I kut leh ke i thunun thei lo chu han mitthla teh. I taksa pengte chu duh loh zawngin a che a, mi pakhatin a zai ang maiin a che thin. Hei hi a takah chuan mi thenkhatin an tawn thin condition a ni. Hei hi hmutu tu emaw chuan an zai mai mai niin a ngai mai thei. Chorea tih hming hi Greek tawng atanga lak a ni a, "lâm" tihna a ni. Mahse he natna tuar tu tan chuan chutiang chuan a awlsam lo. Vawiin hian i zir belh leh ang u.
Chorea hi eng nge ni tak tak?
A awlsam zawngin Chorea hi movement disorder a ni. Thluak chhung thuk taka awm central nervous system, movement control tu basal ganglia-a hnathawh that loh vang a ni. Hei hian duh loh zawnga kut, ke leh hmai chetna a thlen a, chu chu kan thunun theih lohvin a thleng a ni.
Heng chetnate hi a chang chuan a te hle thei a, hma leh hnunglam hawia inher ang maiin. Mi thenkhat chuan hei hi nervous reaction mai mai niin an ngai. Mahse a châng chuan taksa peng khat aṭanga hmun danga luang chhuak, tharum thawhna, rang taka chetna a ni thei bawk.
He natna lan chhuah dan berte chu engte nge ni?
Chorea natna hi doctor-te’n an hman thin symptom bik engemaw zat a awm. Hengte hi he natna hi i nei thei tih chhinchhiahna a ni thei.
| Symptom a ni | A awlsam zawngin sawifiah a ni |
|---|---|
| Milkmaid chuan a rawn kuah a | Heng mite hian taksa ruh (muscle) nghet taka vawn chu an harsat hle. Entirnan, an kut i vawn chuan nghet takin an chelh lovang a, bawnghnute pek ang maiin an chelh ang a, an thlah ang. |
| Jack-in-the-box tawng a ni | A lei chu chhuah tir tura an tih chuan a chhuah nghal a, chutah a hruai lut leh a, box atanga toy atanga zuang chhuak ang mai a ni. Hei hi Harlequin’s tongue an ti bawk. |
| Kal dan danglam tak | Chorea vei te hian kal dan danglam tak an nei a. Neurologist chuan he kal dan hi a enfiah hian a natna hi a hre thei a ni. |
Chorea chi dang
Chorea chi hrang hrang bakah hian a kaihhnawih movement disorder dang engemaw zat a awm bawk.
- Athetosis: Hei hi chorea chi khat, slow-acting chi a ni. Hetah hian movement te hian twitching, writhing nature an nei a.
- Choreoathetosis: Hei hi Chorea leh Athetosis pahnih inzawmkhawm a ni. Hetah hian movement te hi pace leh intensity hniam takah a thleng thin.
- Ballism/Ballismus: Hei hi chorea rang tak, tharum thawhna chi a ni. Mi pakhatin an kut leh ke a thlak ang mai a ni.
Chorea awm chhante chu engte nge ni?
Kan sawi tawh ang khan hei hi a bulpui ber chu thluak peng pakhat, basal ganglia an tih a ni. Scientist-te chuan chorea hi he part hian chemical dopamine an tih tam lutuk a dawn chuan a lo awm niin an ngai a, chu chuan nerve hnathawhna kawngah a pui a ni. Dopamine hi kan taksa tan a pawimawh hle a, mahse a tam lutuk chuan hetiang hian harsatna a thlen thei a ni.
Chorea thlentu ber leh hriat lar ber chu Huntington natna a ni . Hei hi thlahtu natna a ni.
Mahse, hei hi chhan dang tam tak a awm thei a, a then chu a tlem hle.
- Rheumatic fever: Naupang thenkhat chuan an rilru natna (strep throat) emaw scarlet fever emaw an neih hnua rheumatic fever an neih chuan hun eng emaw chen atan chorea state an nei thei.
- Autoimmune diseases : Hetiang dinhmun hi lupus ang chi natna nei te tan a awm thei.
- Brain damage: Chorea hi thluaka tumor emaw stroke emaw ang chi natna avanga lo awm thei a ni.
- Hormonal leh metabolic disorders: Hei hi hypothyroidism ang chi natna vang pawh a ni thei.
