Ni engemaw zat kalta khan khawsik emaw, pum na emaw i nei a, tunah chuan i rilru a hahdam deuh tawh ang tih han ngaihtuah teh. Mahse rang takin i mit chu a fiah deuh niin i hria a, thil chu hmun hnih ah i hmu a. I kal laiin i nghet lo hle a, i ke pawh a inzawm khawm thin. Hetiang thil hi thleng se, mi zawng zawngin an hlau hle ang, a dik em? Vawiin hian hetiang symptoms thlentu condition kan sawi dawn a, chu chu mi tam takin an la hriat ngai loh, mahse hriat a pawimawh hle. Chu chu Miller Fisher Syndrome a ni.
A awlsam zawngin, Miller Fisher Syndrome hi eng nge ni?
Miller Fisher syndrome hi thluak lama harsatna awm lo tak a ni. Guillain-Barré syndrome (GBS) tih hi i hre tawh mai thei. Kan taksa hriselna (immune system) hian mahni nerve (nerve) a bei thin natna a ni bawk. Miller Fisher syndrome hi GBS chi khat a ni a. A tlem em em a, khawthlang ramah GBS vei zinga 1% leh 5% inkar vel a ni. Amaherawhchu, Asia ram thenkhat Taiwan leh Japan-ah chuan a tam deuh hlek a ni. Chuvangin hei hi nitin natna a ni lo tih i hrethiam thei ang. Mahse hei hi hriat chian a pawimawh hle.
Engvangin nge hetiang hi a lo awm? A chhan engte nge ni?
Hei hi a pawimawh ber a ni. Miller Fisher syndrome leh GBS te hi kan taksaa natna hrik lut a nih chuan a lo awm ve ve a ni.
A awlsam zawngin kan defence system, immune system hi tlem a ‘buai’ deuh a, infection do ai chuan kan nerve ngei pawh hi tihsualin a rawn bei tan ta zawk a ni. Doctor-te hian he thil hi eng nge a thlen tih chiang takin an la hre lo. Heng symptoms te hi natna atanga ni engemaw zat atanga kar 4 chhungin a lang tlangpui a, a bik takin pum na, diarrhea ang chi, emaw thawkna lama infection (cold, flu) a awm chuan a lang tlangpui. Hetiang natna thlentu bacteria ber chu `Campylobacter jejuni` a ni. Hei hi a tlangpuiin pum na leh riltamna thlentu a ni. Tin, he natna thlen thei virus pawh a awm bawk:
- Zika virus a ni
- Mihring taksa chak lohna hrik ( HIV ) .
- Epstein-Barr virus, khawsik ang chi natna mononucleosis thlentu a ni.
Eng nge a lan chhuah dan? Engtin nge hei hi i hriat chian?
Mi tam tak chu doctor pan turin an kal a
, a chhan chu ni engemaw zat chhungin an mit a tlahniam rang a ,
kal pawh an harsat phah thin . Miller Fisher syndrome hi a lan chhuah dan lian ber pathum a awm a. Hengte hi table pakhatah i hrethiam ang u.
| A symptom ber a ni | A awlsam zawngin, eng nge thleng? |
|---|
| Mit ruh chak lohna (Ophthalmoplegia) . | Double vision a awm a, mit chu control leh duh lam hawia kaihhruai a harsa ta hle. |
| Balance hloh (Ataxia) 1.1. | Ka kal lai hian ka tlu a, off balance ang maiin ka inhria. Ka taksa peng hrang hrangte coordinate harsa ka ti hle. |
| Areflexia tih hi a ni | Thil chi hrang hrang, doctor-in i khup chu hammer te tak te hmanga a tap chuan i ke a che lo ang. Taksa reflexes te chu a bo vek a. |
Heng symptom lian pathum bakah hian mi thenkhat chuan symptom dang an nei thei bawk:
- A mitmeng (dilated pupils) a awm .
- Facial muscle chak lohna
- Thlarau ruh chak lo (gag reflex tlahniam) .
Pawimawh: Heng symptoms te hi i taksa peng leh thawkna ruh chak lohna nen a awm a nih chuan GBS-MFS overlap syndrome an tih natna a ni thei. GBS chhinchhiahna ber chu chak lohna a ni a, ke atanga intan a, taksa pum puiah a darh thin.
Engtin nge doctor hian hei hi a hriat chian?
