I fate thinlung thisen kalna bulpui chu a block em? He (Coarctation of the Aorta) chungchang hi i zir chiang ang u!

Kan thinlung te te hian mak tak maiin hna a thawk tih i ngaihtuah ngai em? Mahse a chang chuan pianpui harsatna thenkhat avang hian he thinlung hnathawh hi tlem a tibuai thei a ni. Chutiang thinlung natna pakhat, naute thenkhata lo awm thei chu `(Coarctation of the Aorta)` an ti a. A hming hi a buaithlak deuhin a lang thei a, mahse lungngai suh. Hemi chungchang hi awlsam takin han sawi ila.

`(Aorta Coarctation)` tih hi eng nge ni? A awlsam zawngin sawi ila...

A awlsam zawngin sawi ila, Coarctation of the Aorta chu i naute thinlung atanga oxygen tamna thisen taksa pengtu thisen kalna bulpui, aorta tihtlem emaw, zim emaw a ni. Hei hi pianpui thinlung natna a ni.

Ngaihtuah teh, kawngpui lian takah lirthei tam tak an tlan chak hle. Mahse, hmun khatah kawngpui i zim a, kawngpui pakhat chauh i phal chuan eng nge thleng ang? Traffic jam a awm a, driver te pawh an che tan ta a ni lawm ni? Chu chu he dinhmunah pawh hian a thleng thin. Aorta chhunga blockage kaltlangin thisen a kal tha thei lo.

A tam zawkah chuan he narrowing (coarctation) hi aorta atanga taksa hnuai lam thlenga thisen phurtu branch te, ke ang chi te inthen hmain a thleng thin. Eng thilin nge hei hi a thlen? Thisen sang hi naute taksa chunglam, kutphah ang chiah hian a sang a, mahse taksa hnuai lam, ke ang chiah hian a tlahniam thung. Hetianga taksa peng chunglam leh hnuai lam thisen sang inang lo tak hi he natna langsar tak a ni. Symptom dang awm lo mah se, doctor-te chuan he thisen sang inthlauhna hi an hmuh hian an ringhlel mai thei.

United States-a statistics-a a lan dan chuan kum tin naute piang 1,700 zinga pakhat vel chuan he natna hi an nei thei a ni (Aortic Coarctation). Naute thenkhat chuan hei bakah hian pianpui thinlung natna dang an nei thei bawk.

Naupangte hian he natna hi an neih hian eng symptoms nge an lantir?

Heng symptoms te hi aorta a tihtlem danah a innghat a ni. A tlangpuiin a tawi deuh a nih chuan nau piang atanga kar khat emaw kar hnih emaw chhungin symptoms a lang tan ang. Mahse, a narrowing hi a na lo zawk a nih chuan naute a lo puitlin hma loh chuan symptoms a lang lo thei a, a lang ngai lo thei bawk.

Nausen piang tharte natna lan chhuah dan

Nausen piang tharin he natna hi a neih chuan hetiang natna hi an nei thei a ni:

• Mutthilh reng leh bawnghnute in duh lohna
• Thinlung thawk chak (fast pulse) .
• Thaw hah lutuk
• Thinrimna, tap reng reng
• Vun dum emaw, vun dum emaw
• Thâwk rang emaw, thawkrim tak emaw
• Bawnghnute in harsat

Naute hian aorta -a coarctation na tak a neih chuan, hriatchhuah leh enkawl vat a nih loh chuan shock-ah a lut thei a, nunna atana hlauhawm tak a ni thei bawk. Mahse, naute thenkhat chuan a blockage a tlem em avangin symptom an nei lo mai thei.

Naupang tê leh puitling tleirawlte natna lan chhuah dan

Naupang kum upa zawk leh puitling tleirawl Aortic Coarctation vei te chuan hetiang hian natna lanchhuahna an nei thei a:

• Lu na fo thin
• Thisen sang a sang
• Hnar thisen chhuak fo thin
• Exercise, tlan emaw, zuang emaw laiin ke natna

Naupang thenkhat chuan symptom engmah an nei lo thei. Chu ai chuan, buaina chu routine well-check neih laiin thisen sang a nih thu hriat hmasak a ni.

