Vawiin hian naupang tê, a bik takin kum nga hnuai lamte nghawng thei dinhmun hmuh tur awm lo, mahse a chang chuan na tak tak kan sawi dawn a ni. Kawasaki Disease an ti a. Nu leh pa thenkhat chuan he hming an hriat hian an hlauthawng deuh mai thei a, mahse lungngai suh. Uluk taka hriattir i nih a, a hun taka enkawl i nih chuan a tam zawkah chuan i fa chu a dam kim thei a ni.
Kawasaki Natna hi eng nge ni?
A awlsam zawngin sawi ila, Kawasaki natna hi kan taksa chhunga
thisen kalna kawng a inflammation a ni. Doctor te pawhin hei hi ``Vasculitis`` an ti bawk. Tunah chuan han ngaihtuah teh, thisen kalna kawng a lo hring chuan eng nge thleng thin? A chak lo thei a, a inzawm thei a, balloon ang maiin a hring thei bawk. Chutiang a nih chuan an puak darh thei a ni. A chang chuan, he inflammation hian thisen kalna kawng chhungah hliam a siam thei a, thisen kalna kawng a ti tawi thei bawk. Tichuan, taksa peng hrang hrang leh taksa peng hrang hrangin thisen, chu chu ei leh in tur an dawng tlem hle. Kawasaki natna hian
naupang tê thla 6 leh kum 5 inkar a vei tam ber . Taksa chhunga thisen kalna kawng eng pawh a nghawng tak tak thei a, mahse kan ngaihtuah ber tur
chu thinlunga thisen petu thisen kalna kawng lian ber ber, ``Coronary arteries`` te hi a ni . A chhan chu heng thisen kalna kawngte hi a chhiat chuan naupang thinlung hnathawh danah direct-in a nghawng thei a ni. Mahse a tha ber chu
natna hi a hun taka hriat a nih a, enkawl tan thuai a nih chuan naupang tam zawk chu thla hnih vel chhungin an dam chhuak vek ang .
He natna hi engtiang chiahin nge a hluar?
Kawasaki Disease hi a takah chuan
natna hmuh tur awm lo tak a ni . Entirnan, United States leh Canada ang ramah chuan naupang kum 5 hnuai lam 100,000 zinga 10 atanga 20 inkar a vei a, mahse Asia ram Japan, Korea leh Taiwan-ah te chuan he zat hi a tam deuh hlek a ni. Chutah chuan naupang 100,000 zinga 50 leh 250 inkar a nghawng a ni. Mahse, thil pawimawh tak pakhat chu United States leh Japan ang ram changkang zawkah chuan
Kawasaki Disease hi naupangte naupan laia thinlung natna thlentu ber nia hriat a ni Chumi awmzia chu kan hriat chian a pawimawh hle tihna a ni.
Kawasaki Disease symptoms te chu engte nge ni?
Tunah chuan i fate hian Kawasaki Disease a vei em tih hriattir thei symptoms te chu han en ila. Hengte hi pakhat hnu pakhatin i hre reng tur a ni.
- Ni nga tal awm thei khawsik . Hei hi a symptom ber leh a hmasa ber a ni.
- Naupang chu a rilru a hahdam lo va, a tap reng bawk (Irritability) .
- Mit chu a sen emaw, pink emaw a ni a , mahse mit atang chuan tui a chhuak lo.
- A hmui sen, a hring, lei sen, strawberry ang maia lang (`Strawberry tongue`) .
- Kut leh ke a hring leh/ emaw a sen .
- Kut zungtang-a vun hring, a bik takin nail chhehvel .
- Bawl . Hei hi rilru leh pum ang chi hmunah hmuh tur a tam ber. A chang chuan taksa peng dangah pawh a lang thei bawk.
- Kawr chhunga lymph node lo hring chhuak . Pakhat emaw a aia tam emaw a hring thei.
- Pum natna , pum na, luak chhuak , luak chhuak , etc.
