Red blood cells hi i taksa chhunga cell leh tissue tinrengah oxygen thlentu delivery service a ni. He delivery service hian hna a thawk tha lo a nih chuan eng nge thleng ang tih han ngaihtuah teh? I taksain a mamawh oxygen a hmu lo. Chutah chuan kan chau a, kan chau a, kan thawk hah bawk. A awlsam zawngin, hei hi thisen tlakchhamna kan tih, a nih loh leh mi tam takin an hriat angin, ‘anemia’ kan tih hi a ni.
Anemia kan ngaihtuah hian a tam zawk chuan iron deficiency anemia kan ngaihtuah thin. Chu chu a chi hman tlanglawn ber a ni. Mahse, thisen tlakchhamna chi hrang hrang, mi tlemte chauhin an vei hi a tlem hle bawk tih i hria em? Vawiin hian chutiang thisen tlakchhamna chi hrang hrang, kan hriat vak loh te chu kan sawi dawn a ni.
Aplastic thisen tlakchhamna (Aplastic Anemia) a ni
Kan taksa thisen cell, chu chu thisen sen (red blood cells), thisen var (white blood cells) leh platelet te hi ruhro (bone marrow) a stem cells te hian an siam chhuak a ni. Bone marrow hi thisen cell siamna factory angin han ngaihtuah teh. He factory, stem cell tia koh a hnathawkte hi an chhiat chuan thisen cell thar an siam chhuak thei lo. Chu chu aplastic anemia kan tih chu a ni.
Hetiang dinhmun hi pian tirh lamah (nu leh pa hnen atanga gene rochun hmangin) a awm thei a, a hnuah pawh a lo awm thei bawk. Later-onset type hi hmuh tur a tam ber. A châng chuan hei hi rei lo tê chauh a ni thei bawk.
A hnu lama a thlen thei thilte:
- Autoimmune natna, lupus leh rheumatoid arthritis te.
- Chemical, pesticide, arsenic, leh benzene te nena inzawmna.
- Hepatitis, Epstein-Barr virus, leh HIV te ang chi natna hrik kai te.
- Cancer natna hi radiation leh chemotherapy hmanga enkawl dan tur a ni.
Hei bakah hian Fanconi anemia ang chi thlahtu natna avanga lo awm thei a ni bawk. Thâwk harsa, luak chhuak, lu na, vun dum, rilru na, leh tachycardia te ang chi natna lan chhuah theih a ni. Enkawlna hrang hrangah thisen pek leh stem cell thlak te a tel a ni .
Sideroblastic thisen tlakchhamna (Aneemia) a awm
Hei pawh hi thisen lama harsatna a ni. Thil thleng chu i taksain thisena oxygen phurtu protein hemoglobin siam nan a mamawh iron a hmang thei lo. Chumi hnuah chuan hman theih loh iron chu taksaah a pungkhawm a, thisen sen chi danglam tak, sideroblasts an tih chu a siam ta a ni.
Hei pawh hi chi hnih lian tak a awm bawk:
1. Acquired type: Chemical emaw damdawi thenkhat avanga lo awm thei a ni.
2. Hereditary chi hrang hrang: 1.1 .Hemoglobin siam chhuahna tichhe thei gene pakhata mutation avanga lo awm a ni.
Simptom hrang hrang, rilru na, thinlung na rang, lu na, thawk hah, leh hah lutuk te hi chi hnih ah hian hmuh theih a ni. Enkawlna chu a chhanah a innghat. Damdawi emaw chemical emaw avanga lo awm a nih chuan pumpelh tur a ni. Enkawlna dangte chu vitamin B6 therapy leh bone marrow transplant te a ni.
Myelodysplastic Syndrome (MDS) natna a awm thei lo.
Hei hi cancer chi khat anga ngaih a ni. Thil thleng chu i ruhro a chhia a, thisen cell hrisel a siam tling thei lo.
Mi thenkhat chu he natna thlentu gene neia piang an ni. Tin, mi tlemte chauhvin cancer natna atana radiation emaw chemotherapy emaw an pek hnuah MDS an nei thei bawk. Zuk leh hmuam-a awm, benzene ang chi chemical nena inzawmna pawh hi a hlauhawmna a ni.
Mi thenkhat chuan symptom an nei lo mai thei a, thenkhat erawh chuan a hnuaia symptoms te hi an nei thei a ni:
| MDS-a hmuh theih symptoms te |
|---|
| Bruising emaw thisen chhuak emaw awlsam tak |
| Hri kai fo leh khawsik |
| Thâwk harsa |
| Chauhna leh chak lohna nasa tak |
| Rihna tihtlem |
Oncologist leh hematologist te hian he natna hi an enkawl thin. Enkawlna kawng hrang hrangah chemotherapy leh stem cell transplant te pawh a tel.
