Sɔntɛnde, yu kin gɛt pen na yu chɛst wantɛm wantɛm ɛn i nɔ kin izi fɔ yu fɔ blo? If yu gɛt dɛn sik ya wit kɔf ɛn fiva, mɔ if yu gɛt wan sik we dɛn kɔl
Siklɔs Sɛl Disease (SCD) , nɔ tek am layt. Dɛn sayn ya kin bi sayn fɔ wan sik wae gɛt mɔr siriɔs sik wae dɛn kɔl Acute Chest Syndrome. Nɔ wɔri, wi go tɔk bɔt dis klia ɛn simpul we tide.
Wetin na Akyu Chɛst Sindrom? Fɔ tɔk am simpul wan...
Okay, naw luk. dis `Acute Chest Syndrome` na wan siriכs
kכmplikεsh כn fכ sikεl sεl sik (`SCD`) . Fɔ tɔk am simpul wan, na we yu gɛt chɛst pen, kɔf, fiva, ɔksijɛn lɛvɛl smɔl na yu blɔd, ɛn tin dɛn we nɔrmal, spɛshal wan wata, kin bigin fɔ gɛda na di lכng tisu (`lung infiltrates`).
Dis sik kin bi siriɔs wan kwik kwik wan . infakt, dis `Acute Chest Syndrome` na wan big tin we kin mek pipul dεn go na כspitul εn sכmtεm dεn kin day fכ pipul dεm we gεt sik sεl sik . So, i rili impɔtant fɔ mek wi no bɔt dis.
Naw yu kin de wɔnda wetin na Siklɔs Sɛl Disease (SCD). Lɛ wi mɛmba yu smɔl bɔt am. Na
sik we pɔsin kin gɛt frɔm in jɛnɛtiks . Dat min se na tin we pɔsin kin gɛt frɔm dɛn gret gret granpa dɛn. I kin afɛkt di prɔtin we de na wi rɛd blɔd sɛl dɛn we dɛn kɔl
ɛmoglobin . Pan ɔl we pɔsin we gɛt wɛlbɔdi in rɛd blɔd sɛl dɛn kin rawnd, di rɛd blɔd sɛl dɛn we pɔsin we gɛt SCD gɛt kin shep lɛk sikɛl (lɛk kres). So dɛn sɛl dɛn ya we tan lɛk sikl nɔ kin ebul fɔ pas na wi tint blɔd vesel dɛn izi wan. Dɔn, di ɛmoglobin nɔ kin ebul fɔ kɛr ɔksijɛn go ɔlsay na di bɔdi fayn fayn wan. Dis na di men prɔblɛm wit SCD.
Aw kɔmɔn tin na Akyu Chɛst Sindrom?
infakt, `Acute Chest Syndrome` na
wan kכmכn kכndyushכn pan pipul dεm we gεt sikl sεl sik (`SCD`). Akɔdin to sɔm statystik,
lɛk af pan pipul dɛm wae gɛt `SCD` go gɛt dis sik at le wan tɛm na dɛn layf . Pan ɔl we i tan lɛk se i kin bɔku
pan yɔŋ pikin dɛn we ol bitwin 2 ɛn 4 ia ,
i kin tranga pasmak pan big pipul dɛn pas pikin dɛn . Dɛn dɔn si bak se pipul dɛm wae gɛt `SCD` ɛn
asma kin gɛt `Acute Chest Syndrome` pas ɔda pipul dɛm.
Wetin mek Akyu Chɛst Sindrom kin apin? Wetin na di tin dɛn we kin mek i apin?
Sayɛnsman dɛn stil nɔ ebul fɔ tɔk fɔ shɔ wetin rili de mek `Acute Chest Syndrome`. Bɔt dɛn biliv se i kin bi se na wan ɔ mɔ tin dɛn kin mek i apin. Lɛ wi tek wan luk pan wetin dɛn bi:
- Bon mכro nεkrכsis:Yu no se bon mɛro na di pat we saf ɛn we tan lɛk spɔnj insay wi big bon dɛn? if dis bon mכro day sכm we (we dεn kכl `nεkrכsis`), sכm sכm pat dεm pan am kin brok εn go insay di bכdi εn travul כlsay na di bכdi. if dεn pis dεm ya travul go na di lכng dεm, i kin mek `Acute Chest Syndrome`.
- Fεt εmbolizm: כda tin we kin mek di bon mכro dεm we wi bin dכn tכk bכt na fεt εmbolizm. Fɔ tɔk am simpul wan, dis na we wan fat patikyula (tink bɔt am lɛk wan drɔp ɔyl) kin stɔp na wan blɔd vesel ɛn blok di blɔd fɔ flɔ . Dis kin mek bak yu gɛt Akyu Chɛst Sindrom.
