‘Acute Hepatic Porphyria’, a tawi zawnga kan sawi angin AHP i vei tih rinhlelhna tlemte pawh i nei em? I ngaihtuah chuan lungkham leh hlauhna nasa tak, tih leh tur, tu nge hmuh tur tih hriat loh hi thil pangngai tak a ni. A chhan chu hei hi a buaithlak deuh a, kan ramah hian sawi uar lutuk a ni lo. Chuvângin, a chungchâng thu hriat chu hmuh a harsa thei hle. Mahse, lungngai suh, he thu hi chiang tak leh awlsam takin sawi ila.
Engtin nge diagnosis dik tak kan siam theih ang?
AHP-a harsatna lian ber pakhat chu a natna lan chhuah dan hi natna tlanglawn dang tam tak nen a inang hle a ni. Entirnan, AHP-ah hian pum na na tak, luak chhuak, luak chhuak, ke leh ke ruh natna, thau chak lohna te hmuh tur a awm. Tunah chuan natna dang engzat nge heng symptoms te hi a lo awm? Chuvangin hengte hi AHP vang a ni tih ngaihtuah nghal a harsa hle. A chang chuan heng symptoms te hi taksa peng hrang hrang inzawm loah a lang thin a, chuvangin heng zawng zawng hi natna pakhata peng hrang hrang an ni tih hriat nan hun a duh thin.
A pawimawh ber chu AHP hi a awm lo hle a ni . Chuvangin Doctor zawng zawng hian experience tam tak an nei lo mai thei. Chu chu Doctor sualna a ni lo, natna awm dan a ni.
A tlangpuiin, doctor tu pawhin AHP hriat theih nan basic test (urine leh thisen test) a rawt thei a ni. Mahse, chu test report-te chu en a, an result hriatthiam a, "Ni e, hei hi AHP a ni" tih chiang taka hriat theih nan, specialist doctor puihna i mamawh mai thei I chhungkaw doctor chuan specialist doctor hnenah a refer ang che, chu chu:
- Haematologist a ni
- Gastroenterologist a ni
- General Physician a ni
Chuvangin i hmalakna hmasa ber chu i chhungkaw doctor nen i symptoms chungchang zalen taka inbiakna neih hi a ni tur a ni.
Doctor hmuh hmaa inbuatsaih dan tur chu hetiang hi a ni
Doctor nena hun i hman hun hi a tlem hle. I zawhna zawng zawng chhanna tur leh chu hun rei lote chhunga i dinhmun chiang taka doctor hnena pek theih nan chuan inbuatsaihna tlem nen kal a pawimawh hle. Hetah hian inbuatsaih dan tur kan rawn tarlang e.
| I tih tur chu | Engvangin nge a pawimawh? |
|---|---|
| I symptom zawng zawng list siam rawh. | "Pum na" leh "kut na" tih ang chi thil inzawm lo anga lang pawh hi natna inang chiah chhinchhiahna a ni thei. I ziak vek chuan doctor tan chuan a thlalak pum pui a hriatthiam a awlsam zawk. |
| Tuna i ei mek damdawi zawng zawng (vitamin te pawh tel) chipchiar takin ziak rawh. | Damdawi thenkhat hian AHP a tichhuak thei a, chuvangin i damdawi ei zawng zawng hi doctor hnenah hriattir a pawimawh. |
| I medical test report hmasa te kha rawn keng rawh. | Hei hian a tul lova test nawn leh a veng thei a, hun a tikhawtlai thei bawk. |
| Zawhna i hriat duhte chu lehkhaah ziak lawk rawh. | Doctor nena inhmuhna phurna chuan i zawhnate chu a theihnghilh tir thei che a ni. I ziah chhuah hunah chuan zawhna pawimawh ber berte zawh i theihnghilh lovang. |
| I chhungkuaa tu pawhin heng mizia hi an nei a nih chuan hre reng ang che. | AHP hi natna a nih avangin genetic influence a nei thei a, chuvangin i chhungkaw medical history chungchang hriat tur chu i doctor tan chuan a pawimawh hle thei a ni. |
Zawhna i doctor zawh ngei ngei tur
I dinhmun chungchangah zawhna zawh theihna i nei vek. Zawh hlau suh la, i rilrua thil awm zawng zawng zawng chhuak rawh. Hetiang dinhmun nen hian nung turin chakna nasa tak a pe ang che. Zawhna pawimawh tak tak i zawh theihte chu hetiang hi a ni.
AHP natna chungchang bulpui zir rawh
Heng zawhnate hian he natna hi eng nge a nih, engvangin nge a lo awm tih leh engtin nge a hnathawh tih hriat theih nan a pui ang che.
- Engvangin nge chiang takin AHP hi ka neih? Hei hi eng nge a chhan?
- Eng ang AHP nge ka neih? Mi pakhatin a rualin chi khat aia tam a nei thei ang em?
- Hetiang dinhmun hi ka fate hnena kai theih a ni em?
- He natna hian ka nunah eng nghawng nge a neih theih?
AHP leh i liver chungchang
'Hepatic' tih thumal hi "liver nena inzawm" tihna a ni. Chuvangin AHP leh thin inzawmna hi hriat a pawimawh hle.
- He natna hian ka thin a nghawng em?
- Ka liver a thawk tha em tih enfiah nan eng test nge ka tih ang?
- Ka thin venhim nan eng thil chiang tak nge ka tih ang? (e.g., ei leh in tur, damdawi ka ei tawh loh tur)
Enkawlna leh enkawl dan chungchang
Natna hi hriatchhuah a nih veleh a pawimawh ber chu a nunpui dan tur a ni.
- He natna hi eng enkawl dan nge ni?
- Engtin nge attack chu symptoms a lo lan hunah i control theih ang?
- Ka nunphung leh ei leh inah eng inthlak danglamna nge ka siam ang?
- Engtikah nge doctor rawn hmuh leh tur?
Heng zawhnate hi a bul tanna chauh a ni. I rilruah zawhna lo lang apiang chu i doctor hnenah zawh hreh ngai suh, eng ang pawhin tlem pawh ni se.
Take-Home Thuchah a ni
- AHP hi natna awm lo tak a nih avangin a hriat theih nan hun engemaw chen a la ngai thei. Chuvangin dawhtheih a pawimawh.
- Doctor i pan hmain i natna lan chhuah dan te, damdawi i ei dan te, zawhna zawh duh te chu ziakin uluk takin inbuatsaih rawh.
- Zawhna zawh leh i dinhmun hriat hlau ngai suh. I hriselna chungchang hriat theihna tur dikna i nei vek a ni.
- I doctor nen hnaih tak leh tlang taka thawk ho rawh. A thupekte chu dik takin zawm rawh.
- Enkawlna leh enkawl dan dik tak a awm chuan AHP nen hian hlawhtling takin i nung thei ang. Chuvangin, thinlung takin awm rawh.











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