Ke ala aʻe nei ʻoe i ke kakahiaka i kekahi manawa a pehu a puni kou mau maka? A i ʻole pehu kou mau wāwae a me nā kuʻekuʻe wāwae, e paʻakikī ai ke kau i kou mau kāmaʻa? Ua ʻike anei ʻoe ua ʻoi aku ka huʻa o kou mimi ma mua o ka maʻamau? ʻAʻole kēia he mau mea wale nō. Aia paha he pilikia me kou mau puʻupaʻa ma hope o kēia mau hōʻailona. I kēia lā, ke kamaʻilio nei mākou e pili ana i kahi kūlana koʻikoʻi lapaʻau e kū mai ana mai ka hui pū ʻana o nā hōʻailona e like me kēia. ʻO ia ka Nephrotic Syndrome.
He aha maoli ka Nephrotic Syndrome?
ʻO ka mea mua e hoʻomaopopo ai, ʻaʻole kēia he maʻi kikoʻī. Pili ia
i kahi hōʻiliʻili o nā hōʻailona e hiki ke kū mai i ka wā e hana pono ʻole ai ko kākou mau puʻupaʻa. E noʻonoʻo i ko kākou mau puʻupaʻa e like me kahi kānana ʻenehana kiʻekiʻe. ʻO kā lākou hana nui ka hoʻomaʻemaʻe ʻana i ko kākou koko a wehe i nā ʻōpala makemake ʻole ʻia a me ka wai keu mai ke kino e like me ka mimi. Hana ʻia kēia hana kānana e kahi pūnaewele maikaʻi loa o nā kīʻaha koko i loko o nā puʻupaʻa. Kāhea mākou i kēia mau mea he glomeruli. I ke kanaka olakino, ʻaʻole ʻae kēia ʻōnaehana kānana i nā mea e like me nā protein e pono ai ke kino e hele ma waena. Hoʻopaʻa ʻia lākou i loko o ke koko. Akā inā ua hōʻino ʻia kēia mau kānana maikaʻi i kapa ʻia ʻo glomeruli,
nui ka nui o nā protein e pono ai ke kino e hele ma waena o lākou a hoʻomaka e puka i waho me ka mimi. ʻO ia ka mea a mākou e kapa nei he nephrotic syndrome. Hiki i kēia kūlana ke hoʻopilikia i nā pākeke a me nā keiki, akā ʻo ka nūhou maikaʻi he lāʻau lapaʻau no ia.
No ke aha lā e kū mai ai kēia kūlana?
Hiki ke hoʻokaʻawale ʻia nā kumu o kēia i ʻelua mau ʻāpana nui.
Nā kumu e hoʻopilikia wale i nā puʻupaʻa (Nā Kumu Nui)
ʻO ke ʻano kēia, kū mai ka maʻi nephrotic ma muli o kahi maʻi e kū mai ana i loko o nā puʻupaʻa ponoʻī, me ka ʻole o ka mana o kekahi maʻi ʻē aʻe.
- Ka Maʻi Hoʻololi Liʻiliʻi: ʻO kēia ke kumu nui o ka nephrotic syndrome i nā keiki . ʻOiai ke ʻano maʻamau o ko lākou ʻiʻo puʻupaʻa ma lalo o kahi microscope, ua pilikia ke kaʻina kānana. Ua manaʻo ʻia ua hana ʻia e nā maʻi viral , nā maʻi allergies , a i ʻole kekahi mau lāʻau lapaʻau (ʻoi aku hoʻi nā lāʻau ʻeha e like me NSAID ).
- ʻO Focal Segmental Glomerulosclerosis (FSGS): He kūlana kēia kahi e lilo ai nā ʻāpana kānana (glomeruli) o nā puʻupaʻa i ʻeha. ʻO kēia ke kumu nui o ka nephrotic syndrome i nā pākeke . Hiki i nā virus e like me ka HIV , kekahi mau lāʻau lapaʻau, nā kumu genetic, a me ka momona ke kumu o kēia kūlana.Nui nā mea, e like me ke koko kiʻekiʻe, hiki ke hoʻopilikia i kēia.
- ʻO ka Membranous Nephropathy: He mānoanoa kēia o nā membrane o ka glomeruli. Hiki ke hana ʻia kēia e nā maʻi e like me ke kanesa, malaria, hepatitis B, a me lupus.
Nā kumu lua o ka hōʻino ʻana o ka puʻupaʻa ma muli o nā maʻi ʻē aʻe
ʻO ke ʻano kēia, loaʻa ka maʻi nephrotic i ka wā e hōʻino ʻia ai nā puʻupaʻa ma ke ʻano he hopena ʻaoʻao o kekahi maʻi ʻē aʻe i ke kino.
- ʻO ka maʻi diabetes : ʻO ka maʻi diabetes ke kumu lua maʻamau o ka maʻi nephrotic i nā pākeke. ʻO ka maʻi diabetes i kāohi ʻole ʻia e hiki ke alakaʻi i ka hōʻino ʻana o nā puʻupaʻa (diabetic nephropathy).
