A châng chuan i chau hle a, i lu a buai , i mit a fiah deuh bawk em? Hengte hi thil pangngaiah kan ngai a, mahse a chang chuan a chhan chu kan taksaa thisen a pungkhawm vang a ni thei. Hei hi medical science-ah chuan Secondary Polycythemia an ti a. He hming i hriat hian hlau suh, hei hi eng emaw chen chu a awm lo. A awlsam zawngin, hei hian i taksain thisen sen a siam chhuah tur aia tam a siam tihna a ni . Chuvangin he thu hi chipchiar takin, awlsam takin han sawi ila.
Engvangin nge hetiang hian thisen a thip? A chhan engte nge ni?
"Secondary" tih thumal hi "second" tihna a ni. Chuvângin, he natna hi chu hming pawh pêk a ni a, a chhan chu thil lo awm tak a nih loh avângin, damdawi lam dinhmun dang emaw, a chhan dang emaw avânga lo awm a nih avângin .
Hetiang hian han ngaihtuah teh, thisen sen (red blood cells) hian kan taksa tissue-ah oxygen a phur a. Eng emaw chhan vanga thluak emaw kal emaw hian taksain oxygen a dawng tlem tih signal a dawn chuan kal hian hormone `Erythropoietin` emaw ` EPO` emaw a siam chhuak thin. He `EPO` hormone hian kan ruhroah a kal a, "thisen sen tam zawk siam turin, taksain oxygen a hmu tlem hle" a ti a. Chuvangin ruhro hian thisen sen thar a siam tan ta a ni. Hetianga thisen sen (red blood cells) a pun chuan thisen chu a thim zauh zauh thin. He thisen thim tak hian kan taksa chhunga thisen kalna kawng te tak te (`capillaries`) kal tlang harsa a ti hle. Chuvangin ` stroke` ang chi natna khirh tak tak vei theihna a sang hle.
Tunah chuan hei hi eng nge a chhan ber tih i lo en ang u.
| Chhan chi hrang hrang | Entirnan |
|---|---|
| Nunphung nena inzawm chhan |
|
| Thluak lam natna | |
| Damdawi lam thil dang |
Primary leh Secondary Polycythemia hi eng nge an danglamna?
`Primary Polycythemia` tih pawh i hre tawh mai thei.Heng pahnih hi ri inang mahse, an pahnih inkarah hian danglamna lian tak a awm.
A awlsam zawngin kan ruhro hi thisen cell siamna factory ang a ni.
- Primary Polycythemia: Hei hi factory ngei (bone marrow) hian a mah chauhin thisen sen (red blood cells) a siam tam lutuk a, pawn lam signal engmah a awm lo. Hei hi a tlangpuiin genetic change (`mutation`) vang a ni.
- Secondary Polycythemia: Hetah hian factory (bone marrow) chu a thawk tha hle. Mahse, pawn lam atanga signal dik lo emaw, tul lo emaw (e.g., kidney atanga) "produce tam zawk" tura tih a nih avangin thisen sen tam lutuk a siam thin.
An pahnih inthlauhna tur hian doctor-te chuan `JAK2` tih gene an test thin. `Primary Polycythemia` vei tam tak chuan he gene hi `positive` an ni. Mahse, `Secondary Polycythemia`-ah chuan hetiang hi a thleng lo.
Hetiang natna lan chhuah dan hi engte nge ni?
Thisen zawrh chhinchhiahna hi mi hrang hrangah a inang lo thei. Mi thenkhat chuan symptom engmah an nei lo mai thei. Mahse, hengte hi a lan chhuah dan tlangpui a ni.
- Chau
- Lu na
- Luak chhuak thei
- Mit hmuh a fiah lo
- Anorexia a awm
- Taksa chak lohna
- Rilru ngaihtuahna a tlahniam
Pawimawh tak chu heng symptoms te hi thisen zam vang ringawt a ni lo. Symptom dang (khuh, thawk hah) pawh a chhan bulpui (e.g., lung natna) vang a ni thei bawk.