- Damdawi thenkhat: Chorea hi damdawi thenkhat, a bik takin Parkinson natna atana hman thinte side effect angin a awm thei a ni.
Diagnosis leh enkawl dan i zir ang u.
Doctor-in a tih hmasak ber chu i natna lan chhuah dan enfiah hi a ni. TichuanThe challenge is to find the cause of the disease , chu chu thluak scan (imaging test) leh thisen test hmanga puih theih a ni.
Tin, i doctor chuan tuna i damdawi ei zawng zawng hi a zawt ngei ang , a chang chuan hei hi damdawi avanga lo awm thei a nih avangin.
A chhan hriat chhuah a nih veleh i doctor chuan enkawlna i mamawh leh mamawh loh chu a rel ang. Thil engemaw takah chuan, a bik takin damdawi avanga lo awm a nih chuan, damdawi tihtawp emaw, thlak emaw a nih veleh chorea natna chu a bo mai ang. Chutiang a nih loh chuan a chhan bulpui ber chu enkawl a ni ang.
Heng thunun theih loh chetnate hi thunun thei damdawi a awm. Heng damdawi te hian thluaka dopamine hnathawh chu a titawp fo thin. Brain surgery leh deep brain stimulation (DBS) te hi enkawlna atan hman ni mah se, harsatna a thlen theih avangin hman a tlem hle.
Huntington-a Natna leh Chorea natna
Chorea chungchang kan sawi hian Huntington natna hi kan sawi lo thei lo. Hei hi chorea thlentu hriat lar ber a ni. Mahse natna awm lo tak a ni a, mi 10,000 emaw 20,000 emaw zinga pakhat chauh a vei.
He natna hi chhan dang aiin a danglam a , a chhan chu damdawi chiang tak a neih loh vang a ni a , hun kal zelah natna hi a zual zel a thihna a thlen thin . He natna hi thluaka basal ganglia thenkhat a chhiat chuan a lo awm thin.
Chorea hi kum 35 leh 40 inkarah a intan hmasa ber thin a, rilru lam harsatna pawh a rualin a intan thin a, mahse a tir lamah chuan a langsar vak lo.
Huntington natna hi a genetic lam a ni
He natna hi thlahtu a nih avangin Huntington natna vei nu emaw pa emaw atanga lo piang naupang chuan he natna hi a vei theihna chance 50% a nei a ni. A thlentu gene chhia hi scientist-te chuan kum 1993 khan an hmuchhuak a ni.
Tûn laiah chuan he natna chungchâng hi genetic testing hmangin hriat theih a ni .
- Symptoms i neih chuan Huntington natna a nih ngei ngei tur a ni.
- I chhungte (nu leh pa, chhungte) tu emaw hian he natna hi an vei a nih chuan nakin lawkah he natna hi i vei ve dawn em tih zawng chhuak rawh.
- Nausen pum chhunga naute hian naupai laiin he natna hi a vei em tih zawng chhuak rawh (prenatal testing).
Mahse hetiang genetic test neih hma hian a result hmachhawn dan tur chungchangah genetic counseling lak a pawimawh hle. A chhan chu hei hi i nun nghawng thei tur thutlukna a nih vang a ni. Chuvangin, chutiang test i neih hmain doctor hriatna nei tak nen inbia la, uluk takin ngaihtuah hmasa phawt ang che.
Take-Home Thuchah a ni
- Chorea hi movement disorder a ni a, i thunun theih lohvin a awm thin. Thluak lama harsatna awm vang a ni.
- Hei hi damdawi, thlahtu natna (Huntington natna ang chi), leh damdawi lam thil dang avanga lo awm thei a ni.
- Nangmah emaw, i hriat tu emaw chuan heng natna lan chhuah dan hi i neih chuan, tihkhawtlai suh la, doctor thiam tak, a bik takin neurologist .
- Natna hi dik taka hriatchhuah hi a enkawl dan tur dik tak neih hmasak ber a ni.
- Huntington-a ang chi thlahtu natna rinhlelhna a awm chuan genetic testing neih hmain genetic counselling lak hmasak a pawimawh hle.











💬 Comments (0)
Comment a la awm lo. Hetah hian i comment hi a vawikhatna atan add rawh.
I comment kha add rawh