I naute hian thawk leh ei a harsat em? He (Vascular Ring) chungchang hi i zir chiang ang u.

I fate hian a chang chuan thawk harsa ang maiin a inhria em? A nih loh leh chaw a pek lai emaw, a hnute a pek laiin a chok fo thin em? Nge a ei zawhah a luak chhuak em? Hei hi a chhan pakhat chu `(Vascular Ring)` tih hming pu condition a ni thei a, chu chu vawiin hian kan sawi dawn a ni. A hming chu thil lian tak angin a lang thei a, mahse hlau suh . Hemi chungchang hi awlsam takin, i hriatthiam theih dan tur angin sawi ila.

Hei hi eng nge ni `(Vascular Ring)`? A awlsam zawngin...

A awlsam zawngin sawi ila, Vascular Ring hi naute aorta- a thil awm dan dik lo (malformed structure) a ni. Tunah chuan aorta hi eng nge ni tih i ngaihtuah mai thei. Kan thinlung atanga kan taksa peng dang thlenga oxygenated thisen phurtu thisen kalna kawng lian ber, lian ber a ni. Tui dahna atanga in chhung hmun tinah tui phurtu main pipe ang a ni.

Hetiang ``Vascular Ring'' dinhmunah hian aorta emaw a hnah emaw, naute trachea (thâwk chhuahna tube) , esophagus ( ei tur tube), emaw a pahnih emaw chu compress a, a chhehvelah an inkhuh a ni. Thil dang tui pipe-a nghet taka inkhuh, tui luang harsa tak ang maiin han ngaihtuah teh.

Chuti a nih chuan, hetianga i tlakbuak hian eng nge thleng?

• Trachea a constricted chuan naute chuan thawk a harsa thei .
• Esophagus a zim chuan naute chuan ei leh in, nau hnute pek , a nih loh leh ei harsa a ti thei a ni.

Hei hi pianpui chhiatna a ni. Chumi awmzia chu naute chu a pum chhunga a la awm laiin he natna hi neiin a piang tihna a ni. A chang chuan a pawi thei hle a, mahse a tha ber chu surgery hmanga hlawhtling taka enkawl theih a ni.

Engtin nge aorta hi a lo awm tlangpui? Vascular ring-ah hian eng nge thleng?

Naute aorta chu a awm dan pangngaia a awm dan hi han en ila.

A tlangpuiin aorta hi naute thinlung veilam hnuai lam (left ventricle) atanga tan a ni. Chumi hnuah chuan trachea-ah a chho a, arch (aortic arch)-ah a curve a, chutah chuan trachea-ah a chhuk leh a (descending aorta). He arch leh a hnuai lam atang hian thisen kalna kawng tenau zawk tam tak chu a inzar pharh a, taksa peng hrang hrangah thisen a pe chhuak thin.

Mahse, naute ``Vascular Ring'' tih natna neiah chuan he thisen kalna kawng lian tak ``(Aorta)'' emaw, a hnah, trachea, esophagus emaw, a pahnih emaw hian ring angin a khuh a, a pum emaw, a then emaw pawh a ni. Chuvangin ``Vascular Ring'' tih a ni.

Ngaihtuah teh, hei hi kan huana tui pipe chu thing zung bulah tuam ang mai a ni a, chu chuan tui luang zat a tihtlem phah a ni.

`(Vascular Ring)` chi hrang hrangte chu engte nge ni?

He `(Vascular Ring)` hi a lo pian theih dan kawng hrang hrang a awm. A chi pathum awm tam ber chu:

1. `Aortic Arch pahnih`: 1.1.Hemi kawngah hian thil thleng chu aorta hi a pangngaiin a intan a, chutah chuan arch pahnih ah a inthen leh thin. Heng arch pahnih hian naute thlipui, trachea leh esophagus te chu an hual vel a, an tikhauh bawk. Tichuan arch pahnih chu a sir lehlamah chuan an inzawm khawm a, thisen kalna kawng khat an lo ni leh ta a ni.

2. Right Aortic Arch: Hetah hian aorta hi a intan dik lo a, veilam ni lovin trachea dinglamah a intan a ni. Tichuan, thisen kalna kawng pangngai chu a intan dik lo a, chaw kawng hnung lamah a kal ta a ni. He branch hian artery dang (the left subclavian artery ) a siam a , chu chuan naute kut veilam thlengin thisen a phur a ni. He ring hi nausen dam chhunga thisen kalna kawng hawn tawh, a hnua khar (Ligamentum Arteriosum) la awmte hian a ti zo ta a ni. Heng thisen kalna kawngte hi an inzawm khawm thei a, naute trachea, esophagus emaw, a pahnih emaw chu a compress thei a ni.

