Ngaihtuah teh, i pa emaw, i pasal emaw, i hnaih em em tu emaw... Vawikhatmah a nungchang chu a danglam vek. Tun hmaa mi ngilnei tak leh mi khawngaihthlak tak ni thin kha tunah chuan midangte chungah thil tihnatthlak tak tak a sawi thin a, khawtlang nunah pawh a nungchang mawi lo takin a awm ta a ni. Hei hi rilru lama harsatna chi khat, depression ang chi pawh a ni mai thei. Mahse, hei hi thil danglam tak a ni thei a, thluak nena inzawm thil a ni thei. Vawiin hian hetiang inthlak danglamna thlentu, Alzheimer natna nena danglam, mahse mi tam takin an hriat loh dinhmun kan sawi dawn a ni. Chu chu Frontotemporal Dementia, a nih loh leh FTD a ni.
Frontotemporal Dementia (FTD) hi eng nge ni?
A awlsam zawngin sawi ila, FTD hi kan thluak hmalam leh hnunglam (frontal and temporal lobes) a chhiat avanga lo awm thin a ni. Chûngte chu kan mize, kan nungchang leh kan ṭawngkam thununtu pêngte chu an ni. Chuvangin heng parts te hi a chhiat chuan symptoms te hian memory loss aiin a kal pel thin. Mi nungchang te, a thusawi dan te, tawngkam a hriatthiam dan te, a taksa chetna thlengin a danglam thei a ni.
FTD hi Alzheimer’s angin hriat hlawh lo mah se, dementia vei zinga 10% leh 20% inkar chuan FTD chi khat emaw an nei a ni. Dementia chi dang aiin a intan hma thei a, a tlangpuiin kum 45 leh 60 inkar a nih avangin nunah nghawng lian tak a nei thei a ni.
A lan chhuah hmasak ber, mi rilru na, ngilnei lo, emaw, lemchan thiam loh emaw a nih avangin rilru natna anga hriat sual a ni fo. Hei hi FTD hi a tir lama tihkhawtlai fo chhan lian tak a ni. I doctor chuan Pick natna tiin a sawi thei bawk.
FTD chi hrang hrangte chu engte nge ni?
FTD hi a lan chhuah hmasak dan a zirin chi hrang hrangah then theih a ni. Hei hi chiang taka hrethiam tur chuan he table hi han en ila.
| FTD chi hrang hrang | Hmuh theih thil langsar ber ber |
|---|---|
| Frontal variant a ni | Mihring leh nungchang lama inthlak danglamna lian tak tak, mi rilru na leh zak lo nih ang chi te. Hei hi FTD chi khat hman tlanglawn ber a ni. |
| Thusawi leh tawng tichhe thei chi (Primary Progressive Aphasia) . | Hetah hian sub-section lian pahnih a awm a: - Thusawi harsa (Progressive nonfluent aphasia): Thumal siam harsa. - Thumal hriatthiam harsa (Semantic dementia): Thumal awmzia theihnghilh, hmel leh thil hriat theih loh . |
| Taksa chetna tichhe thei chi hrang hrang | Hengte hi hmuh tur a awm lo. - FTD-ALS: Hetiang a nih chuan FTD natna lanchhuahna rual hian taksa ruh tichak lotu Amyotrophic Lateral Sclerosis (ALS) an tih natna lanchhuahna a lo lang bawk. - Parkinsonian ang chi FTD syndromes: Parkinson natna ang chi symptoms, khur leh rigidity te. Chutiang natna pakhat chu Progressive Supranuclear Palsy (PSP) a ni. |
FTD natna lan chhuahna awm thei te chu engte nge ni?
FTD natna lan chhuah dan hi mi hrang hrangah a inang lo. Hun kal zelah an na zual deuh deuh thin. Heng symptoms te hi category engemaw zat hnuaiah han thlir ila.
