Amniotic Band Syndrome hi eng nge ni?
A awlsam zawngin, hei hi nausen pum chhunga naute hualtu amniotic sac (chu chu ``Amniotic Sac'' kan tih) atanga tui band te tak te te chuan naute taksa a khuh hian a thleng thin. Naute chu tuiin a khat balloon ang maiin ngaihtuah rawh. Amniotic chhunga membrane nalh tak chu engti kawng pawhin a chhiat chuan thread ang emaw, band ang emaw-ah a inthen a, amniotic sac chhungah a inphah kual thei a ni. Hei hi ``Amniotic Bands'' kan tih chu a ni. Heng floating band-te hi, thread ball ang maiin, naute pum chhunga naute kut, ke, kut zungtang emaw, a taksa peng dang emaw-ah an inzawm khawm thei a ni. Heng band-te hi an inzawm tlat chuan chu hmuna thisen kal chu a tlahniam a, a châng chuan a tawp vek pawh a ni. Tichuan chu part chu a lo thanglian tha lo. A chang chuan hei hian naute chhungril lam leh umbilical cord thlengin a nghawng thei a ni. Hei hian nau piangsual (Congenital Disorders) a thlen thei a, a nasat chuan ke ruh a tikehsawm thei bawk. He natna hi a nasat dan chu band-te hi engtiang chiahin nge an khuh nghet tih leh naute taksaah khawiah nge an khuh tih a innghat a ni. Naute thenkhat chuan an pian tirh lamah vun tag te tak te, tight tak tak chauh an nei thei. Mahse, nausen thenkhat chu kut, ke, kut zungtang nei lovin an piang thei a ni. Heng band-te hian naute thisen kalna chu nausen (placenta) atanga a tihtawp chuan nunna atana hlauhawm tak a ni thei. Doctor-te chuan naupai laiin ultrasound scan hmangin he natna hi an hre thei ṭhin. Mahse, a tam zawkah chuan hei hi naute pian hnuah chauh a finfiah ngai lo. Hetiang dinhmun hi a tam vak lo. Nau piang nung 1,200 atanga 15,000 zinga 1 vel ah a awm thin. Tin, hetiang hian hriat a ni bawk:- Amniotic Band a awm dan tur
- Constriction Band/Rings Syndrome natna a ni
- Amniotic Band tihbuai theihna Complex a awm
- Congenital Constricting Band/Ring te chu a awm a
- ADAM Complex `(ADAM Complex - Amniotic Deformities/ Adhesions /Mutilations)` tih a ni a, a rilru a hah lutuk chuan a rilru a buai em em a, a rilru a hah lutuk chuan a rilru a buai em em bawk a
- Streeter Anomaly a ni
Hei hi eng symptoms nge ni? Engtin nge kan hriat theih ang?
Hetiang natna lan chhuah dan hi naute taksaah khawiah nge hrui chu a inzawm tih leh engtiang chiahin nge a inzawm tlat tih ah a innghat nasa hle.Za zela 80 velin kut leh ke a nghawng a ni. Mahse heng band te hi lu, kawr leh pum chhungah pawh an inzawm khawm thei bawk. A chang chuan hei hi a pawi lutuk lo. Vun chunglam panna thisen kal chu a ti tlem chauh a ni. Tichuan naute a pian hunah chuan vunah constriction rings, emaw, taksa peng hrang hrangah deformities te te ang chi thil a awm thei bawk. Mahse a châng chuan heng band-te hi a inzawm tlat a, a thuk lutuk a, chu taksa peng emaw, taksa peng emawa thisen kal chu a titawp vek a ni. Tichuan chu pêng chu a bo thei a, thisen supply a bo thei a, a châng chuan nunna atana hlauhawm harsatna a awm thei bawk. Hetiang dinhmunah hian symptom dang hmuh theihte chu:- Kut, ke, kut zungtang nei lo piang.
- Kut zungtang inzawm khawm (Syndactyly). Kut zungtang inkarah hian vun a awm thei a, chu chu duck vun ang mai a ni.
- A ke leh ke te hi a tawi a, a thang tha lo hle.
- Strap te inzawmkhawmna hmunah chuan swelling.
- Clubfoot a ni .
- Cleft Lip leh Cleft Palate a awm bawk .
- Ruh tichhe thei, scoliosis ang chi.
- Choanal Atresia (hnar kawng a lo thang kim lo). Hei hian naute thaw a ti harsa thei a ni.
- Mit te tak te emaw, a lo thang tha lo emaw (Microphthalmia).
Hei hian eng harsatna nge a thlen theih?
Amniotic band syndrome hian harsatna engemaw zat a thlen thei a, a then chu dam chhung zawng a ni thei bawk. Harsatna thenkhat chu a na hle a, nunna atana hlauhawm pawh a ni. Entir nan:- Luruh (Encephalocele) chhunga zungbun awm. Chutiang a nih chuan thluak thenkhat chu luruh kaltlangin a rawn chhuak thei a ni.