Puitlingin heng symptoms te hi a neih hian a hmaa enkawl hnua aorta narrowing lo awm leh vang a ni fo thin. Hetiang dinhmun hi puitling thlenga hriat lohvin a awm hi a tlem hle.

Engvangin nge hetiang dinhmun hi a lo awm? A chhan engte nge ni?

Mithiamte chuan CoA thlen chhan dik tak hi an la hre lo. Mahse, genetic component a awm nia rin a ni. Chu chu nausen pum chhunga a awm laia gene inthlak danglamna thenkhat lo awm chuan naute aorta chu a lo thang tha lo thei tihna a ni.

A châng chuan heng genetic changes te hi chhungkaw kaltlangin a kai darh thei bawk. Zirchianna atanga a lan dan chuan CoA i neih chuan i naute hian CoA nei lo mi aiin CoA emaw thinlung natna dang emaw a vei tam zawk a ni.

Tin, CoA vei theihna hi genetic condition thenkhatah chuan a sang zawk bawk. Entirnan, naute genetic condition Turner syndrome neia piangte hian Coarctation of the Aorta chauh ni lovin, piansualna dang bicuspid aortic valve, thinlung valve-a chhiatna awmte pawh an nei tam zawk.

Thinlung chhiatna dang nei lo `(CoA)` chauh awm chhan

Isolated CoA awm chhan ber chu nausen pian chhuah laiin thisen kalna kawng te tak te, ductus arteriosus an tih chu a dik lo taka khar vang a ni. Ductus arteriosus hi thisen kalna kawng te tak te, nausen aorta leh pulmonary artery thlunzawmtu a ni. Nausen pum chhunga a awm lai hian lung a thawk tha lo a, chuvangin he tube hian naute hian a mamawh thisen oxygen tamna a hmuh theih nan a pui a ni.

Naute a pian hnuah chuan lungin hna a thawk tan a. Tichuan, he `(ductus arteriosus)` hi a tul tawh loh avangin ni rei lo te chhungin a mah chauhin a khar tan ta a ni. Mahse, a khar chuan chu duct chhunga tissue thenkhat chu `(Aorta)` tissue nen an inzawm khawm thei a ni. Chutiang a nih chuan `(ductus arteriosus)` chu khar tir a nih chuan aorta pawh a tawi thei (coarctation)`.

Hetiang dinhmun avang hian eng harsatna nge awm thei?

He natna (Coarctation of the Aorta) hi hun rei tak enkawl loha awm a nih chuan, harsatna hrang hrang:

• Taksa pumpuiah thisen sang (hypertension) a awm.
• Heart muscle chu a tlangpui aia thim zawk (left ventricular hypertrophy) a ni.
• Heart-a thisen pe chhuaktu coronary arteries-a plaque awmkhawm hi a tlangpui aia hmain a thleng thin - hei hi coronary artery disease an ti.
• Aorta-a bulge (aneurysm) emaw tear (dissection) emaw awm lo.
• Brain aneurysm (thluaka thisen kalna kawng bulging) a ni.
• Heart failure hi thinlungin thisen a pump tha thei lo tihna a ni.

He `(CoA)` dinhmun hi hriat chian loh leh enkawl a nih loh chuan a hlauhawm ber a ni. Chuvangin, a rang thei ang bera hriat chian a pawimawh hle a, a naupan lai a, a tul anga enkawl leh check-up (monitoring) neih reng a pawimawh hle.

Engtin nge doctor-te hian hei hi an hriat chian? (Diagnosis) tih a ni.

Naupang rilru lam doctor-te chuan nausen emaw, naupan lai emaw hian he natna (Coarctation of the Aorta) hi an hmuchhuak tlangpui. Engtiang chiahin nge a hriat chhuah thuai tih chu a natna lan chhuah dan a nasat danah a innghat.

Nausen symptoms na lo zawk nei te chu an pian atanga ni engemaw zat chhungin an hre thei a ni. Mahse, naute natna lanchhuahna na lo zawk nei, emaw, engmah nei lo emaw chu an upa a, thisen sang an neih hma loh chuan hriat theih an ni lo thei. Hei hi puitling hunah hriat chhuah a tlem hle.

