Naute thenkhat chu kal pakhat chauh neia piang, a nih loh leh kal pahnih nei lo pawhin an piang tih i hre ngai em? Hei hi a hlauhawm deuhin a lang thei a, mahse he dinhmun hi hriat chian a pawimawh hle. Vawiin hian he natna `(Renal Agenesis)` tih hi kan sawi dawn a ni. Ngaihtuah buai suh, engkim hi awlsam takin i sawifiah ang u.
`(Renal Agenesis)` tih hi eng nge ni? A awlsam zawngin hrethiam ila, kan hrethiam ang em?
A awlsam zawngin `(Renal Agenesis)` tih hi naute chu kal pakhat chauh nei emaw, kal pahnih nei lo emaw a pian hian a ni. Kan taksaah hian a tlangpuiin kal pahnih kan nei vek a. A dam khawchhuah theih nan kal pakhat tal chu a thawk tha a ngai a ni. Hei hi `(Congenital)` condition a ni a, pian tirh atanga lo awm tawh thil a ni tihna a ni.
Tunah chuan heng thumal pahnih awmzia hi a hranin i en chuan i tan a chiang zawk ang:
- Renal: Hei hi " kidneys " tih damdawi lam hming a ni.
- Agenesis: Hei hian naute nu pum, chu chu nausen pum chhunga a awm laiin taksa peng pakhatin a lo thanglian kim lo tihna a ni.
Chuvangin `(Renal Agenesis)` kan tih hian naute kal (kidney) a siam tha lo tihna a ni.
`(Renal Agenesis)` chi hrang hrangte chu engte nge ni?
He dinhmun hi kawng hnihin kan hmu thei a:
1. Unilateral Renal Agenesis tih a ni
Hemiah hian thil thleng chu a hming ang bawkin naute hian a sir khatah kal (kidney) a tlachham tih hi a ni. Chumi awmzia chu kal dang chu a normal tihna a ni. Vanneihthlak takin kal pakhat chauh hmang hian nun pangngai, famkim tak neih theih a ni. Thil tam takah chuan kal pakhat la awm chuan kal bo hnathawh chu a la tan thei a, chuvang chuan a lian deuh thei a ni. Naupangin class-a homework assignment pahnih a tih ang mai a ni.
2. Kal pahnih hloh (Bilateral Renal Agenesis) .
Hei hi a na deuh deuh a ni. Hetah hian naute hian kal pahnih a nei lo. Tin, kidney atanga ``Bladder`` thlenga zun phurtu tube te tak te ``Ureters`` te pawh a lo awm lo. Hemi rual hian naute ``Lungs`` te hi a thang tha lo a, chu chu a te hle tihna a ni ``Pulmonary Hypoplasia`` a ni. He kal tlakchhamna leh lung chak lohna inzawmkhawm hi ``Potter Syndrome`` an ti bawk. Lungchhiatthlak takin he dinhmun hi thihna thlentu a ni tlangpui.
Kan kal (kidney)-ah hian eng nge thleng?
Kan taksaa kal (kidney) pahnih hi kan zun kawnga thil pawimawh tak a ni. Kan in chhunga bawlhhlawh paihna system angin han ngaihtuah teh. Kidney hna ber chu kan thisen atanga bawlhhlawh duh loh filter leh paih chhuah hi a ni. Chumi hnuah chuan heng bawlhhlawh te hi taksa atangin zun angin a chhuak leh thin.
He natna `(Renal Agenesis)` hi engtiang chiahin nge a awm?
Statistics atanga a lan dan chuan naute piang 2,000 zinga pakhat vel chuan ``Unilateral Renal Agenesis`` tih natna an nei thei a, chutah chuan kal pakhat a bo thei a ni. ``Bilateral Renal Agenesis``, kal pahnih awm lohna dinhmun hi a tlem zawk hle. Nau piang thar 8,500 zinga pakhat vel ah a awm thin. A chhan dik tak hriat ni lo mah se, he kal pahnih bo lohna hi naute mipaah a tam zawk.
`(Renal Agenesis)` awm chhante chu engte nge ni?
A tam zawkah chuan `(Renal Agenesis)` awm chhan ber chu genes `(Gene mutation) .` a inthlak danglam emaw, a inthlak danglam emaw a ni.` Tun thlengin zirchiangtute chuan a kaihhnawih gene mutation pasarih vel an hmuchhuak tawh a ni. He gene mutation avang hian nausen pum chhunga kal (kidney) siam dan chu naupai thla thum hmasa ber `(First trimester).` chhungin a tibuai a ni
A chhan tenau dangte chu:
- Nu hian naupai laiin zunthlum (gestational diabetes) a nei a.
- Naupai tam tak (twins, triplets ang chi).
- Naupai laiin damdawi tha lo thenkhat hman.
`(Renal Agenesis)` natna lan chhuah dan chu engte nge ni?
Nausen Potter Syndrome vei, a kal pahnih hloh leh a lung a puitling lo chuan a pian hnu lawkah nunna atana hlauhawm thawkna lama harsatna a nei nghal a ni.
Nausen kal pakhat neia piang chuan natna lan chhuahna a nei lo thei. Mahse symptoms a lo lang a nih chuan:
- Naupang thisen sang .
- Zun chhunga protein level a sang (Proteinuria).
- Vesicoureteral reflux a awm thin.
