Sɔntɛnde yu kin fil lɛk se yu nɔ de blo bɛtɛ, yu chɛst kin tayt? Ɔ yu kin kɔf we kin wɔs na mɔnin, ɔ yu kin fil taya? Dɛn tin ya nɔ kin jɔs bi sayn dɛn fɔ kol. Dɛn kin bi sayn fɔ wan sik na yu lɔng we dɛn kɔl Bullous Emphysema , we yu fɔ wɔri bɔt. So, mek wi tok abaut dis fo likl mo ditel tide, laik se yu de tok to yu padi, okay?
Wetin na Bullous Emphysema?
Fɔ tɔk am simpul wan, Bullous Emphysema na wan kayn sik we dɛn kɔl emphysema . Emphysema kin apin we di wɔl dɛn na di smɔl smɔl ay sak dɛn we de insay yu lɔng, we dɛn kɔl alveoli , kin pwɛl. Mɛmba se na dɛn alveoli ya de du di impɔtant wok fɔ tek ɔksijɛn ɛn pul kabon dayɔgzayd we wi de blo.
naw, insay bullous emphysema, wetin kin apin na dat di wכl dεm fכ dεn alveoli dεm de pwεl, εn dεn kin swel εn fכm big big ay sak dεm, lεk balכn. Wi kin kɔl dɛn bullae . Dɛn bulla dɛn ya kin big pas wan sɛntimita.
we dis sist de fכm, i de ambɔg di lכng dεm fכ wok fayn fayn wan. i kin at fכ di alvεol dεm fכ chenj כksijεn εn kabכn dayכksayd. Dis kכndyushכn kin apin na wan כ tu lכng dεm. Bɔt ivin if dis sist fɔm na wan lɔng, i kin ambɔg di ɔda lɔng in ebul fɔ blo, we min se i de blo. Sɔntɛnde, if dis sist rili big, di lɔng kin fɔdɔm, ɛn dis kin mek i gɛt wan sik we dɛn kɔl Vanishing Lung Syndrome . Pan ɔl we dis kin mek di lɔng dɛn pwɛl fɔ ɔltɛm, if yu trit yu fayn, dat kin mek yu kɔntrol dis sik ɛn mek yu liv lɔng.
Udat kin gɛt dis sik?
Infakt, ɛnibɔdi kin gɛt bullous emphysema, ilɛksɛf na in ej, in trayb, ɔ if na man ɔ uman. Bɔt bɔku tɛm, i kin gɛt fɔ du wit di sik we dɛn kɔl chronic obstructive pulmonary disease (COPD) , we na wan sik we de mek pɔsin in lɔng we pɔsin de smok. Dɔn bak, if yu gɛt sɔm kayn tin dɛn we yu kin gɛt na yu jɛnɛtiks, yu risk kin bɔku. Fɔ ɛgzampul:
- Alfa-1 antitrypsin we nɔ de wok fayn
- Ehlers-Danlos sindrom we gɛt di sik
- Marfan sindrom we gɛt di sik
Apat frɔm dat, pipul dɛn we gɛt di Human Immunodeficiency Virus (HIV) dɛnsɛf kin gɛt mɔ risk fɔ gɛt bullous emphysema.
Aw kɔmɔn tin dis? Wetin mek dis kin apin?
Ɔlsay na di wɔl, dɛn ripɔt se pas 5% pan di pipul dɛn ɛn pas 12% pan di big pipul dɛn we dɔn pas 30 ia gɛt bullous emphysema. Na di tɔd tin bak we kin mek pipul dɛn day na kɔntri dɛn lɛk Amɛrika. So, dis nɔto sɔntin we wi fɔ tek am layt.
Naw lɛ wi si wetin mek dis kin apin.
Di men tin we kin mek pɔsin gɛt bullous emphysema na fɔ smok . Di inflamɛns we nɔ de dɔn we sigrɛt smok kin mek i pwɛl di wɔl dɛn na yu alvɔlɔ. Dis kin mek di ay sak dɛn big, ɛn dis kin mek ɔksijɛn ɛn kabon dayɔgzayd nɔ muv.