- Infεkshכn : Difrεn infεkshכn dεm, spεshal nyumonia we baktri כ vayrus , kin mek yu gεt akyu chεst sεndrכm. Infɛkshɔn na di men tin we kin mek dɛn gɛt dis sik pan yɔŋ pikin dɛn . Bɔt pan big pipul dɛn , i kin bi se na bikɔs ɔf fat ɛmbolizm.
Wetin na di sayn dɛm fɔ pɔrsin wae gɛt Acute Chest Syndrome?
Di sayn dɛm fɔ `Acute Chest Syndrome` kin difrɛn frɔm wan pɔrsin to ɔda pɔrsin. Sɔm difrɛns dɛn de, mɔ bitwin yɔŋ pikin dɛn ɛn big pipul dɛn.
Yכŋ pikin dεm kin sho di mכst sayn dεm fכ wan infεkshכn:
- Kɔf
- Fiva
- di ɔksijɛn we de na di blɔd we de go dɔŋ (hypoxemia) .
- Di rεt we yu de blo fast we nɔrmal (tachypnea) .
- Wheezing (na sawnd we de kɔmɔt na di chɛst we yu de blo) .
Big pipul dɛn kin gɛt dɛn sik ya bak. Apat frɔm dat, yu kin notis bak:
- Chɛst pen , mɔ we yu de blo, kin bɔku.
- siriכs, sכdεn pen na di an, lεg, εn bak we kכz fכ blok fכ fכlכ (dεn kכl am bak `vaso-occlusive crisis`).
- Fluid akyumyuleshכn na di lכng dεm εn di chεst (pleural effusion).
- I nɔ izi fɔ blo (dyspnea).
If yu gɛt wan ɔ mɔ pan dɛn sik ya, mɔ if yu gɛt SCD,
i rili impɔtant fɔ go to dɔktɔ wantɛm wantɛm .
Aw dɛn kin no se pɔsin gɛt Akyu Chɛst Sindrom? (Diagnosis) .
If yu no di `Acute Chest Syndrome` kwik kwik wan, dat kin sev pɔsin in layf.If yu gɛt SCD ɛn yu de na ɔspitul, dɛn go nid fɔ de wach yu ɔltɛm ɛn du di tɛst dɛn we yu nid. Bɔku tɛst dɛn de we kin ɛp dɔktɔ dɛn fɔ no dis prɔblɛm:
- Atrial blɔd gas analisis: Dis kin mek yu no di asid (pH), ɔksijɛn, ɛn kabon dayɔgzayd lɛvɛl na yu blɔd.
- Blɔd tɛst: If yu kɔnt ɔl yu blɔd, dat kin mek yu no bɔt yu rɛd blɔd sɛl dɛn, wayt blɔd sɛl dɛn, ɛn yu pletlɛt dɛn.
- Chɛst X-ray: Dɛn kin yuz dis fɔ chɛk fɔ si if pɔsin gɛt infɛkshɔn na di lɔng ɔ if dɛn nɔmal tin dɛn (infiltrates) we wi bin dɔn tɔk bɔt dɔn gɛda.
- Kɔlchɔ: Dɛn tɛst ya kin ɛp fɔ no difrɛn kayn infɛkshɔn bay we dɛn de chɛk yu blɔd, yu mכkus, ɔ ɔda wata we de na yu bɔdi.
Bay dɛn tɛst rizɔlt ya ɛn yu sayn dɛm, yu dɔktɔ kin kɔl Akyu Chɛst Sindrom as
sayn, smɔl, ɔr siriɔs .
Wetin na di tritmɛnt fɔ Akyu Chɛst Sindrom?
Insay dis kayn tin
, fɔ bigin tritmɛnt kwik na di bɛst we fɔ mek yu nɔ gɛt siriɔs prɔblɛm dɛn . Di tritmɛnt dɛn we yu kin gɛt na:
- Blɔd transfyushɔn: Dis min se dɛn kin pul sɔm pan yu blɔd ɛn gi yu blɔd ɔ sɔm pat dɛn na yu blɔd frɔm pɔsin we gi yu blɔd.
- IV fluid: Dis kin ɛp fɔ mek yu nɔ gɛt wata na yu bɔdi (we kin mek yu nɔ gɛt wata), we kin mek siklɛt sik wɔs ɛn mek yu fil pen mɔ ɛn mɔ.
- Di mɛrɛsin dɛn we de mek pɔsin fil pen: Dɛn kin gi mɛrɛsin lɛk `ketorolac` ɔ `opioids` fɔ kɔntrol di pen.
- Wan Insentif Spiromita: Dis smɔl tin de ɛp yu fɔ blo dip dip wan. I de ɛp fɔ mek yu lɔng dɛn klin ɛn wok fayn fayn wan.
- Sɔplɛnt ɔksijɛn tɛrapi: If di ɔksijɛn lɛvɛl na di blɔd nɔ bɔku, dɛn kin gi ɔksijɛn.