Heng symptoms pakhat emaw pahnih emaw i neih vang mai mai hian Kawasaki natna hi hlau suh. Mahse
ni nga aia tam khawsik i neih a, a sawi lan symptom dang pakhat emaw a aia tam emaw pawh i neih chuan doctor i pan nghal ngei tur a ni .
Eng thilin nge Kawasaki natna hi a thlen?
Kawasaki natna thlen chhan dik tak hi hriat a la ni lo . Chumi awmzia chu a lo awm chhan chiang taka sawi theih a ni lo tihna a ni. Mahse zirchiangtute chuan an chhui chhunzawm zel a ni. Ṭhenkhat chuan
infection ,
environment factor , a nih loh leh
genetic predisposition a awm thei niin an ngai. Thil dang pakhat chu
he natna hi thlasik tawp lam leh thlasik tir lamah hmuh tam ber a ni . Mahse a chhan chiah hriat a la ni lo.
Hei hi natna hrik kai theih a ni em?
No.
Kawasaki Disease hi natna hrik kai theih a ni lo . Taksa tui, khawih leh thawk hah hmanga darh a ni lo. Chuvangin ngaihtuahawm tur a awm lo.
Tute nge Kawasaki Disease vei theihna sang zawk?
Mi thenkhat chuan he natna hi an vei tam zawk. ‘Risk group’ kan ti thin.
- Hmeichhia aiin mipa naupang chu tlemin an thang lian zawk.
- Naupang kum 5 hnuai lam chu a tuar nasa ber a ni.
- Asian emaw Pacific Islander hnam naupangte hian he natna hi an vei tam zawk.
Mahse, heng risk factors nei lote zingah pawh Kawasaki natna hi a lo awm thei tih hriat reng a pawimawh.
Kawasaki Disease avanga harsatna awm thei te chu engte nge ni?
Kawasaki natna hlauhawm ber chu a harsatna thlen thei te hi a ni a, a bik takin thinlung nena inzawm te hi a ni.
- Thinlung coronary arteries te chu a hring a, a chak lo va, balloon ang maiin a awm bawk (Aneurysms) . Hei hi complication hlauhawm ber a ni. A nasat deuhah chuan coronary artery bypass surgery ang chi surgery neih a ngai thei bawk.
- Coronary arteries chhungah thisen zam a lo awm a , thisen kalna kawng a tawi .
- Coronary artery a chhuak a . Hei hi a tlem hle a, mahse a hlauhawm hle.
- Heart valve lama harsatna neiHeng valve te hian thinlung chhunga thisen kal dan tur an control a.
- Lung ruh natna (`Myocarditis` emaw ` Pericarditis` ) .
- Hepatitis natna a ni .
- Lung natna (Pneumonitis) .
- Lung natna nei .
- Pancreas natna (` Pancreatitis` ) .
- Lung lam chak lohna .
- Lung natna . Naupang tê têah chuan a tlem hle nachungin, hei hi Kawasaki natna vang a ni thei.
Heng harsatnate hi hriat a hlauhawm thei hle. Mahse, a hun taka enkawl ṭan a nih chuan heng harsatna tam tak hi pumpelh theih a ni tih hre reng ang che .
Engtin nge Kawasaki Disease hi hmuhchhuah a nih?
Doctor te chuan
naupang pakhatin Kawasaki natna a vei leh vei loh chu an natna lan chhuah dan leh taksa enfiahna atanga an hriat ber a ni . A hmaa kan sawi tawh ang khan symptoms an zawng thin. A châng chuan naupang chuan Kawasaki natna lan chhuahna zawng zawng a lantir lo thei bawk. A lan chhuah dan thenkhat chauh an nei thei. Chutiang a nih chuan
``Atypical or Incomplete Kawasaki Disease'' an ti a ni.Diagnosis an siam hmain doctor-te chuan khawsik chhan dang, chu chu natna dang tihna a ni. Kawasaki natna an finfiah hmain heng zawng zawng hi an paih chhuak vek a ni.
Kawasaki Disease hi eng stage pathum nge ni?
Kawasaki natna hi a tlangpuiin stage thum a paltlang thin.
A hmasa ber (Acute Stage) 1.1.
