nā hōʻailona:

  • Nā lāʻau ʻeha a me nā lāʻau lapaʻau ʻē aʻe.
  • Hoʻōla Kino a me ka Hoʻōla Hou ʻana.
  • Ka palena ʻana i kekahi mau hana, ʻoiai nā mea e kau ai i ke kaumaha ma ke kua (e like me ka hāpai ʻana i nā mea kaumaha, ka lele ʻana).

He aha nā ʻano hana ʻoki e hana ʻia no Syringomyelia?

Inā loaʻa iā ʻoe kahi maʻi i kapa ʻia ʻo "Syringomyelia" e hoʻoulu ai i nā hōʻailona, ​​a inā paha e nui ana ka "Syrinx", e ʻōlelo paha kāu neurologist a neurosurgeon paha i ke ʻoki kino. ʻElua ʻano nui o ke ʻoki kino: e hoʻomaʻamaʻa i ke kahe o ka "CSF" a puni ke kaula spinal a e wehe pololei i ke wai mai ka "Syrinx". ʻO ke ʻano o ke ʻoki kino āu e hana ai e pili ana i ke kumu o kāu mau hōʻailona.

ʻO nā ʻoki kino:

  • ʻO ka Lapaʻau ʻana no ka Maʻi ʻŌpilikia Chiari: ʻO ka pahuhopu o kēia ʻoki kino, ʻo ia ka hana ʻana i kahi ākea ma ke kumu o ke poʻo a me ka piko o ka ʻāʻī. Hoʻemi kēia i ke kaomi ma luna o ka lolo a me ke kaula iwi kuamoʻo, e ʻae ana i ke kahe ʻana o ka wai cerebrospinal (CSF) e hoʻi i ka maʻamau. ʻO ke ʻoki kino maʻamau no kēia ua kapa ʻia ʻo Posterior Fossa Decompression . Ma kēia kaʻina hana, wehe ke kauka ʻoki kino i nā ʻāpana liʻiliʻi o ka iwi mai ke kua o ke poʻo e hana i kahi ākea. Ma hope o kēia ʻoki kino, hiki i ka wai i loko o ka Syrinx ke kahe, i kekahi manawa e emi ana a nalo loa paha. ʻOiai inā e mau ana ka nui o ka Syrinx a i ʻole he liʻiliʻi iki paha, hiki ke hoʻomaikaʻi ʻia nā hōʻailona.
  • Ke mālama ʻana a i ʻole ka pale ʻana i ka syringomyelia post-traumatic: I ka syringomyelia i hoʻokumu ʻia e kahi ulia, ʻo ka pahuhopu nui ka hoʻōki mua ʻana i ka syrinx mai ka hoʻokumu ʻana a i ʻole e hoʻōki i kahi syrinx e ulu nui ana. Ua kapa ʻia kēia ʻoki ʻana he expansive duraplasty . Pili kēia i ka wehe ʻana i ka ʻiʻo ʻeha a puni ke kaula spinal a i kekahi manawa ke hoʻokomo nei i kahi ʻāpana e hoʻonui i ka dura mater. Hoʻokumu kēia i kahi ākea a puni ke kaula spinal a hoʻomaʻemaʻe iā ia, e ʻae ana i ka wai cerebrospinal (CSF) e kahe maʻamau.
  • Ke wehe ʻana i ke ālai: ʻO ke ʻoki ʻana i nā ālai e like me ka ʻiʻo ʻeha, nā ʻāpana iwi ma ke kahawai kuamoʻo, a i ʻole nā ​​puʻupuʻu e hiki ke kōkua i ka hoʻihoʻi ʻana i ke kahe o ka CSF. Inā he puʻupuʻu ke kumu o ka syringomyelia, ʻo ka wehe ʻana i ka puʻupuʻu e hoʻopau pinepine i ka syrinx. I kekahi manawa, hiki i kāu kauka ke ʻōlelo aku i ka radiation therapy e hoʻēmi i ka puʻupuʻu.
  • Ka hoʻokahe ʻana o ka syrinx: Inā ʻaʻohe kumu maopopo no ka syrinx, ʻoiai inā e nui ana, e ʻōlelo paha kāu kauka e hoʻokahe i ka wai. Pili kēia i kahi neurosurgeon e kau ana i kahi stent a i ʻole shunt i loko o ka syrinx. ʻO ka stent kahi paipu liʻiliʻi e hiki ai i ka wai ke kahe mai ke kaula spinal i waho. ʻO ka shunt kahi paipu palupalu me kahi valve e hiki ai i ka wai ke kahe mai ka syrinx i kahi ʻāpana ʻē aʻe o ke kino, ʻo ia hoʻi ka ʻōpū a i ʻole ka umauma. Hiki i kēia mau kaʻina hana ʻelua ke kōkua i ka hoʻokahe ʻana i ka wai mai ka syrinx, hiki ke kōkua i ka pale ʻana i nā hōʻailona mai ka ʻino ʻana.

Ma hope o ke ʻoki ʻana, e hana ke kauka i kahi scan MRI e ʻike ai inā ua paʻa ka syrinx a ua emi paha kona nui.

Hiki i ke ʻoki ʻana no `(Syringomyelia)` ke hoʻomaikaʻi i nā hōʻailona a hoʻopaʻa i ke kūlana i nā poʻe he nui. Eia nō naʻe, hiki i ka `(Syringomyelia)` ke hoʻi hou mai ma hope o ka mālama ʻana i kūleʻa . I kēlā hihia, pono paha ke ʻoki hou aku.

