Zingkar i harh a, i mit vel chu a hring chhuak thin em? A nih loh leh i ke leh kekawrte a hring a, i pheikhawk bun a harsat em? I zun chu a hma aia foamier zawk tih i hmu ngai em? Hengte hi random thil mai a ni lo. Heng symptoms hnung lamah hian i kidney-ah harsatna a awm thei. Vawiin hian damdawi lama pawimawh tak, heng ang symptoms inzawmkhawm atanga lo chhuak kan sawi dawn a ni. Chu chu Nephrotic Syndrome a ni.
Nephrotic Syndrome hi eng nge ni tak tak?
Hriatthiam hmasak tur chu hei hi natna bik a ni lo tih hi a ni. Kan kal (kidney) hnathawh that loh vanga lo awm
thei symptoms awmkhawmna a kawk a ni. Kan kal (kidney) hi high-tech filter angin han ngaihtuah teh. An hna ber chu kan thisen tihfai leh taksa atanga bawlhhlawh duh loh leh tui tam lutuk zun anga paih chhuah hi a ni. He filtering hna hi kal chhunga thisen kalna kawng network tha tak tak hmanga tih a ni. Hengte hi glomeruli kan ti a. Mi hrisel takah chuan he filtering system hian taksa tana thil pawimawh protein ang chi thilte chu a paltlang tir thei lo. Thisenah an awm reng a ni. Mahse heng filter tha tak tak glomeruli an tih te hi a chhiat chuan
taksain a mamawh protein tam tak chu a kal tlang a, zun nen a chhuak tan thin. Chu chu nephrotic syndrome kan tih chu a ni. Hetiang dinhmun hian puitling bakah naupang a nghawng thei a, mahse thu lawmawm tak chu a enkawlna tur a awm tih hi a ni.
Engvangin nge hetiang dinhmun hi a lo awm?
Chutianga a awm chhante chu chi hnihah then theih a ni.
Kidney chauh nghawng thei thil (Primary Causes) .
Chumi awmzia chu nephrotic syndrome hi natna dinhmun avanga kal (kidney) ngeia awm, natna dangin nghawng a neih loh vang a ni tihna a ni.
- Minimal Change Disease: Hei hi naupangte zingah nephrotic syndrome thlentu ber a ni . Microscope-ah chuan an kal tissue chu normal angin lang mahse, filtration process a tichhe hle. Viral infection , allergy , emaw damdawi thenkhat (a bik takin NSAIDs ang chi natna tidamtu ) avanga lo awm niin an ngai.
- Focal Segmental Glomerulosclerosis (FSGS): Hei hi kal chhunga filtering unit (glomeruli) te chu a hliam na a ni. Hei hi puitlingah chuan nephrotic syndrome thlentu ber a ni . HIV , damdawi thenkhat, genetic factors, leh thau lutuk te ang chi virus te hian he natna hi a thlen thei vek a ni .Thil tam tak, thisen sang te hian hei hi a nghawng thei a ni.
- Membranous Nephropathy: Hei hi glomeruli membrane thicking a ni. Hei hi cancer, malaria, hepatitis B, leh lupus ang chi natna vang pawh a ni thei.
Natna dang avanga kal chhiatna thlentu pahnihna
Chumi awmzia chu taksaa damdawi lam thil dang avanga kal (kidney) a chhiat chuan nephrotic syndrome a awm tihna a ni.
- Diabetes : Zunthlum hi puitling zingah nephrotic syndrome thlentu pahnihna a ni ber. Zunthlum thunun loh chuan kal (diabetic nephropathy) a tichhe thei a ni.
- Lupus: Hei hi immune system-a natna khirh tak a ni a, kal (kidney) a tichhe nasa thei hle.
- Amyloidosis: Protein chi khat amyloid an tih chu thisenah a pungkhawm thei a, kal (kidney) a tichhe thei a ni.
Eng symptom nge i neih theih ang?
Nephrotic syndrome hi symptom lian pali a awm a. Hengte hi chiang taka hrethiam tur chuan a hnuaia table hi en la.
| Symptom a ni | A awlsam zawngin... |
|---|
| Proteinuria a awm thin | Zun atanga protein chhuak tam lutuk. Hei hian zun chu a tlangpui aia foamier angin a lang thei a ni . |
| Hyperlipidemia a awm | Thisen thau leh cholesterol level a sang . Taksain protein a hloh chuan liver hian thau leh cholesterol a siam tam zawk a, hei hi a chhan ber a ni . |
| Taksa hring (Edema) . | A bîk takin ke, ke ruh, leh ke-ah a hring chhuak . A chang chuan kut leh hmai, a bik takin zingkar mit velah pawh a hring thei bawk. |
| Hypoalbuminemia natna (hypoalbuminemia) a awm | Thisen a protein chi khat albumin an tih tlahniam. He protein hi thisen kalna kawnga tui awm rengtu a ni. Zun atanga a chhuah chuan a tui chu tissue-ah a luang lut a, taksa chu a lo hring tan thin. |
Hetiang dinhmun hian naupang tê tête chu engtin nge a nghawng?
