E noʻonoʻo ʻaʻole hiki iā ʻoe ke kāohi i kou mau lima a i ʻole kou mau wāwae. Neʻe kou mau ʻāpana kino me ka makemake ʻole, me he mea lā e hula ana kekahi. He ʻano maʻi kēia i loaʻa i kekahi poʻe. Manaʻo paha kekahi e ʻike ana i kēia e hula wale ana lākou. Loaʻa ka inoa ʻo Chorea mai ka huaʻōlelo Helene no "hula". Akā no ke kanaka e ʻeha nei i kēia, ʻaʻole ia he mea maʻalahi. E aʻo hou kākou e pili ana i kēia lā.
He aha maoli ʻo Chorea?
I ka ʻōlelo maʻalahi, he maʻi neʻe ka Chorea. Hoʻokumu ʻia ia e kahi hana hewa i loko o ka basal ganglia, kahi ʻōnaehana nerve waena i loaʻa i loko o ka lolo e kaohi ana i ka neʻe ʻana. Hoʻoulu kēia i nā neʻe ʻana o nā lima, nā wāwae, a me ke alo i hana ʻia me ka ʻole o kā mākou kaohi.
Hiki i kēia mau neʻe ʻana ke liʻiliʻi loa i kekahi manawa, e like me ka wili ʻana i mua a i mua. Manaʻo kekahi poʻe he pane hopohopo wale nō kēia. Akā i kekahi manawa hiki nō hoʻi ke lilo i neʻe wikiwiki a ʻino e kahe ana mai kekahi ʻāpana o ke kino a i kekahi ʻāpana.
He aha nā hōʻailona nui o kēia maʻi?
Aia kekahi mau hōʻailona kikoʻī a nā kauka e hoʻohana ai e ʻike i ka Chorea. Hiki i kēia ke lilo i hōʻailona e loaʻa paha iā ʻoe kēia maʻi.
| Hōʻailona | Ua wehewehe maʻalahi ʻia |
|---|---|
| Ka paʻa ʻana o ka wahine waiū | He paʻakikī i kēia poʻe ke hoʻopaʻa i ka ʻiʻo. Eia kekahi laʻana, inā ʻoe e paʻa i ko lākou lima, ʻaʻole lākou e paʻa pono, akā e ʻomi a hoʻokuʻu iā ia me he mea lā e waiū ana lākou. |
| ʻAlelo Jack-in-the-box | Ke noi ʻia e hoʻopuka i kona alelo, hoʻopuka koke ʻo ia i waho a laila huki hou i loko. Ua like ia me ka lele ʻana ma luna o kahi mea pāʻani mai loko mai o ka pahu. Ua kapa ʻia hoʻi kēia ʻo ke alelo o Harlequin. |
| Ka hele ʻokoʻa | He ʻano hele wāwae ko ka poʻe me ka chorea. Hiki i kahi neurologist ke ʻike i ke kūlana ma ka nānā ʻana i kēia ʻano hele wāwae. |
Nā ʻano chorea ʻē aʻe
Ma waho aʻe o nā ʻano nui o ka chorea, aia kekahi mau maʻi neʻe ʻē aʻe e pili ana me ia.
- ʻAthetosis: He ʻano chorea lohi kēia. Maanei, lilo nā neʻe i ʻano ʻoniʻoni a wili.
- Choreoathetosis: He hui pū ʻana kēia o Chorea a me Athetosis. Maanei, hana ʻia nā neʻe ʻana ma kahi wikiwiki a me ka ikaika kūpono.
- Ballism/Ballismus: He ʻano chorea wikiwiki loa kēia a ʻino hoʻi. Me he mea lā e hoʻolei ana kekahi i ko lākou mau lima a me nā wāwae.
He aha nā kumu o ka chorea?
E like me kā mākou i kūkākūkā ai ma mua, ʻo ke kumu o kēia he ʻāpana o ka lolo i kapa ʻia ʻo ka basal ganglia. Manaʻo nā kānaka ʻepekema e loaʻa ka chorea ke loaʻa i kēia ʻāpana ka nui o kahi kemika i kapa ʻia ʻo dopamine, kahi e kōkua ai i ka hana aʻalolo. He mea nui ka Dopamine no ko mākou kino, akā inā nui loa, hiki iā ia ke hana i nā pilikia e like me kēia.
ʻO ke kumu nui a ʻike nui ʻia o ka chorea ʻo ia ka maʻi Huntington . He maʻi hoʻoilina kēia.
Eia nō naʻe, nui paha nā kumu ʻē aʻe no kēia, ʻo kekahi o ia mau mea he mea kakaikahi loa.
- Fiva Rheumatic: Hiki i kekahi mau keiki ke loaʻa i kahi kūlana chorea no ka manawa pōkole inā loaʻa iā lākou ka fiva rheumatic ma hope o ka maʻi ʻāʻī (strep throat) a i ʻole ka fiva ʻulaʻula.
- Nā maʻi Autoimmune : Hiki ke loaʻa kēia ʻano i nā poʻe me nā maʻi e like me lupus.
- Ka pōʻino o ka lolo: Hiki ke hana ʻia ʻo Chorea e nā kūlana e like me ka ʻōpū o ka lolo a i ʻole ka hahau.
- Nā maʻi hormonal a me ka metabolic: Hiki ke hana ʻia kēia e nā kūlana e like me ka hypothyroidism.
- ʻO kekahi mau lāʻau lapaʻau: Hiki ke hana ʻia ʻo Chorea ma ke ʻano he hopena ʻaoʻao o kekahi mau lāʻau lapaʻau, ʻoi aku hoʻi nā mea i hoʻohana ʻia no ka maʻi o Parkinson.