3. Aberrant Right Subclavian Artery (RSA): Hei hi Arteria Lusoria an ti bawk. A tlangpuiin he artery hi Brachiocephalic Trunk atanga tan a ni a, chu chu Aortic Arch atanga lo chhuak artery pathum zinga pakhat a ni. Mahse, hetiang a nih chuan Aberrant RSA hi Aortic Arch atanga tan nghal a ni. It is not a complete ring , chuvangin symptoms a awm lo mai thei.

He `(Vascular Ring)` natna hi engtiang chiahin nge a awm?

Vascular Ring hi a awm lo hle a ni . Naute 100 zinga pakhat pawhin a nei lo. Congenital heart defects nei pawhin 1% leh 3% inkar chuan vascular ring an nei thin. Chuvangin, mi tam tak chunga thil thleng a ni lo.

He natna hi tuin nge vei tam zawk?

Hetiang dinhmun hi naute chi leh chi hrang hrangah a awm thei a ni. A chhan dik tak hriat ni lo mah se, naute mipaah ​​chuan naute hmeichhia aiin a let hnih zetin a tam zawk tih hmuhchhuah a ni .

Eng thilin nge he `(Vascular Ring)` hi a lo awm chhan?

Scientist te chuan nausen piang chhoh laiin he ``vascular ring'' hi engvangin nge a lo awm tih chiang takin an la hre lo. Naute chu a pum chhungah a lo seilian chhoh zel chuan aorta hmun thenkhat chu a tla mai tur a awm fo thin. Mahse, chutiang dinhmun chu chutiang hmunte chu a tlak loh chuan a thleng niin an ngai .

Vascular Ring natna lan chhuah dan chu engte nge ni?

Vascular ring-in symptom a lantir leh lan loh leh a lan loh chuan, engtikah nge a lan tih chu a chi leh a trachea emaw esophagus emaw a compress nasat danah a innghat a ni.

Naute thenkhat chuan naute an nih laiin symptom an nei thei . Mi dangte chuan an kum upa deuh deuhah emaw, a hnu lamah emaw symptoms an nei thei bawk. Mak tak maiin mi thenkhat chuan symptom engmah an lantir lo mai thei .

A châng chuan, mi pakhatin thawk emaw, ei emaw a harsat rei tawh hle a, pulmonologist emaw gastroenterologist emaw enkawl tura kal mah se, a harsatna chu eng nge ni tih chiang takin an hre thei lo mai thei.

Trachea a nghawng a nih chuan a lan chhuah dan:

Trachea hi thlipui (windpipe) a ni. Chuvangin a zim a nih chuan heng ang symptoms hi i hmu thei ang:

• Khuh fo thin .
• Thluak lam natna (e.g. pneumonia) awm fo thin.
• Nasal flaring ( thawk chhuah laiin hnar kawngkhar a flaring ).
• Thâwk chhuah laiin thawm danglam tak (e.g., `(Wheezing)` - rilru atanga thawm ri, `(Stridor)` - rilru atanga thawm ri nasa tak).
• Respiratory Cyanosis hi thawk harsat vanga vun rawng dum (bluish discoloration) a ni .

Esophagus a nghawng a nih chuan symptoms awm thei:

Esophagus hi ei tur pipe a ni. A zim deuh chuan symptoms i nei thei a, chungte chu:

• Acid reflux a awm thin .
• Thau tihpun loh leh chaw tha ei loh chu ``Failure to Thrive'' a ni.
• I rilruah thil pakhat a innghat ang maia hriatna .
• Difficulty eating , chaw ei laiin chok fo thin.
• Chaw ei harsa (Dysphagia), a bik takin ei tur solid ei hian.
• Luak chhuak fo thin .

Lung lam natna dang: 1.1.

A chang chuan Vascular Ring vei te hian pianpui heart defect dang an nei thei bawk. Chutiang a nih chuan, symptoms te pawh i hmu thei ang:

• Thinlung chhunga thawm danglam tak hriat chu ``Heart Murmur'' tih a ni.
• Palpitations (thinlung thawk chak emaw, a thawk mumal lo emaw).
• Thâwk harsa (Dyspnea).

Engtin nge he `(Vascular Ring)` natna hi hriat chhuah a nih? (Diagnosis) tih a ni.

Doctor-in vascular ring a rinhlelh chuan test eng emaw zat an ti thei a, chu chu a natna hi finfiah theih a ni:

• Chest X-ray: Hei hian naute rilru chhunga taksa peng hrang hrangte thlalak a la a. Hei hi test hmasa ber a ni fo thin.
• CT scan: Hei hian taksa chhunga thil awmte chiang takin a la thei bawk a, a bik takin thinlung, trachea leh esophagus te pawh a la thei bawk.
• Echocardiogram: Echo an ti bawk a, hei hian naute thinlung leh aorta che vel video ang maia thlalak a la a ni.

