A châng chuan i fain a neih, pum na emaw, riltam emaw ang chi thil hi kan ngaihtuah lutuk lo ṭhin a ni lawm ni? Mahse a chang chuan, a bik takin ek chhungah thisen a awm (bloody diarrhea) a nih chuan, a hnung lamah thil pawi zawk thup a awm thei. Chuvangin ngaihven ngai, hlauhawm deuh, mahse dik taka hriattir i nih chuan enkawl theih tur dinhmun kan sawi a ni. Chu chu HUS, a nih loh leh Hemolytic Uremic Syndrome a ni.
HUS chu eng nge ni mai?
A awlsam zawngin, Hemolytic Uremic Syndrome (HUS) hi i kal thisen kalna kawng nalh tak takte tichhe thei natna a ni . Heng thisen kalna kawngte hi a chhiat chuan a chhungah thisen zam te te a lo awm tan thin.
Hetiang hian han ngaihtuah teh: kan kal (kidney) hi kan thisen tifaitu tui filter ang mai a ni. A hmaa kan sawi tawh ang khan thisen zamte hian heng kal (kidney)-a filter tha tak takte chu a tikhawlo a ni. Chumi awmzia chu kal (kidney) te hian an hna pangngai, thisen atanga bawlhhlawh filter leh paih chhuah te hi a thawk tha thei lo tihna a ni. Hetiang dinhmun hi a nasat chuan kal (kidney failure) pawh a thlen thei a ni .
Hetiang dinhmun hi nunah engtik lai pawhin a lo awm thei a, naupang tê têah pawh a lo awm thei a ni. Enkawl vat loh chuan nunna atana hlauhawm a ni thei. Mahse thu lawmawm tak chu naupang tam zawk chu enkawlna dik tak nen an dam kim vek a ni.
HUS thlentu berte chu engte nge ni?
HUS hi intestinal infection na tak hnuah a lo awm fo thin. Heng natna thlentu ber chu a bik takin bacteria chi khat, `E. coli` tih a ni. He bacteria hi tui bawlhhlawh leh ei tur tui lo (a bik takin sa) hmanga kai a ni tlangpui. A châng chuan hri kai pakhat aṭangin mi dangah a darh thei bawk.
Heng hrik te hi taksaa an luh chuan an toxin siam chhuah te chu thisenah a pungkhawm a, kal (kidney)-a thisen kalna kawngte a tichhia a, HUS a siam thin.
E. coli hrik kai bakah hian HUS thlentu dang engemaw zat a awm bawk.
| Chhan | A sawifiahna tawi |
|---|---|
| Hri kai dangte | Viral infection HIV emaw influenza emaw a awm thei. |
| Damdawi thenkhat | A bik takin organ transplantation hnua immunity control nana damdawi pek thin te. |
| Naupai laiin harsatna a awm thin | Hei hi naupai laiin harsatna engemaw zat avanga lo awm a ni thei. |
| Autoimmune natna te | Taksa ngeiin a taksain a taksa a cell a beih nana natna. |
| Cancer (a tlem hle) . | Hei hi cancer natna thenkhat vang pawh a ni thei. |
A chi dang atypical HUS an tih pawh a awm bawk. Hei hi inherited condition a ni. Chumi awmzia chu thlah kal zelah a kal zel tihna a ni. A tlangpuiin a takin a thleng lo va, mahse a chunga kan sawi tak chhan pakhat avang hian chu natna chu “activated” theih a ni.
Engtin nge HUS natna lan chhuah dan hi kan hriat theih ang?
HUS natna lan chhuah dan hi mi hrang hrangah a inang lo thei. Natna thlentuah a innghat bawk. HUS-ah chuan bacteria `E. coli`, i digestive system-a symptoms chu i kidney chhiat hmain a lang hmasa ber .
A lan chhuah hmasak ber
Hengte hi pum na lo lan chhuah hmasak berte chu an ni :
- Thisen chhuak riltam – Hei hi vaukhânna chhinchhiahna pawimawh tak a ni!