He aha nā pilikia e hiki ke loaʻa mai ke ʻoki kino?

Hiki ke loaʻa nā pilikia ma hope o ke ʻoki ʻana no Syringomyelia:

  • Ka liki ʻana o ka wai Cerebrospinal (CSF).
  • Nā maʻi.
  • Ke kahe koko.
  • Ka hōʻino hou ʻana i ke kaula kuamoʻo.
  • Ke kūkulu hou ʻana i ka `(Syrinx)`.

He mea nui loa e kamaʻilio me kāu neurosurgeon e pili ana i kēia mau pilikia e pili ana i kāu ʻoki kino a pehea ka hiki ke loaʻa iā lākou.

He aha ka manaʻo no Syringomyelia? (Prognosis)

He mea nui e hoʻomanaʻo he ʻokoʻa loa nā hōʻailona, ​​ke koʻikoʻi, a me nā kumu o Syringomyelia. Eia kekahi, ʻokoʻa ka wikiwiki o ka holomua ʻana o ka maʻi mai kēlā kanaka a kēia kanaka, a i ʻole ʻaʻole paha e hoʻomaikaʻi iki kekahi poʻe. Ma muli o kēia mau kumu, he paʻakikī i nā kauka ke hāʻawi i kahi wānana pololei no Syringomyelia.

Hiki i ke ʻoki mua ke hōʻemi i nā hōʻailona a loaʻa nā hopena maikaʻi . ʻOiai ʻo ka holomua o nā hemahema neurological ma hope o ka mālama ʻoki ʻana he paʻa mau, a hoʻomaikaʻi kekahi mau hōʻailona, ​​​​nui ka poʻe e noho me nā hōʻailona.

Ma ke ʻano laulā, inā ʻoi aku ke anawaena o ka `(Syrinx)` ma mua o ʻelima millimeters `(5mm)` a aia ka pehu `(Edema)` me ia, hōʻike ia ʻaʻole maikaʻi loa ka nānā ʻana.

ʻO ka Myelopathy (ka hōʻino ʻana i ke kaula iwi kuamoʻo ma muli o ke kaomi nui ʻana) he pilikia nui ia o Syringomyelia a he mea e hopohopo ai. Hiki i kēia ke alakaʻi i ka maʻi lolo/quadriplegia, ka maʻi pneumonia hou, a me nā pilikia me ka hana ʻōpū a me ka ʻōpū mimi.

Hiki ke pale ʻia ka Syringomyelia?

ʻAʻole hiki ke pale ʻia ʻo Syringomyelia. Eia nō naʻe, hiki i ka ʻike mua ʻana a me ka mālama ʻana ke kōkua i ka pale ʻana i nā hōʻailona mai ka ʻino ʻana .

Inā loaʻa iaʻu ʻo Syringomyelia, pehea wau e mālama ai iaʻu iho?

Inā loaʻa iā ʻoe ʻo Syringomyelia, e noʻonoʻo i kēia mau mea e kōkua ai i ka mālama ʻana i kāu mau hōʻailona:

  • E hōʻalo i nā hana e hoʻonui ai i kou mau hōʻailona , ​​e like me ka hāpai ʻana, ka hoʻoluhi ʻana, a i ʻole kekahi mea e kau ai i ke kaomi ma kou kua (e like me ka lele ʻana).
  • E noʻonoʻo i ka hoʻoikaika kino e hōʻemi i nā pilikia hele wāwae, nāwaliwali o nā ʻiʻo a i ʻole ka ʻoʻoleʻa, a me ka ʻeha.
  • Inā loaʻa iā ʻoe ka ʻeha mau loa ma muli o syringomyelia, e kamaʻilio me kāu kauka e pili ana i nā koho lapaʻau.
  • Hiki i ka noho ʻana me Syringomyelia ke lilo i mea kaumaha a hoʻoluhi. He mea nui e ʻimi i ke kākoʻo olakino noʻonoʻo mai nā hoaaloha, ka ʻohana, a/a i ʻole ke kākāʻōlelo. ʻO ka hui pū ʻana me kahi hui kākoʻo me nā poʻe ʻē aʻe i loaʻa iā Syringomyelia hiki ke kōkua iā ʻoe e manaʻo ʻaʻole ʻoe hoʻokahi.

Āhea wau e ʻike ai i kaʻu kauka e pili ana iā Syringomyelia?

Inā ua ʻike ʻia ʻoe me Syringomyelia, e nānā i kāu mau hōʻailona a me ka Syrinx, inā paha ua hana ʻia ke ʻoki kino ʻana a ʻaʻole paha.Pono ʻoe e hālāwai pinepine me kāu hui lapaʻau.

Hiki ke kaumaha ka ʻike ʻana he ʻeha kou iwi kuamoʻo. Akā e hoʻomanaʻo, ʻaʻole ʻoe hoʻokahi, a he nui nā kumuwaiwai e kōkua iā ʻoe. He mea nui e kamaʻilio me ke kauka i ʻike e pili ana iā Syringomyelia a aʻo hou e pili ana i ke ʻano o kona hopena iā ʻoe. Mai makaʻu e nīnau i kāu hui lapaʻau - aia lākou ma laila e kōkua iā ʻoe .

