I kutah, a bîk takin i khup, i hip, i kekawrte, a nih loh leh i kutphahah natna dull, swelling tlem, emaw lump i nei ngai em? Chutiang a nih chuan tlem tal ngaihtuah a tha. A chhan chu vawiin a kan sawi tur dinhmun ‘Giant Cell Tumor (GCT)’ tih chhinchhiahna a nih theih avangin. Ngaihtuah buai suh, hemi chungchang hi chipchiar takin kan sawi dawn a ni.
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Giant Cell Tumor (GCT) hi eng nge ni tak tak?
A awlsam zawngin sawi ila, Giant Cell Tumor (GCT) hi cancer ni lo (leh a tam zawkah chuan benign) tumor a ni . I taksa ruh sei tak tawp lamah an lo awm tlangpui. A bik takin, i thigh bone hnuai lam femur emaw i shin bone chunglam tibia emaw, khup vel a awm emaw ah an awm tlangpui. Mahse, hip, shoulder, wrist, leh tailbone ang hmunah te pawh an lo piang thei bawk. Chungte chu Osteoclastomas an ti bawk.
Hetiang dinhmun (GCT) an tih hi a takah chuan a tlem hle . Mi sang za zelah mi pakhat atanga pahnih vel ah a awm thin. Mahse, ruh atanga tan cancer nei lo tumor zingah chuan (GCT) hi case zawng zawng zinga 15% leh 21% inkar a ni.
A chang chuan heng giant cell tumor te hi ruh ah ni lovin, ruh chhehvel soft tissue ah te an lo awm thin. Tichuan Tenosynovial giant cell tumors'' an ti ta a ni.
A pawimawh ber chu heng (Giant Cell Tumors) te hi cancer ni lo mahse, an thang chak thei a, an chhehvel tissue hrisel tak tak te pawh an tichhe thei a ni . Tin, enkawl hnuah pawh (recurring) chance an nei sang hle bawk. Chuvangin hetiang tumor chhinchhiahna i hmuh chuan a rang thei ang bera doctor pan a pawimawh.
Hei hi eng symptoms nge ni? Hengte pawh hi i nei em tih en rawh...
Giant cell tumor (GCT) chhinchhiahna ber leh langsar ber chu natna hi a ni . A tir lamah chuan natna hi a na lo thei hle nachungin, tumor a lo lian chhoh zel chuan a na zual zel a ni. Ngaihtuah teh, zing khat chu i harh a, i khup bulah natna tlem i nei a. A tirah chuan i ngaihsak lo. Mahse rei vak lo hnuah a na zual zel a, i khawih chuan zung te tak te ang maiin a awm thin. Chutah chuan i hlauthawng deuh thin a ni lawm ni?
Symptom dang engemaw zat a awm bawk:
- Kut chhunga hnim hring emaw, hliam emaw hriat theih chu chu hmunah chuan a lang a.
- Tumor awmna hmunah hian ruh chu a kal tha thei lo tihna a ni.
- Joint pain , a bik takin joint tihchet hian.
- Vung .
- Tumor hian ruh a tichak lo thei a , ruh a tikehsawm thei bawk .
Heng symptoms pakhat emaw a aia tam emaw i neih chuan doctor rawn la.
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Dik tak chuan damdawi lam zirchiangtute chuan giant cell tumor thlentu hi eng nge ni tih chiang takin an la hre lo. Mahse, he natna vei thenkhat chuan an gene-ah hian inthlak danglamna (mutations) engemaw zat an nei tih hmuhchhuah a ni. Mahse, tunah chuan hei hi rochun thil a ni lo tih rin a ni a, i chhehvel emaw, i nunphung emaw avanga lo awm a ni lo .
Risk factors a awm em?
Ni e, dinhmun thenkhatah chuan he (GCT) lo awm theihna chance hi tlem a sang thei a ni:
- (Hyperparathyroidism) (parathyroid hormone i siam tam lutuk) i neih chuan i taksa hmun engemaw zatah (GCT) a lo awm thei a ni.
- A tlem hle a, ruh natna Paget's disease of the bone'' an tih nei te pawhin heng giant cell tumor te hi an nei thei bawk.
