I inbual lai te, i inchei lai te, a nih loh leh i fa te chu i chelh mai mai a, an pum chhungah hnah te tak te i hriat chuan engtin nge i awm ang? Chu chu a hlauhawm takzet a ni lawm ni? Hetiang hunah hian Wilms-a tumor an tih hi kan ngaihtuah a ngai a ni. Vawiin hian awlsam takin sawi ila.
Wilms Tumor hi eng nge ni tak tak?
A awlsam zawngin sawi ila, Wilms tumor hi kidney cancer chi khat a ni a, naupang tê tête zingah a awm ṭhin. Naupangte kal cancer zinga zaa 90 vel a ni. A châng chuan Wilms tumor hi nau piang laia awm natna dang nen a awm dun thei bawk. Hengte hi ``congenital syndromes'' emaw, nau piang laia awm thin dinhmun hrang hrang inzawmkhawm emaw kan ti thin.
Hei hi `(Wilms' tumor)` leh `(nephroblastoma)` an ti bawk. A tam zawkah chuan kal pakhatah hian tumor pakhat chauh a awm thin. Mahse, naupang thenkhat chuan kal pahnih `(bilateral),` ah tumor an nei thei a, kal pakhatah cancer awmna hmun pakhat aia tam a awm thei bawk.
He thil hi tuin nge hmu tam ber?
Hei hi puitlingte nghawng thei thil awm lo tak a ni. Wilms tumor hi cancer a ni a, naupang kum 15 hnuai lam a vei ber a, he natna vei zinga 95% chu kum 10 an tlin hmain an vei tih hmuhchhuah a ni.
African hnam chhuak naupang dumte chu an hlauhawmna a sang deuh hlek a ni. Asian naupangte hi an hlauhawmna a hniam zawk. Tin, mipa aiin hmeichhe naupangin an vei tam deuh bawk.
Chhungkaw za zela tlemteah pawh hei hi gene atanga lo chhuak thil a nih thu an sawi bawk.
Hetiang dinhmun hi engtiang chiahin nge a awm?
America ang ramah chuan kum tin Wilms tumor vei thar 500 vel an awm niin an sawi. Sri Lanka-a a awm dan tur statistics dik tak hmuh a har hle a, mahse hei hi naupang zinga hmuh theih cancer a ni.
Wilms tumor-a congenital syndromes hmuh theihte chu engte nge ni?
Wilms tumor nei naupangte hian pianpui natna dang an neih hi a tlem hle. Mahse a thleng thei tho. Syndrome lian ber ber thenkhat chu hetiang hi a ni:
- Beckwith-Wiedemann syndrome: Hetiang syndrome nei naupangte hi Wilms tumor vei theihna chance 5% atanga 10% vel an ni. Hei hi taksa peng hrang hrangte chu a tlangpui aia lian zawka lo thanglian zelna dinhmun a ni. A chang chuan taksa sir khat chu a sir dang aiin a lian zawk thei bawk.
- WAGR syndrome: Hetiang syndrome nei naupangte hian Wilms’ tumor (a hminga W hi Wilms tihna a ni) vei theihna chance 50% an nei a ni. Hei hian iris (Aniridia) thenkhat a hloh thei a, chubakah genital leh renal problem a thlen thei bawk.
- Denys-Drash natna hi a ni:Hetiang symptoms inzawmkhawm nei naupangte hian Wilms tumor an vei theihna chance a sang hle a, hei hian reproductive organs leh kidney-ah pawh harsatna a thlen thei bawk.
Wilms tumor hi eng symptoms nge ni?
I fate zingah hian heng chhinchhiahnate hi zawng rawh:
- Pum (belly) chhunga lump emaw firmness/lump emaw a awm. He lump emaw lump emaw hian a chang chuan a na thei a, mahse a tam zawkah chuan a na lo.
- A pum na.
- Zun chhunga thisen (hematuria) a awm.
- Khawsik.
- Thisen sang (hypertension). Hei hian naupang chu hnar thisen, lu na, thisen chhuak mit a thlen thei a ni.
Heng symptoms pakhat emaw a aia tam emaw i neih chuan , doctor i pan nghal tur a ni.
Eng thilin nge Wilms tumor hi a thlen?
Dik tak chuan Wilms-a tumor hi eng nge ni tih chiang takin kan la hre lo. Mi tlemte chauhvin genetic predisposition nei mahse, a tam zawkah chuan engvangin nge a lo awm tih erawh a chiang lo.
Engtin nge Wilms tumor hi hmuhchhuah (diagnose) theih?
I naute diaper area-ah lump i hmuh chuan, emaw, lump vangin diaper lian zawk i hmang a nih chuan, i doctor chuan Wilms tumor test a duh mai thei. Heng tumor te hi a chang chuan kal aiin a lian thei bawk.