Nungchang a inthlak danglam thin
- Socially indecent: I rilru a awm chu zahpui lovin a sawi thin. Midangte hnenah thil tihnatthlak tak tak a hrilh a, midang hnaih lutuk a duh.
- Lainatna hloh: Midangte rilru put hmang hrethiam thei lo. Mi pakhat chu thinlung lum tak ang maiin a che thei.
- Apathy: Hmanlai thil hlimawm tak takte ngaihvenna emaw, ngaihsak lohna emaw.
- Thil inang sawi nawn leh nawn leh: Kut beng, hmui seh, etc. Thu leh ri inang lo sawi nawn leh.
- Mimal faina ngaihthah: ha sil loh leh inbual loh.
- Ei leh in lama inthlak danglamna: Vawi khata sweets tam tak ei, a chang chuan i tana tha lo thil ei tum.
Thusawi leh tawng inthlauhna
- Thusawi lai hian thu dik tak hmuh a har khawp mai.
- Thumal hian awmzia a hloh zel a.
- Thumal awlsam tak, thumal tawi tak tak hmangin a sawi thin.
- A châng chuan thil sawite hian awmzia a nei lo mai thei.
Taksa chetna inthlak danglamna
- Mit tihchet harsat.
- Taksa a khur, taksa ruh a ti na.
- Taksa a nghet lo.
- Taksa thununna hloh.
- Chaw ei harsa.
- A thawnthu hi a buaithlak khawp mai.
- Ka tlu dawn a, kal a har dawn khawp mai.
A bik takin, FTD nena inzawm Progressive Supranuclear Palsy (PSP) vei te dinhmun hi Parkinson’s vei te nen a danglam hle. Parkinson vei te chu hmalam hawia an awm laiin PSP vei te chu ding chungin emaw, hnunglam hawiin emaw an ding thung. Hei hian hnunglam hawia tlu duhna a siam a ni.
FTD vei chhan leh hlauhawmna te chu engte nge ni?
FTD vei te thluak cell (neurons) an thih chuan thluak hmun thenkhat chu a tlahniam thin. Scientist-te chuan hei hi kan taksa siam protein thenkhat hnathawh dan pangngai lo avanga lo awm niin an ngai. A bik takin, he chhiatna hi thluaka protein pahnih tau leh TDP-43 an tih, chi danglam tak tak a awm khawm vang a ni.
FTD vei zinga 40% vel chuan chhungkaw history-ah he natna hi an nei tawh a ni . Hei hian genetic a ni thei tihna a ni. Chu bâkah, thil dangin a hlauhawmna a tipung thei bawk:
- Lu hliam na tak: Hei hian FTD vei theihna chu a let thum velin a tipung thei a ni.
- Thyroid natna: Hei hian a hlauhawmna chu a let hnih aia tam a tipung a ni.
Engtin nge FTD hi hmuhchhuah a nih?
FTD hi dik taka hriat a harsa thei a, a chhan chu a lan chhuah dan chu natna dang, Parkinson’s, Alzheimer’s, depression, leh schizophrenia te nen a inang thei a ni.
Chuvangin, i hnaih bertu nungchangah hetiang thil mak tak, sawifiah theih loha inthlak danglamna hi i hmu a nih chuan ngaihthah suh. Doctor hmu ngei ang.
Doctor chuan i chhungkaw chanchin a zawt ang a, natna dang a awm loh nan thisen test a ti mai thei bawk. Neurologist hnenah an refer fo ang che. I balance, reflexes, memory, leh ngaihtuahna thiamna ang chi thilte chu a test ang. FTD finfiah nan hetiang test hi order theih a ni:
- CT scan: Thluak X-ray hmanga thlalak chipchiar tak.
- MRI scan: Magnet leh radio wave hmangin thluak thlalak chiang tak tak a siam chhuak thin.
- FDG-PET scan: Thluak peng hrang hrangte chu engtiang chiahin nge an active tih hriat nan radioactive substance chu thisenah inject a ni.
