I taksa hmun dangah lump lo lian leh lian zel ang chi hi i hre ngai em? A châng chuan, chhan hriat lohvin, kut emaw, ke emaw-ah a hring emaw, a hring emaw a awm thei bawk. Heng thilte hi kan ngaihven vak lo tlangpui a, mahse a hnungah hian thil pawi tak thup a awm thei. Vawiin hian cancer chi bik, mi tam takin an hriat fo loh chungchang kan sawi dawn a, mahse kan zavaia kan hriat chian a pawimawh hle. Hlau suh, hei hi awlsam takin i hrethiam ang u.
``Undifferentiated Pleomorphic Sarcoma - UPS'' tih hi eng nge ni?
A awlsam zawngin sawi ila, ``Undifferentiated Pleomorphic Sarcoma'' emaw ``UPS'' kan tih hian a tawi zawngin cancer chi khat soft tissue sarcoma an tih hi a ni. Hei hi kan taksa peng nêm tak tak, taksa ruh, thau leh thisen kalna kawng hrang hranga cancer cell lo awm hi a ni.
A tam zawkah chuan he `(UPS)` hi i kut emaw i ke emaw soft tissue atang hian a intan thin . A châng chuan pum hnunglam thuk takah pawh a awm thei a, chu chu `retroperitoneum` an ti a ni. A tlem hle a, he `(UPS)` hian ruh a nghawng a ni. Thil lungchhiatthlak tak chu, hei hi a tlangpuiin cancer chi khat, a nasat em em a ni . Chuvângin, taksa pêng dang, a bîk takin lung emaw, lymph node emaw-ah a darh tam zâwk a ni .
Tun hma chuan he `(UPS)` hi `malignant fibrous histiocytoma` an ti thin a. A chhan chu zirchiangtute chuan he cancer hi immune cell bik `histiocytes` an tih atanga lo chhuak niin an ngai a ni. Mahse, a hnu lama zirchianna chuan kan taksaa connective tissue siamtu `mesenchymal cells` an tih cell -ah a intan ber tih hmuhchhuah a ni.
Tunah chuan he hminga thumal pahnih awmzia hi han thlir ila.
"Undifferentiated" tih hian heng cancer cells te hian chaotic tak, disorganized appearance an nei tihna a ni . Order awm lovin inkhelhna thil chi hrang hrang theh darh ang maiin. An danglam tawh a, puitling lo an lo ni ta a, eng cell hrisel nge an tan tih leh eng hna nge an thawh tum tih chiang taka hriat theih a ni lo.
"Pleomorphic" tih thumal hian heng cell te hi an pianzia, an lian leh te, a nih loh leh nucleus, cell control center te an danglam tihna a ni . Furniture pakhat, mold khat atanga siam ni lo, pakhat zel chu a pianzia leh a lian zawng a inang lo ang maiin han ngaihtuah teh. Cell thenkhat chu a te a, thenkhat chu a lian bawk. Ṭhenkhat chu a zungpui a, a then chu a sei hle. Cell chhunga chromosome awm nucleus pawh hi cell tinah a inang lo. Hei vang hian heng cancer cell te hi a mumal lo hle a, thunun theih lohvin rang takin an thang lian a ni.
UPS hi a takah chuan cancer chi khat hmuh tur awm lo tak a ni . Entirnan, United States-ah chuan he natna hian kum khatah mi 5,000 aia tlem lo a vei a ni. Mahse, soft tissue sarcoma chi hrang hrang zingah chuan .Liposarcoma (thau tissue-a lo awm cancer) leh leiomyosarcoma (smooth muscle-a lo awm cancer) te bakah hian (UPS) hi soft tissue sarcoma chi thumna a ni
`(UPS)` natna lanchhuahna chu engte nge ni?
`Undifferentiated Pleomorphic Sarcoma (UPS)` natna lan chhuah dan hi mi hrang hrangah a inang lo thei. Mi thenkhat chuan symptom engmah an nei lo mai thei. Mahse, a lan chhuah dan tlangpui thenkhat chu:
- Lump emaw mass emaw lo thang zauh zauh: Hei hi a lan chhuah dan ber a ni. Taksa khawi hmunah pawh lump ang maiin a lang thei a, a bik takin kut, ke emaw, pum chhungah emaw a awm thei.
- Natna nei lo lump, khawih a nih chuan a che thei emaw, a che thei lo emaw: A tam zawkah chuan heng lumps hian a tir lamah natna a thlen lo. Chuvangin mi thenkhat chuan an ngaihven vak lo mai thei.
- Tumor-in nerve a press avanga rilru hahna emaw, kang emaw: A châng chuan, he tumor hi a lo lian chhoh zel chuan a bula nerve a press thei bawk. Hei hian kut emaw ke emaw a ti na thei a, tingling sensation a thlen thei a, a kang thei bawk.
- Kut emaw ke emaw a hring: A chhan hriat loha kut emaw ke emaw a hring a nih chuan chu pawh chu ngaihtuah tel tur a ni.