- Ni nga emaw a aia rei emaw chhung khawsik atanga tan a ni .
- Taksaah hliam an tuar a, a bik takin rilru, pum leh kekawrteah hliam an tuar a ni.
- Mit chu a sen (Pink eye).
- A hmui leh lei chu a sen a, a lei chu strawberry ang maiin a lang.
- Ke kutphah leh kephah chu a sen a, a hring bawk.
- A kawng a lumps te chu a hring vek a.
Stage pahnihna (Subacute Stage) a ni.
- He stage hi khawsik a reh hnuah a intan thin .
- Pum natna, luak chhuak, leh luak chhuak a awm thei.
- Joint na leh pum na a awm thei.
- Kut leh ke vun chu a hring tan a , a bik takin kut zungtangah.
Stage pathumna (Convalescent Stage) a ni.
- Hetih lai hian a natna lan chhuah dan chu a tlahniam zauh zauh a .
- Mahse, a hmaa harsatna tawh (a bik takin thinlung lam thil) chu a la awm reng thei a, chuvangin he hun chhung hian doctor-te chuan naute hi uluk takin an enfiah chhunzawm zel dawn a ni.
Heng stage hrang hrangte hi chiang taka hriat a harsa a, a chang chuan an inthlak danglam thei bawk.
Eng test nge natna hriat theihna tura puitu?
Kawasaki Disease hi hei hi a lan chhuahna direct a ni a, .
``Test bik`` a awm lo . Chu chu thisen tla khat pawh la in, ‘Aw, hei hi Kawasaki a ni’ i ti thei lo tihna a ni.
- Thisen test : Hengte hian inflammation marker, anemia, leh liver function te an enfiah thin.
- Urinalysis tih a ni .
- Echocardiogram : Hei hi test pawimawh tak a ni . Nausen pum chhunga ultrasound scan ang bawkin naute thinlung leh coronary arteries dinhmun te, aneurysm awm leh awm loh te chiang takin a hmu thei a ni. Hei hi test hrehawm lo tak a ni.
- Electrocardiogram (ECG/EKG) : Hei hian naute thinlung electrical activity a enfiah a, chu chu heartbeat pattern a ni. Hei pawh hi test na tak a ni.
- A chang chuan CT angiogram ( X-ray leh computer hmanga test) emaw MRA (Magnetic Resonance Angiogram) (MRI machine hmanga test) emaw pawh tih theih a ni.
Doctor-te chuan heng test atanga information an hmuhte leh naupang symptoms te khaikhin a, naupang hian Kawasaki natna a vei tih an sawi chhuak a ni.
Kawasaki Disease hi engtin nge enkawl a nih?
Kawasaki Disease a awm tih hriat a nih veleh
naupang chu damdawi inah dahin enkawl tan a ni . A rang thei ang bera enkawl tan a pawimawh hle a, hei hian thinlunga chhiatna thleng thei chu a ti tlem thei a ni. Enkawlna pek dan tlangpui chu:
- Intravenous Immunoglobulin (IVIG) : Hei hi damdawi bik, mihring thisena protein awm atanga siam a ni. Saline ang chi vein-ah pek a ni. Taksa a hring (swelling) a tiziaawm. Naupang tam zawk chu hei hian an dam tha zawk thin. Mahse, naupang 100 zinga 10 vel chuan IVIG dose hmasa ber chu an chhang tha lo thei a ni. Chutiang a nih chuan second dose emaw damdawi dang emaw a ngai mai thei.
- Aspirin : Aspirin dose sang tak pek hi khawsik tihziaawmna atan te, natna tihziaawmna tur te, thisen zam tur venna atan te a ni. Khawsik a reh hnuah, thinlunga thisen kalna kawng a chhiat chuan thisen zam a veng loh nan aspirin a dose tlem zawka chhunzawm thin a ni.
- IV fluids : Naupang tui a tlakchham loh nan a veng tur a ni.
- Damdawi dang natna leh hliam tihziaawmna .
- Naupang thisen zam hlauhawm tak takte tan anticoagulants .