Hei hi a hlauhawm thei ang em? Eng harsatna nge a awm?
Heng tumor te hi cancer ni lo mahse, a tlem hle, chu chu a tlem hle a ni, heng giant cell tumor te hi lungah a darh thei a ni . Amaherawhchu, cancer a darh ang a ni lo va, hetiang hian a darh a nih pawhin a tlangpuiin nunna atana hlauhawm a ni lo.
Chu aia tlem zawk chu GCT vei zinga 4% vel ah chuan heng tumor te hi cancer (malignant) a lo ni thei a ni . Chuvangin, i doctor chuan i dinhmun chu a enfiah fo ang a, tumor-ah hian danglamna hlauhawm tak a awm leh awm loh a en reng ang. Hei vang hian doctor pan fo a, thurawn lak a pawimawh hle.
Doctor-te hian engtin nge hei hi an hmuh?
Giant cell tumor (GCT) i neih leh neih loh finfiah nan biopsy an ti thin. Hei hian tumor atanga tissue sample te tak te lak a, microscope hmanga enfiah a huam a ni. He test hi pathologist, tissue lama tui tak doctor-in a ti thin. Amah chuan cell te hi "giant cells" an nih leh nih loh a enfiah ang a, GCT ang chi mizia an nei em tih a enfiah ang.
Chu bakah, i taksa chhunga tumor awm chu enfiah nan heng ang imaging test te hi tih theih a ni bawk:
- X-ray : Ruh dinhmun enfiah thin.
- CT scan : Tumor lian leh te chipchiar takin en rawh.
- MRI : Tissue nem, ruhro, etc. te a enfiah thin.
- Bone scans : Ruh hmun dangah harsatna a awm leh awm loh enfiah thin ang che.
- PET scans : Tumor chu cancer-ah a chantir tih hriatna a awm em tih enfiah nan.
Heng test zawng zawng hi i dinhmun hriatthiamna famkim neih theihna tur leh enkawlna tha ber hriat theihna tura tih a ni.
Okay, tunah chuan hei hi eng enkawlna nge ni?
Giant cell tumor hi operation hmanga enkawl a ni fo thin . Doctor chuan ruh (curettage) atanga tumor chu a la chhuak thin. Tichuan, ruh (bone graft) chu hmun ruak hmunah dah a ni.Chu ruh chu grafting (hmun dang atanga ruh chi khat emaw, thil siam emaw atanga lak chhuah) hmangin a tichak a ni. A chang chuan tumor hi a lian hle a nih chuan tumor awmna ruh zawng zawng chu lak chhuah a ngai mai thei. Chutiang a nih chuan a hmunah artificial joint emaw bone prosthesis emaw dah theih a ni.
Mahse, operation hmanga tumor chu a chhuak kim thei lo emaw, surgery a risky a nih chuan non-surgical treatment a awm a ni. Chung zingah chuan:
- Denosumab - Xgeva®) : Hei hi damdawi chi khat, monoclonal antibody an tih a ni. Tumor chu a ti tlem a, a chhehvel ruh a tichak bawk.
- Embolization : Hei hian tumor-a thisen petu thisen kalna kawngte chu a block a ni. Hei hian tumor chu thisen a hloh a, zawi zawiin a thi ta a ni.
- Ablation therapy : Hei hian microwave energy ang chi hmangin tumor chu a tichhia a ni.
- Radiation therapy : Hei hian high-energy X-ray hmangin tumor chu a ti tlem a, cell a tichhia a ni.
I doctor chuan eng enkawlna nge i tan a tha ber tih a rel ang.
Enkawl hnua dam leh theih nan eng chen nge a duh?
I dam leh theih hun chhung chu i enkawlnaah a innghat a ni. Surgery i neih chuan hliam a dam chhung hian kar engemaw zat bandage i vuah a ngai dawn a ni. Chutih lai chuan kekawrte pawh i hman a ngai mai thei bawk. Prosthetic device i neih chuan i hman thiam theih nan physical therapist nen thawhhona tha tak i neih a ngai dawn a ni.
