Kei te iti te maha o ngā toto toto mā i roto i tō tinana? Me ako tātou mō te Autoimmune Neutropenia (AIN)!

Kua whakaaro koe he aha tā tātou ake pūnaha ārai mate, i te kore e tiaki i a tātou, ka tīmata te whakaeke i ō tātou ake pūtau i ētahi wā? He āhua uaua rawa tēnei, engari he mārama te āhua, ko te Autoimmune Neutropenia (AIN) . Ko te mea ka tupu, ko tā tātou ake pūnaha ārai mate e whakaeke ana i tētahi momo toto ma tino nui i roto i tō tātou tinana, ko ngā 'neutrophils' te ingoa. Nō reira, me kōrero ngāwari tātou mō tēnei, i roto i tētahi huarahi e mārama ai koe.

Nā, he aha te Autoimmune Neutropenia (AIN)?

Ki te kī ngāwari, ko te 'Autoimmune Neutropenia' (AIN) he mate e pā ana ki te toto. Ko te mea e tupu ana i konei ko te pūnaha ārai mate, e tika ana kia tiaki i a tātou, ka whakaeke hē i ō tātou ake toto ma e kiia nei ko ngā 'neutrophils'. Whakaarohia tēnei, pērā i te ope taua e tiaki ana i tō tātou whenua e whakaeke hē ana i ō tātou ake iwi.

He aha ngā 'Neutrophils'?

He wāhanga tino nui ngā neutrophil o tō tātou pūnaha ārai mate. He rite rātou ki ngā hōia ririki i roto i ō tātou tinana. Ko tā rātou mahi matua he kimi me te whakangaro i ngā mea kino e uru ana ki te tinana, pērā i ngā huakita me ngā harore e puta ai ngā mate. Nō reira, i roto i te take o te 'Autoimmune Neutropenia', ka whakangaromia e tō tātou ake pūnaha ārai mate ēnei pūtau 'neutrophil' nui, nō reira ka heke te maha o ngā 'neutrophil' i roto i te toto i raro i ngā taumata noa.

E rua ngā momo matua o te AIN:

1. Te Mate Pūnaha Mate Pūnaha Ārai Mate Tuatahi (AIN): Ka kitea nuitia tēnei i roto i ngā pēpi me ngā tamariki nohinohi . Ko te mea e tupu ana i konei ko te hekenga o te maha o ngā 'mate pūnaha kore' me te kore he take kē atu. Engari ko te rongo pai ko te nuinga o te wā ka ea tēnei mate i roto i ētahi tau.

2. Te Mate Pūnaha Ārai Mate Tuarua (AIN): He nui ake te kitea o tēnei i roto i ngā tamariki pakeke me ngā pakeke . I konei, ko te iti o te maha o ngā neutrophils ka puta mai i tētahi atu mate hauora. Hei tauira, ka puta mai i tētahi mate pāwera, i tētahi atu mate toto, i tētahi atu mate pūnaha ārai mate rānei (he mate e whakaekehia ai e te pūnaha ārai mate tōna ake tinana). He mate mau tonu tēnei mate AIN tuarua.

Kia pēhea te iti o te maha o ngā neutrophils e kiia nei ko te neutropenia?

Ko te Neutropenia Ā-tinana he momo noa iho o te mate whānui e kiia nei ko te Neutropenia. Ka whakarōpūtia te Neutropenia ki te ngawari, ki te āhua waenga, ki te kino rānei, i runga i te maha o ngā neutrophils i ia microliter (microL) o te toto.

• Neutropenia Ngāwari: 1,000 – 1,500 neutrophils ia microL.
• Neutropenia Waenga: 500 – 1,000 neutrophils ia microL.
• Neutropenia kino: Ko ngā neutropenia he iti iho i te 500 i te microL.

Ko te mea nui ko te whakaū i ēnei uara e te tākuta. Mena he ruarua āu mō tēnei, he mea tino nui kia rapu tohutohu hauora.

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He aha te pānga o te AIN ki tōku tinana?

Ka rerekē pea te pānga o te AIN ki a koe i ia tangata, i ia tangata. He maha ngā āhuatanga e whakawhirinaki ana ki tēnei, nō reira he pai ake te kōrero ki tō tākuta mō tēnei. Ki te tino heke te maha o ngā neutrophils, ka nui ake te tūponotanga ka pāngia koe e ngā mate . I ētahi wā ka mōrearea te ora o ēnei mate, inā koa ki te kore koe e tere te rapu awhina hauora.

