I kut, ke, a nih loh leh i kekawrteah taksa ruh a inthlak nghal tih i hria em? A nih loh leh, i thusawi laiin i thusawi chu a hlim lo ang maiin i hria em, a nih loh leh i taksa pengte chu a hlim lo ang maiin i inhria em? Chûngte chu thil pangngaiah kan ngai a, mahse, a châng chuan hengte hi nervous system nena inzawm natna khirh zawk, ALS ( Amyotrophic Lateral Sclerosis ) ang chi chhinchhiahna hmasa ber a ni thei bawk. He hming i hriat hian hlau suh. Vawiin hian he natna ALS an tih hi kan sawi dawn a, ṭhian nena inbiakna mai mai ang maiin.
A awlsam zawngin, ALS chu eng nge ni?
Ngaihtuah teh, kan taksa hi machine complex ang mai a ni. Kan thluak hian he machine peng hrang hrangte hi hna thawk turin thuchah a thawn thin. Heng thuchahte hi taksa peng hrang hranga thlentu nerve cell chi khat bik a awm a. Hengte hi motor neurons kan ti a . I kal, i ei, i thusawi, i thawh hian heng zawng zawng hi heng motor neurons atanga message lo chhuak hian a thunun vek a ni.
ALS-ah hian eng emaw chhan vangin heng motor neurons te hi an chak lo zauh zauh a, an thawk thei lo va, an thi ta a ni. Tichuan, thluak hian duh mah se, taksa ruhte hnena thuchah thawn dan tur a nei lo. Thuchah an dawn loh chuan taksa ruhte chu a lo tlem zauh zauh a, a chak lo bawk. Hei hi atrophy kan ti a ni .
ALS hi natna zual zel a ni a, chu chu hun kal zelah a natna lan chhuah dan chu a zual zawi zawi tihna a ni. Chumi awmzia chu, kea kal, thusawi, ei leh in leh thawk ang chi thilte chu taksa ruhte a chak loh deuh deuh chuan a harsa zual sauh tihna a ni.
He natnain a tihchhiat hi tihdanglam theih ni lo mah se, damdawi leh enkawlna chi hrang hrang hmangin nitin nun a ti awlsam thei a, natna a zual zel dan pawh a thunun thei bawk.
ALS hi chi hnih a awm a.
ALS hi chi hnih ah then theih a ni:
1. Sporadic ALS : Hei hi a tam ber a ni. ALS vei zinga 95% vel chuan hetiang chi hi an nei a ni. "Sporadic" tih hian a chhan chiang tak awm lovin, random-a thleng tihna a ni.
2. Chhungkaw ALS (FALS): Hei hi thlahtute atanga lo piang a ni. ALS vei zinga 5% leh 10% inkar chuan hetiang chi hi an nei a ni. Hetah hian natna hi genetic defect (gene mutation) avanga lo awm a ni a, chu gene defective chu nu leh pate hnen atangin fate hnenah a inthlunzawm a ni.
Eng thilin nge ALS hi a thlen tak tak?
Dik tak chuan zirchiangtute chuan ALS thlentu dik tak chu an la chhui chhuak zel a ni. Mahse, a thawhhlawk nia ngaih thil tlemte a awm a:
- Gene mutations: Gene thenkhat inthlak danglam vang a niMotor nerve cell te hi a chhe thei tih hmuhchhuah a ni.
- Glutamate imbalance: Glutamate hi chemical (neurotransmitter) a ni a, thluak leh nerve inkarah thuchah a thawn chhuak thin. He glutamate hi ALS vei te nerve cell vel ah a awm khawm a, nerve a tichhe thei niin an ngai.
- Immune system lama harsatna: A chang chuan kan taksa ngei pawh hian motor nerve cell hrisel tak takte chu a bei thei a, a tichhe thei bawk.
- Oxidative stress : Kan cell-in chakna a siam chhuah atanga byproduct tha lo (free radicals) thenkhat lo awm hian nerve cells a tichhe thei a ni.
- Environment factors: Chemical emaw hrik emaw thenkhat nena inzawmna hi a chhan a ni thei em tih zirchianna pawh neih mek a ni.
ALS natna lan chhuahna chu engte nge ni?
ALS natna lan chhuah dan hi mi hrang hrangah a inang lo thei a, mahse a tlangpuiin a lan chhuahna ber chu hun kal zelah taksa ruh (muscle control) hloh hi a ni.
| Natna Stage a ni | A lan chhuah dan tlangpui |
|---|---|
| A lan chhuah hmasak ber |
|
| Natna a zual zel lai a symptoms awm thin |
Engtin nge ALS hi hriat chhuah a nih?
ALS hmuhchhuah hi a harsa deuh thei a, a lan chhuah dan hi natna dang nen a inang thei a ni. Chuvangin, doctor pakhat chuan test eng emaw zat a kalpui ang a, natna dang a awm loh nan a enfiah ang.
