Heng Motor Neuron Diseases te hi engte nge ni? Anmahni hi i hrethiam mai ang u.

Kan kal lai te, kan thian nena kan inbiak lai te, kan chaw ei lai te hian heng thilte hi engtiang chiahin nge tih a awlsam tih i ngaihtuah ngai em? Kan chetna tinreng, thiltih tinreng hnung lamah hian kan taksaah hian palai pawimawh tak tak pawl a awm a. Motor neuron kan tih te hi an ni. Kan thluak atanga chhiahhlawh pawl pakhatin kan taksa ruhte chu "hei hi ti rawh" ti turin an hrilh ang mai an ni.

Mahse, kan taksa peng dang ang bawkin heng tirhkohte hi an chhe thei bawk. Chutah chuan ‘motor neuron diseases’ an tih condition kan siam thin. ALS chungchang hi i hre tawh ngei ang. Chu chu he category-a natna lian ber pakhat a ni. Mahse motor neuron natna chi dang engemaw zat kan hriat tam loh pawh a awm bawk. Chuvangin vawiinah hian awlsam takin an chungchang hi han sawi ila.

Heng ‘motor neurons’ te hi tute nge ni?

A awlsam zawngin sawi ila, motor neurons hi nerve cell chi khat a ni. An hna ber chu kan taksain a che tur a mamawh thuchah phurh hi a ni. Chungte chu chi hnih lian tak a ni.

1. Upper motor neurons: Hengte hi i thluaka awm a ni . I thluak atang hian i spinal cord ah message an thawn thin. Office lian takah boss ang maiin.

2. Lower motor neurons: Hengte hi i ruhroah a awm a . Thluak atanga message an la a, kan taksa ruh te hnenah, "Okay, tunah hian hna thawk tan rawh," an ti thin. Branch pakhata manager ang mai a ni.

Tunah chuan motor neuron natna i neih hian eng nge thleng tih hi han ngaihtuah teh. Heng nerve cell te hi zawi zawiin an thi tan thin. Tichuan thluak atanga electrical message lo lut te chu taksa ruh (muscles) ah a thleng tha thei lo. Message transmission chu a chanve vel a tawp ta. Hun a kal zel a, taksa ruhte chu a chak lo a, an tan hmantlak loh avangin an lo tlem tan ta a ni . Hei hi Doctor-te chuan ‘atrophy’, a nih loh leh taksa ruh tihchhiat (muscle wasting) an ti a.

Chutiang a lo thlen chuan kan chetna thunun theihna kan hloh a ni. Kal, tawng, ei leh a tawpah thawk pawh a harsa zual sauh sauh a.

Motor neurone natna chi hrang hrangte chu engte nge ni?

Tunah hian he category-a natna hriat lar leh hriat hlawh lo deuh thenkhat hi han thlir ila.

A rilru a buai em em a, a rilru a hah em em bawk a.

Hei hi puitling zinga motor neuron natna hmuh tam ber a ni .ALS hian motor neuron chunglam leh hnuai lam a nghawng vek a ni. Hei hian kea kal, thusawi, ei, ei leh thawk leh thawk thununtu ruhte chu a chak lo zauh zauh a, a tichhe zauh zauh a ni. Muscle stiffness leh twitches pawh a awm thei bawk.

A tam zawkah chuan ALS hi a chhan chiang tak hmuh tur a awm lo. Doctor-te chuan 'sporadic' an ti. Chumi awmzia chu tu pawhin an tipung thei tihna a ni. Mahse, 5% leh 10% inkar chu hereditary a ni . Kum 40 leh 60 inkar ah hian symptoms hi a lang tlangpui.

A rilru a buai em em a, a rilru a hah em em bawk a. Primary Lateral Sclerosis (PLS) .

PLS hi ALS nen a inang a, mahse upper motor neurons chauh a nghawng a ni . Hei hian ALS aiin natna hi a ti slow zawk hle. A lan chhuah dan chu kut leh kea chak lohna leh nghet lo, kal zawi, balance leh coordination hloh te a ni. Thusawi chu a slow thei a, a slurred thei bawk. ALS angin a na lo va, mi a that lo bawk.

Progressive Bulbar Palsy (PBP) natna hi a lo awm tawh a ni.

Hei hi a takah chuan ALS chi khat a ni. PBP vei tam tak chuan a tawpah chuan ALS an nei a, chu chuan thluak bul hnaia awm thluak stem-a motor neurons te chu a nghawng a ni.

Thluak zung chhunga heng neurons te hian kan chew, ei leh in leh thusawi te min pui thin. Chuvângin, PBP a lo awm chuan thu chu a hrual a, ei tûr chu ei harsa a ni a, rilru put hmang thunun a harsa bawk . Chhan awm lovin i nui thut emaw, i tap emaw pawh a ni thei.

Muscular Atrophy a lo awm chho zel

Hetiang chi hi ALS emaw PBP emaw angin a awm lo. A bik takin motor neurons hnuai lam a nghawng a ni . Chak lohna hi kut atanga intan a ni tlangpui. Tichuan taksa peng dangah a darh ta a ni. Muscle te a chak lo a, cramps a awm thei bawk. He natna hi a chang chuan ALS ah a lo chang thei bawk.

Spinal Muscular Atrophy (SMA) a awm a, a rilru a hah lutuk a, a rilru a buai em em bawk a.

Hei hi genetic condition a ni a . SMA hi gene pakhat `SMN1` tihchhiatna avanga lo awm a ni. He gene hian motor neurons venghimtu protein a siam chhuak a. Chu protein chu a bo chuan motor neurons te chu an thi ta a ni. Hei hian motor neurons hnuai lam a nghawng a ni. SMA hi a natna lanchhuahna kum a zirin chi hrang hrangah then a ni.

Kennedy-a Natna a ni

Hei pawh hi thlahtu natna a ni. Mahse he pakhat specialty chu he natna hian mipa chauh a vei tih hi a ni . Hmeichhia hian he natna thlentu gene (carrier) nei mah se, symptoms an nei lo. Mahse, chu nu fa mipain he natna hi a rochun theihna chance 50% a awm.

Hetiang natna vei mipa hian kut a nghing thei a, taksa ruh a ti na thei a, a hrual a, hmai, kut leh ke a chak lo thei bawk. Chaw ei leh tawng harsa an nei thei bawk.

Hetiang natna hi engtin nge i khawsak?

Motor neurone natna vei mi pakhat hmalam hun chu natna chi hrang hrangah a innghat a ni. Kan hmuh tawh angin chi thenkhat chu a dang aiin a thang zawi zawk a, a na lo zawk bawk.

Tuna damdawi hman mek leh enkawl dan hrang hrang (e.g., physical therapy, speech therapy) hian natna lan chhuah dan a thunun thei a, nunphung pawh nasa takin a tichangtlung thei a ni Chuvangin, nangmah emaw, i hriat miin emaw heng symptoms te hi i tawk a nih chuan, a rang thei ang bera doctor thiam tak pan a, a rang thei ang bera diagnosis dik tak neih a, enkawl dan tur ruahmanna siam hi a ni.