Hetiang dinhmun hi naute leh naupang tê têteah hian taksa enfiahna neih laiin thil rinhlelh awm tak tak (red flags) hmuh a nih vang a ni fo ṭhin. Chutiang feature-te chu:

• Naute hian a kut leh a taksa chunglam ah thisen sang a nei a, mahse a ke leh a hnuai lam ah thisen sang a nei hniam thung.
• Kawr chhunga pulse rate leh groin-a pulse rate hi a danglamna a awm a.
• Doctor-in naute hnungzangah stethoscope a dah a, a ngaithla chuan thinlung atanga thawm danglam tak, khauh tak (‘harsh heart murmur’) a ri a.

Nau piang thar thenkhat chu natna lanchhuahna pawh an lan hmain an vei tih hriatchhuah an ni. Engtin nge i hriat? An thisena oxygen level tehna ``pulse oximetry`` tih test an tih chuan oxygen level a hniam tih an hmuchhuak. Oxygen level hniam hi pianpui heart disease na tak chhinchhiahna a ni thei a, chuvangin heng naute hi eng nge dik lo tih chiang taka hriat tumin test an ni.

He `(CoA)` dinhmun hi nemnghet turin doctor-te chuan `(Echocardiogram)`, heart scan, emaw `(echo)` emaw an hmang tlangpui. Naute aorta pianzia leh insiam dan hriat belh nan `(CT scan)` emaw `(MRI scan)` ang chi test an ti thei bawk.

``Coarctation of the Aorta'' nena inzawm thinlung natna dang a awm em?

Ni e, naute CoA vei te hi thinlung lam natna dang an nei tih hriat theih a ni. Entirnan, CoA vei zinga 45% leh 75% inkar hian bicuspid aortic valve tih natna an nei bawk. Chumi awmzia chu thinlung atanga aorta thlenga thisen phurtu valve hian a tlangpuiin a neih tur pathum ni lovin leaflet pahnih chauh a nei tihna a ni.

Chu mai ni lovin, `(CoA)` hi a hnuaia dinhmunte hian a zui thei bawk:

• Thinlung chhunga khur awm - chu chu `(atrial septal defect)` emaw `(ventricular septal defect)` emaw an ti.
• Nausen dam chhunga thisen kalna (`ductus arteriosus`) awm tawh chu beisei aia rei a inhawng reng a - hei hi ``patent ductus arteriosus`` an ti.
• Aortic arch hypoplasia emaw hypoplastic left heart syndrome emaw a awm thei.
• Heart valve a nghet lo - chu chu aortic valve stenosis emaw mitral valve stenosis emaw tihna a ni.

Cardiac surgeon-te chuan i naute thinlunga heng thil zawng zawng hi an en a, anmahni ta bik taka enkawl dan tur ruahmanna an siam thin. Hei hian a awmzia chu naute thinlung lama harsatna tam tak nei enkawl chu CoA pakhat chauh nei naute enkawl ai chuan a buaithlak deuh thei tihna a ni.

Hei hi eng enkawlna nge ni?

Enkawl dan tur chu i fa kum, aorta a tawi nasat dan leh thinlung lama harsatna dang a neih leh neih lohah a innghat a ni. Nausen leh naupang te te coagulopathy enkawl dan tha ber chu surgery hi a ni. Naupang kum upa zawk tan chuan narrowing a na lo zawk a nih chuan cardiac catheterization, surgery aiin invasive lo zawk hi a tha mai thei. Naupang leh puitling, a hmaa enkawl hnua a narrowing lo lang leh tawhte tan pawh hman a ni.

Inzai

He `(CoA)` dinhmun siamthat nan hian surgery chi hrang hrang tih a ni a:

• End-to-end anastomosis hmanga resection: Coarctation a tlem deuh chuan surgeon chuan naute aorta blocked part chu resect in a tawp la awmte chu a inzawm leh thei a ni.
• Resection chu a tawp atanga a tawp thlenga anastomosis tihzauh a ni:Naute aortic arch pawh a block a nih chuan surgeon chuan aorta blocked chu a cut chhuak thei a, descending aorta hnuai lam chu aortic arch-a incision sei takah a thlunzawm thei a ni. Hei hi naute hian transverse aortic arch hypoplasia leh aortic coarctation a neih chuan a tha ber.