E aʻo kākou e pili ana i ka hōʻoia ʻana a me ka mālama ʻana.
ʻO ka mea mua a ke kauka e hana ai, ʻo ia ke nānā i kāu mau hōʻailona. A lailaʻO ka pilikia, ʻo ia ka ʻimi ʻana i ke kumu o ka maʻi , hiki ke kōkua ʻia e nā scan lolo (nā hoʻāʻo kiʻi) a me nā hoʻāʻo koko.
Eia kekahi, e nīnau pono kāu kauka e pili ana i nā lāʻau lapaʻau āpau āu e lawe nei, no ka mea, i kekahi manawa hiki ke hana ʻia kēia e ka lāʻau lapaʻau.
Ke loaʻa ke kumu, e hoʻoholo kāu kauka inā pono ʻoe i ka lāʻau lapaʻau a i ʻole. I kekahi mau hihia, ʻoiai inā i hoʻokumu ʻia e ka lāʻau lapaʻau, e nalowale ke ʻano chorea iā ia iho ke hoʻōki ʻia a hoʻololi ʻia paha ka lāʻau lapaʻau. A i ʻole, e mālama ʻia ke kumu kumu o ke ʻano.
Aia nā lāʻau lapaʻau e hiki ke kōkua i ka kaohi ʻana i kēia mau neʻe hiki ʻole ke kaohi. Hana pinepine kēia mau lāʻau lapaʻau ma ke ālai ʻana i ka hana o ka dopamine i loko o ka lolo. ʻOiai ke hoʻohana ʻia nei ke ʻoki lolo a me ka hoʻoulu ʻana i ka lolo hohonu (DBS) ma ke ʻano he lāʻau lapaʻau, ʻaʻole lākou i hoʻohana pinepine ʻia ma muli o ka hiki ke loaʻa nā pilikia.
ʻO ka maʻi o Huntington a me Chorea
I ke kamaʻilio ʻana e pili ana i ka chorea, ʻaʻole hiki iā mākou ke pale aku i ka haʻi ʻana i ka maʻi Huntington. ʻO kēia ke kumu kaulana loa o ka chorea. Akā, he maʻi kakaikahi loa ia, e hoʻopilikia wale ana i hoʻokahi i loko o 10,000 a i ʻole 20,000 poʻe.
He ʻokoʻa kēia maʻi mai nā kumu ʻē aʻe no ka mea ʻaʻohe ona lāʻau lapaʻau kūikawā a holomua ka maʻi i ka hala ʻana o ka manawa a alakaʻi i ka make . Hana ʻia kēia maʻi ke luku ʻia nā ʻāpana o ka basal ganglia i loko o ka lolo.
Hoʻomaka mua ʻo Chorea ma waena o 35 a me 40 mau makahiki. ʻOiai hoʻomaka pū nā pilikia noʻonoʻo i ka manawa like, ʻaʻole maopopo loa ia i nā pae mua.
ʻO ka ʻaoʻao genetic o ka maʻi Huntington
No ka mea he maʻi hoʻoilina ia, ʻo kahi keiki i hānau ʻia e kahi makuahine a makua paha me ka maʻi Huntington he 50% ka manawa e loaʻa ai ka maʻi. Ua ʻike ʻia ka gene kīnā e ke kanaka ʻepekema i ka makahiki 1993.
I kēia lā, hiki ke loaʻa ka ʻike e pili ana i kēia maʻi ma o ka hoʻāʻo genetic .
- Inā loaʻa iā ʻoe nā hōʻailona, e hōʻoia he maʻi Huntington ia.
- Inā loaʻa kēia maʻi i kekahi o kou ʻohana (nā mākua, nā hoahānau), e ʻike inā e loaʻa pū iā ʻoe kēia maʻi i ka wā e hiki mai ana.
- E ʻike inā loaʻa kēia maʻi i ka pēpē i loko o ka ʻōpū i ka wā hāpai (hoʻāʻo prenatal).
Akā ma mua o ka hana ʻana i ia ʻano hoʻokolohua genetic, he mea nui loa ia e ʻimi i ka ʻōlelo aʻoaʻo genetic no ke ʻano e hana ai me nā hopena. No ka mea, he hoʻoholo kēia e hoʻopilikia i kou ola. No laila, pono ʻoe e kamaʻilio me ke kauka ʻike e pili ana i ia mea a noʻonoʻo pono ma mua o ka hana ʻana i ia ʻano hoʻokolohua.
Leka Lawe-Home
- He maʻi neʻe ka Chorea i hana ʻia me kou kaohi ʻole. Hoʻokumu ʻia ia e kahi pilikia ma ka lolo.
- Hiki ke hana ʻia kēia e nā lāʻau lapaʻau, nā maʻi hoʻoilina (e like me ka maʻi Huntington), a me nā kūlana olakino ʻē aʻe.
- Inā loaʻa iā ʻoe a i ʻole kekahi mea āu i ʻike ai i kēia mau hōʻailona, mai hoʻokaʻulua a ʻike i ke kauka kūpono, ʻoi aku hoʻi ka neurologist .
- ʻO ka ʻike pololei ʻana i ka maʻi ka hana mua i ka mālama kūpono.
- Inā he kānalua no kahi maʻi hoʻoilina e like me Huntington, he mea nui loa ia e ʻimi i ka ʻōlelo aʻoaʻo genetic ma mua o ka hoʻāʻo genetic.











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