A chang chuan thawk hah deuh i nei em, a nih loh leh i rilruah thil mak tak a awm em? I lung chhunga thisen kalna kawng chhunga pressure a sang deuh vang pawh a ni thei. Hei hi natna bik `(Chronic Thromboembolic Pulmonary Hypertension)` emaw `(CTEPH)` emaw an tih a ni. Lungngai suh, he thu hi awlsam takin, i hriatthiam theih dan tur angin kan sawi dawn a ni.
Hei hi eng nge ni `(CTEPH)`? I hrethiam ang u!
A awlsam zawngin sawi ila, CTEPH hi lung chhunga thisen kalna kawng te tak te chhunga thisen sang tihsan dan pangngai lo a ni. Tui pipe chhunga pressure ang mai a ni. Mahse a chhan ber chu i lungah thisen zam i lo nei tawh a (hei hi Pulmonary Embolism kan ti a) chu thisen zam chu a lo hmin tha lo . Chutah chuan he pressure hi a lo sang chho ta a ni.
Tute nge CTEPH vei tam zawk?
Hei hi a pawimawh hle. CTEPH hi pulmonary embolism nei tawhte tan chauh a awm thin . I lungah pressure sang tak nei mahse thisen zam a awm lo a nih chuan CTEPH a ni lo mai thei a, mahse dinhmun danglam tak a ni thei. Chuvangin he danglamna hi hriatthiam a pawimawh.
Hetiang dinhmun hi engtiang chiahin nge a awm?
CTEPH hi a takah chuan natna hlauhawm tak a ni . Entirnan, United States ang ramah chuan kum tin mi 5,000 vel chauh hri kai thar an awm thin. Mahse, a châng chuan a hriat chian loh avângin, a tam zâwk pawh a ni thei. Chuvang chuan a natna lan chhuah dan fimkhur a pawimawh hle.
CTEPH hian i hriselnaah eng ang nghawng nge a neih theih?
I lung chhunga pressure a san chuan, a bik takin CTEPH-ah chuan i thinlung dinglam chuan pressure nasa tak a nei thin . Ngaihtuah teh, i thinlung hian i lung chhunga thisen pump turin a thawkrim zawk a ngai a ni. Thil thleng chu oxygen tlakchhamna thisen thenkhat chu i thinlungah a tang a, i lungah a thlen theih nan hun rei tak a ngai a ni. Hei hian i taksaah oxygen level a ti hniam thei a ni. Hei hi natna khirh tak a ni a, a dik lo em ni?
Engvangin nge he `(CTEPH)` hi a lo thanglian? A chhante chu engte nge ni?
Hei hi a chhan ber chu lung chhunga thisen kalna kawng te tak tea thisen zam (blood clots) lo awm thin te hi a inthiar tha tawk lo vang a ni. When this happens , scar ang chi tissue chu clots awmna hmunah a lo piang thin. He hliam hian thisen kalna kawng a tizau a, tui pipe a inkhar ang maiin a ti tawi a ni. He narrowing hi a san chhoh zel chuan pressure pawh a sang chho zel bawk.
CTEPH vei theihna tur risk factors te chu engte nge ni?
`(CTEPH) lo piang chhuak thei tur risk factor thenkhat a awm. Eng nge an nih hi han thlir ila:
- Type O tih loh thisen chi dang nei.
- Ruh chhunga natna hrik (Osteomyelitis) neih.
- Cancer chi hrang hrang.
- Intestinal natna rei tak, entirnan, `(Inflammatory Bowel Disease)` ang chi natna te.
- Hmeichhia nih hi. (Hmeichhia hian mipa aiin he natna hi an vei tam zawk deuh.)
- Pacemaker hmanga thinlung tissue infection.
- Nang emaw, i chhungte emaw hian thisen zam natna, Antiphospholipid Syndrome ang chi hi i nei tawh a ni.
- Tun hmain a spleen lakchhuah (Splenectomy) a nih tawh avangin.
- Thyroid hormone thlak danglamna therapy ei.
Heng zawng zawng hian mi zawng zawng a nghawng vek lo a, mahse risk factor anga hriat chhuah a ni.
`(CTEPH)` natna lanchhuahna chu engte nge ni?
CTEPH vei chuan a natna lan chhuahna a nei thei a, chungte chu:
- Chest na emaw tightness emaw hriatna .
- Thisen khuh (hei hi thil thleng tlem tak a ni).
- Kut zungtang leh ke ruhte chu blue discoloration (Cyanosis) a ni.
- Luak chhuak tih hriatna .
- Syncope a ni.
- Chau lutuk tih hriat (`Fatigue`) .
- I rilru a na ang maia i hriat chuan hei hi ``Heart Palpitations'' kan ti thin.
- Thâwk harsa , a bik takin thil tih emaw, kea kal emaw hian.
- Ke a hring, chu chu taksaa tui awmkhawm (edema) vang a ni.
Heng symptoms pakhat emaw pahnih emaw i neih vang mai mai hian CTEPH i nei tih ngaihtuah suh. Mahse heng symptoms te hi a awm reng chuan doctor pan a tha ber.
He natna `(CTEPH)` hi engtin nge an hriat chhuah?
Doctor i hmuh hian CTEPH a awm leh awm loh enfiah nan test thenkhat a ti hmasa thei a, chungte chu:
- Thlawhna leh thisen kal dan enfiahna test (`(Lung ventilation-perfusion scan - V/Q scan)`).