Apat frɔm smok, ɔda tin dɛn de we kin mek pɔsin smok:
- Fɔ smok krak kɔkɛyn ɔ marijuana.
- Yuz drɔgs insay di bɛlɛ.
- di jεnεtik kכndishכn dεm we wi bin dכn tכk bכt kin mek bak di alvεolar wכl dεm wik εn dεm, we kin mek i gεt bullous εmfysema.
Wetin na di sayn dɛm fɔ dis?
Di men ɛn mɔs kɔmɔn sayn fɔ bullous emphysema na we yu nɔ de blo fayn . Dis min se yu nɔ kin ebul fɔ blo fayn, nɔto jɔs we yu taya smɔl, we yu de klaym stej, bɔt sɔntɛnde ivin we yu jɔs tinap.
Ɔda sayn dɛn de we kin apin:
- Fɔ fil se yu chɛst de pen ɔ yu tayt.
- Fɔ gɛt kɔf (bɔku tɛm dis kin wɔs na mɔnin).
- Fɔ fil taya ɛn taya ɔltɛm (Fatigue).
- Di it nɔ de te.
- Vɔmit.
- Trobul fɔ blo.
Bɔt sɔm pipul dɛn kin gɛt bullous emphysema bɔt dɛn nɔ kin sho ɛni sayn. If di bullae dɛn kin rili big, wi kin kɔl dɛn jayant bullae , den di sayn dɛn kin rili bad.
We yu go to dɔktɔ, i go luk fɔ sayn dɛn lɛk dɛn wan ya we i de chɛk yu:
- Wan chɛst we tan lɛk barɛl.
- Finga dɛn we gɛt klab.
- Fɔ yɛri yu at bit lawd wan bikɔs ɔf di pulmonary hypertension.
- Swɛlin (Ɛdima).
- We pɔsin de swɛt.
Aw yu no dis klia wan?
Yu dɔktɔ go aks yu fɔs bɔt yu sik, yu wɛl bɔdi istri, ɛn if ɛnibɔdi na yu famili dɔn gɛt dis kayn sik. Dɔn dɛn go du ɛgzam fɔ dɛn bɔdi.
If dɛn tink se yu gɛt bullous emphysema, yu dɔktɔ go ɔda fɔ mek dɛn du pulmonary function testing (PFT) . Dɛn tɛst ya de chɛk aw yu lɔng dɛn de muv di briz fayn fayn wan ɛn if di bulla dɛn de ambɔg di briz we de flɔ.
As pat pan dɛn tɛst ya, na spirometryYu kin gɛt tɛst. Dis min se yu de blo tru wan tiub insay wan mashin (spirometer). Dis de mכsu aw bכku briz de muv insay εn kכmכt na yu lכng we yu de blo εn kכmכt.
Apat frɔm dat, yu dɔktɔ kin tɛl yu fɔ du imej tɛst fɔ chɛk if di alviɔl dɔn big ɔ dɔn pwɛl. Dɛn tin ya kin bi:
- Chɛst X-ray: Dis kin ɛp fɔ no if ɛni bulla de ɛn usay dɛn de na di lɔng.
- CT skan: Dis kin ɛp fɔ no di rayt say, di nɔmba, ɛn di sayz we di sist de.
Dɛn kin tɔk bɔt ɔda tɛst dɛn, fɔ ɛgzampul:
- Blɔd tɛst: Chɛk fɔ si if di kabon dayɔgzayd dɔn bɔku na di lɔng, we de mek di blɔd gɛt asid (dɛn kɔl dis respiratory acidosis ), ɔ di ɔksijɛn nɔ bɔku.
- Kɔmplit blɔd kɔnt (CBC): I de chɛk fɔ si if di ɛmoglobin lɛvɛl smɔl.
