Waliwo ekifo ekyewuunyisa ku lususu lwo? Kiyinza okuba nga kya DFSP (Dermatofibrosarcoma Protuberans)!

Wali olabye ku lususu lwo akatono akazimba oba okukyuka langi? Oluusi tetukifaako nnyo, nedda? Naye oluusi n’ekintu ekitono nga kino kiyinza okuba ekintu eky’okweraliikirira. Leero, tugenda kwogera ku kika kya kookolo w’olususu atatera kulabika naye nga kikulu. Kiyitibwa Dermatofibrosarcoma Protuberans , oba DFSP mu bufunze.

DFSP (Dermatofibrosarcoma Protuberans) kye ki?

Mu ngeri ennyangu, DFSP kika kya kookolo w’olususu akula mpola, naye nga tekitera kubaawo. Kitandikira mu kitundu eky’omu makkati eky’olususu lwaffe, olususu . Oyinza n’okuwulira omusawo ng’agiyita DFSP.

Olw’okuba ono kookolo akula mpola, tatera kusaasaana mu bitundu by’omubiri ebirala. Kyokka, si kirungi okukibuusa amaaso. Kikulu nnyo okufuna obujjanjabi obutuufu n’okuggyawo ekizimba kino. Olwo lwokka kookolo w’asobola okulekera awo okudda (okuddamu) oba okusaasaana mu bitundu by’omubiri ebirala (metastatic cancer) n’aziyizibwa. Omuntu alina DFSP bw’afuna obujjanjabi obutuufu, alina emikisa mingi nnyo okuwona.

DFSP eno kizimba kyokka? Oba kookolo?

Nedda, DFSP si kizimba ekitali kya bulabe kyokka. Embeera embi . Okubeera omutuufu, kika kya kookolo w’ebitundu ebigonvu, ekika kya kookolo w’ebitundu ebigonvu . Sarcomas ye kookolo akola mu bifo ng’ebinywa, amasavu n’olususu. Oluusi, era zisobola okukosa amagumba.

DFSP esobola okusaasaana (okusaasaana) mu bitundu by’omubiri ebirala?

DFSP si kika kya kookolo asaasaana mangu nnyo mu mubiri gwonna. Wabula, si bulijjo nnyo, nga omu ku buli bantu 20 abalina DFSP asobola okuba ne kookolo okusaasaana okusukka we yasooka okutandikira. Kino kiyitibwa kookolo agenda mu bitundu ebirala .

Kino kisinga kusaasaana singa kirekebwa nga tekijjanjabiddwa, oba singa kookolo asaasaanidde wansi mu lususu, mu masavu n’ebinywa.

Ekirala, wadde ekituufu ekivaako tekimanyiddwa, singa DFSP ekula ng’oli lubuto, eyinza okweyongera okubeera ey’amaanyi.

Ate era, abantu abatono abalina DFSP basobola okukulaakulanya ekika ekizibu ennyo, ekisaasaana amangu ekiyitibwa fibrosarcomatous dermatofibrosarcoma protuberans (DFSP-FS) . Ebizimba bino ebya DFSP-FS ne bwe biba bilongooseddwa, bitera okuddamu era bisobola okusaasaana mu bitundu ebirala.

Embeera eno eyitibwa DFSP ya bulijjo etya?

DFSP kika kya kookolo ekitali kya bulijjo nnyo. Mu nsi yonna, bukosa abantu nga bana bokka ku buli bukadde bw’abantu buli mwaka. DFSP ekola wakati wa 1% ne 6% ku sarcomas zonna ez’ebitundu ebigonvu.

Kookolo ono asinga kubeera mu bantu abakulu abali wakati w’emyaka 20 ne 50. Kyokka n’abaana abato basobola okufuna kookolo ono ow’olususu. Abalongo abamu basobola okuba ne DFSP nga bazaalibwa. Okunoonyereza kulaga nti abaddugavu batera okubufuna okusinga abantu ab’amawanga amalala.

Bika ki ebikulu ebya DFSPs?