Nausen pian hnua natna lanchhuahna na tak nei te pawh zai hmain damdawi pek a ngai thei bawk. Entir nan:

• Naute `(ductus arteriosus)` inhawng reng turin damdawi `(Prostaglandin (PGE-1))` tih hi pek theih a ni. Hei hian naute chu a mamawh oxygen a hmu thei ang a, operation atana an inpeih hma loh chuan a nghet thei ang.
• Naute chu a thinlungin thisen a pump theih nan damdawi i pe thei bawk.

Cardiac catheter hmanga tih a ni

I fain aortic narrowing a tihziaawm a nih chuan, emaw, operation hnua narrowing chu a lo lang leh a nih chuan, doctor chuan hetiang enkawlna tur a rawt thei ang:

• Balloon angioplasty: Surgeon chuan balloon te tak te hmangin naupang aorta a zim tawh chu a tizau thin.
• Balloon angioplasty with stent placement: Surgeon chuan naupang aorta a tihzauh laiin, a block leh loh nan tube te tak te, stent an tih chu a dah bawk.

Engtikah nge ka fa chu doctor hnenah ka hruai ang? (Examination nawn leh tur) .

I fa medical team chuan i fa hruai luh hun tur an hrilh ang che, i fa dam chhung zawng hian congenital heart disease specialist nen follow-up an neih a ngai dawn a ni. He specialist hian:

• Naupang thisen sang hi enfiah fo thin ang che.
• Naupang thinlung hnathawh dan leh harsatna a awm leh awm loh enfiah nan a hun taka scan (imaging test) tih.
• Lung hrisel ei leh in leh exercise chungchangah thurawn pek.
• Damdawi pek leh a tul angin a dose thlak danglam.

Hetiang natna vei hi eng chen nge a dam theih ang?

Diagnostic leh treatment method hmasawn tak tak hmangin Coarctation of the Aorta vei te chu kum 60 tal an dam thei tawh a ni. Tun hma chuan he natna vei te dam rei zawng chu kum 35 vel a ni. Chuvangin hei hi chanchin lawmawm tak a ni.

I naute hian Coarctation of the Aorta a nei a nih chuan engvangin nge a lo awm tih i ngaihtuah mai thei. Congenital heart disease awm chhan dik tak hi kan hmu chiang thei ngai lo. Mahse, a hmaa hriatchhuah leh enkawl hian he natna hian naupang nunah nghawng a neih chu nasa takin a tihziaawm thei tih kan hria.

Medical team te chu i fate tanpui turin an awm reng a ni. Zawhna i neih apiang chhang turin an inpeih reng a, he (CoA) diagnosis hian i fate a nghawng dan tur hriatthiamna atan an inpeih reng bawk. Hetiang thinlung natna nei naupang nu leh pa dangte nena inbiakna neih pawh a \angkai hle mai thei bawk.

Thil pawimawh hriat reng tur (Take-Home Message) .

Tunah chuan kan sawi tawh ``Coarctation of the Aorta'' tih dinhmun hi hriatthiamna engemaw chen in neih ka beisei. Hriat reng tur pawimawh tak tak thenkhat chu hetiang hi a ni:

• Hei hi pianpui thinlung natna a ni a ; thinlung atanga taksa panna thisen kalna main artery-a blockage.
• Nausen laiah symptoms a awm thei a, a hnuah pawh a lo lang thei bawk. I naute chu mutthilh lutuk, thawk harsa lutuk, emaw, hnute pek duh lohna i hriat chuan doctor thurawn zawng nghal rawh.
• Natna hi a hmaa hriatchhuah leh enkawl a nih chuan naupang chu nun pangngai, hrisel taka nun theihna chance a pe tam zawk a ni.
• He natna hi surgery leh enkawlna dang hmangin hlawhtling takin enkawl theih a ni.
• Enkawl hnuah pawh dam chhung specialist medical supervision hi a pawimawh hle.

Hlau suh. Tunlai hian Medical science hi a lo changkang hle a. I fa enkawlna tha ber pe thei doctor thiam tak tak an awm a. A pawimawh ber chu hei hi i hriat chian a, i fa inthlak danglamnate ngaihven a, a hun taka damdawi lam thurawn i lak hi a ni.

` Coarctation of the Aorta, Lung natna, Naupang enkawl, Pianpui Lung natna, Aortic Stenosis, Naupang hriselna, Thisen sang