- Ilɛktrokardiogram (EKG): Fɔ chɛk fɔ ɛni at ifɛkt we di lɔng sik kin kam wit, lɛk di rayt ventrikul aypatrofi ɔ rayt atria big .
Yu dɔktɔ kin chɛk bak if yu gɛt Alpha-1 antitrypsin dɛfisiɛns tru blɔd tɛst.
Yu tink se kɔmplit mɛrɛsin de fɔ dis?
Bɔt i sɔri fɔ no se, no mɛrɛsin nɔ de fɔ bulɔs ɛmfisɛma. Dis min se wans i dɔn divɛlɔp, dɛn nɔ go ebul fɔ rivɛns am. Bɔt nɔ wɔri! Tritmɛnt de wae kin ɛp yu fɔ liv wit de sik ɛn stɔp de sik fɔ wɔs.
So wetin na di tritmɛnt dɛn?
Fɔ ɛp fɔ kɔntrol yu sik dɛn, yu dɔktɔ kin gi yu mɛrɛsin dɛn we dɛn kɔl bronchodilators . Bɔku tɛm dɛn kin inhal dɛn tin ya tru wan inhala . Bronchodilators de wok bay we dɛn de rilaks di mɔsul dɛn na yu aywe, mek am izi fɔ mek di briz pas insay yu lɔng, ɛn mek yu nɔ blo shɔt.
Imajin, dɛn mɛrɛsin ya kin wok lɛk fɔ mek rod we ful-ɔp wit pipul dɛn big smɔl, ɛn dis kin mek i izi fɔ mek motoka dɛn pas.
If yu gɛt siriɔs sik ɔ yu gɛt infekshɔn na yu lɔng, dɛn kin gi yu antibayɔtik ɔ kɔtikosterɔyd bak fɔ shɔt tɛm.
If yu ɔksijɛn nɔ bɔku, yu dɔktɔ kin tɛl yu fɔ gi yu bɔdi ɛkstra ɔksijɛn tru wan tiub we dɛn put insay yu nos ɔ wan mask we dɛn put na yu fes.
Sɔntɛnde, mɔ we yu de tɔk datIf big big bulla de, if di prɔblɛm fɔ blo rili bad, ɔ if ɔda prɔblɛm dɛn de bikɔs ɔf dis sik, fɔ ɛgzampul:
- Lɔng we dɔn kol (Pneumothorax) .
- Fɔ kɔf blɔd (Hemoptysis) .
- Infεkshכn dεm na di lכng
If tin dɛn lɛk dis apin, yu go nid fɔ du ɔpreshɔn.
Di kayn ɔpreshɔn fɔ bullous emphysema:
- Bullectomy: Insay dis prosidur, di ɔspitul kin pul di bulla (air sac) na yu lɔng. dis kin bi as opin כpεrayshכn (Toracotomy) כ as minimally invasive prosidכs (Video-assisted thoracic surgery - VATS).
- Bronchoscopic lung volume reduction (BLVR): Insay dis minimally invasive prosidur, di sajin kin put wan valv insay yu lכng εn i kin shrink wan pat pan di lכng bay wilful.
- di lכng volyum ridyusכn כpεrayshכn (LVRS): Insay dis, di sכjaman de pul di lכng tisu dεm we dεn dכn pwεl so dat di rεst tisu go wok bεtεh.
If nɔbɔdi pan dɛn tritmɛnt ya nɔ wok, ɛn if i fayn, yu dɔktɔ kin sɛn yu fɔ mek dɛn transplant yu lɔng .
Aw dɛn go ebul fɔ ridyus dis prɔblɛm?
Di bɛst tin we yu kin du fɔ ridyus yu risk fɔ gɛt bullous emphysema na fɔ nɔ smok, ɔ if yu de smok, fɔ lɛf fɔ smok. Tɔk to yu dɔktɔ bɔt aw fɔ ɛp yu fɔ lɛf fɔ smok. Wi no se i nɔ izi, bɔt i fayn fɔ yu lɔng dɛn wɛlbɔdi.
Wetin yu fɔ ɛkspɛkt we yu de liv wit dis sik?