Abakugu mu by’endwadde, abasawo abakebera ebitundu by’omubiri nga bakozesa microscope, basobola okukubuulira ddala ekika kya DFSP ky’olina nga bakebera obutoffaali. Waliwo ebika ebikulu ebiwerako:

• Ebizimba bya Bednar (era ebimanyiddwa nga pigmented DFSP): Ebika by’obutoffaali bino birimu ekirungo kya melanin ekinene , ekirungo ekiwa olususu langi yaalwo. Eno y’ensonga lwaki ebizimba bino bisobola okulabika mu langi ez’enjawulo omuli emmyufu, kitaka, bbulu ne kakobe. Ekika kino kikola ebitundu nga 5% ku bizuuliddwa mu DFSP.
• Giant cell fibroblastoma: Ekika kino kimanyiddwa olw’okubeerawo kw’obutoffaali obunene. Ekika kino era kiyitibwa juvenile DFSP kubanga kisinga kubeera mu baana n’abato abakulu.
• Fibrosarcomatous dermatofibrosarcoma protuberans (DFSP-FS): Nga bwe kyayogeddwako emabegako, kino kika kya sarcoma eky’ebitundu ebigonvu ekizibu ennyo, ekisaasaana amangu.
• Myxoid DFSPs: Zino zikolebwa ekika ky’ebitundu ebiyunga ekitali kya bulijjo ekiyitibwa myxoid stroma. Ekika kya DFSP kino tekitera kubaawo nnyo.

Kiki ekivaako DFSP?

Ekyewuunyisa, abantu 9 ku buli 10 abafuna DFSP balina enkyukakyuka mu buzaale ereeta embeera eno . Enkyukakyuka eno ey’obuzaale ebaawo mu butoffaali bwaffe nga tumaze okuzaalibwa. Kino kitegeeza nti DFSP teva ku buzibu bwa buzaale obusikira bazadde baffe.

Biki ebiyinza okuleeta akabi mu kukola DFSP?

Ng’oggyeeko emisinde, okubeera n’obuvune obw’ekika kyonna ku lususu oba enkovu kiyinza okwongera ku bulabe bw’okufuna DFSP. Waliwo engeri eziwerako olususu gye luyinza okulumwa:

• Okwokya
• Okufuna obujjanjabi obw’amasannyalaze (radiation therapy).
• Okulongoosa okutemebwa
• Tattoos

Teebereza, wali oyokeddwa nnyo n’ofuna enkovu ennene. Oba, obadde n’obujjanjabi bwa radiation ku bulwadde obulala. Olususu bwe lwonoonebwa ebintu nga bino, wabaawo emikisa mitono nti embeera nga DFSP ejja kubaawo mu biseera eby’omu maaso, wadde nga tezitera kubaawo. Eno y’ensonga lwaki bulijjo tusaanidde okumanya enkyukakyuka mu lususu.

Bubonero ki obulaga DFSP?

Obubonero obusooka obwa DFSP buba bwa maanyi nnyo ne kiba nti tuyinza obutabutegeera oba n’okubulaba. Ebizimba bino bisinga kukula ku kifuba, mu mugongo, ku bibegabega, mu lubuto oba mu bisambi. Era zisobola okukula ku mikono, amagulu, ku mutwe, ne munda mu kamwa.

Mu kusooka oyinza okulaba akatundu akatono akalinga ebiwundu ku lususu.Kiba kipapajjo era tekiruma. Kiyinza okuwulira nga kikaluba katono ng’okikwatako, era langi eyinza okukyuka katono.

Mu baana abawere n’abaana abato, DFSP esobola okulabika ng’akabonero k’okuzaalibwa . Ebitundu bino bitera okuba nga kitundu kya yinsi okutuuka ku yinsi bbiri (sentimita emu ku ttaano) obugazi.

Obubonero bwa DFSP bweyoleka nga kookolo akula. Ekizimba bwe kikula, kinyigiriza mu lususu olw’okungulu (epidermis). Kino kireetera ebizimba ebikalu (nodules) okulabika ku lususu . Ekigambo "okufuluma" kitegeeza "okufuluma."

Oyinza okulaba obubonero buno mu bikonde bino:

• Kiyinza okwatika oba okuvaamu omusaayi mu ngeri ennyangu.
• Kinyweredde nnyo ku lususu (tekisobola kutambuzibwa).
• Bw’ogenda okaddiwa, olususu lwo lugolola.
• Kiwulira nga kizibu okukikwatako, oba nga kapiira.
• Langi eyinza okuba eya kitaka-kiragala, eya kakobe, eya bbululu oba emmyufu.
• Kiyinza okuba nga kiweweevu katono ng’okikwatako.