Heng test bakah hian test dang pawh tih theih a ni a, trachea emaw esophagus emaw chu eng dinhmunah nge a awm tih hriat theih a ni:

• Barium hnim hring `(Barium hnim hring)` / `(Esophagogram)`:Hemiah hian tui bik `(Barium)` an tih chu naute in turin an pe a. Tichuan, he `(Barium)` tui hi chaw kawng `(Esophagus) hnuai lama a kal dan tur X-ray lak a ni. Esophagus `(Esophagus)` chu `(Vascular Ring) hmanga block a nih chuan he test hmang hian hriat theih a ni.
• Bronchoscopy: Hemiah hian camera te tak te leh light nei tube te tak te chu naute hmui emaw hnar emaw kaltlangin, thlipui (trachea) kaltlangin lung chhungah an lut a, a chhung lam an enfiah thin.
• Upper Endoscopy: Hei pawh hi tube a ni. Mahse a chhung lam en turin ka chhungah leh chaw kawng hnuai lamah a kal tlang a ni.

He `(Vascular Ring)` hi eng enkawlna nge ni?

Vascular ring avanga naute trachea emaw esophagus emaw a tikhawlo a, thawk emaw ei emaw a harsat chuan operation neih a ngai mai thei

Mahse, nausen lai hian vascular ring zawng zawng hi surgery hmanga siamthat a ngai lo. Mahse, chi thenkhat, double aortic arch ang chi erawh chu operation hmaa tih a ngai thung.

Surgery tih chi chu naute dinhmun, vascular ring chi leh a nasat danah a innghat a ni. Surgery-ah hian a tlangpuiin:

• Pressure tihhniam nan vascular ring hmun thenkhat tan leh then hran.
• Aorta emaw artery dang emaw atanga a tlem ber lakchhuah.

A tam zawkah chuan he surgery hi naute rilru sir lama incision te tak te hmanga tih a ni (an open procedure - `(Thoracotomy)`) . Chumi awmzia chu incision lian deuh deuh a ngai tihna a ni. Mahse, a tlem berah chuan naupang kum upa lam tlem tân chuan minimally invasive procedure tih theih a ni .

He `(Vascular Ring)` lo piang tur hi ven dan tur a awm em?

Dik tak chuan scientist-te chuan embryonic stage-a ``vascular ring'' hi engvangin nge a lo awm tih hi an la hrethiam tawk lo a, chuvangin tunah hian a ven dan tur chiang tak a la awm lo

Hetiang dinhmun nei hian eng ang hmalam hun nge a beisei theih ang?

Vascular Ring siamna tur surgery hi a him hle a , a hlawhtling hle bawk . Operation hnuah pawh natna lan chhuahna ṭhenkhat chu thla engemaw zât chhûng awm reng thei mah se, mi tam zâwk chu kum khat chhûngin natna lan chhuahna chu an nei lo vek tawh mai thei .

Mi tam zawk chuan operation neih a ngai tawh lovang. Mahse, a tlem hle a, operation dang neih leh a ngai mai thei.

Operation hnuah pawh kum tam tak chhung chu specialist-te hnena thurawn (follow-up) dil a ngai mai thei. Chûng zîngah chuan:

• Cardiologist pakhat a ni.
• Doctor pakhat, chaw ei leh in lama tui (Gastroenterologist) a ni.
• Doctor, thawkna lama tui tak (Pulmonologist) a ni.

Vascular Ring chungchang hi doctor hnenah eng nge zawh belh tur?

Nangmah emaw i fa emaw hian ``Vascular Ring'' tih natna i neih chuan i doctor hnenah heng zawhnate hi zawh a tha ang:

• Hei hi eng chi `(Vascular Ring)` nge ni?
• Hei hi ka trachea, esophagus vel emaw, a pahnih emaw vel a ni em?
• Surgery neih i rawt em? Chutiang a nih chuan open nge minimally invasive?
• Eng chen nge a dam theih ang?
• Ka symptoms te hi operation hnuah a bo vek dawn em ni?
• Specialist dang ka hmu tur em ni?
• Lung lam natna dang ka nei em? Chutiang a nih chuan he surgery neih rual hian enkawl theih an ni em?

A tawi zawngin, kan hriat reng tur thilte chu hetiang hi a ni (Take-Home Message):

Vascular ring hi naute aorta chu a pianpui atanga lo piang chhuak a ni a, chu chuan trachea emaw esophagus emaw, a pahnih emaw ah pressure a siam thin. Hei hian thawk harsatna emaw, ei harsa emaw a thlen thei a ni.

A pawimawh ber chu he natna hi surgery hmanga hlawhtling taka siamthat theih a nih bakah a symptoms te pawh tihbo theih a ni.

Hemi chungchanga zawhna dang i neih chuan doctor nen inbiakna neih hreh suh. I mamawh zawng zawng an pe vek ang che.

` Vascular Ring, Aorta, Trachea, Esophagus, Nau piangsual, Thâwk harsa, Ei leh in lama harsatna