- Pum emaw, rilru emaw bang-ah khur emaw, deformities emaw a awm.
- System pawimawh tak tak, gastrointestinal system emaw genitourinary system emaw tihchhiat.
- Heng hrui te hi umbilical cord-ah an inzawm a, naute thisen kal dan a tikhawlo a nih chuan harsatna awm thei .
Engvangin nge amniotic band syndrome (ABS) hi a lo awm? A chhante chu engte nge ni?
Zirna tam takah chuan hei hi chhan chiang tak, chiang tak a awm lo tih a lang.A chhan ber chu amnion (naute hualtu tui bawm) chhung lam a chhiat vang nia ngaih a ni. He tui bawm chhiatna thlen thei thenkhat chu:- Test thenkhat chu naupai laiin tih thin a ni , chu chu Chorionic Villus Sampling (CVS) emaw Amniocentesis emaw te hi a ni. Hei hian tui bag chu needle hmanga hrual a, naute hnen atanga tui emaw tissue emaw sample lak a huam a ni. Mahse, heng test te hian harsatna a thlen hi a tlem hle.
- Open Fetal Surgery: Hei hi case na tak tak, nunna atana hlauhawm tak takah chauh tih a ni.
Mahse, amniotic band syndrome vei thenkhatah chuan tui bag hi a chhe lo tak zet a ni. Chuvangin, mithiam thenkhat chuan hei hi naute taksaa thisen kal dan lama harsatna awm vang niin an ngai. Naute thenkhat chu genetic influence vangin thisen kal tha lo an tam zawk mai thei.
Hetiang dinhmun hi tute nge hlauhawm ber?
Hetiang natna nei naute neih theihna chance hi a sang deuh thei a, chu chu:- Naupai laiin harsatna dang i neih chuan.
- `(Vascular Ehlers-Danlos Syndrome)` tih natna i neih chuan.
- Naupai laiin meizuk i nih chuan.
- Damdawi thurawn tel lova an pek loh damdawi i hman a nih chuan, emaw, naupai laiin damdawi thenkhat i ei a nih chuan.
Engtin nge hetiang chiah hian i diagnose?
Doctor chuan naute a pian hnuah, naute a enfiah hian he natna hi a hmuchhuak fo thin. Mahse a châng chuan, naupai laiin ultrasound scan-ah pawh hetiang chhinchhiahna hi hmuh theih a ni. Scan-ah hian tight bands avanga line awmte a lang thei. Mahse a tam zawkah chuan scan-ah hian ke leh ke a bo tih a lang a, a nih loh leh taksa peng hrang hrang a lo thang tha lo tih a lang.Hei hi engtiang chiahin nge scan-ah hmuh theih a nih?
Amniotic band syndrome symptoms hi a chang chuan naupai kar 12 hnuah pawh hmuh theih a ni a, mahse a harsa hle. A tam zawkah chuan i doctor chuan hetiang chhinchhiahna hi anatomy scan-ah a hmu ang a, chu chu kar 20 vel hnuah tih a ni. Ringhlelna a awm chuan i doctor chuan test dang, MRI (Magnetic Resonance Imaging) tih ang chi chu a ti thei ang.Hei hi eng enkawlna nge ni?
Enkawlna hi i naute pian hnuah tih thin a ni tlangpui. Enkawlna chi chu tape awmna hmun leh a tight danah a innghat. A nasat loh chuan doctor-in ngun taka enfiah a ngai mai thei.Mahse naute hriatna tichhe thei khawpa natna a nasat chuan enkawl vat a ngai a ni. A châng chuan operation hian clubfoot, cleft lip and palate, leh syndactyly ang chi harsatnate chu a siam ṭha thei ṭhin. Nausen leh naupang ke ruh bo emaw, tawi emaw nei te chuan prosthetics hmangin hlawkna an hmu thei a ni. Physical therapy leh occupational therapy hian heng artificial limbs te hi an hmang tangkai thei a, an hnathawh zawng zawng a ti tha thei bawk.A tlem hle a, doctor chuan naute chu nausen pum chhunga a la awm laiin amniotic sac lakchhuah nan fetoscopy an tih procedure a ti thei a ni. He surgery hian a tum ber chu tight sac chu chhuah zalen a, chhiatna dang a awm loh nan a ni. Mahse, he tih dan hian nu leh naute tan pawh hriselna atana hlauhawmna nasa tak a thlen thei a ni. Hei hi a tlangpuiin sac a tight lutuk a, nunna atana hlauhawm tak a nih chauhvin tih thin a ni.
He natna nen hian naute hi a dam thei ang em?
Ni e, naute tam tak chu he natna hi an nei a ni. An dam khawchhuah leh dam loh chu strap awmna hmun leh an tight dan ang chi thilah a innghat a ni.Heng amniotic band te hi an bo dawn em ni?
