E noʻonoʻo ua loaʻa iā ʻoe ke anu a ʻeha paha ka ʻōpū i kekahi mau lā i hala aku nei a ke manaʻo nei ʻoe ua ʻoi aku ka maikaʻi. Akā i kēia manawa ua manaʻo ʻoe ua pōkole iki kou ʻike, ʻike ʻoe i nā mea ma nā ʻāpana ʻelua. Manaʻo ʻoe ua kūpaʻa ʻole ʻoe i kou hele ʻana, ua hihia kou mau wāwae. Inā hana ʻia kekahi mea e like me kēia, e makaʻu loa nā mea a pau, ʻeā? I kēia lā ke kamaʻilio nei mākou e pili ana i kahi maʻi e hoʻoulu ai i nā hōʻailona e like me kēia, kahi i lohe ʻole ʻia e ka poʻe he nui, akā he mea nui loa ia e ʻike. ʻO ia ka Miller Fisher Syndrome.
I ka ʻōlelo maʻalahi, he aha ka Miller Fisher Syndrome?
He maʻi neurological laha ʻole ka Miller Fisher syndrome. Ua lohe paha ʻoe i ka Guillain-Barré syndrome (GBS). He maʻi nō hoʻi ia e hoʻouka ai kā mākou ʻōnaehana pale i ko mākou mau aʻalolo ponoʻī. He ʻano like ʻole ka Miller Fisher syndrome o GBS. He mea laha ʻole ia e pili ana ma waena o 1% a me 5% o nā maʻi GBS ma nā ʻāina Komohana. Eia nō naʻe, ma kekahi mau ʻāina ʻĀsia e like me Taiwan a me Iapana, ʻoi aku ka nui o ka helu. No laila hiki iā ʻoe ke hoʻomaopopo ʻaʻole kēia he maʻi o kēlā me kēia lā. Akā he mea nui loa ia e makaʻala i kēia.
No ke aha e hana ʻia ai kēia? He aha nā kumu?
ʻO kēia ka mea nui loa. Hoʻomohala ʻia ka maʻi Miller Fisher a me GBS ma muli o kahi maʻi e komo i loko o ko kākou kino.
I ka ʻōlelo maʻalahi, loaʻa i kā kākou ʻōnaehana pale ponoʻī, ʻo ia hoʻi ka ʻōnaehana pale, kahi "huikau" iki a ma kahi o ke kaua ʻana i ka maʻi, hoʻomaka ia e hoʻouka i ko kākou mau aʻalolo ponoʻī ma ke kuhihewa. ʻAʻole maopopo i nā kauka ke kumu o kēia. ʻIke pinepine ʻia kēia mau hōʻailona i loko o kekahi mau lā a i 4 mau pule o kahi maʻi, ʻoiai ka ʻeha ʻōpū e like me ka maʻi diarrhea, a i ʻole ka maʻi hanu (anu, flu). ʻO ka bacteria nui e hiki ai ke hana i kēia maʻi ʻo 'Campylobacter jejuni'. ʻO kēia ka mea maʻamau e hoʻoulu ai i nā ʻōpū ʻeha a me ka diarrhea. Eia kekahi, aia kekahi mau virus e hiki ke hana i kēia maʻi:
- ka maʻi Zika
- ʻO ka maʻi pale ʻole kanaka ( HIV )
- ʻO ka maʻi Epstein-Barr, ka mea e hoʻoulu ai i ka maʻi mononucleosis e like me ke kuni.
He aha nā hōʻailona? Pehea ʻoe e ʻike ai i kēia?
He nui ka poʻe e hele e ʻike i ke kauka
no ka mea e emi koke ana ko lākou ʻike i loko o kekahi mau lā a
he paʻakikī iā lākou ke hele . ʻEkolu mau hōʻailona nui o ka Miller Fisher syndrome. E hoʻomaopopo kākou i kēia mau mea ma kahi papa.
| ʻO ka hōʻailona nui | I ka ʻōlelo maʻalahi, he aha ka mea e hana ʻia? |
|---|
| Ka nāwaliwali o nā ʻiʻo maka (Ophthalmoplegia) | Loaʻa ka ʻike pālua, a lilo ia i mea paʻakikī ke kaohi a kuhikuhi i nā maka i ke kuhikuhi i makemake ʻia. |
| Ka nalowale o ke kaulike (Ataxia) | Kūlou koʻu wāwae i koʻu hele ʻana, manaʻo wau ua hewa koʻu kaulike. He paʻakikī iaʻu ke hoʻonohonoho i koʻu mau lālā. |
| ʻAreflexia | Nā mea e like me ke kuʻi ʻana o ke kauka i kou kuli me ka hāmare liʻiliʻi, ʻaʻole e neʻe kou wāwae. Ua nalowale nā reflexes o ke kino. |
Ma waho aʻe o kēia mau hōʻailona nui ʻekolu, hiki i kekahi poʻe ke hōʻike i nā hōʻailona ʻē aʻe:
He mea nui: Inā hele pū kēia mau hōʻailona me ka nāwaliwali o kou mau lālā a me nā ʻiʻo hanu, he ʻano paha ia i kapa ʻia ʻo GBS-MFS overlap syndrome. ʻO ka hōʻailona nui o GBS ka nāwaliwali e hoʻomaka ana ma nā wāwae a laha a puni ke kino.
Pehea e ʻike ai ke kauka i kēia?