Waliwo embeera endala ezireeta obubonero obufaananako ne DFSP?

Yee, waliwo embeera y’olususu etali ya kookolo eyitibwa cellular dermatofibroma . Kino kiyinza okufaanana ennyo ne DFSP naddala mu mitendera gyayo egy’olubereberye. Cellular dermatofibromas bizimba bya bitundu ebigonvu ebitali bya bulabe. Zisinga kubeera ku magulu. Oluusi ziyinza okusiiwa ne ziruma. Dermatofibromas ezisinga tezeetaaga bujjanjabi. Kyokka kiba kya magezi obutabuzaabuza byombi, n’olwekyo kiba kya magezi okugenda ew’omusawo singa olaba ekipya ku lususu lwo.

DFSP (Dermatofibrosarcoma Protuberans) ezuulibwa etya?

DFSP ezuulibwa abakugu mu by’ensusu , nga bano basawo abatendekeddwa mu ngeri ey’enjawulo mu kookolo w’olususu n’endwadde z’olususu. Omusawo wo ajja kusooka kukwata akatundu akatono ak’ekizimba oba ekifo ky’olususu n’akisindika mu laabu okukeberebwa (okukebera olususu) . Ekizimba kyonna kiyinza okuggyibwamu ne kisindikibwa mu laabu. Olwo abakugu mu by’endwadde bajja kutunuulira ekitundu ekyo nga bakozesa ekyuma ekirabika obulungi okulaba oba kirimu obutoffaali bwa kookolo.

Singa okukebera olususu kukakasa nti olina DFSP, olwo oyinza okusabibwa okukeberebwa MRI scan . Kino kijja kuyamba okuzuula obunene bwennyini obw’ekizimba n’obuziba bwe kibunye mu lususu. Amawulire gano makulu nnyo mu kutegeka obujjanjabi.

Bujjanjabi ki obuweebwa DFSP (Dermatofibrosarcoma Protuberans)?

Obujjanjabi obukulu era obusinga obulungi ku DFSP kwe kuggyawo ekizimba nga balongoosa. Abasawo b’ensusu batera okukozesa enkola ey’enjawulo eyitibwa Mohs surgery okuggyawo ebizimba bya DFSP. Bino bye bigenda mu maaso mu kulongoosa kuno:

• Okusooka, eddagala eribudamya mu kitundu liteekebwa mu kifo awajjanjabirwa, kale tojja kuwulira bulumi bwonna.
• Oluvannyuma, omusawo asalako n’aggyawo ekizimba kya kookolo. Naye si kizimba kyokka, wabula n’ekitundu ekitono eky’olususu olulamu olukyetoolodde. Kino kiyitibwa margin .
• Ekiddako, empenda (ensalosalo) z’ekitundu ekiggiddwamu zeekebejjebwa wansi wa microscope okulaba oba waliwo obutoffaali bwa kookolo obusigaddewo.
• Singa wakyaliwo obutoffaali bwa kookolo ku mbiriizi, omusawo ajja kuggyamu ebitundu ebirala okuva mu kifo we baalongoosezza.
• Mu ngeri eno, okuggyawo ebitundu by’omubiri kugenda mu maaso okutuusa nga tewali butoffaali bwa kookolo busangibwa ku mabbali.
• Oluvannyuma lwa kookolo okuggyibwawo ddala, bamulongoosa okuddamu okuzimba bwe kiba kyetaagisa.

Waliwo obujjanjabi obulala ku DFSP nga tewali kulongoosebwa?

Ebizimba bya DFSP ne bwe biba bilongooseddwa, oluusi bisobola okuddamu. Oluvannyuma lw’okusalako okugazi okwa bulijjo, waliwo emikisa gya 20% ku 30% nti zijja kudda mu myaka esatu. Oluvannyuma lw’okulongoosebwa Mohs, akabi kano kakendeera okutuuka ku bitundu 4% okutuuka ku bitundu 5%. Wabula kikulu okubeera obulindaala, kubanga ebizimba bisobola okuddamu ne bwe wayise emyaka 10 oba okusingawo.

