Nang emaw i hriat emaw hian Gaucher’s Disease i nei em? Chutiang a nih chuan ‘Imiglucerase’ tih vaccine hi i hre tawh mai thei. He damdawi hi kan ramah ‘Cerezyme’ brand name hmanga hralh a ni fo. Chuvangin, vawiinah hian he damdawi hi eng ang damdawi nge a nih, a nena thil thleng, leh he damdawi ei huna fimkhur tur thilte chauh kan sawi dawn a ni.
Imiglucerase hi eng damdawi nge ni?
A awlsam zawngin sawi ila, Gaucher’s Disease hi kan taksain a pianphung a siam enzyme kan neih loh vang a ni. He enzyme hi a tlakchham chuan taksa cell thenkhat chhungah hian thau tak tak a awm tan thin. Hei hian ruh, ruh, leh thin ang chi taksa peng hrang hrang a tichhe thei a ni.
Imiglucerase hi synthetic enzyme a ni a, enzyme tlakchhamna chu a thlak a ni. He damdawi hi thisen kal tlanga pek a nih chuan natural enzyme hnathawh chu a la a, cell-a thau awmkhawm chu a control a ni. Hei hian symptoms nasa takin a tihziaawm thei a ni.
Mahse hei hi a pawimawh hle: Imiglucerase hi Gaucher natna chhinchhiahna control tu damdawi a ni a, natna damdawi a ni lo.
He damdawi hi i ei hmaa doctor hnena hrilh tur thil
He enkawlna i tan hma hian heng thilte hi chiang takin i doctor nen in sawiho a ngai a ni.
- Imiglucerase emaw damdawi dang emaw, ei tur emaw, preservative dang emaw allergy i nei em?
- Naupai nge naupai i beisei ?
- Nu hnute pe thin i ni em ?
Heng thute a\ang hian doctor chuan he enkawlna hi i tan a tha em tih leh a kalpui dan tur a rel ang.
Engtin nge a enkawl dan chu pek a nih?
He damdawi hi vein-a infusion angin pek a ni a, saline nen a inang. Hei hi in lama tih theih a ni lo. Damdawi in emaw clinic emaw- ah medical professional trained-in a pe thin. Kar hnih danah pek thin a ni tlangpui.
He damdawi hi naupangte hnenah pek theih a ni em?
Ni e, he damdawi hi naupang kum 2 chunglam tan chuan case thlan bik thenkhatah chuan a tha hle. Amaherawhchu, naupang hnena pek dawnin fimkhur tur thenkhat a awm. Chuvangin, i fate hi he damdawi hi an lo hrilh tawh a nih chuan, i naupang enkawltu doctor nen sawiho la, engkim chiang takin sawi rawh.
Damdawi dose hi tihpalh palh a nih chuan engtin nge ni ang?
He enkawlna hi damdawi ina pek a nih avangin overdose theihna a tlem hle. Mahse, thil thleng nia i rinhlelh chuan Colombo National Hospital-a National Poisons Information Center-ah phone nghal emaw, damdawi in hnai ber Emergency Department (ETU)-ah emaw kal nghal rawh.
Damdawi ei tur ni khat ka tlakchham chuan engtin nge ni ang?
He enkawlna hi ni leh hun ruat saah dawn a pawimawh hle. Hei hi taksaa enzyme level awm zat chu kawng engemaw takin i vawng reng thei a ni. Ni ruat chhunga enkawlna i dawng thei lo a nih chuan doctor hnenah hriattir nghal rawh. Chumi hnuah chuan a tuk zingah enkawlna dawng turin thurawn a pe ang che.
He damdawi nena inzawm thei thil dang
Damdawi thenkhat chuan he damdawi nen hian an inzawm thei a ni. Entirnan, damdawi pakhat miglustat an tih. Mahse, he list hi a kim lo.
Chuvangin i damdawi ei zawng zawng (vitamin, herbal remedies, leh dietary supplement te pawh tel) te chu i doctor hnenah hrilh rawh. Tin, zu i in emaw, zu i in emaw, ruihhlo i hman emaw chuan i doctor hnenah i hrilh tur a ni.
Side effect awm thei te chu engte nge ni?
Damdawi dang ang bawkin Imiglucerase hian mi thenkhatah side effect a nei thei a ni. Chungte chu chi hnihah then theih a ni. Ṭhenkhat chu doctor hnenah report nghal tur a ni a, ṭhenkhat erawh chu a tlangpuiin a na lo hle nachungin, a awm reng chuan report tur a ni.
| Side effect chi hrang hrang leh a sawifiahna |
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| Side effects te chu doctor hnenah hriattir nghal tur a ni |
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| Side effects te chu a awm reng emaw, a buaithlak emaw a nih chuan doctor hnenah hriattir tur a ni |
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He list-a tarlan loh symptom dang danglam tak i neih chuan i doctor nen pawh chutiang lam chu sawipui rawh.
Take-Home Thuchah a ni
- Imiglucerase hi Gaucher natna lanchhuahna control-na a ni a, mahse a damdawi erawh a ni lo.
- He enkawlna hi damdawi in emaw clinic emaw-ah vein-ah infusion angin pek thin a ni.
- Enkawl i tan hmain i doctor hnenah allergy i neih leh damdawi dang i ei zawng zawngte hrilh hmasa phawt ang che.
- Thâwk harsa emaw, hmai hring emaw ang chi side effect na tak i neih chuan doctor rawn la nghal rawh.
- A hun taka enkawl hi a pawimawh hle. Eng vang pawha ni khat i tlai chuan doctor hnenah hriattir tur a ni.











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