- A nasat deuh chuan steroid emaw, natna dotu damdawi dang emaw pek theih a ni.
- Tui lum a puan hnim hmanga taksaah cold compress hnawih hian khawsik a tiziaawm thei a ni.
Enkawlna tum berte chu:- Taksa chhunga inflammation tihziaawmna.
- Thisen kalna kawng, a bik takin thinlunga coronary arteries tihchhiat ven emaw tihtlem emaw.
- Naupang coronary artery lama harsatna nei te thisen zam venna.
- Lung lam thila harsatna awm thei venna.
Enkawlna hian side effect a nei em?
Damdawi dang ang bawkin heng enkawlna hian side effect engemaw zat a thlen thei a ni. IVIG hi a tlangpuiin an tuar tha hle. Mahse, a chang chuan:
- Hemolytic anemia ( thisen zam (red blood cells) te hi a tlangpui aiin an thi rang zawk) .
- Infusion reaction - khawsik leh khawsik ang chi.
- A rilru a na.
- Thâwk harsa.
- Pum a na.
- Muscle emaw joint emaw a na.
Thisen tithianghlimtu (anticoagulants) pek i nih chuan thisen chhuah theihna a sang deuh. Chuvangin, hliam tenau tak pawhin thisen chhuah a reh theih nan hun rei tak a la ngai thei a ni.
Kawasaki Disease hi ven theih a ni em?
Vanduaithlak takin,
ni lo . Kawasaki Disease awm chhan dik tak hriat a la nih loh avangin ven dan tur a la awm lo.
Ka fa hian Kawasaki Disease a vei a nih chuan eng nge ka beisei ang?
I fa chu Kawasaki Disease vei nia rinhlelh a nih veleh doctor-te chuan damdawi inah an dah ang. Damdawi inah hian a tul anga test neih a ni a, enkawl tan a ni. Naupang chu a haw thei ang:
- Fluids i in tha thei hunah.
- Damdawi ka ei theih hunah.
- Khawsik a reh vek tawh a, taksaa hliam chhinchhiahna a bo tawh chuan.
In i haw hnuah chuan
i chhungkaw doctor (primary healthcare provider), natna hrik kai doctor (infectious disease doctor), leh cardiologist (cardiologist) te i pan chhunzawm a ngai ang I fa chu uluk takin an enfiah ang a, thisen test an ti leh ang a, enkawlna dang a ngai tawh lo tih an sawi hma loh chuan an enkawl leh ang. Cardiologist chuan i fate inah a tlawh ang
a, kar hnih hnuah echocardiogram a ti ang a, kar li atanga kar ruk hnuah a ti leh ang . I fain coronary arteries-ah harsatna a neih chuan echocardiogram tih fo a ngai mai thei.
Kawasaki Disease hi tihdam theih vek a ni em?
Kawasaki natna lan chhuah dan hi
kar li atanga kar ruk vel a awm thei . Naupang chu kar riat thleng chau leh hahdam lo takin a inhria thei. Naupang thenkhat,
100 zinga 2 emaw 3 emaw vel chuan Kawasaki natna an vei leh thei a ni . Chubakah, Kawasaki natna hian
hun rei tak chhung chu coronary arteries a tichhe thei a, puitlingah chuan thinlung natna a thlen thei bawk.. Entirna pakhat chu atherosclerosis hi a ni. He natna avanga aneurysm nei te hian an dam chhungin cardiologist hnenah checkup an neih a ngai dawn a, kum khatah vawi khat emaw kum engemaw zat danah emaw checkup an neih a ngai dawn a ni. A châng chuan thisen kal ṭhat nân procedure a ngai thei bawk. I doctor chuan i fain thisen zam a neih loh nan leh heart muscle-in oxygen a dawng tlem em tih a enfiah ang.
Kawasaki Disease hi a hlauhawm em?