I fa hian a hmaa kan sawi tawh syndrome zinga pakhat emaw, genetic problem emaw a neih chuan i doctor nen inbiain test chhunzawm leh chhunzawm leh tur loh chu i rel thei ang.
Wilms tumor hriat theihna atana test hmante chu:
- Taksa enfiahna: Hemi chhung hian doctor chuan uluk takin naupang pum chu a palpate thin.
- Imaging test hrang hrang:
- Pum chhunga ultrasound scan hmanga enfiah a ni.
- CT scan - Hei hi tui bik (contrast) inject hmanga tih a ni fo.
- Doctor chuan chest X-ray emaw CT scan emaw hmangin cancer chu lungah a metastasized em tih a enfiah thei bawk.
- Heng imaging test te hian i fain tumor a neih leh neih loh a hriat theih nan a pui thei a ni. Wilms tumor leh kidney cancer chi dang thliar hrang turin an pui thei bawk.
- Thisen leh zun test: Heng zingah hian liver function test leh thisen zam test te a tel.
- Biopsy: Hei hi tumor atanga tissue te tak te la chhuakin lab-ah test turin thawn a ni.
Cancer staging chungchangah eng nge hriat tur i neih?
Wilms tumor stage hriat theih dan kawng hnih a awm a, chu chu cancer hi eng chen nge a darh tih hi a ni. Hei hi ``staging'' an ti a, a tam poh leh cancer hi a darh zau zawk a ni.
Europe ram hrang hranga Doctor-te chuan International Society of Pediatric Oncology (SIOP) system an hmang a. United States leh Canada-a Doctor-te chuan Children’s Oncology Group (COG) system an hmang a.
Heng method pahnih inthlauhna pakhat chu COG method-ah hian operation hnuah leh chemotherapy (anti-cancer drugs) pek hmain tumor stage enfiah thin a ni. SIOP method-ah chuan chemotherapy zawhah surgery tih a ni a, chumi hnuah chauh stage enfiah a ni.
COG system hnuaia stage hrang hrangte chu hetiang hian then a ni.
- Stage I: Tumor hi naupang kal (kidney)-ah chauh a awm a, operation hmangin a pumin lakchhuah theih a ni.
- Stage II: Tumor hi kal atang hian a lo thang chhuak tawh a, mahse operation hmangin a bo vek thei.
- Stage III: Tumor hi a chhuak kim thei lo. Cancer cells chu naupang pum chhungah (abdominal cavity) a awm reng a.
- Stage IV: Cancer hi naupang pum leh pelvis piah lamah hmun dang, lung, thin, ruh leh thluak thlengin a darh tawh a ni.
- Stage V: Tumor hi kal pahnih (bilateral) ah a awm a. Hetiang stage-ah hian doctor-te chuan kal pahnih stage chu a hranin an en thin.
Wilms tumor hi engtin nge enkawl a nih?
Wilms-a tumor hi surgery leh chemotherapy hmanga enkawl a ni fo. A châng chuan radiation therapy pawh hman theih a ni.
Naupang low-risk tumor nei, cancer a darh lohna leh tumor chu a chhuah vek theihna hmunah chuan anmahni chauhin operation an nei thei mai thei. A châng chuan, operation hmain chemotherapy pek theih a ni a, chu chuan tumor chu a ti tlem thei a, chu chuan operation chu a him zawk a ni.
Chemotherapy hi thisen zam (IV) hmanga pek a ni fo. Hei hi outpatient basis emaw hospital setting-ah emaw tih theih a ni.
I fa hian chemotherapy emaw radiation therapy emaw a\angin side effect a nei thei a ni. Hetiang a nih chuan doctor hnenah hrilh ngei ang che. I fate side effects tihziaawmna tur leh damdawi i pek theih tur te pawh a awm.
Wilms-a tumor hi a veng thei ang em?
Wilms tumor thlen leh venna tur hian nangmah emaw i fa emaw hian engmah tih theih a awm lo tak zet a ni. Hei hi kan thunun theih loh thil a ni.
Wilms tumor vei tan chuan eng prognosis nge a awm?
Wilms’ tumor prognosis hi a tlangpuiin a tha ber a ni. A rah chhuah chu a tha hle tlangpui a, a bik takin doctor-in tumor chu a paih chhuak vek thei a, cancer chu taksa hmun dangah a darh lo a nih chuan a tha hle. Mahse, Wilms-a tumor hi ``a lo lang leh'' theihna chance tlemte a awm.
Wilms tumor hian thihna a thlen thei em?