Pawimawh tak chu UPS hian symptoms langsar tak tak a lantir ngai lo. They are often painless , leh vunah hian lump chungah danglamna a awm lo (a rawng danglam emaw, hliam emaw ang chi). Tin, natna lan chhuah dan tlangpui, khawsik, taksa rihna tlahniam, leh malaise te hi hmuh tur a awm lo.
`(UPS)` awm chhante chu engte nge ni?
Mithiamte chuan UPS hi eng nge a thlen tih chiang takin an la hre lo . An hriat chian chu cell hrisel DNA (kan genetic information awmna molecule) inthlak danglamna (mutations) avanga lo awm a ni. Mahse, DNA-a chutiang inthlâk danglamna thlentu chu eng nge ni tih erawh hriat chian a la ni lo.
UPS siam chhuahna Risk Tipungtu Risk Factors
Risk factor chu natna vei theihna tipungtu thil a ni. `(UPS)` tan hian risk factor engemaw zat hmuhchhuah a ni. Mahse hre reng ang che, heng risk factors nei zawng zawng hian `(UPS)` an nei vek dawn lo va, chutiang risk factors nei lote chuan `(UPS)` an nei lo ang tih pawh sawi theih a ni lo.
Tuna risk factors hmuhchhuah te chu:
- Mipa nih: Hmeichhia aiin mipain he natna hi an vei tam zawk a, a bik takin mipa var zingah a hlauhawm hle.
- Kum 50 chunglam: Kum upat deuh deuh hian he natna vei hi a pung zel a.
- Damdawi lam dinhmun thenkhat: Entirnan, neurofibromatosis (nervous system-a tumor siamna natna) emaw, Paget’s disease of bone (ruh than dan pangngai lo thlentu natna) ang chi natna nei te chu an vei theihna a sang hle (UPS).
- Genetic condition thenkhat: 1.1.Li-Fraumeni syndrome ang chi genetic condition rare tak tak nei te chu cancer chi hrang hrang vei theihna a sang hle a, (UPS) pawh a tel.
- Chemical thenkhat nena inzawmna: Hun rei tak chhunga chemical thenkhat, arsenic emaw vinyl chloride emaw nena inzawmna pawh hi a hlauhawm thei hle.
- A hmaa a natna hmuna radiation therapy: Natna dang avanga hmun pakhata radiation therapy i pek tawh chuan, chu hmunah chuan a hnuah sarcoma (UPS) i vei theihna a tlem hle.
- Occupational exposure to radiation: Hna thenkhatah radiation exposure i neih a ngai a nih chuan chu pawh chu risk factor a ni thei bawk.
UPS vei tam tak hian heng risk factors te hi an nei lo tih hi thil mak tak a ni . Chuvangin i taksaah hian lump danglam tak ang maia lang i hmuh chuan, "Hetiang risk factors hi ka nei lo" tih ngaihtuahin ngaihthah suh.
Doctor-te hian engtin nge `(UPS)` an hriat chian?
Hetiang lump nei doctor i hmuh chuan i hriselna chungchang te, i chhungte zingah cancer (family history), etc. ang chi natna an nei tawh em tih te a zawt hmasa ang che, chutah chuan i symptoms te a zawt ang. He lump hi eng chen nge a awm tawh? A lian chho zel em? A hrehawm em? Hei bakah hian a hnuaia test te hi a ti ang:
1. Taksa enfiahna: Doctor chuan tumor awmna hmun, a lian leh te, leh khawih (hard or soft) a a awm dan te a enfiah ang.
2. Imaging test: Heng test te hian tumor chhungril chu eng ang nge a nih tih leh eng chen nge a darh tawh tih hriat nan a pui thin. A tlangpuiin test pakhat emaw a aia tam emaw, X-ray, ultrasound scan, leh/ emaw MRI scan te hi tih theih a ni.
3. Biopsy: Hei hi natna chiang taka hriat theihna tur test pawimawh ber a ni . Hei hian tumor atanga tissue te tak te (needle ang chi hmanrua te tak te hmang pawh a ni mai thei) lak a, microscope hmanga pathologist (natna hriat chian thiam doctor) te enfiah tir a huam a ni. Chumi hnuah chauh chuan UPS nge condition dang a ni tih chiang takin kan sawi thei ang.
`(UPS)` enkawlna tur engte nge ni?
UPS enkawlna hi tumor lian leh te, cancer a darh leh darh loh te a innghat a ni. UPS hmasa ber enkawlna ber chu tumor lakchhuahna operation a ni . Hei hi radiation therapy nena hman dun a ni fo thin . Mahse, a châng chuan cancer enkawlna dang a ngai thei bawk.
Inzai
UPS tana surgery neih tum ber chu cancer natna hrik awm chu paih chhuah vek a ni.. Doctor-te chuan cancer chauh ni lovin, a chhehvela tissue hrisel tlemte (hei hi "margin" an ti) te pawh paih chhuah an tum thin. Huana hnim kan paih chhuah ang bawkin, a thlai chauh ni lovin, a chhehvel leilung te tak te pawh kan paih chhuak thin. Tichuan, buh zung tlemte pawh a awm tawh lo. Chutiang bawkin doctor-te chuan he cancer hi an paih chhuah hian a chhehvela tissue hrisel tlemte nen an paih chhuak thin. Chumi hnuah chauh chuan cancer cell zawng zawng chu a la awm lova paih chhuah vek a ni tih kan chiang thei ang. Tumor lakchhuahna kil lamah cancer cell a awm chuan taksaah cancer cell tam zawk a la awm thei tihna a ni.