ʻO kā mākou leka lawe-i-ka-home

ʻAe, ke lana nei koʻu manaʻo ua maopopo iā ʻoe kekahi mea mai kā mākou i kamaʻilio ai e pili ana i ka `(Syringomyelia)`. ʻOiai he maʻi laha ʻole kēia, he mea nui loa ia e ʻimi koke i ke kōkua lapaʻau inā loaʻa iā ʻoe nā hōʻailona . ʻOiai inā loaʻa iā ʻoe ka ʻeha mau o ke kua, ka mae ʻana o nā lālā, a i ʻole ka nāwaliwali, pono ʻoe e ʻike i ke kauka. Inā ʻike mua ʻoe i ka maʻi, hiki iā ʻoe ke ʻimi i ka lāʻau kūpono a mālama i kahi ola maikaʻi. Mai hopohopo, aia nā hopena i nā mea āpau, a inā he mau nīnau kāu, e nīnau i kāu mau kauka.

👩🏽‍⚕️ Nā nīnau hou aku (FAQs)

💬 He maʻi anei ʻo Syringomyelia kahi e hoʻokumu ʻia ai kahi puʻupuʻu i loko o ka iwi kuamoʻo?

ʻAʻole he puʻupuʻu! He maʻi neurological weliweli loa kēia. He kūlana weliweli kēia kahi e hana ʻia ai kahi lua ma waenakonu o ke aʻalolo nui (Spinal cord) i loko o ko kākou iwi kuamoʻo, kahi e piha ai i ka wai (ka wai o ka lolo) a lilo i mea nui (Syrinx). I ka ulu ʻana o kēia lua i piha i ka wai, ua luku loa ʻia ko kākou mau aʻalolo i kēlā me kēia lā.

💬 Pehea ka manaʻo o ko kākou kino inā ua piha ko kākou kua i ka wai e like me kēia?

ʻO ka hōʻailona weliweli loa o kēia, ʻo ia ka nalowale loa ʻana o kou mau lima a me kou umauma i ko lākou ʻano o ka 'wela a me ke anu' (ʻoiai inā loaʻa iā ʻoe ka wai wela, ʻaʻole ia e ʻeha). Me kēia, loaʻa iā ʻoe ka ʻeha hiki ʻole ke hoʻomanawanui ma kou ʻāʻī, nā lima, ka umauma, a me ke kua, a lilo nā ʻiʻo o kou mau lima i mea maneʻo a make.

💬 Pono anei au e hana i ke ʻoki kino e wehe ai i kēia cyst (lua) ma koʻu kua?

ʻAʻole pono nā kānaka a pau i ke ʻoki kino (inā ʻaʻohe o lākou mau hōʻailona, ​​kali wale lākou). Akā inā holomua ka maʻi a e luku ʻia nā aʻalolo, a laila pono ʻoe e hana i ke ʻoki kino nui (ʻoki kino Shunt / Decompression) ma ka lolo a i ʻole ke kaula spinal e hana i ala no ka wai i hōʻiliʻili ʻia e kahe i waho.


ʻO Syringomyelia, kaula kuamoʻo, ʻeha kua, syrinx, CSF, maʻi neurological, Chiari malformation

Frequently Asked Questions (FAQ)

He aha nā hoʻokolohua e hana ʻia e ʻike ai i kēia maʻi?

Inā kānalua kāu kauka i ka syringomyelia, hiki iā ia ke kauoha i hoʻokahi a ʻoi aku paha o kēia mau hoʻokolohua:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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He cyst anei kou i loko o kou iwi kuamoʻo? (Syringomyelia) E aʻo kākou e pili ana i ia mea.

He cyst anei kou i loko o kou iwi kuamoʻo? (Syringomyelia) E aʻo kākou e pili ana i ia mea.

Ke ʻeha nei ʻoe i ke kua i kekahi manawa, ka mae ʻana o kou mau lima, a i ʻole ka paʻakikī i ka hele ʻana? Manaʻo kekahi poʻe he mau mea maʻamau kēia, akā ma hope o kēia mau hōʻailona aia paha kahi maʻi koʻikoʻi. I kēia lā e kamaʻilio mākou e pili ana i kahi maʻi laha ʻole e hoʻopilikia ana i ko mākou kaula iwi kuamoʻo. ʻO ia hoʻi ʻo syringomyelia .

He aha ka Syringomyelia?

I ka ʻōlelo maʻalahi, ʻo Syringomyelia kahi kūlana kahi e hana ʻia ai kahi ʻeke piha i ka wai (i kapa ʻia he syrinx) i loko o kou iwi kuamoʻo . E noʻonoʻo e pili ana, holo ke kaula kuamoʻo ma kou iwi kuamoʻo. Ua like kēia kaula kuamoʻo me kahi 'ʻelele' e lawe ana i nā leka mai kou lolo a i ke koena o kou kino, a mai kou kino hoʻi i kou lolo. No laila, hiki i kēia 'syrinx' ke nui a lōʻihi i ka hala ʻana o ka manawa. He aha ka mea e hana ʻia ke hana ʻia kēlā? Hoʻomaka ka hōʻino ʻia o ke kaula kuamoʻo. ʻUmi ʻia a hōʻino ʻia nā olonā nerve e lawe ana i kēlā mau leka.

He aha kēia wai?

ʻO ka wai i loko o kēia cyst ua kapa ʻia ʻo Cerebrospinal Fluid (CSF) . ʻO kēia wai, i kapa ʻia ʻo CSF, e hoʻopuni maʻamau i ko mākou lolo a me ke kaula spinal e pale iā lākou. Ua like ia me nā mea hoʻokuʻu haʻalulu i loko o ke kaʻa. ʻAʻole wale ia, akā ua piha pū nā lua i loko o ko mākou lolo (i kapa ʻia ʻo Ventricles) me kēia CSF. Hoʻopili ʻia kēia mau lua i kahi kahawai liʻiliʻi (Central Canal) e holo ana ma ke kaula spinal.