- Lupus: He maʻi mau kēia o ka ʻōnaehana pale e hiki ai ke hōʻeha nui i nā puʻupaʻa.
- Amyloidosis: Hiki i kahi ʻano protein i kapa ʻia ʻo amyloid ke kūkulu i loko o ke koko, e hōʻino ai i ka puʻupaʻa.
He aha nā hōʻailona e loaʻa paha iā ʻoe?
ʻEhā mau hōʻailona nui o ka nephrotic syndrome. No ka hoʻomaopopo pono ʻana i kēia mau mea, e nānā i ka papa ma lalo.
| Hōʻailona | I ka ʻōlelo maʻalahi... |
|---|
| Proteinuria | Ka hoʻokuʻu nui ʻia ʻana o ka protein i loko o ka mimi. Hiki i kēia ke hana i ka mimi e ʻike ʻia he huʻa ma mua o ka maʻamau . |
| Hyperlipidemia | Hoʻonui ʻia ka momona koko a me nā pae kolesterol . Ke nalowale ke kino i ka protein, hana ke akepaʻa i ka momona a me ka kolesterol hou aku, ʻo ia ke kumu nui o kēia . |
| Pehu kino (Edema) | Pehu, ʻoi aku hoʻi ma nā wāwae, nā kuʻekuʻe wāwae, a me nā wāwae . I kekahi manawa, pehu paha nā lima a me ke alo, ʻoi aku hoʻi a puni nā maka i ke kakahiaka. |
| Hypoalbuminemia | ʻO ka emi ʻana o kahi ʻano protein i kapa ʻia ʻo albumin i loko o ke koko. ʻO kēia protein ka mea e mālama ai i ka wai i loko o nā kīʻaha koko. Ke hoʻokuʻu ʻia i loko o ka mimi, kahe ka wai i loko o nā ʻiʻo a hoʻomaka ke kino e pehu. |
Pehea ka hopena o kēia kūlana i nā keiki ʻōpio?
He maʻi laha ʻole ka maʻi nephrotic i nā keiki ʻōpio. Eia nō naʻe, inā loaʻa i kahi keiki ke ʻano, ʻokoʻa iki paha nā hōʻailona.
- Ka pehu ʻana a puni nā maka, ʻoiai i ke ala ʻana i ke kakahiaka.
- Ka pehu ʻana o ka maka, nā lima, nā wāwae, a me ka ʻōpū.
- Mimi huʻa .
- Manaʻo nui a luhi hoʻi ma mua o ka maʻamau.
ʻO nā Corticosteroids ka lāʻau lapaʻau i hoʻohana pinepine ʻia no nā keiki. Hiki i kēia ke hoʻomalu i nā hōʻailona a hoʻoulu i ka hoʻomaha.
E ke kauka, pehea ʻoe e ʻike ai i kēia?
Inā loaʻa iā ʻoe kēia mau hōʻailona, he mea nui e ʻike koke i ke kauka. E nīnau mua ke kauka iā ʻoe e pili ana i kāu mau hōʻailona. A laila,
- Hoʻāʻo Mimi: He mea nui kēia no ke ana ʻana i ka nui o ka protein i hoʻokuʻu ʻia i loko o ka mimi.
- Nā Hoʻāʻo Koko: E nānā i ka cholesterol koko, nā pae albumin, a me nā hana puʻupaʻa ʻē aʻe.
- Biopsy Kidney: I kekahi mau hihia, pono paha e lawe i kahi ʻāpana liʻiliʻi loa o ka ʻiʻo mai ka puʻupaʻa a nānā iā ia ma lalo o kahi microscope. ʻO kēia ka mea e kōkua ai e hoʻoholo pono i ke kumu o ka hōʻino ʻana o ka puʻupaʻa.
ʻOi loa aku inā hui pū nā hōʻailona o ka nui o ka protein ma mua o 3.5 grams i kēlā me kēia lā i loko o ka mimi, ka haʻahaʻa o ka albumin i loko o ke koko, a me ka pehu ʻana o ke kino, ʻo ia ke kumu nui no ka ʻike ʻana i ka maʻi nephrotic.
He aha nā pilikia e hiki mai ana inā ʻaʻole mālama ʻia?
Inā ʻaʻole mālama pono ʻia kēia maʻi, hiki iā ia ke alakaʻi i nā pilikia olakino koʻikoʻi ʻē aʻe.
- ʻO ke kiʻekiʻe o ka cholesterol a me ka pilikia o ka maʻi puʻuwai: ʻO ke kiʻekiʻe o ka momona koko a me nā pae cholesterol e hoʻonui i ka pilikia o ka maʻi puʻuwai.
- Ke koko kiʻekiʻe: Ke hōʻino ʻia nā puʻupaʻa, emi iho ko lākou hiki ke wehe i ka sodium (paʻakai) a me ka wai mai ke kino, kahi e piʻi ai ke koko.
