Ngaihtuah teh, i hriat mi pakhat chuan a hriatrengna, a nungchang leh a kal dan chu a thlak danglam nghal vat a. Doctor-te tana hriat harsa leh zual chak em em natna hi i hre ngai em? Vawiin hian chutiang natna mak leh hmuh tur awm lo tak zinga pakhat chu kan sawi dawn a ni. Hengte hi prion natna kan ti a.
A awlsam zawngin, heng prion natna te hi engte nge ni?
Prion natna hi i thluak leh nervous system tichhe thei natna chi khat a ni.
Dementia na tak emaw, i taksa thunun harsa emaw a thlen thei a, a na zual nghal vat thei bawk. An tlem hle a, kum tin United States-ah hian hri kai 350 vel chauh an awm. Eng thilin nge an thlen tih hi han en ila.
Prions hi protein te tak te, kan thluaka awm a ni. Mahse chhan hriat loh eng emaw avangin heng protein te hi a inzawm sual a, a inzawm khawm a, a pianzia a dik lo ta a ni. Thil hlauhawm ber chu he prion protein fold dik lo hian protein hrisel dangte pawh a fold dik lo thei a ni. Thian tha lo chuan midang a ti na thei ang bawkin. Heng misfolded proteins te hi thluak ah an pung khawm a, thluak cell (neurons) te chu an tichhia tan thin. Hei hi a symptoms thlentu a ni.
Mi tam tak chuan prion natna hi Alzheimer natna nen an inzawm tir thin . An pahnih hian hriatrengna hlohna thlentu natna ni mah se, an pahnih inkarah hian danglamna lian tak a awm. Alzheimer natna hi kum tam tak chhung chu zawi zawiin a zual zel tlangpui. Prion natnaah chuan a natna hi a na zual nghal vat a, hun rei lote chhung, a tlangpuiin thla engemaw zat chhungin a na zual thin. Tin, Alzheimer natna ang bawkin prion natna hi damdawi a la awm lo.
Prion natna chi hrang hrangte chu engte nge ni?
Prion natna hian mihring leh rannung a nghawng thei a ni. Mihringte nghawngtu chi hrang hrang a awm a. Eng nge an nih i han thlir teh ang.
| Natna Hming | A sawifiahna tawi |
|---|
| Creutzfeldt-Jakob natna (CJD) natna a ni. | Hei hi mihringah prion natna awm tam ber a ni a, kum 60 chunglamte a vei tlangpui. |
| Creutzfeldt-Jakob natna chi hrang hrang (Variant CJD - vCJD) . | Hei hi thalaite chungah pawh a thleng thei a ni. "Mad Cow Disease" vei bawnghnute ei hian kai theih a ni tih hmuhchhuah a ni. |
| Gerstmann-Sträussler-Scheinker-a natna a ni | Hei pawh hi a tlem hle a, thlahtute atanga lo chhuak genetic disease a ni bawk. |
| Chhungkaw mut theih lohna thihna thlen thei | Hei hi genetic condition a ni bawk a, thlah khat atanga thlah dangah a kal zel a ni. A lan chhuah dan ber chu mut theih lohna nasa tak a ni. |
| Kuru | Papua New Guinea rama hnam thenkhat zinga mihring sa ei dan phung atanga lo darh natna. Hei hi tunah chuan hriat tur a awm tawh lo tluk a ni. |
Prion natna lan chhuah dan chu engte nge ni?
Prion natna chhinchhiahna a lo lang nghal thei. Chûng zîngah chuan i rilru put hmang, i hriatrengna, leh i chetna inthlâk danglam nghâlte pawh a tel.
| A nghawng sector | Hmuh theih symptoms te |
|---|
| Rilru leh nungchang lam | Lungkhamna nasa tak emaw lungngaihna nasa tak Nungchang emaw mize emaw inthlak danglam nghal Rapidly progressive forgetfulness (Dementia) . |
| Taksa leh che vel | Balance problems, Unsteady walk, Muscle control hloh, rang taka jerking emaw trembling, Slurred Speech, Trouble swallowing |
| Thil dang pawh a awm | Seizures Mit hmuhna lama harsatna nei |
He natna vei chhan leh vei theihna tur risk factors
A tam zawkah chuan CJD ang natna hi chhan chiang tak awm lovin a lo awm thin a, mahse risk factor thenkhat chu hmuhchhuah a ni.
- Chhungkaw chanchin : Mi 15% velin heng natna hi an vei chhan chu thlah kal zelah genetic defect (genetic defect `PRNP` an tih) vang a ni.