- Khawsik
- Pum natna nasa tak
- Abdominal bloating emaw swelling emaw a awm
- Luak chhuak
A hnu lama lo awm thei symptom na tak tak
Heng chhinchhiahnate hi natna a lo nasat a, thisen kalna kawng a chhiat a, thisen zam (red blood cells) a chhe tan (hei hi anemia kan ti a), kal (kidney)-ah thisen zam (blood clots) a lo awm hian a lo lang thei a ni.
| Symptom a ni | Awmzia |
|---|---|
| A vun rawng dum (pale complexion). | Anemia vangin vun rawng a danglam thin. |
| Mutthilh lutuk, rilru hah lutuk | Taksa chak lohna avanga hah lutuk. |
| Thisen sang a sang | Kidney hnathawh that loh vang a ni. |
| Thâwk harsa | Taksa chhunga tui awmkhawm vang emaw, thisen tlakchham vang emaw. |
| Zun a tlem emaw, zun chhunga thisen a awm emaw | Kidney failure chhinchhiahna lian tak a ni. |
| Chhan awm lovin a hliam | Thisen zam tura puitu platelet a tlem avangin. |
| Hnar leh ka atanga thisen chhuak | Hei hi platelet tlakchhamna chhinchhiahna dang a ni. |
| Vung | Kidney-in tui tam lutuk a paih theih loh vang a ni. |
| Seizures emaw stroke emaw a awm thei | Thluak a nghawng chuan natna khirh tak tak a awm thei. |
HUS hi engtin nge enkawl a nih?
Hei hi in lama enkawl theih natna a ni lo. Damdawi ina dah vat a pawimawh. Damdawi inah chuan damdawi lam enkawlna bik a ngai a ni.
Enkawl dan hrang hrang a awm a:
- Transfusions: Thisen sen (red blood cells) hi thisen sen (red blood cells) chhe tawhte thlak nan pek thin a ni. Platelet a tlem chuan thisen chhuahna control nan platelet pek a ni bawk.
- Intravenous fluids (IV fluids): Taksa hydration leh salt balance vawng reng turin saline ang chi fluid pek thin a ni.
- Damdawi: Atypical HUS ang chi special case-ah chuan doctor chuan thisen kalna kawng a tihchhiat belh loh nan `Eculizumab (Soliris)` ang chi damdawi bik a pe thei a ni.
- Dialysis: Kal (kidney) a chhiat nasat chuan an tih tur, thisen atanga bawlhhlawh awmte filter leh paih chhuah hi machine ‘Dialysis’ an tih hmangin an ti thin.
- Plasma transfusion: Thisen kal dan tur siam that nan thisen plasma pek.
- Kidney transplant: Damlo, permanent kidney chhiatna nasa tak tuar tawhte chuan kidney transplant thar an neih a ngai mai thei.
HUS laka inven nan eng nge kan tih theih ang?
HUS thlentu ber chu intestinal infection a nih avangin chutiang infection te chu kan pumpelh theih chuan HUS vei theihna chu nasa takin kan ti tlem thei a ni. Chumi awmzia chu faina hi a pawimawh ber tihna a ni.
Thil awlsam tak tak i zawm theihte chu hetiang hi a ni:
- Kut sil fo tur: Chaw i buatsaih hma te, chaw ei hma te, bathroom hman zawh te, leh i fate diaper i thlak zawhah te, sahbawn hmangin i kut i silfai tur a ni.
- Ei leh in himna: Thei leh thlai te hi ei hmain uluk takin silfai thin ang che. Sa, a bik takin bawnghnute chu uluk takin chhum rawh (a tha ber chu 71 degree Celsius emaw 160 degree Fahrenheit aia tlem lo emaw a ni).
- Refrigeration: Refrigerator atanga sa chu direct-a chhum loh tur. A thaw hnuah microwave-ah emaw, room temperature-ah emaw chhum rawh. Sa raw leh chaw chhum tawh chu a hranin refrigerator-ah dah la.
- Pasteurized loh ei tur: Pasteurized loh bawnghnute, cheese emaw, thei in tur emaw hman loh tur.
- Swimming pool: Kawchhung i neih chuan swimming pool-ah lut suh. Tin, hmun bawlhhlawhah tui chawi loh tur a ni.
Take-Home Thuchah a ni
- Hemolytic Uremic Syndrome (HUS) hi a tir lamah thisen chhuak ang chi atanga tan a ni a, chutah chuan kal (kidney) nasa takin a nghawng thei a ni.
- Hei hi naupangte zingah a tam ber a, a bik takin bacteria `E. coli` tih a ni.
- I fa emaw nangmah emaw hian thisen chhuak riltam, hah lutuk, vun rawng, leh zun chhuah tlem ang chi natna lan chhuahna i neih chuan hun khawhral suh la , doctor hmu nghal la , damdawi in Emergency Department (ETU) ah kal nghal rawh.
- Hei hi dinhmun hlauhawm tak ni mah se, mi tam tak chuan damdawi ina enkawl dan dik tak an neih chuan an dam kim vek a ni.
- Faina te, ei leh in himna te, tui thianghlim in te hian he natna thlentu hri kai lakah a veng thei a ni.
HUS Sinhala, Hemolytic Uremic Syndrome Sinhala, Kal Natna, E. coli Infection, Thisen chhuak riltam, Naupang Natna, Kal Failure











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