Autoimmune Hemolytic Anemia atanga lo chhuak a ni
Kan ram venhimna sipaite hian pawn lam atanga hmelma lo kalte hi theihnghilhin kan ram mipuite bei tan ta se eng nge thleng ang tih han ngaihtuah teh? Chu chu he natna nei hian kan taksa chhungah a thleng thin.
A awlsam zawngin, i taksa ngeia immune system chuan i thisen sen hrisel tak takte chu hmêlmaah a ngai sual a, a tichhe ṭan ta a ni. Thisen sen thar siam theih ai pawhin an chhe chak zawk a ni.
Lupus ang chi autoimmune disease i neih chuan he natna hi i vei theihna a sang zawk. Damdawi thenkhat, penicillin ang chi te pawh a awm thei bawk. A lan chhuah dan chu hah, vun sen, thinlung na rang, thawk hah, khawsik, hnungzang na, vun sen (jaundice) te a ni. Immune system control thei tur enkawlna a awm a, chu chu steroid pek leh surgery hmanga spleen lakchhuah te hi a ni.
Anemia chi dang hmuh tur awm lo thenkhat
A chunga kan sawi tak chi hrang hrangte bakah hian thisen tlakchhamna chi dang engemaw zat hmuh tur awm lo tak tak a awm bawk.
Congenital Dyserythropoietic Anemia (CDA) atanga lo chhuak a ni.
Hei hi thisen tlakchhamna chi khat a ni a, rochun a ni. Taksa chhunga thisen sen hrisel tak tak tlem vang a ni. A chi hrang hrang 4 a awm a, mi thenkhat chuan enkawlna engmah an mamawh lo mai thei. Mahse, natna a nasat dan azirin thisen pek leh stem cell transplant ang chi enkawlna a ngai thei a ni.
Diamond-Blackfan atanga thisen tlakchhamna
Hei hi genetic changes avanga natna a ni bawk. Hetiang a nih chuan ruhro hian thisen sen (red blood cells) a siam tling thei lo. A lan chhuah dan chu thinlung thawk chak, hah, vun dum, sei tawi, leh ruh chak lo te a ni.
Megaloblastic thisen tlakchhamna (anemia) a awm
He thisen tlakchhamnaah hian ruhro hian thisen sen lian, puitling lo tak tak a siam chhuak thin. Hengte hian oxygen an phur tha thei lo. A chhan ber chu vitamin B12 emaw vitamin B9 (folate) emaw tlakchham vang a ni. Simptoms, luak chhuak, hah, luak chhuak, luak chhuak, leh taksa ruh na te a awm thei. Vitamin B12 leh B9 supplement te hi enkawlna atan pek thin a ni.
Fanconi thisen tlakchhamna
Hei pawh hi thlahtu natna a ni. Chutiang a nih chuan ruhro hian thisen cell a siam tlem hle. A lan chhuah dan chu ke ruh lian pangngai lo, hliam/thisen chhuah awlsam, natna hrik kai fo, thinlung leh kal lama harsatna nei, taksa leh lu te te a ni. He natna vei te hian cancer an vei theihna a sang hle a, a bik takin thisen cancer chi khat AML (Acute Myeloid Leukemia) .
Nang emaw i fa emaw hian heng symptoms pakhat emaw a aia tam emaw i neih chuan a tul lovah hlauthawng suh. Amaherawhchu, doctor pan vat a, thurawn lak a pawimawh.
Take-Home Thuchah a ni
- Anemia, a nih loh leh thisen tlakchhamna hi natna pakhat chauh a ni lo. A chi hrang hrang hman tlanglawn tak tak leh hmuh tur awm lo tak tak a awm.
- Chauhna, vun rawng hring, leh thawk hah ang chi symptoms hi thisen tlakchhamna chi hrang hrangah hian a awm fo thin. Hengte hi ngaihthah suh.
- Heng symptoms te hi i neih chuan mahni inhriatchhuah tir suh la, thu hriat atanga doctor thurawn pawh la suh. Damdawi thiam tak hmuh ngei ngei tur a ni.
- Anemia chi tin hi a chhan leh a enkawl dan a inang lo va, chuvangin diagnosis dik tak neih a pawimawh hle.
- Anemia chi hrang hrang hmuh tur awm lo thenkhat chu thlahtute atanga lo chhuak a nih avangin i chhungkaw damdawi lam chanchin i doctor hnena hrilh pawh a pawimawh hle thei bawk.











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