Connective Tissue Disease chungchanga hriat tur pawimawh te

I taksaah natna leh natna, ruh natna emaw, i vunah danglamna dang emaw i nei fo em? A châng chuan heng thilte hi kan theihnghilh a, hahdamna pangngai emaw, tar chakna emaw mai mai niin kan ngai. Mahse, a châng chuan heng inzawmna nei lo anga langte hi kan taksa chhungril takah thil thleng chhinchhiahna a ni thei bawk. Chu chu vawiina kan sawi tur natna pakhat a ni. Chu chu connective tissue disease a ni a, English-a kan sawi angin ‘Connective Tissue Disease’ a ni.

A awlsam zawngin, connective tissue chu eng nge ni?

Kan taksa hi building ang maiin han ngaihtuah teh. He building chhunga hmun hrang hrangte inzawmkhawm leh vawn tlat nan, a nghet taka awm theih nan cement leh mortar ang chi thil kan hmang thin a ni lawm ni? Chutiang bawkin, kan taksaa thil awm zawng zawng, taksa peng hrang hrang, ruh, leh taksa peng hrang hrangte inzawmkhawmtu, thlawptu, leh humhimtu tissue chi chu connective tissue . Hengte hi protein tamna tissue an ni. Thau, ruh leh ruh (cartilage) te hi he connective tissue entirnan thenkhat an ni.

Chuvangin, heng connective tissue tichhe thei condition te hi ‘Connective Tissue Disease’ kan tih hi a ni. Hemi zingah hian natna chi hrang hrang 200 chuang a tel a ni. Hengte hian i ruh, ruh leh vun a nghawng ber a ni. Tin, chhungril peng hrang hrang mit, thinlung, lung, kal leh thisen kalna kawng te pawh a nghawng thei bawk.

Heng natnate hi chi hnih a awm a.

He natna pawl hi chi hnihah then theih a ni. Chu chu hriatthiamna chuan heng natnate hi hriatthiamna nasa zawk i neih theih nan a pui ang che.

Hriselna lama natna lian tham thenkhat

• Ehlers-Danlos Syndrome (EDS): Hei hian ruh a ti na lutuk a, vun a ti hrual a, hliam dam laiin hliam pangngai lo a awm bawk. Spinal deformities leh heart valve lama harsatna te pawh a awm thei bawk.
• Marfan Syndrome: Heng mite hi an sang hle tlangpui. Kut zungtang chu a sei em avangin rulhut ke ang maiin a lang thei. Mit, thinlung leh thisen kalna bulpui (aorta)-ah harsatna a awm thei.
• Osteogenesis Imperfecta: Hei hi "brittle bone disease" tia hriat a ni bawk. Ruhte chu a chhe awlsam hle. A lan chhuah dan chu mit var-ah blue/gray tinge a awm a, ha a chhe awlsam a, hriatna a hloh bawk. Hei hi ruh leh vun tana protein pawimawh tak collagen siamna kawnga genetic defect vang a ni.
• Epidermolysis Bullosa (EB): Vun hi a sensitive hle. A hliam tenau emaw, thawmhnaw a hnawih emaw pawh hian blister leh hliam a thlen thei.

Autoimmune natna engemaw zat

Hengte hi connective tissue natna chi hrang hrang zingah chuan a tam ber a ni.

• Rheumatoid Arthritis (RA): Hei hi ruh natna mai a ni lo. Hetiang dinhmunah hian immune system hian ruhkawr khuh tu membrane te tak te chu a bei thin. Hei hian ruh natna, a hring, a lum, leh zing lama ruh a ti na . Chu bâkah, hah lutuk te, thisen tlakchhamna te, chak lohna inhriatna te a awm thei bawk.
• Systemic Lupus Erythematosus (SLE) - Lupus: Lupus hi a rualin taksa peng tam tak a nghawng thei a, a rualin taksa peng tam tak a nghawng thei a ni. Butterfly rash hi a lan chhuah dan tlangpui a ni . Chu bakah, hmui na, sam tlakchham, ni êng laka sensitivity, kal harsatna, leh ruh na te a awm thei bawk.
• Scleroderma: Hei hi a lan chhuahna ber chu vun a thim leh a khauh hi a ni. A stretch tha lo. Hei hi vunah chauh a ni thei a, a nih loh leh chhungril taksa peng hrang hrang a nghawng thei bawk.
• Sjögren’s Syndrome: Hetiang dinhmunah hian immune system hian hmui leh mittui siamtu glands te chu a bei thin. Mit vawt leh hmui vawt hi a lanchhuahna ber a ni. Chauhna leh ruh natna te pawh a awm fo.
• Polymyositis leh Dermatomyositis: Heng natna pahnih hian taksa ruh a ti na a, chu chuan taksa ruh a tichak lo ., a bik takin kekawrte leh kekawrteah. Chair atanga tho emaw, stairs chhoh emaw chu a harsa ta hle. Dermatomyositis hian vun a tichhia bawk a, a bik takin mit vel leh kut chungah a tichhia a ni.

Engtin nge he natna hi i neih leh neih loh i hriat theih ang?

Heng symptoms te hi i neih chuan i tih theih pawimawh ber chu doctor thiam tak i pan a ni. Mahni inhriatthiamna hian hlauhna tul lo tak a thlen mai dawn a ni. I doctor chuan a enfiah ang che a, i symptoms leh chhungkaw medical history te a zawt ang che.

Chumi hnuah chuan test eng emaw zat neih a rawt thei a, chu chu a natna hmuhchhuah a ni:

• Thisen leh zun test: Taksa chhunga inflammation leh specific antibody awm leh awm loh enfiah thin.
• X-ray leh MRI scan: Ruh, ruh leh taksa peng hrang hrangte dinhmun enfiah thin.
• Tissue Biopsy: Vun emaw, ruh emaw te tak te tak tak lak a, microscope hmanga enfiah.
• Mit leh hmui a vawt leh vawt loh enfiah: Sjögren’s Syndrome ang chi natna te hriatchhuah.

Engtin nge enkawl a nih?

Enkawl dan tur chu natna chi khat i neih leh a nasat danah a innghat vek a ni. Mi zawng zawng tan enkawlna pakhat chauh a awm lo.

• Mi thenkhat tan chuan vitamin emaw nutritional supplement emaw pek hi a tawk mai thei.
• Autoimmune natna tam tak tan chuan immune system hnathawh control thei damdawi pek thin a ni.
• Damdawi hi natna leh hliam thunun nan pek thin a ni.
• Joint leh muscle function tha tak neih theih nan physiotherapy treatment hi a pawimawh hle.
• Specialist hrang hrang, dermatologist emaw mit surgeon emaw tanpuina i lak a ngai thei bawk.

A pawimawh ber chu doctor nen inbiak reng hi a ni . Symptom-ah danglamna a awm emaw, symptom thar a awm chuan doctor hnenah hriattir nghal tur a ni.

Heng natnate hi a pawi thei em?

Ni e, connective tissue natna thenkhat hi enkawl that loh chuan harsatna lian tak a thlen thei a ni. Entir nan:

• Pulmonary Hypertension tih a ni
• Interstitial Lung natna a ni
• Lung natna leh kal (kidney) a chhia
• Thisen tlakchhamna (Anaemia).

Mahse hetah hian hlauh a ngai lo.Heng harsatna tam tak hi a hun takah natna hriatchhuah a, damdawi lam enkawlna leh thurawn dik tak zawm a, ven leh thunun theih a ni. Chuvang chuan i taksaah natna i hriat veleh enkawl vat tur kan ti a ni.