Heoi, i ētahi wā, ka taea e te neutropenia ā-tinana te whakaputa i ngā mate ngawari noa iho. Kāore rānei e kitea he tohu. Koia te mea nui kia mahi tahi me te tākuta kia kitea ai te take o tō neutropenia. I runga i te take, ka taea e tō tākuta te aroturuki i tō āhua me te āwhina i a koe ki te whakahaere i te mate.

Ko wai ka pāngia e te Autoimmune Neutropenia (AIN)?

• AIN Matua: Ka pāngia ngā pēpi me ngā tamariki nohinohi e tēnei mate. I te nuinga o te wā ka kitea i te 8 marama te pakeke.
• AIN Tuarua: He maha ngā wā ka puta tēnei me tētahi atu mate pūnaha ārai mate, pērā i te lupus, te rumatiki rheumatoid rānei. Ko ngā tamariki he AIN tuarua ka kitea i te nuinga o te wā i te 10 tau te pakeke. Ko ngā pakeke he AIN ka kitea i waenga i te 40 me te 60 tau te pakeke.

He pēhea te noa o te neutropenia ā-pūnaha ārai mate?

He tino onge te mate AIN tuatahi. Kotahi anake i roto i te 100,000 tamariki kei raro iho i te 10 tau te pakeke ka pāngia. Nō reira, ka kite koe i tōna onge.

He aha ngā tohu o te Autoimmune Neutropenia?

Kāore te Autoimmune Neutropenia e puta tonu mai i ngā tohu nui. Heoi, i ētahi wā ka kite pea koe i ngā tohu o te mate. Hei tauira:

• Ngā mate taringa: Koinei tētahi o ngā tohu tino kitea. Whakaarohia kei te mamae tonu te taringa o tāu tamaiti, ā, ina haere koe ki te tākuta, ka kī mai rātou he mate taringa anō tēnei.
• Ngā mate manawa: Te makariri pinepine, te maremare, me te kirika.
• Ngā mate waha: Ngā mate pēnei i te mate pukupuku me te mate kapia.
• Ngā mate kiri.
• Pūngāwerewere.
• Te mate kiriuhi.
• Ngā mate urutā o te ara mimi (UTI).
• Sepsis: He mate tino kino tēnei, he mate morearea hoki.

He ngawari noa iho ngā mate e pā ana ki te AIN tuatahi, engari he nui ake te kitea o ngā mate kino pērā i te niumōnia, te meningitis, me te sepsis i roto i te AIN tuarua.

He aha te take o te neutropenia ā-tinana?

Ka whakarōpūtia te AIN hei tuatahi, hei tuarua rānei, i runga i te pūtake o te iti o ngā taumata neutrophil.

Te Mate Pūnaha Ārai Mate Pūnaha Tuatahi (AI Matua)

I roto i te AIN tuatahi, ka aro atu ngā paturopi ki ngā neutrophils, ā, ka whakangaro i aua paturopi. He momo pūmua ngā paturopi i roto i tō tātou pūnaha ārai mate. Ko tā rātou mahi noa he whakangaro i ngā matū kino, pērā i ngā huaketo me ngā huakita, e uru ana ki te tinana. Engari i tēnei wā, kāore anō kia tino mōhio ngā kairangahau he aha i whakaeke ai ā tātou ake paturopi i ēnei neutrophils.

Te Mate Pūnaha Ārai Mate Tuarua (AI Tuarua)

I roto i te AIN tuarua, ka whakaitihia te maha o ngā neutrophils nā tētahi atu take, āhuatanga rānei. Mā tēnei ka whakangaromia e te pūnaha ārai mate ngā neutrophils.

Ko ētahi o ngā mea ka puta ai tēnei:

• Ētahi atu mate pūnaha ārai mate: Ko ētahi tauira ko te rumatiki rheumatoid, te lupus, me te anemia hemolytic pūnaha ārai mate.
• Matepukupuku: Hei tauira, ko te 'matepukupuku lymphocyte granular nui'.
• Ngā mate urutā: Ngā mate urutā pēnei i te 'HIV', te 'Parvovirus', te 'hepatitis B'.
• Ngā pukupuku: Pērā i te 'pukupuku Wilms' me te 'mate a Hodgkin'.
• Ngā mate pūnaha io: Hei tauira, te sclerosis maha.
• Ngā whakawhitinga whatukuhu, wheua rānei.
• Ngā rongoā motuhake: Tērā pea ko ētahi rongoā chemotherapy e hoatu ana mō te mate pukupuku.

Me pēhea te tātaritanga o te Autoimmune Neutropenia? (Tauātanga)

Ina pāngia koe e te kirika, e te mate pāwera rānei, tera pea ka kitea e tō tākuta he iti te maha o ō neutrophil i te wā e tirotirohia ana te take. He uaua pea te tautuhi i te AIN, nā te mea he maha ngā take pea. Tērā pea ka tautuhia e tō tākuta te AIN i muri i te whakakore i ētahi atu āhuatanga e raru ai te iti o tō maha o ngā neutrophil.