Oluusi, singa kookolo asaasaanidde mu bitundu by’omubiri ebirala (metastatic DFSP), oba singa ekizimba kiba kinene nnyo oba nga kiri mu kitundu ekisusse nga tekisobola kulongoosebwa, abasawo bakozesa eddagala eriyitibwa Imatinib . Eddagala lino era lisobola okukendeeza ku kizimba, ne kibanguyira okukiggyamu ng’olongooseddwa.

Ate era, singa okulongoosebwa tekusobola kuggyawo kookolo ddala, oba singa okulongoosa tekusoboka n’akatono, obujjanjabi obw’amasannyalaze buyinza okukozesebwa.

Endowooza etya eri omuntu alina DFSP?

Gano ddala mawulire gabudaabuda. Okuva DFSP bwe kiri kookolo akula mpola, atakola, ng’afunye obujjanjabi obutuufu, abantu abasukka mu 99% bajja kuwangaala okumala emyaka 10 oba okusingawo. Kale, ekisinga obukulu si kutya n’ogoberera amagezi g’omusawo wo.

Kiki kye nnyinza okukola okulongoosa endowooza yange?

Waliwo ebintu ebiwerako by’oyinza okukola okulongoosa endowooza yo:

• Kola okwekebera olususu buli kiseera. Noonya enkyukakyuka yonna empya, amabala oba ebizimba ku lususu lwo. Bw’olaba ekintu kyonna, tegeeza omusawo wo amangu ago.
• Oluvannyuma lw’okujjanjabibwa, laba omusawo akukebere olususu waakiri buli luvannyuma lwa myezi esatu oba mukaaga okumala emyaka esatu egisooka. Oluvannyuma genda okwekebejjebwa omulundi gumu mu mwaka, oba ng’omusawo bw’akulagidde.
• Kikendeeze ku musana. Emisinde gya UV egiva mu musana gyongera obulabe bwa kookolo w’olususu omulala. Kale, yambala eddagala eriziyiza omusana ng’ogenda mu musana, yambala engoye ezikuuma , era kendeeza ku budde bwo ebweru mu kiseera ky’olunaku olusinga okubeera olw’ebbugumu.

Ddi lwe nnina okulaba omusawo?

Bw’olaba enkyukakyuka empya mu lususu lwo naddala ng’olina ekimu ku bino wammanga, kakasa nti ogenda ew’omusawo:

• Ebizimba oba amabala ebipya ebitaggwaawo, oba okukula kw’olususu okupya.
• Enkyukakyuka mu nkwaso, obubonero bw’okuzaalibwa, enkovu enkadde oba ttatu.
• Singa ebizimba ku lususu bivaamu omusaayi mangu.

Jjukira nti enkyukakyuka mu lususu emirundi mingi teziyinza kuba za bulabe. Kyokka enkyukakyuka ezimu ziyinza okuba akabonero ka kookolo w’olususu. Kale, bw’oba ​​olina okubuusabuusa kwonna, kirungi okugenda ew’omusawo akugonjoole.

Kiki kye nsaana okubuuza omusawo wange?

Bw’oba ​​ozuuliddwa nti olina DFSP, oyinza okwagala okubuuza omusawo wo ebibuuzo nga:

• Lwaki nnafuna kookolo ono ow’olususu?
• Ndi mu bulabe bw’okufuna ebika bya kookolo w’olususu ebirala?
• Bujjanjabi ki obusinga okunkwatako?
• Waliwo obulabe bwa kookolo ono okusaasaana mu bitundu by’omubiri ebirala?
• Mirundi emeka gye nnina okujja okwekebejjebwa kookolo?

Okumanya eby’okuddamu mu bibuuzo bino kijja kukuyamba okutegeera obulungi embeera eno era kiyinza okukuyamba okunnyonnyola obujjanjabi bwo n’enteekateeka z’omu maaso.

N’ekisembayo, ebintu by’olina okujjukira

Wadde nga DFSP kookolo w’olususu atatera kulabika, tatera nnyo kusaasaana mu bitundu by’omubiri ebirala. Kyokka, obujjanjabi bw’okulongoosa kyetaagisa nnyo okuyimiriza okukula. Okuzuula amangu n’okujjanjabibwa obulungi kiyinza okulongoosa ennyo endowooza yo. Kale, beera mwegendereza olususu lwo era olabe omusawo singa olaba ekintu kyonna ekitali kya bulijjo. Si ggwe wekka, era waliwo abasawo abasobola okukuyamba mu lugendo luno.

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