A châng chuan chhan awm lovin a danglamin i chau emaw, i chau emaw tih i inhria em? I vun hi a sen hmel em? A nih loh leh i naute piang thar jaundice chu kar hnih hnuah a reh lo em ni? Heng thilte hi i taksaa enzyme pakhat G6PD an tih tlakchham vang a ni thei. Ngaihtuah buai suh, hei hi a awm fo thin. Vawiin hian G6PD chu eng nge a nih, a hniam laiin eng nge thleng tih leh G6PD test chungchang te chu awlsam tak leh chiang takin kan sawi dawn a ni.
G6PD hi eng nge ni mai?
Kan taksaa thisen sen (red blood cells) te hi hnathawhna hmuna sipai angin han ngaihtuah teh. Heng sipaite hi thil pawi chi hrang hrang laka vengtu ‘guard’ a awm a. Chu guard chu enzyme pakhat G6PD an tih a ni.
A awlsam zawngin sawi ila, G6PD (Glucose-6-Phosphate Dehydrogenase) hi enzyme pawimawh tak a ni a, kan cell, a bik takin kan thisena thisen sen (red blood cells) te hi chemical tha lo lakah a venghim a ni. Kan taksa hian thil tha lo ( ‘Free Radicals’ emaw ‘Reactive Oxygen Species’ tia koh bawk) a siam chhuak a, chu chu hnathawh dan pangngaiah a siam chhuak thin. G6PD enzyme hian heng thil tha lo tak takte hi an khawlkhawm loh nan leh cells an tihchhiat loh nan a ti a ni.
G6PD a hniam chuan eng nge thleng?
Tunah chuan chu ‘protector’ (G6PD) chu taksaah a hniam a nih chuan eng nge thleng ang tih han ngaihtuah teh? Tichuan chu thil tha lo tak takte chu a lo thleng a, kan thisen sen (red blood cells) te chu a tichhe tan ta a ni. Hetianga thisen sen siam theih aia rang zawka a chhe chakna hi hemolysis an ti a .
Hetianga thisen zam (red blood cells) tam tak i hloh chuan i taksain a mamawh oxygen a hmu lo. Chu chu anemia kan tih chu a ni a, a dik zawk chuan hemolytic anemia . Hei vang hian i chau a, i chak lo va, i hlim reng bawk.
Engtin nge G6PD tlakchhamna hi a lo awm?
G6PD tlakchhamna hi thlahtute atanga lo piang a ni . Chumi awmzia chu i nu leh pate hnen atanga i rochun thil a ni tihna a ni. G6PD enzyme siam tura hrilhtu gene-a mutation a awm chuan taksaa he enzyme siam chhuah zat hi a tlahniam a ni.
Mahse hetah hian thil pawimawh tak chu G6PD tlakchhamna nei zawng zawng hian symptoms an nei vek dawn lo tih hi a ni. Mi tam tak chuan harsatna nei lovin nun pangngai an hmang a. Mahse, pawn lam thil thenkhat (hengte hi ‘triggers’ kan ti) hian symptoms a rawn lang nghal thei a ni.
G6PD symptoms tichhuaktu trigger te
Heng trigger te hian taksaah chuan chutiang ‘free radicals’ hlauhawm tak tak kan sawi tawhte chu a tipung nghal vek a ni. G6PD tlakchhamna nei chuan heng thil tha lo pung zelte hi a thunun thei lo. Chutah chuan thisen sen (red blood cells) te chu a chhe tan a, symptoms a lo lang ta a ni.
| Trigger Type a ni | Hrilhfiahna |
|---|---|
| Chaw thenkhat | Fava beans a bik takin. Symptoms hi ei emaw, an pollen inhal emaw pawhin a awm thei. Hetiang dinhmun hi ‘Favism’ an ti bawk. |
| Damdawi thenkhat | Painkiller thenkhat Aspirin, Acetaminophen (Paracetamol), Sulfa damdawi thenkhat, antibiotics thenkhat leh Malaria damdawi te hi a bulpui ber an ni. Damdawi engmah ei loh tur a ni a, damdawi lam thurawn tel lo chuan ei loh tur a ni. |
| Viral leh bacteria infection te | Infection eng pawh, common cold atanga infection na tak thlengin G6PD symptoms a thlen thei a ni. |
G6PD tlakchhamna hi hmeichhia aiin mipaah a tam zawk a, African, Asian leh Mediterranean hnam chhuak zingah a tam zawk bawk.