No laila, inā loaʻa iā ʻoe ʻo `(Syringomyelia)`, ʻo ka mea e hana ʻia, ʻo ia ka hōʻiliʻili ʻana o kēia wai `(CSF)` i loko o ka ʻiʻo o ke kaula kuamoʻo, e hoʻonui ana i kēlā kahawai waena `(Central Canal)` a hana i kahi `(Syrinx)`. ʻO ka hapa nui o ka manawa, hana ʻia kahi `(Syrinx)` i ka wā ʻaʻole e hana maʻamau ka `(CSF)` kahe a puni ke kaula kuamoʻo a i ʻole a puni ka ʻaoʻao haʻahaʻa o ka lolo (`(Brain Stem)`), ʻo ia hoʻi, aia kekahi mea e ālai ana i kēlā kahe. Inā pili kēia `(Syrinx)` i ka `(Brain Stem)`, ua kapa ʻia kēlā ʻano `(Syringobulbia)`.

ʻO ka Syringomyelia pinepine e hoʻopilikia i nā ʻāpana o luna o ke kaula spinal, ʻo ia hoʻi, nā ʻāpana cervical a me thoracic.

ʻO wai ka mea e loaʻa pinepine ai kēia maʻi? Pehea ka maʻamau?

ʻO ka maʻi Syringomyelia ka mea i ʻike pinepine ʻia i nā kānaka ma waena o 20 a me 50 mau makahiki. Eia nō naʻe, hiki ke loaʻa i nā keiki a me ka poʻe ʻelemakule. Eia nō naʻe, he maʻi kakaikahi loa ia. Hoʻopilikia ia ma kahi o 8 o 100,000 mau kānaka. ʻO ia ke kuleana no kahi o 5% o nā hihia o ka paraplegia, ʻo ia ke ʻano i palaho ai nā wāwae a me ke kino haʻahaʻa.

He aha nā hōʻailona o Syringomyelia?

ʻO ka maʻamau, e ulu mālie nā hōʻailona, ​​a hiki ke ʻoi aku ka ʻino i nā makahiki.Hiki i kekahi poʻe ke loaʻa kahi `(Syrinx)` liʻiliʻi a hele no ka manawa lōʻihi me ka ʻole o nā hōʻailona. ʻOkoʻa nō hoʻi nā hōʻailona, ​​ma muli o kahi o ka `(Syrinx)` i loko o ka iwi kuamoʻo, pehea kona nui, a pehea kona lōʻihi. Hiki ke ʻike ʻia nā hōʻailona ma kekahi ʻaoʻao o ke kino a i ʻole ma nā ʻaoʻao ʻelua. ʻOiai he liʻiliʻi loa paha kekahi poʻe, hiki i kekahi ke hoʻopilikia nui ʻia.

ʻO nā hōʻailona maʻamau e ʻike ʻia:

  • ʻEha poʻo .
  • ʻO ka ʻeha e hele ana i lalo ma nā lima, i lalo o ka ʻāʻī, i lalo o ke kua, a i ʻole i lalo o nā wāwae (Radiculopathy).
  • Ka nāwaliwali holomua a me ka nawaliwali o nā ʻiʻo ma nā lima a me/a i ʻole nā ​​​​wāwae (Muscle Atrophy).
  • ʻO ka ʻūmiʻi a i ʻole ka paʻa ʻana o nā ʻiʻo o ke kua, nā poʻohiwi, ka ʻāʻī, nā lima, a i ʻole nā ​​​​wāwae.
  • Ka nalowale o ka ʻike i ka ʻeha a i ʻole ka mahana , ʻoi aku hoʻi ma nā lima.
  • ʻO ka maneʻo a i ʻole ke ʻāʻī ʻana ma nā lima a me/a i ʻole nā ​​wāwae.
  • Nā pilikia me ke kaulike a me ka paʻakikī i ka hele wāwae.
  • Ka nalowale ʻana o ke kaohi ʻana i ka ʻōpū a me ka mimi.
  • Nā pilikia e pili ana i ka hana moekolohe.

Ma waho aʻe o kēia mau hōʻailona, ​​​​aia kekahi mau hōʻailona e pili nui ana i nā keiki ʻōpio:

  • ʻO ke skoliosis.
  • Ka hele wāwae.

ʻO ka mea nui loa, inā loaʻa iā ʻoe a i ʻole kāu keiki kekahi o kēia mau hōʻailona, ​​​​pono ʻoe e ʻike i ke kauka i ka wā hikiwawe loa.

No ke aha e ulu ai ʻo Syringomyelia? He aha nā kumu?

ʻO kaʻoiaʻiʻo, ʻaʻole i ʻike pono nā kānaka ʻepekema i ke kumu nui o ka syrinx. Akā, ʻo ka hapa nui o nā kumumanaʻo e hōʻike ana ʻo ke kumu nui he ālai ʻia a i ʻole he pilikia me ke kahe ʻana o ka wai cerebrospinal (CSF) a mākou i kamaʻilio ai ma mua.

Hiki ke hoʻokaʻawale ʻia nā kumu o syringomyelia i ʻelua mau ʻāpana nui: congenital (ʻo ia hoʻi ke ola i ka wā hānau) a loaʻa (ʻo ia hoʻi ka ulu ʻana ma hope o ke ola) .