Hei tātaritanga, hei aroturuki rānei i te 'Autoimmune Neutropenia', ka whakahaerehia pea e tō tākuta ēnei whakamātautau e whai ake nei:

• Tatau toto katoa (CBC): Ka taea e te CBC te tirotiro i te maha o ngā neutrophils i roto i tō toto. Nā te mea ka rerekē pea ēnei taumata, ka mahi pinepine tō tākuta i te neke atu i te kotahi CBC hei whakaū i te neutropenia me te aroturuki i ō taumata neutrophil. Ka taea hoki e ngā CBC auau te āwhina ki te whakatau mena he roa tō AIN.
• Te whakamātautau toto ā-taha: Ka tirohia he tauira toto i raro i te karuārai hei tirotiro i te āhua me te āhua o ngā neutrophils. He āwhina anō hoki tēnei ki te tautuhi mate.
• Ngā whakamātautau huaora B12, folate, me te parahi: Ka taea e ēnei whakamātautau te tirotiro mō ngā ngoikoretanga o ēnei matūkai. E hiahiatia ana ēnei e te tinana hei hanga i ngā neutrophils.
• Ngā whakamātautau mahi ate: Ka taea hoki e ēnei te tirotiro i te mahi ate me te tirotiro mēnā he mate hepatitis huaketo.
• Te HIV me ētahi atu rangahau huaketo: Ka taea hoki e ngā mate huaketo pēnei i te HIV te whakaheke i te nui o ngā toto toto mā.
• Te whakamātautau rere toto: He whakamātautau taiwhanga tēnei e tirotiro ana i ngā pūtau mō ngā tohu o te mate. Ka whakamahia hei whakatau mēnā he mate pūnaha ārai mate te take o te neutropenia.
• Whakaahua: Mena kei te whakapaetia kei te puta te AIN i te mate pukupuku pēnei i te lymphoma, ka taea te whakahaere i te matawai MRI, CT rānei.
• Te tango i te hinu wheua me te koiora: I konei, ka tangohia e te tākuta he tauira iti o te hinu wheua ka tirohia mō ngā tohu o te mate. Ka āwhina tēnei ki te whakatau mēnā ko te neutropenia te take o te mate pukupuku toto, pērā i te leukemia.

Tērā pea ka tonoa e tō tākuta he whakamātautau toto hei tirotiro mō ngā paturopi i roto i ō toto e whakaeke ana i ngā neutrophils. Ko ngā whakamātautau tino noa ko te I-GIFT (Whakamātautau ārai mate granulocyte ā-kore) me te GAT (Whakamātautau whakaahuru granulocyte).

Engari, kāore i te pono tonu ēnei whakamātautau ki te kite i te AIN. I runga i te pūtake o tō neutropenia me te wā o te whakamātautau, kāore pea ēnei whakamātautau e kite i ngā paturopi, e puta rānei he hua teka-pai. Ko te hua teka-pai ko te whakaatu a te whakamātautau kei te kitea ngā paturopi i te mea kāore.

Mena kei te whakapae te tākuta he mate motuhake te take o te neutropenia, ka taea e ia te tono i ētahi atu whakamātautau.

Me pēhea te rongoā i te Autoimmune Neutropenia?

Ko te maimoatanga e whakawhirinaki ana ki te kaha o tō mate. Hei tauira, ko te pēpi he kore tohu te neutropenia, me whiwhi pea i ngā CBC me ngā tau neutrophil auau, engari kāore pea e hiahiatia he maimoatanga tonu. Mena he maha ngā mate pāwera o tō pēpi, ka tohua pea e tō tākuta he paturopi ārai mate hei ārai i ngā mate. Ko te tikanga ka hoatu ngā paturopi hei rongoā i ngā mate, engari ka hoatu ēnei paturopi ārai mate hei ārai i ngā mate kei puta.

Mō te tangata whai AIN tuarua, ka rongoā te tākuta i te mate pūtake e hua ai te iti o ngā taumata neutrophil. Tērā pea ka tohua e rātou:

• Te matū whakaoho koroni granulocyte (G-CSF): Koinei te maimoatanga matua mō ngā take kino o te neutropenia. Ka āwhina i te tinana ki te hanga i ngā neutrophils. Ka taea hoki e te G-CSF te ārai i ngā mate pāwera e pā ana ki te AIN tuatahi.
• Corticosteroids: Ko ngā corticosteroids, pērā i te prednisone, ka pehi i te urupare a te pūnaha ārai mate o tō tinana, ka whakaiti i te maha o ngā antibodies e whakaeke ana i ngā neutrophils.
• Ētahi atu maimoatanga: Kua whakamahia hoki ētahi atu rongoā pēnei i te IVIG, rituximab, me te alemtuzumab i roto i ngā tūroro tino mate me te neutropenia autoimmune kino.