- ``Pulmonary Angiogram'' tih hi lung chhunga thisen kalna kawng (blood vessels) a thisen zam emaw, a zim emaw enfiahna a ni.
- Pulmonary Function Test neih a ni.
- Transthoracic Echocardiogram (TTE) hi thinlung ultrasound scan ang a ni.
Heng test hmasa berte hnuah hian CTEPH natna hmuhchhuah leh a nasat dan hriat chian nan test dang neih belh a ngai mai thei. Chûng zîngah chuan:
- Right Heart Catheterization hi thinlung dinglamah tube te tak te dahin pressure tehna test a ni.
- CT Pulmonary Angiography (CTPA) emaw Digital Subtraction Angiography emaw ang chi advanced imaging technique hmangin lung chhunga thisen kalna kawngte chu enfiah thin ang che.
- MRI scan a ni.
- Exercise neih laiin thinlung hnathawh dan enfiahna ``Exercise Stress Test'' a ni.
Heng test te hian doctor te chu CTEPH i vei em tih leh eng stage ah nge a nih tih chiang taka hriat theihna a ni.
`(CTEPH)` enkawlna tur engte nge ni?
CTEPH enkawlnaah hian operation emaw chutiang chi emaw a ni tlangpui. Thil tih theih chi hnih a awm a, chungte chu:
1. Pulmonary Endarterectomy : Hei hi open surgical procedure a ni. Hetiang tih danah hian thisen zam hlui leh scar tissue chu lung thisen kalna kawng chhunga tangte chu operation hmangin an la chhuak thin. Hei hi lung chhunga thisen kal lehna tura tih a ni.
2. ``(Pulmonary Balloon Angioplasty) tih a ni ang.: Hetah hian balloon te tak te chu tube sei tak (catheter) tawp lamah an bun a, chu chu lung chhunga thisen kalna kawng zim takah chuan a lut a ni. Balloon chu scar tissue chu a sir lamah nawr turin an inflated a, thisen kalna chu a zau leh ta a ni.
Heng kawng hnih zinga pakhat thlan hi thil tam takah a innghat a, chu chu damlo dinhmun leh thisen zam awmna hmun te hi a ni.
Enkawlna dang a awm em?
Ni e, mi thenkhat chuan he surgery hi an nei thei lo mai thei. Chutiang mite tan emaw, operation hnua an lungah pressure nei chhunzawm zelte tan chuan `(Riociguat)` an tih pill hi pek theih a ni. Hei hi pulmonary hypertension damdawi pek a ni. Hei hian symptoms a ti reh thei a ni.
CTEPH hi ven theih a ni em?
CTEPH hi hriselna lama harsatna dang tam tak nena inzawm a ni. Thil thenkhat chu kan thunun thei lo. Mahse i tih theih pawimawh ber chu i lung enkawl that hi a ni . Chu chu zuk leh hmuam i zuk chuan bânsan a, zuk leh hmuam laka inthiarfihlim chu a pawimawh hle tihna a ni.
CTEPH vei damlote tan eng nge an hmalam hun?
Hei hi chanchin tha ber a ni! Pulmonary Endarterectomy leh Pulmonary Balloon Angioplasty hmangin CTEPH hi a tidam vek thei a ni . Heng enkawlna hmang tam tak hian result tha tak tak an tawng thin.
Mahse, heng result \ha tak takte hi awm mah se, damlo ṭhenkhat chuan rilru lama harsatna, lungkhamna, leh lungngaihna engemaw chen an nei thei a ni. Hei hi a bik takin a chunga kan sawi tak damdawi hmanga enkawlna dawng thei lote tan chuan a dik thei hle. Heng rilru lama harsatna te hi i tawk a nih chuan i doctor nen inbia ang che. I lungkhamnate chu an ngaithla thei a, i rilru hahdamna tur enkawlna an rawt thei bawk.
`(CTEPH)` nena kan khawsak hian eng thil nge hriat tur pawimawh?
- I dam chhung zawng thisen tithianghlimtu damdawi i ei a ngai mai thei .
- Warfarin ang damdawi i ei a nih chuan ei tur thenkhat (soy leh broccoli ang chi, vitamin K tamna) kha tihtlem a ngai mai thei. Hemi chungchang hi doctor zawt rawh.
- Light exercise , kea kal ang chi hian mi tam tak chu chakna an neih leh theih nan leh hrisel taka awm turin a pui thei a ni. I doctor chuan supervised exercise program (pulmonary rehabilitation) neih a rawt thei bawk.
A tawp berah chuan hei hi hre reng ang che.
Chronic Thromboembolic Pulmonary Hypertension (CTEPH) hi natna hlauhawm tak a ni a, chu chu lung thisen kalna kawnga thisen sang a sang a, mahse a hmaa hmuhchhuah a nih a, a \ha taka enkawl a nih chuan enkawl theih natna a ni Heng symptoms te hi i neih chuan doctor thurawn la hreh suh. Inenkawlna mumal tak an neih chuan mi tam zawk chu an dam tha thei tih hre reng ang che. Chuvangin hlauthawng suh. Doctor thupek chu uluk takin zawm la, i dam thuai thei ang!
`CTEPH, Pulmonary Hypertension, Thisen zam, Thâwk harsa, Lung natna, Pulmonary Embolism, Pulmonary Hypertension











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