- Infection : Hei hi a tlem hle. A chang chuan he natna hi natna vei atanga tissue transplant lai te, a nih loh leh surgery neih laia hmanrua hmante chu a sterilized tha lo a nih chuan a kai theih a ni.
- Sa hri kai ei: " mad cow disease " (Bovine Spongiform Encephalopathy ) vei bawnghnute ei hian natna chi khat vCJD an tih chu a thlen thei a ni. Kum 1990 chhoa Europe rama he natna a darh khan mi tlemte chauh he natna vang hian an thi a ni. Tunah chuan bawng chaw pek dan leh thisen pek chungchangah dan khauh tak siam a ni tawh a, chuvangin he hlauhawmna hi nasa takin a tlahniam ta a ni.
Engtin nge prion natna hi hriat chhuah a nih?
He natna hi hriat chian a harsa thei a, a chhan chu a natna lan chhuah dan hi natna dang nen a inang thei a ni. Theihnghilh ang chi symptom i neih chuan i doctor chuan a chhan dang, stroke emaw thluaka tumor emaw te chu a paih hmasa ang. A hnuaia test te hi tih theih a ni:
- Spinal Tap / Lumbar Puncture: Hei hi i vertebrae pahnih inkarah needle te tak te dahin i thluak leh spinal cord (cerebrospinal fluid) vel tui sample tlemte lak a ni. A chhunga protein thenkhat level chu test theih a ni a, natna chungchang hriat theih a ni.
- MRI scan (Magnetic Resonance Imaging): Hei hian magnet chak tak tak leh radio wave hmangin thluak chipchiar taka thlalak a la thin. A chang chuan prion natnaah thluaka inthlak danglamna chiang tak hmuh tur a lantir thei bawk.
- CT scan (Computerized Tomography): X-ray hrang hrang lakkhawmin thluak thlalak chiang tak siam a ni.
A pawimawh ber: Mi pakhatin prion natna a vei tih 100% a hriat theihna awmchhun chu thluak atanga tissue te tak te (brain biopsy) lak hi a ni. Mahse hei hi surgery risky tak a ni. Chuvangin hei hi enkawl theih natna dang a ni thei tih rinhlelhna a awm chauhvin tih a ni.
Natna enkawl dan leh ven dan tur
Hetih lai hian prion natna damdawi a la awm lo. Tuna enkawlna hian natna lan chhuah dan chauh a control a, damlo tan hahdamna engemaw chen a pe bawk. Hei hian natna tidamtu, lungngaihna tidanglamtu, leh lungkhamna dona damdawi te a huam a ni. Prion natna vei dinhmun chu nitin a zual zel avangin nitin hnathawhnaah tanpuina an mamawh ngei ang. Zun chhuahna tur catheter dah a ngai mai thei, tui tlakchhamna tur saline dah a ngai mai thei a, ei theih loh chuan tube feeding pek a ngai mai thei.
He natna hi ven theih a ni em?
Hereditary prion natna hi ven theih dan tur a awm lo a, mahse heng step te hian infection emaw ei leh in emaw hmanga natna kai theihna tur a tihziaawm thei a ni:
- Damdawi hmanrua te uluk taka tihfai leh tihthianghlim.
- Prion natna i neih emaw, chhungkaw history i neih emaw chuan tissue emaw organ emaw pek loh tur a ni.
- Sa him tih certified chauh ei.
Tunah chuan khawvel ram tam takin bawnghnute hnena ran chaw leh bawnghnute pek chungchangah dan khauh tak an siam avangin "mad cow disease" darh dan hi a thunun tha hle a ni.
Take-Home Thuchah a ni
- Prion natna hi natna hlauhawm tak tak, mahse natna khirh tak tak, thluak tichhe thei pawl a ni.
- Hêng natnaah hian hriatrengna, nungchang, leh taksa chetnate chu a chhe chak hle a ni . Hetiang rang lutuk hi Alzheimer’s ang natna atanga a danglamna ber a ni.
- Natna hi chiang taka hriat a harsa a, chutiang tur chuan test bik eng emaw zat neih a ngai a ni.
- Tunah hian hei hi damdawi chiang tak awm lo mah se, a natna lan chhuah dan chu thunun theih a ni a, damlo chu hahdamna pek theih a ni.
- Nangmah emaw, i hriat mi emaw chuan an hriatrengnaah, an mizia, a nih loh leh an cheziaah inthlâk danglamna rang tak, sawifiah theih loh i hmuh chuan, thurâwn dîl tûrin doctor pan nghâl a pawimawh hle
Prion Diseases, Creutzfeldt-Jakob natna, CJD, thluak natna, nervous system, hriatrengna hloh, dementia, mad cow natna, mad cow natna
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