Nā kumu hānau

Hoʻopili pinepine ʻia ʻo Syringomyelia me kahi maʻi i kapa ʻia ʻo Chiari Malformation Type 1. ʻO kēia ka manawa e puka ai ka ʻaoʻao haʻahaʻa o kā mākou cerebellum i loko o ka foramen magnum, kahi lua ma ke kumu o ke poʻo. ʻO ka maʻamau, hele ke kaula spinal ma o kēia lua. Ke ālai nei kēia pilikia kūkulu i ke kahe maʻamau o ka wai cerebrospinal (CSF).

I ka manawa pinepine, ʻo kēia "Chiari Malformation" kahi mea i loaʻa i ka wā hānau. Eia nō naʻe, ʻaʻole paha e loaʻa i kekahi poʻe me ka "Chiari Malformation Type I" kekahi mau hōʻailona, ​​a i ʻole ʻaʻole paha lākou e loaʻa nā hōʻailona a hiki i ko lākou wā ʻōpiopio a ʻelemakule paha.

ʻO nā kumu hānau ʻē aʻe:

  • Myelomeningocele: Ua kapa ʻia hoʻi ʻo Open Spina Bifida, he kīnā hānau kēia. ʻO kēia kahi e pani pono ʻole ai ke kaula spinal a me ke kahawai spinal ma mua o ka hānau ʻana. He ʻano kīnā neural tube (NTD) kēia.
  • ʻO ka maʻi kaula i hoʻopaʻa ʻia:He maʻi neurological laha ʻole nō hoʻi kēia. ʻO ka mea e hana ʻia ma ʻaneʻi, ʻo ia ka hoʻopili ʻia ʻana o ke kaula spinal i nā ʻiʻo a puni ka iwi kuamoʻo (ʻo ia ka mea i kapa ʻia ʻo ke kaula hoʻopaʻa ʻia). Hoʻopili pinepine ʻia kēia me ka "Spina Bifida" a me ka "Scoliosis".

Nā Kumu i Loaʻa

ʻO nā kumu e kōkua ai i ka ulu ʻana o "Syringomyelia" ma hope o ke ola:

  • Nā ʻeha o ke kaula kuamoʻo: ʻO kēia ʻano syringomyelia i kekahi manawa i kapa ʻia ʻo post-traumatic syringomyelia. Hiki ke hana i nā mahina a i ʻole nā ​​​​makahiki ma hope o ka ʻeha mua. Hoʻokumu pinepine ʻia e ka ʻiʻo ʻeha e ālai ana i ke kahe o ka CSF.
  • Nā Puʻupuʻu o ke kaula kuamoʻo: ʻO nā puʻupuʻu, ʻoiai ʻo hemangioblastomas a me ependymomas, hiki ke ālai i ke kahe o ka wai cerebrospinal (CSF), e hana ana i ka syringomyelia.
  • ʻAraknoiditis: ʻO ka membrane arachnoid kekahi o nā membrane e hoʻopuni a pale i ke kaula spinal. Inā lilo kēia membrane i mumū (pehu), hiki iā ia ke hana i ka syringomyelia. Hiki ke hana ʻia kēia e nā maʻi e like me ka sarcoidosis, transverse myelitis, a me ka multiple sclerosis (MS).
  • Meningitis: ʻO ka meningitis kahi maʻi o nā membrane pale (meninges) e hoʻopuni ana i ka lolo a me ke kaula spinal. Hiki i kēia ke hana i ka syringomyelia.

I kekahi manawa, hiki ke ulu aʻe ka syringomyelia me ke kumu ʻole. Ua kapa ʻia kēia he idiopathic syringomyelia .

Pehea e ʻike pono ai i kēia maʻi?

I mea e ʻike pono ai inā loaʻa iā ʻoe ʻo `(Syringomyelia)`, e lawe mua kāu kauka i kāu mōʻaukala olakino a laila e hana i kahi hoʻokolokolo kino. E nānā pono ʻo ia i ka hana aʻalolo. Hiki iā ia ke kuhikuhi iā ʻoe i kahi `(Neurologist)` - he kauka loea i nā maʻi o ka lolo a me ka ʻōnaehana nerve.

ʻO ka mea aʻe, e noi ʻia ʻoe e hana i nā hoʻokolohua kiʻi e kiʻi i nā kiʻi o kou iwi kuamoʻo a i ʻole kou lolo. I kekahi manawa, hiki ke ʻike ʻia ka syringomyelia ma kahi hanana i ka wā e hana ana i kēia mau hoʻokolohua kiʻi no kekahi maʻi ʻē aʻe.

He aha nā hoʻokolohua e hana ʻia e ʻike ai i kēia maʻi?

Inā kānalua kāu kauka i ka syringomyelia, hiki iā ia ke kauoha i hoʻokahi a ʻoi aku paha o kēia mau hoʻokolohua:

  • MRI (Magnetic Resonance Imaging) Scan: ʻO ke ala hilinaʻi loa e ʻike ai i ka `(Syringomyelia)` he scan MRI.Hoʻohana kēia i kahi magnet nui a me kahi kamepiula e kiʻi i nā kiʻi kikoʻī o nā mea i loko o kou kino. Me kēia hoʻāʻo, hiki i kāu kauka ke ʻike inā he `(Syrinx)` kou i loko o kou iwi kuamoʻo, a inā paha he mea ʻē aʻe, e like me ka puʻupuʻu. Hiki i kahi `(MRI)` ke hōʻike maopopo i kahi o ka `(Syrinx)`, kona nui, a me ka mamao o kona laha ʻana.
  • MRI Dynamic: Hōʻike kēia ʻano MRI pehea e kahe ai ka wai cerebrospinal (CSF) a puni ke kaula spinal a i loko o ka syrinx. Pono paha kēia i kahi mea hoʻohālikelike (kahi wai kūikawā e hoʻomālamalama i nā kiʻi) e hoʻokomo ʻia i loko o kou aʻa.
  • Myelogram me ka CT scan: Inā ʻaʻole hiki iā ʻoe ke loaʻa i kahi MRI, ʻo ke koho aʻe he CT scan. ʻO ka myelogram kahi hoʻāʻo e hoʻohana ana i kahi dye kūikawā i kapa ʻia he dye contrast a me kahi CT scan (Computed Tomography) e ʻimi i nā pilikia ma ke kaula spinal.