A pawimawh ber chu heng symptoms te hi i neih chuan doctor pan nghal mai tur a ni a, a bik takin neurologist hnenah i kal nghal tur a ni.
| Fiahna | Eng nge a tih? |
|---|---|
| Electromyogram (EMG) hmanga tih a ni. | Muscle chhungah hian needle ang chi hmanrua dah a ni a, a electrical activity chu teh a ni. ALS i neih chuan taksa peng hrang hrang (muscle activity) hi a pangngai lo. |
| Nerve Conduction chungchang zirchianna | Nerve leh muscle inkara thuchah inthlunzawm dan a enfiah thin. |
| MRI Scan a ni | Tumor emaw, harsatna dang emaw a awm leh awm loh enfiah nan thluak leh ruhro (spinal cord) chipchiar taka thlalak lak a ni. |
| Thisen leh zun test a ni | Chûngte chuan damdawi lam dinhmun dangte chu paih bo tûrin a ṭanpui a ni. |
| Muscle Biopsy tih a ni | Muscle te tak te pakhat chu la in microscope hmangin an enfiah thin. Hei hian taksa peng natna dang a awm leh awm loh hriat theih nan a pui thei a ni. |
ALS leh MS hi thil hrang hrang pahnih a ni em?
Mi tam tak chuan ALS (Amyotrophic Lateral Sclerosis) leh MS (Multiple Sclerosis) te hi an buaipui nasa hle. An pahnih hian nervous system nghawng nei mah se, natna chi hrang hrang pahnih an ni.
- MS (Multiple Sclerosis) hi autoimmune disease a ni a, nerve cell vel a protective covering (myelin) a tichhia a ni.
- ALS -ah chuan motor neurons chu direct-in a chhe vek a.
ALS enkawl dan leh enkawl dan
Tunah hian ALS hi damdawi a la awm lo. Mahse, natna zual zel tur tikhawtlai thei, dam rei thei leh nitin nun ti awlsam thei damdawi engemaw zat a awm. Entirnan, Riluzole leh Edaravone hi hemi atan hian pawm a ni. I doctor chuan i tan enkawlna tha ber a rawn pe ang che.
Hei bakah hian symptom management atan hian enkawlna chi hrang hrang a awm bawk.
- Pum, natna, chaw ei kham, leh hahna ang chi thilte damdawi.
- Physical Therapy: A theih ang anga rei tak chhung taksa ruh chak leh mobile-a awm tir thei.
- Occupational Therapy: Nitin hna awlsam zawka thawk thei tur hmanrua leh hmanraw hrang hrang a zirtir che a ni.
- Speech Therapy: Thusawi leh ei harsatnaah a pui thin.
- Respiratory Therapy: Thâwk lama harsatna a awm hunah ṭanpuina a pe.
ALS natna vei huna hriat tur thil
ALS diagnosis hi nun tidanglam thei harsatna a ni. Mahse, chu dinhmun nen chuan chak taka nun dan tur a awm.
- I rilru put hmang chu i hriat theih nan phal rawh: Lungngaih te, thinrim te, hlauhna te chu thil pangngai a ni. Chutiang rilru put hmang chu bottle up suh, i rintlak tak nen inbiakna nei rawh.
- Hriat tur: I dinhmun hi zir rawh. I doctor hnenah zawhna zawt rawh.
- Support group-ah tel ve rawh: Nangmah ang bawka he natna vei midangte nena inbiakna neih hi rilru chakna nasa tak a ni.
- In lamah inthlâk danglamna siam rawh: Natna a zual zêl chuan kea kal a harsa zual thei. Chuvângin, carpet hnim hring hrual chhuah te, bathroom-a grab bar dah te, leh wheelchair-a hman awlsam zâwk tûra kawngkhârte siamrem te ang chi thilte ngaihtuah rawh.
- I enkawltute thlawp rawh: He zinkawng zawh tura puitu i chhungte leh i thiante tan phurrit lian tak a ni. An chawlh hahdam theih nan leh an rilru hriselna enkawl turin tanpui ang che.
Take-Home Thuchah a ni
- ALS hi natna a ni a, zawi zawiin motor neurons a tichhia a, chu chuan thluak atanga taksa peng hrang hrangah thuchah a thawn chhuak thin.
- Muscle twitching, muscle chak lohna, tawng harsa tih ang chi symptoms i neih chuan ngaihthah suh la , doctor pan nghal rawh.
- He natna hi tihdam kim theih ni lo mah se, natna kal zel dan tur thunun thei tur leh nun awlsam zawkna tur damdawi tha tak tak a awm a.
- Physics therapy, occupational therapy, leh speech therapy ang chi enkawlna hian nunphung a tichangtlung thei a ni.
- He zinkawngah hian nangmah chauh i ni lo. I chhungte, i thiante, i medical team, leh support group te tanpuina hi a pawimawh hle.











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