He natna hi chiang taka hriat a harsa deuh. A chhan chu thluak lam natna dang tam tak, chutiang bawka chhinchhiahna nei an awm avangin. Entirnan, natna hrang hrang `Basal meningitis`, `Botulism`, `Brainstem stroke`, `Myasthenia Gravis` te hi a ni. Chuvangin doctor chuan uluk takin a enfiah ang che, i natna lan chhuah dan leh tun hnaia i natna te a zawt ang che. Tichuan, a natna hriat chian nan test eng emaw zat a ti ang.
| Fiahna | A awlsam zawngin, eng nge i tih/i hmuh? |
|---|
| Lumbar puncture a awm | I ruhro (cerebrospinal fluid) vel a tui tlem te chu lak a, protein a tam em tih enfiah thin a ni. Hei hi Miller Fisher damlote zingah a sang fo thin. |
| Thisen Test a ni | Thisenah hian he natna atana bik antibody `anti-GQ1b` an tih chu an test a ni. He antibody hi damlo 95% ah hmuh theih a ni. |
| Nerve Conduction chungchang zirchianna / EMG | Electrical current te tak te, hrehawm lo tak hmangin i nerve leh muscle te hnathawh that dan tehna a ni. He natna hian nerve-ah thil danglam engemaw zat a lantir a. |
| MRI Scan a ni | He test hi natna dang, stroke ang chi te tihbo nan an ti thin. Miller Fisher-ah chuan MRI-ah chuan result pangngai a lang tlangpui. |
Hei hi eng enkawlna nge ni? A dam leh theih nan eng chen nge hun a duh?
A hmasa berah chuan he natna hi tidam kim thei tur ‘damdawi’ bik a awm lo.
Mahse, enkawlna tha tak tak a awm a, chu chuan a natna lan chhuah dan a thunun thei a, a dam thuai thei bawk. Heng symptoms nei mi chu damdawi inah dah a ni tlangpui. Hei hi GBS natna khirh tak tak awm leh awm loh uluk taka enfiah nan a ni. A chhan chu GBS hian a chang chuan nunna a tichhe thei a ni. Enkawlna atan hmanraw lian pahnih hman a ni a, chungte chu: 1.
Intravenous Immunoglobulin (IVIg): Hei hi saline ang chi liquid medicine a ni a, vein-ah dah a ni. Mi hrisel sang tam tak thisen plasma atanga thliar hran tawh antibody thianghlim tak tak a pai a ni. Hei hi ni 5 vel pek chhunzawm zel a ni. 2.
Plasma Exchange (Plasmapheresis): Hei hi thil buaithlak deuh a ni. A awlsam zawngin, i taksa atanga thisen tlemte lak chhuah a ni a, machine bik chuan harsatna nei plasma (nerve beitu antibodies awmna hmun) chu a paih chhuak a, chu chu i thisen cell ngeiin a thlak a, chu chu replacement plasma nen a thlak bawk. Hei hi kar hnih chhungin vawi 5 vel tih thin a ni. Heng enkawlna hnua i taksa ruhte hi a chak lo hle a nih chuan
a tichak leh theih nan physiotherapy i mamawh mai thei.A tul a ni. Damna chungchang erawh chuan damna tha tak neih nan kar 8 atanga kar 12 inkar a ngai tlangpui.
Mi tam zawk chu thla 6 chhungin an dam vek. Recurrence rate hi 3% aia tlem a ni. Chuvangin, a hmaa hriatchhuah leh enkawl dan hi a pawimawh ber a ni.
Take-Home Thuchah a ni
- Miller Fisher syndrome hi natna hmuh tur awm lo tak a ni a, tun hnaia kan natna vei avanga kan taksa hriselna (immune system) hian kan nerve a rawn beih hian a lo awm thin.
- A lan chhuah dan ber chu mit ruh chak lohna (double vision ), balance hloh (kal harsa), leh reflexes hloh te hi a ni.
- Nangmah emaw, i hriat miin emaw heng symptoms te hi a lo neih thut chuan doctor pan nghal rawh. Hlauthawng suh, mahse tihkhawtlai suh.
- Hei hi damdawi ina dah leh physical therapy hmanga enkawl theih a ni a, mi tam zawk chuan an dam kim vek a ni.
Miller Fisher Syndrome, Guillain-Barré syndrome, Thluak lam natna, Mit hmuh lohna, Kea kal harsa, GBS, Autoimmune natna
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