- Antibayɔtik: If na baktri infɛkshɔn mek dis sik, dɛn kin gi am antibayɔtik.
- Antivayrɔs: If di kɔz na vayral infɛkshɔn, dɛn kin gi am di rayt antivayral mɛrɛsin.
Yu tink se dɛn kin ridyus di risk fɔ gɛt Akyu Chɛst Sindrom?
If yu gɛt siklɛt sik (SCD), i impɔtant fɔ tɔk to yu mɛdikal tim bɔt aw fɔ mek yu nɔ gɛt Akyu Chɛst Sindrom. Dɛn kin tɔk bɔt tin dɛn lɛk:
- Fɔ blo insay bɔtul ɔltɛm: Pan ɔl we i kin tan lɛk se na simpul tin, dis kin ɛp fɔ mek yu aywe dɛn klin ɛn i kin mek di wata we nɔ nid fɔ gɛda rawnd yu lɔng dɛn nɔ bɔku.
- Ɛksesaiz ɔltɛm: Dis kin mek yu lɔng trɛnk go ɔp.
- Blɔd transfyushɔn ɔltɛm: Sɔm pipul dɛn kin nid dis.
- Fɔ tek mɛrɛsin lɛk `Hydroxyurea` ɔ `L-glutamine`: Dɛn mɛrɛsin ya kin ɛp fɔ ridyus pen ɛn ridyus di risk fɔ go na ɔspitul ɔltɛm. Bɔt dɛn fɔ tek dɛn tin ya ɔnda dɔktɔ advays nɔmɔ.
Wetin na de luk (recovery) fɔ pɔrsin wae gɛt dis sik?
I impɔtant fɔ go to tritmɛnt kwik kwik wan we `Acute Chest Syndrome` apin. If yu nɔ du dat, i kin mek yu gɛt siriɔs prɔblɛm dɛn lɛk:
- Acute Respiratory Distress Syndrome (ARDS): Dis na wan bad bad sik we de mek pɔsin in layf de pan denja.
- Altered mental stetmɛnt.
- Kidni injury.
- Liva nɔ de wok fayn.
- Bɔku ɔgan dɛn we nɔ de wok fayn.
- Kɔmplit respiratory failure.
- Pen we rili bad.
- Bɔt i sɔri fɔ no se ivin day kin apin.
akɔdin to di stεti, di rεt we de day fכ `Acute Chest Syndrome` pan big pipul dεm na lεk 4% . Pan pikin dɛn, dis nɔmba na lɛk 1% . Dis min se dɛn kin sev bɔku pipul dɛn layf if dɛn trit dɛn kwik kwik wan.
Dɔn bak, mɛmba se ivin if dɛn dɔn trit `Acute Chest Syndrome` fayn fayn wan ɛn mɛn am, pɔsin we gɛt `SCD`
kin gɛt dis sik bak tumara bambay .
A gɛt sik we dɛn kɔl sikɛl sɛl. Wetin a fɔ du if a gɛt sayn dɛn fɔ Akyu Chɛst Sindrom?
Dis na di tin we impɔtant pas ɔl. If yu gɛt SCD ɛn bigin fɔ gɛt ɛni wan pan di sayn dɛm fɔ Akyu Chɛst Sindrom (chɛst pen, shɔt briz, kɔf, fiva),
nɔ delay fɔ wan minit ɛn go to dɔktɔ wantɛm wantɛm .
- Tɛl di dɔktɔ dɛn se yu gɛt siklɛt sik we yu go na di imejensi rum ɔ ɔda say usay dɛn de mɛn pipul dɛn.
- Aks fɔ mek dɛn tek ɛkstrem rayt na yu chɛst wantɛm wantɛm . Dis kin kɔnfɔm kwik kwik wan if yu gɛt Akyu Chɛst Sindrom ɛn bigin tritmɛnt kwik kwik wan.
Mɛmba se if yu du tin kwik kwik wan na dis kayn tɛm, dat kin ɛp yu fɔ sev yu layf.
Mɛsej we dɛn kin kɛr go na os
Yu no naw se `Acute Chest Syndrome`, we wi bin de tɔk bɔt, na wan siriɔs kɔmplikeshɔn we kin kam wit siklɛt sik. Di men sayn dɛm na
we yu de fil pen na yu chɛst, yu nɔ de blo fayn, yu de kɔf, ɛn yu gɛt fiva . If yu gɛt siklɛt sik,
go to dɔktɔ wantɛm wantɛm if yu gɛt ɛni wan pan dɛn sayn ya.. Nɔ fɔgɛt fɔ mek yu dɔktɔ dɛn no se yu gɛt siklɛt sik. Fɔ no if yu gɛt dis sik kwik kwik wan ɛn fɔ trit yu kwik kwik wan na di bɛst we fɔ protɛkt yusɛf frɔm dis sik. Stay wit wɛlbɔdi!
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