He mea paʻakikī iki ke ʻike pololei i kēia maʻi. No ka mea, he nui nā maʻi neurological ʻē aʻe i loaʻa nā hōʻailona like. No ka laʻana, nā maʻi e like me ka 'Basal meningitis', 'Botulism', 'Brainstem stroke', 'Myasthenia Gravis'. No laila, e nānā pono ke kauka iā ʻoe, e nīnau e pili ana i kāu mau hōʻailona a me nā maʻi i hala koke aku nei. A laila, e hana ʻo ia i kekahi mau hoʻokolohua e hōʻoia i ka maʻi.
| Hoʻāʻo | I ka ʻōlelo maʻalahi, he aha kāu e hana ai/ʻike ai me ia? |
|---|
| ʻO ke kī ʻana o ka lumbar | Lawe ʻia kahi liʻiliʻi o ka wai a puni kou iwi kuamoʻo (wai cerebrospinal) a nānā ʻia no nā pae kiʻekiʻe o ka protein. Hoʻonui pinepine ʻia kēia i nā poʻe maʻi Miller Fisher. |
| Hoʻāʻo koko | Hoʻāʻo ʻia ke koko no ke alo o kahi antibody i kapa ʻia ʻo `anti-GQ1b`, nona ka mea kūikawā no kēia maʻi. Hiki ke ʻike ʻia kēia antibody i loko o 95% o nā maʻi. |
| Haʻawina Hoʻokele Aʻalolo (EMG) | Hoʻohana ʻia kahi au uila liʻiliʻi loa a ʻeha ʻole e ana i ka maikaʻi o ka hana ʻana o kou mau aʻalolo a me nā ʻiʻo. Hōʻike kēia maʻi i kekahi mau ʻano ʻē i loko o nā aʻalolo. |
| MRI Scan | Hana ʻia kēia hoʻāʻo e kāpae i nā kūlana ʻē aʻe, e like me ka hahau ʻana. Ma Miller Fisher, hōʻike pinepine ka MRI i nā hopena maʻamau. |
He aha nā lāʻau lapaʻau no kēia? Pehea ka lōʻihi e hoʻōla ai?
ʻO ka mea mua, ʻaʻohe 'lāʻau lapaʻau' kikoʻī e hiki ke hoʻōla loa i kēia maʻi.
Eia nō naʻe, aia nā lāʻau lapaʻau kūpono loa e hiki ke kōkua i ka kaohi ʻana i nā hōʻailona a kōkua iā ʻoe e hoʻōla koke. ʻO ka mea maʻamau, hoʻokomo ʻia ke kanaka me kēia mau hōʻailona i ka haukapila. ʻO kēia ke nānā pono ʻana i nā hihia koʻikoʻi o ka maʻi GBS. No ka mea, hiki i ka GBS ke hoʻoweliweli i ke ola i kekahi manawa. ʻElua mau ʻano nui e hoʻohana ʻia ma ke ʻano he lāʻau lapaʻau: 1.
Intravenous Immunoglobulin (IVIg): He lāʻau lapaʻau wai e like me ka saline kēia i hāʻawi ʻia i loko o kahi vein. Loaʻa iā ia nā antibodies i hoʻomaʻemaʻe ʻia i hoʻokaʻawale ʻia mai ka plasma koko o nā tausani o nā kānaka olakino. Hāʻawi mau ʻia kēia no kahi o 5 mau lā. 2.
Plasma Exchange (Plasmapheresis): He hana paʻakikī kēia. I ka ʻōlelo maʻalahi, lawe ʻia kahi koko liʻiliʻi mai kou kino, wehe kahi mīkini kūikawā i ka plasma pilikia (ka ʻāpana e loaʻa ana nā antibodies e hoʻouka i nā aʻalolo) a hoʻololi iā ia me kāu mau cell koko ponoʻī me ka plasma pani. Hana ʻia kēia ma kahi o 5 mau manawa i loko o ʻelua pule. Inā nāwaliwali loa kou mau ʻiʻo ma hope o kēia mau lāʻau lapaʻau,
pono paha ʻoe i ka physiotherapy e hoʻoikaika hou iā lākou.He mea pono ia. No ka ho'ōla hou ʻana, maʻamau ma waena o 8 a me 12 mau pule no ka ho'ōla maikaʻi ʻana.
Ho'ōla piha ka hapa nui o ka poʻe i loko o 6 mau mahina. ʻOi aku ka liʻiliʻi o ka hoʻi hou ʻana ma mua o 3%. No laila, ʻo ka ʻike mua a me ka mālama ʻana nā mea nui loa.
Leka Lawe-Home
- He maʻi laha ʻole ka Miller Fisher syndrome i ka wā e hoʻouka ai ko kākou ʻōnaehana pale ponoʻī i ko kākou mau aʻalolo ma muli o kahi maʻi i hala koke aku nei.
- ʻO nā hōʻailona nui ka nāwaliwali o nā ʻiʻo maka ( ʻike pālua), ka nalowale o ke kaulike (paʻakikī i ka hele wāwae), a me ka nalowale o nā reflexes.
- Inā loaʻa koke iā ʻoe a i ʻole kekahi āu i ʻike ai kēia mau hōʻailona, e ʻike koke i ke kauka. Mai hopohopo, akā, mai hoʻokaʻulua pū kekahi.
- He kūlana kēia e hiki ke mālama ʻia me ka hoʻokipa ʻia ʻana i ka haukapila a me ka hoʻōla kino , a ua hoʻōla piha ka hapa nui o ka poʻe.
ʻO ka Miller Fisher Syndrome, Guillain-Barré syndrome, nā maʻi Neurological, ka nalowale o ka ʻike, ka paʻakikī o ka hele wāwae, GBS, nā maʻi Autoimmune
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