He aha nā lāʻau lapaʻau no Syringomyelia?

ʻO ka mālama ʻana no ka syringomyelia e pili ana i ke koʻikoʻi o kāu mau hōʻailona a me ka wikiwiki o ko lākou holomua.

Inā ʻaʻohe hōʻailona , ​​ʻaʻole mālama pinepine nā kauka i ka `(Syringomyelia)`. Eia nō naʻe, ke ʻōlelo nei lākou e nānā pono ʻia ka `(Syrinx)` e kahi `(Neurologist)` a i ʻole `(Neurosurgeon)`. No ka mea, hiki ke ʻike ʻia a ʻoi aku paha ka ʻino o nā hōʻailona i ka hala ʻana o ka manawa. ʻO ka maʻamau, hoʻokomo pū kēia nānā ʻana i nā scan `(MRI)` a me nā hoʻokolohua neurological i kēlā me kēia manawa.

No ka poʻe me nā hōʻailona, ​​​​ʻo nā pahuhopu nui o ka mālama ʻana no Syringomyelia:

  • Inā hiki, e mālama i ke kumu nui o ka syrinx.
  • Ke kāohi nei i nā hōʻailona .
  • Hoʻihoʻi i ke kahe kūpono o ka wai cerebrospinal (CSF) a pale i ka hōʻino hou ʻana i ke kaula spinal.

Hana pinepine ʻia kekahi ʻano hana ʻoki kino e mālama i ke kumu kumu a hoʻōki i ka hōʻino hou ʻana i ke kaula iwi kuamoʻo. ʻO nā lāʻau lapaʻau maʻamau e kāohi i nā hōʻailona:

  • Nā lāʻau ʻeha a me nā lāʻau lapaʻau ʻē aʻe.
  • Hoʻōla Kino a me ka Hoʻōla Hou ʻana.
  • Ka palena ʻana i kekahi mau hana, ʻoiai nā mea e kau ai i ke kaumaha ma ke kua (e like me ka hāpai ʻana i nā mea kaumaha, ka lele ʻana).

He aha nā ʻano hana ʻoki e hana ʻia no Syringomyelia?

Inā loaʻa iā ʻoe kahi maʻi i kapa ʻia ʻo "Syringomyelia" e hoʻoulu ai i nā hōʻailona, ​​a inā paha e nui ana ka "Syrinx", e ʻōlelo paha kāu neurologist a neurosurgeon paha i ke ʻoki kino. ʻElua ʻano nui o ke ʻoki kino: e hoʻomaʻamaʻa i ke kahe o ka "CSF" a puni ke kaula spinal a e wehe pololei i ke wai mai ka "Syrinx". ʻO ke ʻano o ke ʻoki kino āu e hana ai e pili ana i ke kumu o kāu mau hōʻailona.

ʻO nā ʻoki kino:

  • ʻO ka Lapaʻau ʻana no ka Maʻi ʻŌpilikia Chiari: ʻO ka pahuhopu o kēia ʻoki kino, ʻo ia ka hana ʻana i kahi ākea ma ke kumu o ke poʻo a me ka piko o ka ʻāʻī. Hoʻemi kēia i ke kaomi ma luna o ka lolo a me ke kaula iwi kuamoʻo, e ʻae ana i ke kahe ʻana o ka wai cerebrospinal (CSF) e hoʻi i ka maʻamau. ʻO ke ʻoki kino maʻamau no kēia ua kapa ʻia ʻo Posterior Fossa Decompression . Ma kēia kaʻina hana, wehe ke kauka ʻoki kino i nā ʻāpana liʻiliʻi o ka iwi mai ke kua o ke poʻo e hana i kahi ākea. Ma hope o kēia ʻoki kino, hiki i ka wai i loko o ka Syrinx ke kahe, i kekahi manawa e emi ana a nalo loa paha. ʻOiai inā e mau ana ka nui o ka Syrinx a i ʻole he liʻiliʻi iki paha, hiki ke hoʻomaikaʻi ʻia nā hōʻailona.
  • Ke mālama ʻana a i ʻole ka pale ʻana i ka syringomyelia post-traumatic: I ka syringomyelia i hoʻokumu ʻia e kahi ulia, ʻo ka pahuhopu nui ka hoʻōki mua ʻana i ka syrinx mai ka hoʻokumu ʻana a i ʻole e hoʻōki i kahi syrinx e ulu nui ana. Ua kapa ʻia kēia ʻoki ʻana he expansive duraplasty . Pili kēia i ka wehe ʻana i ka ʻiʻo ʻeha a puni ke kaula spinal a i kekahi manawa ke hoʻokomo nei i kahi ʻāpana e hoʻonui i ka dura mater. Hoʻokumu kēia i kahi ākea a puni ke kaula spinal a hoʻomaʻemaʻe iā ia, e ʻae ana i ka wai cerebrospinal (CSF) e kahe maʻamau.
  • Ke wehe ʻana i ke ālai: ʻO ke ʻoki ʻana i nā ālai e like me ka ʻiʻo ʻeha, nā ʻāpana iwi ma ke kahawai kuamoʻo, a i ʻole nā ​​puʻupuʻu e hiki ke kōkua i ka hoʻihoʻi ʻana i ke kahe o ka CSF. Inā he puʻupuʻu ke kumu o ka syringomyelia, ʻo ka wehe ʻana i ka puʻupuʻu e hoʻopau pinepine i ka syrinx. I kekahi manawa, hiki i kāu kauka ke ʻōlelo aku i ka radiation therapy e hoʻēmi i ka puʻupuʻu.
  • Ka hoʻokahe ʻana o ka syrinx: Inā ʻaʻohe kumu maopopo no ka syrinx, ʻoiai inā e nui ana, e ʻōlelo paha kāu kauka e hoʻokahe i ka wai. Pili kēia i kahi neurosurgeon e kau ana i kahi stent a i ʻole shunt i loko o ka syrinx. ʻO ka stent kahi paipu liʻiliʻi e hiki ai i ka wai ke kahe mai ke kaula spinal i waho. ʻO ka shunt kahi paipu palupalu me kahi valve e hiki ai i ka wai ke kahe mai ka syrinx i kahi ʻāpana ʻē aʻe o ke kino, ʻo ia hoʻi ka ʻōpū a i ʻole ka umauma. Hiki i kēia mau kaʻina hana ʻelua ke kōkua i ka hoʻokahe ʻana i ka wai mai ka syrinx, hiki ke kōkua i ka pale ʻana i nā hōʻailona mai ka ʻino ʻana.