Bullous emphysema na wan sik wae de kam wae yu de liv yu layf. Dis min se wans yu lɔng dɛn dɔn pwɛl, dɛn nɔ go ɛva wɛl. Bɔt, di kwik we yu bigin fɔ tek tritmɛnt, na di mɔ yu go stɔp di sik fɔ mek i nɔ wɔs. So, i impɔtant fɔ go to dɔktɔ kwik kwik wan if yu gɛt sɔm sayn dɛn.
Aw a kin kia fɔ misɛf?
Yu kin ebul fɔ kɔntrol yu sik dɛn ɛn liv fayn fayn wan. If yu fɛn di rayt tritmɛnt fɔ yu, dat kin rili ɛp yu fɔ liv yu layf.
I impɔtant bak fɔ gɛt wɛl bɔdi ɛn avɔyd siriɔs wɛlbɔdi prɔblɛm. So, tɔk to yu dɔktɔ bɔt di kayn vaysin dɛn we yu go nid, lɛk di flu vaysin, COVID vaysin, ɛn Nyumokɔk vaysin .
Ustɛm a fɔ go to dɔktɔ?
If yu notis ɛni sayn fɔ bullous emphysema, ɔ if yu gɛt nyu sayn dɛn, mek shɔ se yu go to dɔktɔ.
If yu gɛt dɛn sik ya, i impɔtant fɔ go to dɔktɔ wantɛm wantɛm:
- Wan blu ɔ grey kɔlɔ to yu lip ɔ finga nel (cyanosis).
- I nɔ kin izi fɔ mek yu de wach yu maynd.
- I de mek i nɔ izi fɔ blo mɔ ɛn mɔ.
- At bit kwik kwik wan (Tachycardia).
We pɔsin nɔ de blo fayn, dat kin mek pɔsin fred. If yu gɛt bullous emphysema, yu kin fil lɛk se yu de tray tranga wan fɔ blo ɔltɛm. Mɛmba se na di men tin we kin mek pɔsin smok. Dɔn bak, sɔm tin dɛn we kin apin to yu jɛnɛtiks kin mek yu gɛt mɔ prɔblɛm. Fɔ lɛf fɔ smok na di bɛst tin we yu kin du fɔ stɔp di bullɔs ɛmfisema fɔ mek i nɔ wɔs. Yu dɔktɔ kin tɛl yu bɔt tritmɛnt dɛn we go ɛp yu fɔ blo izi wan ɛn mek yu ebul fɔ kɔntrol yu ɛvride layf.
Mɛmba di tin we impɔtant pas ɔl (Take-Home Message) .
Okay, so na sɔm pan di impɔtant tin dɛn we wi dɔn tɔk bɔt tide fɔ ɛp yu fɔ mɛmba:
- Bullous emphysema na wan kכndyushכn we di ay sak dεm na di lכng dεm de pwεl εn big big ay sak dεm (bullae) de fכm.
- Smok na di men tin we kin mek dis apin, so i rili impɔtant fɔ lɛ wi nɔ smok.
- If yu gɛt sɔm sayn dɛn lɛk fɔ mek yu nɔ ebul fɔ blo fayn, yu nɔ de kɔf ɔltɛm, ɔ yu de fil pen na yu chɛst, mek shɔ se yu go to dɔktɔ.
- Pan ɔl we no kɔmplit mɛrɛsin nɔ de fɔ dis, fayn tritmɛnt dɛn de fɔ kɔntrol di sayn dɛm ɛn fɔ mek di sik nɔ wɔs.
- If yu no di sik kwik kwik wan ɛn trit yu, dat kin mek yu layf bɛtɛ.
So, if yu ɔr pɔrsin wae yu sabi gɛt dɛn sik ya, nɔr panik ɛn go to dɔktɔ fɔ advays. Stay wit wɛlbɔdi!
` Bullous emphysema, lכng sik, respiratory distress, smok, COPD, bullae, alveoli











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