I doctor chuan heng zawng zawng hi a hrilhfiah vek ang che, chuvang chuan ngaihtuah tur a awm lo.
Hetiang thil thleng tur hi ven dan tur a awm lo em ni? Hriat lawk hian eng hlawkna nge a neih?
Giant cell tumor lo awm chhan dik tak hriat a nih loh avangin tunah hian a lo awm lohna tura ven theih a ni lo . Mahse, i tih theih ṭha ber chu i natna lan chhuah dan i hriat veleh damdawi lam thurawn lak hi a ni . I ruh emaw, i ruh emaw pakhatah na, a hring emaw, a hring emaw i hmuh chuan ngaihthah suh la, doctor pan nghal rawh. (GCT) ang tumor hi hmuh hmasak a nih chuan enkawl a awlsam zawk a , harsatna a awm tlem zawk bawk.
A theih chuan ruh nena inzawm cancer lam thiam doctor, orthopaedic oncologist .
Chuti a nih chuan engtin nge he dinhmun hi i nunpui? Doctor i hmuh fo a ngai em?
Giant cell tumor hi nunna atana hlauhawm a ni tlem hle. Mahse, i ruh leh a chhehvel tissue te an tichhe thei a, chuvang chuan enkawl hmasak a pawimawh hle.
Thu lawmawm tak chu tumor peng zawng zawng surgery hmanga lak chhuah vek a nih chuan he natna hi a dam vek thei a ni. Mahse, GCT hi tumor chi khat, rilru na tak a ni a, a lo thang leh thei bawk .
Enkawlna i neih zawh chuan i doctor chuan follow-up appointment neih leh neih loh a enfiah fo ang che . Hei hi tumor chu a lo let leh tawh em tih enfiah nan a ni. A tam zawkah chuan heng tumor te hi operation hnu kum hnih atanga kum nga chhungin an lo lang leh thin. Mahse, i dam chhung zawngin check-up neih fo a ngai mai thei. I doctor chuan heng check-up te hi eng chen nge i lo kal tur tih a hrilh ang che.
Engtikah nge doctor i hmuh leh a ngaih?
I giant cell tumor a lo kir leh tih hriatna i neih chuan doctor pan nghal rawh. Ruh emaw ruh emaw thar na emaw, a hring emaw a awm chuan fimkhur rawh. I doctor-in a check fo che a nih pawhin, danglamna i hmuh chuan i appointment leh tur nghak lovin i doctor biak nghal mai a tha ber.
Doctor hnenah eng nge zawh i duh ang?
Doctor i hmuh hian heng zawhnate hi zawh a tha ang:
- He tumor hi engtiang chiahin nge a aggressive ?
- Eng enkawlna kawng nge ka neih?
- Heng enkawlna pakhat zel hian eng hlawkna leh hlauhawmna nge a neih?
- He giant cell tumor hi enkawl hnuah a lo lang leh theihna chance chu engzat nge ni?
- Follow-up appointment atan engzat nge ka lo kal a ngai dawn ?
Hêng zawhnate chhânna i hriat hian i dinhmun chu i hrethiam zâwk ang a, enkawlna i hmachhawn pawh a awlsam phah ang.
Chuti a nih chuan, he thawnthu atang hian eng thil nge kan hriat reng tur pawimawh ber?
Giant cell tumor (GCT) chu "benign" a nih vang mai mai chuan harsatna a thlen dawn lo tihna a ni lo. Enkawl loh chuan heng GCT te hian i ruh te chu nasa takin a tichhe thei a ni.
A tha ber chu operation hmanga tihbo theih a ni a, tumor hnuhma zawng zawng chu paih vek a ni. Mahse, heng (GCT) te hi an rilru a na deuh a, an lo thang leh thei bawk. Chuvang chuan i doctor chuan enkawl hnuah uluk takin a lo vil reng ang che. Tumor chu a la te laiin lakchhuah chuan ruhte hun rei tak a tihchhiat loh nan a veng thei a ni.
Chuvangin, heng symptoms te hi i neih chuan doctor pan hreh suh la, thurawn la rawh. Inenkawl hmasak hi nun hrisel neihna kawng tha ber a ni!
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