Ni e, Kawasaki natna hi natna khirh tak a ni . Mahse,
natna hi hriat hmasak a nih a, a hun taka enkawl tan a nih chuan naupang tam zawk chu an dam kim thei a ni . Lung lam harsatna, a chang chuan thihna pawh hi khawsik a lo chhuah atanga ni 15 leh ni 45 inkarah a thleng thei a ni. Vanneihthlak takin enkawlna hian thinlung natna tam zawk a veng thei a ni. Enkawl loh chuan naupang 100 zinga 25 velin coronary artery aneurysm an nei ang. Mahse, a hun taka enkawl a nih chuan he zat hi 100 zinga 6 aia tlem loah a tlahniam a, enkawl a nih chuan coronary artery aneurysm nei naupang 50% vel chu kum khat emaw kum hnih emaw chhungin an dam leh thin.
Engtin nge ka fa ka enkawl ang?
I fa chu Kawasaki Disease atanga a dam chhoh lai hian thil engemaw zat tih theih a awm a:
- I fa chu an vaccine pek zawng zawng chu a update vek tur a ni . A bik takin i fain aspirin a ei lai hian COVID-19, influenza, leh varicella vaccine lakah fimkhur hle ang che. Naupang tê tête zingah hian virus natna nena aspirin ei hian natna hlauhawm tak, Reye’s syndrome tih chu a awm theihna a tlem hle.
- IVIG hmanga enkawl hnuah thla 11 chhung chu i fate chu live virus vaccine pe suh . Entirnan, measles-mumps-rubella (MMR), chickenpox (varicella), leh hnar influenza nung vaccine te hi a ni. IVIG hian taksain heng virus laka antibody a siam chhuah theihna a tibuai thei a ni.
- I fate echocardiogram-ah thil danglam a awm chuan doctor thurawn angin thil engemaw tih kha tihtlem la .
Engtik hunah nge Doctor ka hmuh ang?
I fain in lama a lo haw hnua heng symptoms zinga pakhat tal a lan chuan doctor pan ngei ngei tur a ni:
- Khawsik a lo let leh chuan .
- I ruh natna nasa tak i neih chuan .
- Tun hmaa symptoms te a lo lang leh a , a zual zel ang tih a nih chuan .
Doctor hnenah eng zawhna nge ka zawh ang?
I fain Kawasaki natna a vei tih i hriat chuan doctor hnena zawhna i zawh theih tur thenkhat chu hetiang hi a ni:
- 'Ka fa dinhmun hi engtiang chiahin nge a pawi?'
- 'Naute chu damdawi inah eng chen nge a awm i rin?'
- 'Kawasaki natna vei naupang nu leh pate tan support group a awm em?'
- 'Ka fa thiltih hi eng chen nge ka tihtlem ang?'
I fate chu khawsik leh natna dang a vei lai en chu thil awlsam a ni lo. Mahse hre reng ang che, zirchiangtute chuan he natna enkawl dan tha tak tak an hmuchhuak a, naupang tam takin an dam chhuak tawh bawk. I fa thlamuan nan doctor hnenah i duh ber toy emaw blanket emaw damdawi inah i rawn keng thei em tih zawt la. I hmangaihna leh i aw muang tak chu he hun harsa tak karah hian i fa tan chakna nasa tak a ni ang.
Take-Home Thuchah hnuhnung ber
Kawasaki natna hi a tlem hle a, mahse natna khirh tak a ni a, naupang te te a nghawng a, thinlung a nghawng thei a ni.
- Ni 5 aia rei khawsik leh a kaihhnawih mit sen, hmui/lei sen, taksa na, ke ruh hring, leh kawr hah ang chi symptoms te chu fimkhur rawh.
- Heng symptoms te hi i hriat chuan Doctor pan nghal tur a ni. A pawimawh ber chu a hun taka enkawl tan hi a ni.
- Naupang tam tak chu enkawl a nih chuan an dam vek.
- A dam hnuah pawh naupang chu doctor thupek angin enfiah chhunzawm zel tur a ni , a bik takin cardiologist-in a enfiah chhunzawm zel tur a ni.
Hlau suh, fimkhur rawh. I fa enkawlna tha ber pe thei doctor an awm. I ngaihvenna leh hmalak thuai chu i fa dam lehna tura puitu lian ber a ni ang.
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