Wilms tumor hi surgery, chemotherapy, leh/ emaw radiation therapy hmanga enkawl hlawhtling thei mah se,Hei hi cancer a la ni reng a ni. Chuvangin, thihna thlen thei a ni. Chuvang chuan hriat hmasak a, enkawl tan a pawimawh.
Wilms tumor hi engzat nge damchhuah?
Wilms tumor vei hmuhchhuah zinga 90% vel chu kum nga hnuah pawh an la dam tawh a ni. He rate hi cancer stage, tumor lian leh te, microscope (histology) hmanga cancer cell awm dan te a zirin a danglam deuh thei a ni. Naupang kum 2 hnuai lam chuan natna lo lang leh theihna an nei tlem zawk tih sawi thin a nih laiin, tunah chuan kum hi a hma aia factor a ni tawh lo.
Wilms tumor chungchangah hian engtikah nge ka doctor ka hmuh ang?
I fa chu Wilms-a tumor enkawl mek a nih chuan, ngaihtuahna emaw zawhna emaw i neih chuan doctor rawn rawh. A bik takin symptom thar i hmuh emaw, thil a na zual ang tih emaw a nih chuan hriattir nghal rawh.
I enkawl chhung hian i medical team chuan i fimkhur tur, zun kawng natna chhinchhiahna te chu an hrilh ang che. Chutiang a nih chuan emergency room-ah i kal a ngai mai thei.
Naupang chu a dam tha em tih enfiah nan a hun takah follow-up visit neih a ngai bawk ang. Doctor chuan naupang chu kidney specialist (nephrologist) emaw, urinary system specialist (urologist) emaw hnenah a refer thei bawk.
Wilms tumor enkawl hnuah engtin nge ka fa chu a hrisel theih nan ka puih theih ang?
I fain heng thilte hi a tih a pawimawh:
- I kal (kidney) a thawk tha thei tur khawpa tui in thin ang che.
- Damdawi aspirin, ibuprofen, leh naproxen te hman tlem. I fa doctor hnenah eng product nge i fa kal (kidney) tichhe lo ber tih sawipui rawh.
- I thisen sang chu a hun takah enfiah thin ang che.
Wilms tumor hi a na em?
Wilms-a tumor hi a chang chuan a na thei a, mahse a na reng reng lo.
Wilms-a tumor (nephroblastoma) leh neuroblastoma hi eng nge an danglamna?
Heng thumal pahnih hi a ri inang viau nachungin, cancer chi hnih, cell chi hrang hrang pahnih atanga intan an ni. Nephroblastoma hi kal cancer a ni. Neuroblastoma hi cancer a ni a, nerve cell atanga intan a ni. Adrenal glands-ah a intan tam ber a, mahse kal (kidney) pawh a rawn lut thei bawk. Cancer chi hnih hi naupangah a awm a, an pahnih hian pum chhungah lump angin an lang thei bawk. Chuvangin diagnosis dik tak neih a pawimawh hle.
I fa chu Wilms tumor a vei tih hmuhchhuah a nih chuan i doctor chuan naupang cancer enkawlna lama tui tak medical center pan turin a rawt mai thei. Wilms tumor hi a tlem hle nachungin, enkawl theih natna a ni. I fa chu clinical trial-ah pawh a tel thei bawk. Wilms tumor nei naupang tam tak chu he program-ah hian an inziak lut a ni. Wilms tumor enkawlna lama hmasawnna tam tak hi heng clinical trial te atanga lo chhuak a ni.
A pawimawh ber (Take-Home Message) .
Okay, chuti a nih chuan Wilms-a tumor chungchang hi kan sawi nasa hle a ni lawm ni? Hriat tur pawimawh tak chu i fa pum chhungah hian thil danglam tak tak, lump emaw, a hring emaw i hmuh chuan hlauthawng suh la, doctor pan nghal rawh.
- Wilms-a tumor hi naupang tê tête kal (kidney)-a lo awm ṭhin a ni.
- Hei hi a chhan dik tak hriat ni lo mah se, genetic influence engemaw zat a awm thei.
- A hmaa hmuhchhuah a nih a, uluk taka enkawl a nih chuan a dam theihna chance a sang zawk hle.
- Surgery, chemotherapy, a chang chuan radiation therapy te hi a enkawl dan ber a ni.
- Enkawlna kan neih zawh hnuah pawh doctor thupek uluk taka zawm a, a hun ruatah check-up neih a pawimawh hle.
Hlau suh. Tunlai hian Medical science hi a lo changkang hle a. A pawimawh ber chu i ngaihvenna leh i hmalak thuai hi a ni. I fa chu dam thuai turin duhsakna ka hlan e!
` Wilms tumor, nephroblastoma, naupan lai cancer, kal cancer, naupang hriselna, cancer symptoms, cancer enkawl dan











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