Tumor chu i kut emaw ke emaw ah a awm a nih chuan i surgeon chuan cancer chu paih chhuah a tum ang a, chu kut emaw ke emaw ah chuan a theih ang anga hnathawh chu a humhim ang. Mahse, thil na tak ṭhenkhatah chuan ke ruh chu tihtlak a ngai mai thei . Chuvangin, i dinhmun atana enkawlna tha ber tur chu i oncologist nen inbiakna neih a pawimawh hle.
Cancer enkawlna dang a awm bawk
Oncologist-te pawhin operation hma emaw, operation hnuah emaw enkawlna dang an hmang thei bawk. Heng enkawlnate hian tumor chu a ti tlem fo lo nain, tumor lakchhuahna tur operation atan a him a, emaw, operation hnua cancer cell awm thei zawng zawng tihhlum nan emaw a pui thei a ni.
Heng enkawlna dangte hi:
- Chemotherapy: Cancer cell that thei damdawi pek.
- Immunotherapy: Cancer cells do turin taksain a taksa a taksa hriselna a tichak a.
- Radiation therapy: Energy sang tak nei rays hmanga cancer cell tihchhiat.
I enkawlna ruahmanna hi i tan chuan a danglam bik a ni. Midang ta nen a danglam thei. Chuvangin i oncologist nen i duhthlan tur chungchang sawipui rawh. Multidisciplinary team ten an enkawl fo ang . He team-ah hian surgeon, radiation oncologist leh medical oncologist te pawh an tel thei. Specialist tinte hian chanvo hrang hrang nei mah se, an vai hian an thawk dun a, an enkawl che a ni. I dinhmun atân eng nge ṭha ber tih ngaihtuah tûrin an ṭanpui ang che.
Engtikah nge Doctor ka hmuh ang?
I taksa hmun dangah pawh zawi zawiin a lo thang lian zel tih i hmu a nih chuan , a bik takin natna, hliam, emaw i ke leh ke tha taka che thei lo ang chi symptoms nena inzawm a nih chuan doctor i pan nghal tur a ni
`(UPS)` i nei tih i hriat chian tawh chuan iSymptom thar i neih chuan, emaw, i symptoms a na zual a nih chuan, i oncologist hnenah hrilh nghal rawh .
`(UPS)` nei chuan eng ang thil nge a beisei theih ang?
Mi tin dam rei zawng hi a inang lo. Sarcoma lian tham leh natna stage ah a innghat a ni . A tlangpuiin, high-grade (UPS) tan kum nga chhunga damchhuah zat chu 60% vel a ni . Chumi awmzia chu he natna vei hmuhchhuah zinga 60% vel chu kum nga hnuah pawh an la dam tawh tihna a ni. Kum 10 chhunga damchhuah zat hi 48% vel a ni .
Mahse, heng damchhuah zat hi general estimate mai a ni tih hre reng ang che . Eng chen nge i dam dawn tih leh eng enkawlna nge i tan a hlawk ber ang tih chiang takin an sawi lo. Damchhuah zat leh a nghawng dan hriat belh duh chuan i oncology team nen inbiakna neih a tha ber.
`(UPS)` hi a dam kim thei em?
(UPS) hi tihdam theih vek a ni a, a bik takin a hmaa hriat chhuah a nih chuan . Natna a darh tawhna hmunah pawh i nunphung tihchangtlun thei leh i dam rei thei tur enkawlna kawng hrang hrang a awm. Cancer chi hrang hrang ang bawkin, (UPS) hi a hmaa hriatchhuah leh enkawl hi a hlawhtlinna tur kawng tha ber a ni .
Ngaihtuah tur thilte
Cancer i vei tih hriat a nih chuan i nun kawng tinreng a nghawng thei a ni. Undifferentiated Pleomorphic Sarcoma (UPS) ang cancer hmuh tur awm lo tak a nih chuan mahni chauha awm leh tumahin an hrethiam lo ang maiin i inhria thei. Hetiang hun lai hian, nangmah ang bawka thil tawn tawh mi dangte awmna support group-a tel chu a ṭangkai thei a ni . Anmahni biakna chuan i rilru put hmang hriatthiamna leh thunun tûrin a ṭanpui thei che a ni.
Tin, i medical team te pawhin tanpui turin an awm reng bawk . I enkawlna kawng hrang hrangte an sawipui thei che a, an thlawp thei che a, hriselna chungchanga thutlukna dik siam theihna tura i mamawh thu leh hla leh hmanrua te an pe thei bawk che a ni. Zawhna i neih chuan zawt hlau suh . Nangmah chauh i ni lo tih hre reng ang che.
` Undifferentiated Pleomorphic Sarcoma, UPS, sarcoma, soft tissue cancer, cancer, tumor, cancer symptoms, cancer enkawlna











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