Ka taea te ārai i te Autoimmune Neutropenia?

Kāore e taea te ārai i te AIN Tuatahi, te AIN Tuarua rānei. Heoi, ka taea e koe te ārai i ngā raruraru e pā ana ki te 'Autoimmune Neutropenia', arā, te whanaketanga o ngā mate. Hei mahi i tēnei, me mahi koe i ngā mahi e tika ana hei tiaki i a koe mai i ngā mate. Hei tauira, karohia ngā wāhi e kī ana te tangata, horoia ō ringaringa i ngā wā katoa, me te noho tawhiti atu i te hunga mate.

He aha te momo āmua ka taea e te tangata whai Autoimmune Neutropenia te tumanako atu?

Ko te AIN tuatahi ka memeha noa iho . Tata ki te 95% o ngā tamariki whai AIN ka hoki anō ō rātou taumata neutrophil ki te āhua noa i te rua ki te toru tau te pakeke. Tata ki te katoa o ngā tamariki whai AIN tuatahi ka ora katoa i te 11 tau te pakeke. He tino whakamarie tēnei, kāore?

I ētahi atu wā, e kiia ana ko te AIN tuarua, ka whakawhirinaki tō whakaoranga ki ētahi āhuatanga, inā koa ko te mate taketake i puta ai tō neutropenia. Mā te rongoā i taua mate me te ārai i ngā mate ka āwhina i te whakahoki i tō tau neutrophil ki te noho noa.

Āhea ahau me rapu tohutohu hauora?

Mena he nui te mate pūkahukahu ā-tinana kei a koe, ā, ka pāngia koe e te kirika, me toro atu ki te tākuta tonu . I ētahi wā, kua tohua pea e tō tākuta he rongoā paturopi hei tango mēnā ka pāngia koe e te kirika. I te nuinga o te wā, me rongoa koe ki te hōhipera.

Mena he mate pūkahukahu kino tōu, he roa hoki te wā, ka whakamāramahia e tō tākuta ngā tohumate me mōhio koe ki ēnei, me ngā mea ka taea e koe te mahi hei ārai i ngā raruraru.

Kia maumahara: Ki te mea kua tāpaetia koe, tāu tamaiti rānei, ki te mate AIN, kōrero ki tō tākuta mō tōna pānga ki a koe. Ahakoa he rerekē ngā tohu me ngā take, ko te rongo pai ko ngā maimoatanga pēnei i te G-CSF he tino whai hua ki te whakapiki i ngā taumata neutrophil.

Mena kei a tāu tamaiti te AIN, me whakamātau toto i ia wā, i ia wā, kia rite ki ngā tohutohu a tō tākuta. Kia tūpato ki ngā tohu o te mate, ā, me rapu wawe tonu i te maimoatanga mēnā ka kite koe i tētahi, hei ārai i ngā raruraru ka pā mai.

Whakarāpopototanga (Karere hei tango ki te kāinga)

Āe, ko tāku tumanako kua mārama ake koe ki te 'Autoimmune Neutropenia' (AIN) i kōrerohia e tātou.

• Ko te AIN he āhuatanga e whakangaro ai tō tātou ake pūnaha ārai mate i ō tātou toto mā e kiia nei ko ngā 'neutrophils'.
• Ka pā tēnei ki ngā tamariki nohinohi (AIN Tuatahi) me ngā pakeke rānei (AIN Tuarua). He maha ngā wā ka memeha haere te AIN Tuatahi i roto i ngā tamariki nohinohi.
• Ko te mōrearea matua ko ngā mate urutā pinepine.
• He whakamātautau toto me ētahi atu whakamātautau hei tātaritanga.
• Kei roto i te maimoatanga te tirotiro haere, ngā rongoā ārai-pēhanga, te G-CSF, me ngā corticosteroids.
• Ko te mea nui kia kaua e mataku, kaua hoki e mataku, me rapu tohutohu hauora mēnā kei a koe, kei tāu tamaiti rānei ēnei tohu. Mēnā ka kitea wawetia, ka whakahaerea hoki, ka taea e koe te ora hauora ahakoa kei a koe te AIN.

Mena he pātai anō āu mō tēnei, me kōrero ki tō tākuta. Ko rātou te hunga ka taea te tuku tohutohu pai rawa atu ki a koe.