Ma hope o ke ʻoki ʻana, e hana ke kauka i kahi scan MRI e ʻike ai inā ua paʻa ka syrinx a ua emi paha kona nui.

Hiki i ke ʻoki ʻana no `(Syringomyelia)` ke hoʻomaikaʻi i nā hōʻailona a hoʻopaʻa i ke kūlana i nā poʻe he nui. Eia nō naʻe, hiki i ka `(Syringomyelia)` ke hoʻi hou mai ma hope o ka mālama ʻana i kūleʻa . I kēlā hihia, pono paha ke ʻoki hou aku.

He aha nā pilikia e hiki ke loaʻa mai ke ʻoki kino?

Hiki ke loaʻa nā pilikia ma hope o ke ʻoki ʻana no Syringomyelia:

  • Ka liki ʻana o ka wai Cerebrospinal (CSF).
  • Nā maʻi.
  • Ke kahe koko.
  • Ka hōʻino hou ʻana i ke kaula kuamoʻo.
  • Ke kūkulu hou ʻana i ka `(Syrinx)`.

He mea nui loa e kamaʻilio me kāu neurosurgeon e pili ana i kēia mau pilikia e pili ana i kāu ʻoki kino a pehea ka hiki ke loaʻa iā lākou.

He aha ka manaʻo no Syringomyelia? (Prognosis)

He mea nui e hoʻomanaʻo he ʻokoʻa loa nā hōʻailona, ​​ke koʻikoʻi, a me nā kumu o Syringomyelia. Eia kekahi, ʻokoʻa ka wikiwiki o ka holomua ʻana o ka maʻi mai kēlā kanaka a kēia kanaka, a i ʻole ʻaʻole paha e hoʻomaikaʻi iki kekahi poʻe. Ma muli o kēia mau kumu, he paʻakikī i nā kauka ke hāʻawi i kahi wānana pololei no Syringomyelia.

Hiki i ke ʻoki mua ke hōʻemi i nā hōʻailona a loaʻa nā hopena maikaʻi . ʻOiai ʻo ka holomua o nā hemahema neurological ma hope o ka mālama ʻoki ʻana he paʻa mau, a hoʻomaikaʻi kekahi mau hōʻailona, ​​​​nui ka poʻe e noho me nā hōʻailona.

Ma ke ʻano laulā, inā ʻoi aku ke anawaena o ka `(Syrinx)` ma mua o ʻelima millimeters `(5mm)` a aia ka pehu `(Edema)` me ia, hōʻike ia ʻaʻole maikaʻi loa ka nānā ʻana.

ʻO ka Myelopathy (ka hōʻino ʻana i ke kaula iwi kuamoʻo ma muli o ke kaomi nui ʻana) he pilikia nui ia o Syringomyelia a he mea e hopohopo ai. Hiki i kēia ke alakaʻi i ka maʻi lolo/quadriplegia, ka maʻi pneumonia hou, a me nā pilikia me ka hana ʻōpū a me ka ʻōpū mimi.

Hiki ke pale ʻia ka Syringomyelia?

ʻAʻole hiki ke pale ʻia ʻo Syringomyelia. Eia nō naʻe, hiki i ka ʻike mua ʻana a me ka mālama ʻana ke kōkua i ka pale ʻana i nā hōʻailona mai ka ʻino ʻana .

Inā loaʻa iaʻu ʻo Syringomyelia, pehea wau e mālama ai iaʻu iho?

