I fa chu a hliam tenau a\angin thisen a chhuak nasa em? Hemophilia B a ni thei ang em?

I fate hian inkhelh laiin cut leh scrape tenau te a neih hi thil pangngai a ni. Mahse, hliam tenau emaw, hnar thisen chhuak emaw chu a tawp theih nan a hma aia rei a ngai em? I taksa hi a hliam awlsam em? Nu leh pa i nih angin hetiang thil hi i ngaihtuah a, i lungkham mai thei tih hi hriatthiam theih a ni. Chuvangin vawiin hian, hetiang thil thlen thei dinhmun chungchang hi sawi ila, mahse enkawl tha a nih chuan , i fate chu nun pangngaia nunpui thei turin a phalsak thei a ni. Chu chu hemophilia B a ni.

A awlsam zawngin, hemophilia B hi eng nge ni?

Awle, hetiang hian han sawi ila. Kan taksa hmun dangah hliam kan neih chuan kan thisenah protein bik a awm avangin thisen chhuahna chu rei lo te chhung a reh thin. Hengte hi ‘ clotting factors’ emaw clotting factors emaw kan ti thin. Chûngte chu hliam siamṭhat thuai tûra lo kal hnathawk team angin han ngaihtuah teh. Heng hnathawkte hian thawk hovin ‘clot’ an siam a, chu chuan thisen chhuah a titawp a ni.

Kan thisenah hian clotting factor chi 13 a awm a. Naupang hemophilia B vei chuan factor IX a tlachham nasa hle a, heng clotting factors zinga 9-na a ni . He clotting factor pawimawh tak hi awm lo se chuan hliam a awm laia thisen chhuah titawptu clot chu a lo piang tha lo. Chuvang chuan thisen chhuah hi a tlangpui aia rei a daih thin.

Hetiang dinhmun hi naupan lai atanga hmuhchhuah a ni tlangpui. Hemophilia vei zinga za zela tlemte chauhvin type B. Hmeichhia aiin mipaah ​​a tam zawk bawk.

Hetiang dinhmun a lo awm chhan hi eng nge ni?

A tam zawkah chuan naupang hian nu hnen atangin hei hi a rochun thin. Nu chu he natna thlentu gene tha lo phurtu a ni thei. Mahse, a chang chuan chhungkaw zingah tumahin he natna hi an nei lo a nih pawhin, nu nausen pum chhunga a awm laiin gene pakhata random change (gene mutation) avang hian naupang hian he natna hi a vei thei a ni.

Engtin nge heng symptoms te hi kan hriat theih?

A lan chhuah dan ber pahnih chu a tlangpui aia rei thisen chhuak leh hliam awlsam tak a ni . I fate zingah heng chhinchhiahnate hi en reng ang che.

I lu i vuak chuan i fimkhur hle a ngai!

Hetiang dinhmunah hian lu-a vuakna tenau pawh hi a hlauhawm hle thei a ni. Thluak chhungah thisen a chhuak thei a ni. I fain khawi hmunah pawh an lu a vuak chuan a hnuaia symptoms te hi zawng rawh. An tih chuan damdawi in hnai ber Emergency Department (ETU)-ah hruai nghal tur a ni.

Engtin nge doctor hian he natna hi dik taka a hriat theih ang?

Naute thla 6 hmasa berah hian hei hi hmuh a harsa deuh tlangpui a, a chhan chu chutih chhung chuan naute chu chutiang chuan an tlu lo va, an hliam lo bawk. Mahse, i naute chu a chet chhuah leh a kal tan tirh hian heng harsatnate hi i hre tan mai thei.

I fa chu doctor hnena i hruai hunah hetiang thilte hi a zawt ang che:

• "Engtin nge heng hliam leh hliam te hi a lo awm?"
• "Engtia rei nge thisen chhuak chu a reh theih?"
• "Naupang hian damdawi a ei em?"
• "Hriselna lama harsatna dang a awm em?"
• "Chhungkaw zingah hian hetiang harsatna hi thisen chhuah emaw, thisen zam emaw nei an awm em?"

Tichuan, a natna hriat chian nan doctor chuan naupang thisen test eng emaw zat a ti ang. Chungte chuan thisen a inzawm rei zawng leh eng clotting factors nge tlakchham tih te an en ber a ni.

Enkawlnate chu engte nge ni?

Hetiang dinhmun hi damdawi a awm lo a , mahse enkawl dan tha tak a nih chuan i fa chu active, hlim takin nun a hmang thei a ni.

Enkawlna ber chu Replacement Therapy a ni . A awlsam zawngin, naupangin a tlakchhamna factor, chu chu taksain a siam theih loh factor, Factor IX tia koh chu thisen zam chhunga injection angin pek a ni. Factor IX pek hi mihring thisen plasma atanga lak chhuah a ni thei a, recombinant a ni thei bawk.

• A natna a nasat chuan: Thisen chhuah loh nan naupang chuan he enkawlna hi a dawng fo a ngai dawn a ni.
• A natna a na lutuk lo a nih chuan: Thisen chhuah tan a nih chuan tihtawp nan chauh enkawl a ngai mai thei.

He enkawlna hi clinic-ah pek theih a ni. A châng chuan, i inah nurse a lo kal thei a, a nih loh leh nu leh pate chu in lama an fate pe tûra zirtîr an ni thei bawk.

Naupang kan enkawl dawna kan fimkhur ngai thilte

• First aid: Minor cut emaw scrape emaw i hmuh veleh chu hmun chu tifai la, nghet takin chelh la, bandage hnawih rawh. Mahse, hliam na tak tuar tan chuan damdawi lam thurawn i la ngei tur a ni .
• Exercise leh rit: taksa chakna tichaktu exercise hi a pawimawh a, a chhan chu taksa chakna hian hliam atanga thisen chhuah a tihtlem avangin. Tin, taksa rihna hrisel neih hi a pawimawh hle a, a chhan chu taksa rihna tam lutuk hian ruh (joint)-ah pressure a pe tam zawk a, thisen chhuah harsatna a tipung thei bawk.
• Doctor dangte hriattir: Naupang ha enkawltu pawh tiamin, healthcare provider zawng zawngte hnenah i fa dinhmun hrilh la, ha lak chhuah ang chi thil tih hmain thisen zam chhuahna tur damdawi bik pek a ngai mai thei.
• Damdawi lam thurawn tel lo chuan pe suh: Natna tidamtu thenkhat, ibuprofen ang chi hian thisen chhuahna a tipung thei a ni . Chuvangin, i fa chu i doctor rawn hmasa lovin i fa chu over-the-counter damdawi engmah pe suh.
• Hriselna: I fa chu accident laka humhim turin theihtawp chhuah rawh. Inkhelh laiin khup khup, elbow pad leh helmet vuah tur a ni. In lama dawhkan leh ṭhutphah-a kil hrual hrual (sharp edges) lakah fimkhur rawh.

Hemophilia B, thisen zam, factor ix, naupang natna, genetic natna, thisen chhuah tam lutuk