- Nā ʻūpā koko:Ma muli o ka hoʻokuʻu ʻia ʻana o nā protein e pale ai i ke kāpili ʻana o ke koko i loko o ka mimi, piʻi aʻe ka pilikia o ke kāpili ʻana o ke koko i loko o ke kino.
- Nā maʻi: I ka nalowale ʻana o nā protein e like me nā immunoglobulins, he mea nui no ka ʻōnaehana pale o ke kino, ʻoi aku ka nui o ka loaʻa ʻana o nā maʻi e like me ka niumonia.
- Ka Holo ʻole ʻana o ka Puʻupaʻa: Inā waiho ʻole ʻia no ka manawa lōʻihi, hiki i nā puʻupaʻa ke hāʻule loa, e pono ai ka dialysis a i ʻole ka hoʻoili ʻana i ka puʻupaʻa e ola.
He aha nā lāʻau lapaʻau no kēia?
ʻO ka hoʻolālā lapaʻau e pili ana i ke kumu nui o kāu nephrotic syndrome.
Nā ʻano lāʻau lapaʻau
Hiki i kāu kauka ke kuhikuhi i nā lāʻau lapaʻau penei:
- Nā lāʻau lapaʻau koko: ʻO nā lāʻau lapaʻau e like me nā ACE inhibitors a me nā ARBs e hōʻemi i ke kaomi ma luna o nā puʻupaʻa a hoʻemi i ka hoʻokuʻu ʻia ʻana o ka protein i loko o ka mimi.
- Nā Diuretics: Kāhea ʻia hoʻi ʻo "nā pila wai," kōkua kēia i ka hōʻemi ʻana i ka pehu ʻana i loko o ke kino.
- Nā lāʻau hoʻohaʻahaʻa kolesterol.
- Nā lāʻau hoʻokahe koko (Anticoagulants): E hōʻemi i ka pilikia o ke kāpili ʻana o ke koko.
- Nā lāʻau lapaʻau e kāohi ana i ka pale ʻana: ʻO nā lāʻau lapaʻau e like me corticosteroids e kāohi i ka hana o ka ʻōnaehana pale a hōʻemi i ka hōʻino ʻana i nā puʻupaʻa.
ʻO kēia ke kumu he mea nui ka kaohi ʻana i ka ʻai
Me ka lāʻau lapaʻau, he mea nui loa ka ʻai ʻana i ka mālama ʻana i kēia maʻi.
- E hōʻemi i ka paʻakai (sodium): ʻO ka ʻai nui ʻana i ka paʻakai hiki ke hoʻopaʻa i ka wai, pehu, a me ke koko kiʻekiʻe. E pale i nā meaʻai kiʻekiʻe i ka paʻakai, e like me nā sausage, nā ʻiʻo i hoʻōla ʻia, nā mea kanu i loko o ka pahu, nā sopa, nā biscuits, a me nā mea ʻono.
- E hōʻemi i ka momona a me ka cholesterol: E hahai i kahi papaʻai haʻahaʻa i ka momona saturated a me ka cholesterol.
- E kaupalena i nā wai: I kekahi manawa e haʻi aku kāu kauka iā ʻoe e kaupalena i ka nui o ka wai āu e inu ai i kēlā me kēia lā.
E hoʻomanaʻo, pono e mālama ʻia kēia mau kapu meaʻai e like me nā kuhikuhi i hāʻawi ʻia e kāu kauka a meaʻai meaʻai paha.
Leka Lawe-Home
- ʻO ka maʻi Nephrotic kahi hōʻiliʻili o nā hōʻailona i hoʻokumu ʻia e ka hōʻino ʻana i ka ʻōnaehana kānana palupalu i loko o nā puʻupaʻa.
- ʻO nā hōʻailona nui ka pehu ʻana o ke kino (ʻoi aku hoʻi ma nā wāwae a puni nā maka), ka mimi huʻa (ma muli o ka nui o ka protein), a me ke kiʻekiʻe o ka cholesterol koko.
- Hiki ke hana ʻia kēia kūlana e nā maʻi ʻē aʻe e like me ka maʻi diabetes a me ke koko kiʻekiʻe.
- Ma waho aʻe o ka lāʻau lapaʻau no ka mālama ʻana, he mea nui loa hoʻi e hahai i kahi ʻai haʻahaʻa i ka paʻakai a me ka momona.
- Inā loaʻa iā ʻoe kēia mau hōʻailona, mai hoʻowahāwahā iā lākou . E ʻike i kāu kauka i ka hikiwawe loa no ka ʻōlelo aʻoaʻo kūpono a me ka lāʻau lapaʻau.
ʻO ka maʻi Nephrotic, Nephrotic Syndrome, maʻi puʻupaʻa, pehu ʻana, protein i loko o ka mimi, mimi foamy, maʻi puʻupaʻa ma Sinhala, cholesterol
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