Inā loaʻa iā ʻoe ʻo Syringomyelia, e noʻonoʻo i kēia mau mea e kōkua ai i ka mālama ʻana i kāu mau hōʻailona:

  • E hōʻalo i nā hana e hoʻonui ai i kou mau hōʻailona , ​​e like me ka hāpai ʻana, ka hoʻoluhi ʻana, a i ʻole kekahi mea e kau ai i ke kaomi ma kou kua (e like me ka lele ʻana).
  • E noʻonoʻo i ka hoʻoikaika kino e hōʻemi i nā pilikia hele wāwae, nāwaliwali o nā ʻiʻo a i ʻole ka ʻoʻoleʻa, a me ka ʻeha.
  • Inā loaʻa iā ʻoe ka ʻeha mau loa ma muli o syringomyelia, e kamaʻilio me kāu kauka e pili ana i nā koho lapaʻau.
  • Hiki i ka noho ʻana me Syringomyelia ke lilo i mea kaumaha a hoʻoluhi. He mea nui e ʻimi i ke kākoʻo olakino noʻonoʻo mai nā hoaaloha, ka ʻohana, a/a i ʻole ke kākāʻōlelo. ʻO ka hui pū ʻana me kahi hui kākoʻo me nā poʻe ʻē aʻe i loaʻa iā Syringomyelia hiki ke kōkua iā ʻoe e manaʻo ʻaʻole ʻoe hoʻokahi.

Āhea wau e ʻike ai i kaʻu kauka e pili ana iā Syringomyelia?

Inā ua ʻike ʻia ʻoe me Syringomyelia, e nānā i kāu mau hōʻailona a me ka Syrinx, inā paha ua hana ʻia ke ʻoki kino ʻana a ʻaʻole paha.Pono ʻoe e hālāwai pinepine me kāu hui lapaʻau.

Hiki ke kaumaha ka ʻike ʻana he ʻeha kou iwi kuamoʻo. Akā e hoʻomanaʻo, ʻaʻole ʻoe hoʻokahi, a he nui nā kumuwaiwai e kōkua iā ʻoe. He mea nui e kamaʻilio me ke kauka i ʻike e pili ana iā Syringomyelia a aʻo hou e pili ana i ke ʻano o kona hopena iā ʻoe. Mai makaʻu e nīnau i kāu hui lapaʻau - aia lākou ma laila e kōkua iā ʻoe .

ʻO kā mākou leka lawe-i-ka-home

ʻAe, ke lana nei koʻu manaʻo ua maopopo iā ʻoe kekahi mea mai kā mākou i kamaʻilio ai e pili ana i ka `(Syringomyelia)`. ʻOiai he maʻi laha ʻole kēia, he mea nui loa ia e ʻimi koke i ke kōkua lapaʻau inā loaʻa iā ʻoe nā hōʻailona . ʻOiai inā loaʻa iā ʻoe ka ʻeha mau o ke kua, ka mae ʻana o nā lālā, a i ʻole ka nāwaliwali, pono ʻoe e ʻike i ke kauka. Inā ʻike mua ʻoe i ka maʻi, hiki iā ʻoe ke ʻimi i ka lāʻau kūpono a mālama i kahi ola maikaʻi. Mai hopohopo, aia nā hopena i nā mea āpau, a inā he mau nīnau kāu, e nīnau i kāu mau kauka.

👩🏽‍⚕️ Nā nīnau hou aku (FAQs)

💬 He maʻi anei ʻo Syringomyelia kahi e hoʻokumu ʻia ai kahi puʻupuʻu i loko o ka iwi kuamoʻo?

ʻAʻole he puʻupuʻu! He maʻi neurological weliweli loa kēia. He kūlana weliweli kēia kahi e hana ʻia ai kahi lua ma waenakonu o ke aʻalolo nui (Spinal cord) i loko o ko kākou iwi kuamoʻo, kahi e piha ai i ka wai (ka wai o ka lolo) a lilo i mea nui (Syrinx). I ka ulu ʻana o kēia lua i piha i ka wai, ua luku loa ʻia ko kākou mau aʻalolo i kēlā me kēia lā.

💬 Pehea ka manaʻo o ko kākou kino inā ua piha ko kākou kua i ka wai e like me kēia?

ʻO ka hōʻailona weliweli loa o kēia, ʻo ia ka nalowale loa ʻana o kou mau lima a me kou umauma i ko lākou ʻano o ka 'wela a me ke anu' (ʻoiai inā loaʻa iā ʻoe ka wai wela, ʻaʻole ia e ʻeha). Me kēia, loaʻa iā ʻoe ka ʻeha hiki ʻole ke hoʻomanawanui ma kou ʻāʻī, nā lima, ka umauma, a me ke kua, a lilo nā ʻiʻo o kou mau lima i mea maneʻo a make.

💬 Pono anei au e hana i ke ʻoki kino e wehe ai i kēia cyst (lua) ma koʻu kua?

ʻAʻole pono nā kānaka a pau i ke ʻoki kino (inā ʻaʻohe o lākou mau hōʻailona, ​​kali wale lākou). Akā inā holomua ka maʻi a e luku ʻia nā aʻalolo, a laila pono ʻoe e hana i ke ʻoki kino nui (ʻoki kino Shunt / Decompression) ma ka lolo a i ʻole ke kaula spinal e hana i ala no ka wai i hōʻiliʻili ʻia e kahe i waho.


ʻO Syringomyelia, kaula kuamoʻo, ʻeha kua, syrinx, CSF, maʻi neurological, Chiari malformation

Frequently Asked Questions (FAQ)

He aha nā hoʻokolohua e hana ʻia e ʻike ai i kēia maʻi?

Inā kānalua kāu kauka i ka syringomyelia, hiki iā ia ke kauoha i hoʻokahi a ʻoi aku paha o kēia mau hoʻokolohua:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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