Naupang tê têah chuan Nephrotic syndrome hi a awm lo hle. Mahse, naupangin he natna hi a neih tak tak chuan a natna lan chhuah dan chu a danglam deuh thei a ni.
- Mit vel a hring, a bik takin zing thawh hunah.
- Hmai, kut, ke leh pum a hring.
- Foamy zun a awm.
- A hma aia chau leh chau zawka inhriatna.
Corticosteroids hi naupang enkawlna atana hman tlanglawn ber a ni. Hengte hian symptoms a control thei fo a, remission a thlen thei bawk.
Doctor, engtin nge hei hi i diagnose?
Heng symptoms te hi i neih chuan a rang thei ang bera doctor pan a pawimawh. Doctor chuan i symptoms te a zawt hmasa ang che. Tichuan,
- Urine Test: Hei hi zun atanga protein chhuak zat tehna atan a pawimawh hle.
- Thisen Test: Thisen cholesterol, albumin level leh kal hnathawh dangte enfiah thin ang che.
- Kidney Biopsy: A then phei chuan kal atanga tissue te tak te tak tak lak a, microscope hmanga enfiah a ngai mai thei. Hei hian kidney chhiatna thlentu dik tak hriat theihna a pui a ni.
A bik takin ni khata protein gram 3.5 aia tam zunthlum, thisena albumin level hniam, leh taksa hring (swelling) te hi a awm dun a nih chuan nephrotic syndrome hriat theihna atana thil pawimawh ber a ni.
Enkawl loh chuan eng harsatna nge thleng thei?
Hetiang dinhmun hi uluk taka enkawl a nih loh chuan hriselna lama harsatna lian tham dang a thlen thei a ni.
- Cholesterol sang leh lung natna hlauhawmna: Thisen thau leh cholesterol level sang chuan lung natna a tipung a.
- Thisen sang: Kal a chhiat chuan taksa atanga sodium (salt) leh tui lakchhuah theihna a tlahniam a, chu chuan thisen sang a tisang thin.
- Thisen zam: 1.1.Thisen zam vengtu protein te chu zun atanga chhuak a nih avangin taksaa thisen zam awm theihna a sang hle.
- Infection: Taksa taksa hriselna atana pawimawh immunoglobulins ang chi protein te a bo avangin pneumonia ang chi natna kai theihna a sang zawk.
- Kidney Failure: Hun rei tak enkawl loh a nih chuan kal chu a fail vek thei a, a dam theih nan dialysis emaw kidney transplant emaw a ngai a ni.
Hei hi eng enkawlna nge ni?
Enkawl dan tur ruahmanna chu i nephrotic syndrome awm chhan bulpuiah a innghat a ni.
Damdawi chi hrang hrang
I doctor chuan a hnuaia damdawi te hi a pe thei ang:
- Thisen sang damdawi: ACE inhibitor leh ARB ang chi damdawi te hian kal (kidney) a pressure a tihziaawm bakah zun atanga protein chhuak a ti tlem bawk.
- Diuretics: "Tui pills" tia koh bawk, hengte hian taksaa hliam (swelling) tihziaawmna kawngah a pui thin.
- Cholesterol tihhniamna damdawi.
- Thisen tithianghlimtu (Anticoagulants): Thisen zam awm theihna a tiziaawm.
- Immune-suppressing medications: Damdawi corticosteroid ang chi hian immune system hnathawh a control a, kal chhiatna a ti tlem bawk.
Hei vang hian diet control hi a pawimawh hle
Damdawi bakah hian he natna hi enkawl nan hian ei leh in pawh a pawimawh hle.
- Chi (sodium) tihtlem): Chi ei tam lutuk hian tui a tikhawlo thei a, a hring a, thisen sang a thlen thei bawk. Chaw chi tamna, sausage, sa cured, canned vegetables, soup, biscuit, leh sauce te ei loh tur.
- Thau leh cholesterol tihtlem: Saturated fat leh cholesterol tlemna eitur zawm tur a ni.
- Fluids tihtlem: A chang chuan i doctor chuan ni khata tui i in zat tihtlem turin a hrilh ang che.
Heng ei leh in khapnate hi i doctor emaw nutritionist emaw thupek angin zawm tur a ni tih hre reng ang che.
Take-Home Thuchah a ni
- Nephrotic syndrome hi kal chhunga filtration system nalh tak tihchhiat avanga natna lanchhuahna hrang hrang awmkhawm a ni.
- A lan chhuah dan ber chu taksa a hring (a bik takin ke leh mit vel), zun (foamy urine) (protein tam lutuk vang), leh thisen cholesterol sang te hi a ni.
- Hetiang dinhmun hi natna dang, zunthlum leh thisen sang vang pawh a ni thei.
- Inenkawlna atana damdawi bakah hian chi leh thau tlemna ei leh in zawm a pawimawh hle bawk.
- Heng symptoms te hi i neih chuan ngaihthah ngai suh . A rang thei ang bera doctor rawn la, thurawn leh enkawl dan dik tak i dawng ang.
Nephrotic Syndrome, Nephrotic Syndrome, kal natna, hring, zun a protein, zun foamy, Sinhala tawngin kal natna, cholesterol
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