- EEG (electroencephalogram): Thluak electric hnathawh dan tehna a ni.
- Spinal tap: Thluak leh ruhro vel tui awmte enfiah.
- Neuropsychological testing: Rilru lama theihna tehna, hriatrengna, tawng thiamna leh ngaihtuahna thiamna te chu zawhna chhanna, thlalak siam leh puzzle chinfelna hmanga teh a ni.
FTD enkawlna tur engte nge ni?
Vanduaithlak takin FTD hi damdawi leh enkawlna a la awm lo. Alzheimer natna enkawlna atana hman damdawi te hian FTD tan hna a thawk lo. A then phei chuan heng damdawi te hian symptoms a ti na zual thei bawk.
Mahse, natna lan chhuahna enkawlna atana pui thei damdawi leh enkawlna thenkhat a awm a:
- Antidepressants: Mood leh nungchang lama harsatna awmte control.
- Antipsychotics: Nungchang lama harsatna lian tak takte control thei mah se, side effect na tak a nei thei a ni. Chungte chu doctor enkawlna hnuaiah chauh hman a ni.
- Speech therapy: Inbiakpawhna lama harsatna awmte tanpui.
FTD nena khawsa leh enkawl
He natna hi damlo leh chhungte tan pawh harsatna lian tak a ni. Chuvang chuan natna a hriat chian veleh doctor thiam tak hnen atanga tanpuina lak a pawimawh hle.
FTD vei enkawltu i nih chuan...
He zinkawng hi enkawltu tan chuan hahthlak tak a ni thei. I tanpui thei tur thil thenkhat chu hetiang hi a ni:
- Diary vawng rawh: Damlo nungchang inthlak danglamna leh a thlentu trigger te chhinchhiah rawh. Hei hian harsatna awm thei dinhmunte pumpelh turin a pui thei che a ni.
- Thil tih dân mumal tak siam rawh: Damlo chuan a ruala chaw ei leh inbual ang chi thil aṭangin hahdamna engemaw chen a hmu thei a ni.
- Mi dangte hnênah thil awm dân hrilhfiah rawh: Tlawhtute leh chhûngte hnênah damlo dinhmun chu hrilh lâwk rawh.
- Nangmah pawh inngaihtuah teh: Hei hi a pawimawh hle. Damlo chu taksa leh rilru i dam phawt chuan i enkawl tha thei chauh a ni. Chaw ei \ha la, mut \ha la, exercise la. Midang hnen atangin chawlh hahdamna pe turin tanpuina la rawh (respite care).
- Nakin hun atana ruahmanna: Hun kal zelah damlo chu darkar 24 chhung enkawl a ngai dawn a ni. Hei hian nursing home-ah enkawl a ngai mai thei. Hemi atan hian ruahmanna siam lawk a pawimawh.
FTD hmuhchhuah a nih hnua dam rei zawng chu kum 7.5 vel a ni. Thihna hi natna atanga lo awm ai chuan natna khirh tak avanga lo awm a tam zawk. Entirnan, ei harsa vanga pneumonia hi thihna thlentu lian ber a ni.
Take-Home Thuchah a ni
- Frontotemporal Dementia (FTD) hi hriatrengna aiin nungchang, mize leh thusawi a nghawng ber a ni.
- Hei hi Alzheimer’s aiin kum naupang zawk (kum 45-60) atanga tan theih a ni.
- FTD hi damdawi chiang tak awm lo mah se, a natna lan chhuah dan enkawl dan leh nun awlsam zawka siam dan tur leh hmanraw hrang hrang a awm.
- I chhungkuaa mi tuemaw nungchang inthlak danglam thut, sawifiah theih loh i hmuh chuan ngaihthah suh. Damdawi lam thurawn zawng nghal rawh.
- Damlo taksa leh rilru hriselna humhim a pawimawh hle a, chutiang bawkin i enkawltu pawh humhim a pawimawh hle.











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