Tute nge G6PD test neih ngai?
I doctor chuan G6PD test (thisen test awlsam tak) a rawt thei a, a bik takin a hnuaia symptoms te hi i neih chuan:
- Sawifiah theih loh hahna leh chak lohna
- Vun dum (pale skin) a ni
- Thâwk harsa emaw, thawk hah emaw
- Lung na tak tak
- Vun leh mit sen (jaundice) .
- Zun dum (cola rawng) .
- Hnunglam emaw pum na emaw
- Tuna kan buaina dinhmun hi
Nausen piang tharte chu a bik takin enkawl rawh.
Nausen piang thar tan jaundice vei hi thil pangngai a ni. But if it lasts for more than two weeks , naute zun a dum a, a bawlhhlawh a sen a nih chuan doctor chuan G6PD tlakchhamna a ringhlel thei a, he test hi a ti thei a ni.
Test report hi engtin nge kan hriatthiam ang?
G6PD test result hi lab hrang hrangah a inang lo deuh thei a, chuvangin i doctor chauh hian thu dik ber a pe thei che a ni . Mahse, a tlangpuiin result chi thum a awm.
- Normal: I taksaah G6PD enzyme i nei tling a. G6PD tlakchhamna i nei lo.
- Moderate Deficiency: Enzyme level hi a pangngai aia 10% leh 60% inkar a ni. Heng mite hian natna hrik an neih emaw, damdawi tha lo an ei emaw chauhvin symptom an nei tlangpui.
- Severe Deficiency: Enzyme hi a level pangngai atanga 10% aia tlem lovah a awm a. Heng mite hian thisen tlakchhamna (persistent anemia) emaw, symptoms nei fo emaw an nei thei.
G6PD tlakchhamna enkawl leh enkawl dan
G6PD tlakchhamna hi natna tihdam theih vek a ni lo, genetic condition a nih avangin. Mahse, uluk taka enkawl a nih chuan harsatna awm lovin nun hrisel tak i hmang thei a ni .
A tha ber chu symptoms rawn thlentu ‘triggers’ te hi pumpelh hi a ni. Hei hi a enkawlna ber a ni.
I tih tur chu:
- Fava bean ei loh vek tur a ni.
- Doctor phalna la hmasa lovin natna tidamtu Aspirin leh Acetaminophen (Paracetamol) te ei loh tur a ni.
- Damdawi engmah i pek hmain i doctor hnenah G6PD tlakchhamna i nei tih hrilh hmasa phawt ang che .
- Infection i neih chuan damdawi lam pan nghal rawh.
I natna lan chhuah dan a na lo a nih chuan i doctor chuan folic acid leh iron pills a pe thei ang. I thisen tlakchhamna a nasat chuan damdawi inah dah a ngai mai thei a, thisen pek emaw, oxygen therapy emaw pek i ngai mai thei.
Vitamin E ang antioxidants hian he natna hi a pui dawn lo tih hre reng ang che.
Take-Home Thuchah a ni
- G6PD tlakchhamna hi genetic condition tlanglawn tak a ni a, thlah kal zelah a kal zel a, hlauh tur a ni lo.
- Mi tam tak chuan symptoms an nei lo tak zet a ni. Fava bean, damdawi thenkhat, infection ang chi ‘triggers’ an tawrh hian symptoms a lang thin.
- Management ber chu heng triggers te hi pumpelh a ni.
- G6PD tlakchhamna i neih chuan enkawlna i zawn hmain doctor tu hnenah pawh hriattir hmasak a pawimawh hle.
- I rilru hahna nasa tak, vun sen emaw, zun dum emaw ang chi symptoms i neih chuan doctor pan nghal rawh.











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