A châng chuan naute kal pakhat neia piangte pawhin natna dang an nei thei bawk a, chungte chu:
- Clubfoot a ni.
- Congenital heart diseases , chu chu thinlung atria emaw ventricles inkara khur (ASD emaw VSD emaw) te hi a ni.
- Congenital urological anomalies a awm thin.
- Anus-ah perforate emaw Anal atresia emaw a awm thei.
Naupai lai hian engtin nge `(Renal Agenesis)` hi kan hriat theih ang?
A tam zawkah chuan naupai hmaa ultrasound scan hi nu naupai laiin an ti thin.Hetiang dinhmun hi hriat theih a ni. He scan hian kal (kidney) a bo tih a hriat theih. Tin, naute pum chhehvela amniotic fluid a hniam (Oligohydramnios) a nih chuan Renal Agenesis an tih natna chhinchhiahna a ni thei bawk. Hei hi naute kal (kidney)-in zun a siam chhuah loh vang a ni a, chu chuan he tui hi a tihtlem phah a ni. He tui hi a tlem chuan naute lung a lo thang tha lo ang.
Naute pian hnua `(Renal Agenesis)` hi engtin nge kan hriat theih ang?
Naute pian hnu lawkah imaging scan hmangin a natna hriat chian theih a ni. Mahse, a châng chuan naupang chu a lo upa deuh hma chuan a natna chu hriat theih a ni lo. A châng chuan naupangin natna lan chhuahna dang a neih a, scan a nih lai te, a nih loh leh chhan dang, urinary tract infection (UTI) ang chi ultrasound scan an tih lai emaw pawhin a lo lang thei a ni.
`(Renal Agenesis)` hriat theihna atana scan chi hrang hrang hman ber chu:
- Abdominal Ultrasound emaw Kidney Ultrasound emaw hmanga tih theih a ni.
- CT scan a ni.
- MRI scan `(MRI)` tih a ni.
Bilateral Renal Agenesis hi engtin nge enkawl a nih?
Tun hnai thleng khan naute kal leh lung tha lo pahnih nei lo chuan nausen pum pawn darkar tlemte aia rei dam theihna beiseina a nei lo. Mahse, tunah chuan experimental treatment tharte chuan beiseina engemaw zat a pe ta a ni. Hei hian naupai laiin nausen pum chhungah saline solution inject a, chu chuan amniotic fluid level a siam tha leh thin. He tui hian naute lung a tipung thei a ni. Tichuan, naute a pian hnuah, naute chu kal (kidney transplant) tih theih a nih hma loh chuan dialysis-ah dah a ni. Mahse, he enkawlna hi experimental stage-ah a la awm a, hmun tinah a awm lo tih hre reng ang che.
Unilateral Renal Agenesis hi engtin nge enkawl a nih?
Kidney pakhat nei te hian an thisen sang tihhniam nan damdawi an ei a ngai fo thin . Nangmah emaw i fa emaw hian hetiang dinhmun hi i nei a nih chuan kidney specialist (Nephrologist) pan fo a pawimawh a, kum khatah vawi khat tal, a aia tam emaw taksa enfiahna, zun enfiahna leh scan neih a pawimawh bawk. I fa pawhin heng test te hi a nei thei bawk:
- Kidney function test a ni.
- Zun protein test a ni.
I kal awmchhun humhim turin eng nge i tih theih ang?
Kidney pakhat nei tam tak chu kidney-friendly (DASH) diet zawm turin an fuih a ni . He diet hian chi leh sugar tihtlem a, fiber leh potassium tamna ei tur ei a huam a ni.
Naupang leh puitling Renal Agenesis vei te chuan an kal hriselna humhim nan a hnuaia mite hi an ti thei ang:
- Non-steroidal anti-inflammatory drugs (NSAIDs) leh natna tidamtu thenkhat ei loh tur. Hengte hian i kal (kidney) a tichhe thei a ni. Acetaminophen ang chi thil hmang zawk rawh.
- I taksa rihna hrisel tak vawng reng la, active takin awm rawh. Mahse, infiamna sang tak tak football, rugby, leh martial arts te hi i kal la awmte tan chuan hlauhawm tak a nih theih avangin inthiarfihlim a tha ber.
- In lamah i thisen sang enfiah fo thin ang che.
A tawp berah chuan thil hriat reng tur (Take-Home Message) .
Nangmah emaw, i naute piang lai emaw, i fa naupang emaw hian ``Renal Agenesis`` an nei tih i hriat chuan lungngaihna leh lungngaihna i neih hi thil pangngai a ni.Mahse, hre reng ang che, ``Unilateral Renal Agenesis`` neia piang naupangte chu puitling an nih hunah kal lama harsatna nei thei an ni a, mi tam tak chuan nun hlim tak, hrisel takin an hmang a ni. I fate kal (kidney) hriselna venhim dan tur tha ber berte chu i fa doctor nen inbiakna neih a pawimawh hle.
Bilateral Renal Agenesis hi a na zawk a, a tam zawkah chuan thihna thlen thei a ni. Mahse, damdawi lama hmasawnna thar a awm avangin tunah chuan beiseina engemaw zat a awm ta.
A pawimawh ber chu he thil hi hlauthawng lo ila, damdawi lam thurawn mumal tak zawng a, chumi ang zela thil tih hi a ni. Nangmah chauh i ni lo, he zinkawng zawh tura pui turin doctor leh healthcare staff an awm bawk.











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