Entirnan, a chhan chu `Sleep Apnea` a nih chuan chhun lamah mutthilh lutuk i nei thei a, zanah i bengchheng thei bawk.
Engtin nge hei hi i hmuh theih, Doctor?
Heng symptoms te hi i doctor hnena i hrilh hian a tih hmasak ber tur chu i medical history kimchang a zawt che a ni. Chu chu, zu i in a nih chuan, tun hnaiah i thau a tlahniam em, i khuh em, i rilru a na em, i thawk harsa em, zanah i bengchheng em . I chhungkuaah hian heng natna hi an nei tawh em tih pawh a zawt bawk ang.
Tichuan, taksa enfiahna neih a ni a, a tul chuan test engemaw zat neih a tha a, chungte chu:
- Thisen test: Thisen sen zat, EPO hormone level, leh thisen oxygen level (hei hi Arterial Blood Gas - ABG hmanga tih theih) test te enfiah thin ang che.
- ECG (Electrocardiogram): Thinlung hnathawh dan enfiah thin ang che.
- Imaging Tests: Chest X-ray, CT scan emaw ultrasound scan emaw hmangin thinlung, thin, emaw, spleen emaw a hring em tih a enfiah thei a ni.
Heng test hmang hian doctor chuan he natna thlentu dik tak hi a hmu chhuak thin.
Hei hi eng enkawlna nge ni?
Hemi chungchanga a tha ber chu secondary polycythemia hi thisen thimna chhan bulpui hriatchhuah leh enkawl hmanga tihdam theih a ni
Enkawlna tum ber chu thisen zam chhan tihbo hi a ni.
- A bulpui ber enkawl dan:
- Meizial zu mi i nih chuan: Meizial zuk bansan a pawimawh hle. Hemi atan hian doctor chuan thurawn leh damdawi tul tak tak a pe ang.
- Thau lutuk vang a nih chuan: I nunphung thlak danglam tur, exercise la tur leh i taksa rihna tihtlem turin thurawn i dawng ang.
- COPD ang chi lung natna i neih chuan: Low-flow oxygen therapy hian taksaa oxygen level a siam that theih nan a pui thei a ni.
- Tumor vang a nih chuan: He natna hi surgery hmanga lakchhuah a nih chuan a tidam vek thei a ni.
- Symptoms tihziaawmna atana enkawlna: 1.1.
- Phlebotomy: Hei hi thisen pek nen a inang a. Thisen pint chanve emaw pint khat vel chu vein atang hian lakchhuah a ni a, chu chuan thisen sen (red blood cells) a ti tlem a, thisen chu a ti thim bawk. Hei hian lu na leh luak chhuak ang chi symptoms lakah a reh nghal vat thin.
- Damdawi: I doctor chuan natna tihziaawmna turin aspirin ang chi damdawi a pe thei a, natna lan chhuahna tur antihistamines te pawh a pe thei bawk.
Condition dang i hmachhawn laiin condition dang hriat chu a lungchhiatthlak hle. Mahse hre reng ang che, `Secondary Polycythemia` thlentu natna tam zawk hi hriat lar tak leh enkawlna hrang hrang nei an ni. Chuvangin, a chhan bulpui chu uluk taka enkawl a nih chuan he natna hian i dam chhung a nghawng lo tlangpui.
Take-Home Thuchah a ni
- Secondary polycythemia chu taksaa thisen sen (red blood cells) a pun a, damdawi lam thil dang avanga thisen a thim chhoh hi a ni.
- Hei hi ruhro (bone marrow) a chhiatna mai mai a ni lo.
- Meizial zuk te, thau lutuk te, lung natna te, thinlung natna te hi a chhan ber thenkhat an ni.
- Enkawlna tum ber chu thisen thimna chhan bulpui (underlying condition) enkawl hi a ni.
- Chauhna, lu na, lu na emaw, luak chhuak emaw ang chi symptom i neih chuan i doctor nen inbiakna neihpui ngei ang che.











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