No. In most cases , amniotic bands avanga indentations emaw scars emaw te chu a bo lo. Hei hi band-te hian vun chhunga an luh thuk danah a innghat a ni. Heng hliam chi hrang hrang enkawlna tur awm thei te hi i doctor zawt rawh.Hei hi ven dan tur a awm em?
A nihna takah chuan amniotic band syndrome ven dan tur chiang tak a awm lo. Doctor-te chuan a tam zawkah chuan random-a thleng, chhan awm lovin a thleng niin an ngai.He dinhmun hi hmalam pan zelin engtin nge kan ngaihtuah ang? (Hmuh dan tur) .
Naute ABS na lo nei tan chuan outlook a tha hle. Naute piang, kut leh ke thenkhata danglamna nei te chu prosthetics leh rehabilitation programme-ah an insiamrem tha tlangpui. Mahse, naute taksa peng chhiatna nasa tak nei leh umbilical cord kaltlanga thisen kal tlem te chu an dam thei lo tlangpui. Nau piang thi 70 zinga 1 vel chu amniotic band syndrome vang a ni.I naute hian amniotic band syndrome a neih chuan eng nge i tih ang?
Hetiang natna vei naupangte hian puihna chak tak leh hun rei tak enkawlna an mamawh a ni.Nu leh pate, chhûngte, leh doctor-te chuan i fate chu he natnain a thlen ṭhin hmel lan dân inthlâk danglamna leh hnathawhna lama harsatnate chu a insiamrem theih nân an thawhho a ngai a ni. I fa hian specialist chi hrang hrang a hmuh a ngai mai thei. Entirnan, orthopaedic surgeon leh neurologist (taksa peng eng nge a nghawng dan a zirin). Chhungkaw member leh unaute pawhin he natna vei naupang nei chhungkaw tanpuitu pawlah tanpuina an hmu thei bawk. I naute hian amniotic band syndrome a nei tih i hriat chuan zawhna leh hlauhna tam tak i nei thei. A hmasa berah chuan i medical team te chu nang leh i naute tanpui tur, enkawl tha turin an awm tih hre reng ang che. I dinhmun dik tak chu band-te tight dan leh an awmna hmunah a innghat ang. Hei hian naupai laiin ultrasound scan neih fo a ngai dawn tihna a ni thei. A nih loh leh naute pian hnua operation neih a ngai thei a, hun rei tak chhung insiamthat a ngai thei bawk a, a nih loh leh taksa peng hrang hrang hmanga hnathawh leh theihna tur i mamawh thei bawk. He diagnosis chungchang leh i chhungte a nghawng dan tur chungchang hi i antenatal clinic doctor emaw i naute medical team emaw hnenah sawipui hlau suh.Take-Home Thuchah hnuhnung ber
Amniotic Band Syndrome hi thil hlauhawm tak a ni a, mahse hriat chian a pawimawh hle.- Hei hi thil awmdan a tlem hle.
- A tam zawkah chuan hetiang hi random takin a thleng thin a, chu chu tumah sualna a ni lo tihna a ni.
- Hetiang natna neia piang naute tam tak chu damdawi lam enkawlna tha leh chhungkaw puihna tha tak an neih chuan an dam tha hle.
- Hei hi naupai laiin hriat theih a nih chuan naute enkawlna mamawh tur ruahmanna siam a pui ang.
- Ringhlelna emaw zawhna emaw i neih chuan i doctor nen inbia ngei ang che. I mamawh information leh support zawng zawng an pe ang che. Lungngai suh, nangmah chauh i ni lo.
👩🏽 ⚕️ Zawhna dang (FAQ)
💬 Amniotic Band Syndrome hi nausen pum chhunga natna chi hrang hrang a awm?
Hei hi nu pum chhunga naute hualtu tuiin a khat sac (amniotic sac) chhunga membrane te tak te te chu a chhe vek a, naute kut, ke emaw, kut zungtang emaw a nghet taka inzawm khawmna dinhmun a ni. Hei hian nausen chhunga chu a inkhuh laiah thisen a kal loh nan a veng a, chu chuan nausen thanna a tikhawtlai a ni.
💬 He natna hian naupang tan eng ang harsatna nge a thlen?
Band hi engtiang chiahin nge a tight tih a zirin damage hi a inang lo. A châng chuan tlêm tê chauh a thlen thei a, mahse a tuam nghet lutuk chuan naute kut zungtang, kut leh ke te chu a ṭhang ṭha lo thei a, a piang lo emaw, a chhuak vek emaw a, amniotic fluid a leak chhuak thei bawk.
💬 Hei hi hriatchhuah leh enkawl hmasak theih a ni em?
Doctor-te chuan thla engemaw zat danah ultrasound scan hmangin an hre thei fo thin. A nasat em avangin tunah chuan fetoscopic surgery tih theih a ni tawh a, chutah chuan naute pian hmain nu pum chhungah camera bik dahin a membrane chu tan a, lakchhuah a ni.











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