He wā poto te manawa, he āhua rerekē rānei kei roto i tō uma? Tērā pea he teitei te pēhanga i roto i ngā uaua toto i roto i ō pukahukahu. He āhuatanga motuhake tēnei e kiia nei ko te (Chronic Thromboembolic Pulmonary Hypertension), (CTEPH) rānei. Kaua e manukanuka, ka kōrerohia tēnei i roto i te huarahi māmā noa iho, kia mārama ai koe.
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He aha tēnei (CTEPH)? Kia mārama tātou!
He whakarāpopototanga noa iho, ko te CTEPH he pikinga rerekē o te toto toto i roto i ngā oko toto iti o ngā pukahukahu. He rite ki te pēhanga i roto i te paipa wai. Engari ko te take matua mō tēnei he toto toto kua pā ki roto i ō pukahukahu i mua (e kiia ana tēnei he Pulmonary Embolism) ā, kāore te toto toto e memeha tika . Koinā te wā ka piki ake ai tēnei pēhanga.
Ko wai te hunga ka nui ake te tūponotanga ka pāngia e te CTEPH?
He mea tino nui tēnei. Ka puta noa te CTEPH i roto i te hunga kua pāngia e te pulmonary embolism i mua . Mena he nui te toto i roto i ō pukahukahu engari kāore he toto totoka, ehara pea i te CTEPH, engari he āhuatanga rerekē. Nō reira, he mea nui kia mārama ki tēnei rerekētanga.
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Check Availability →He pēhea te noa o tēnei āhuatanga?
He mate tino onge te CTEPH. Hei tauira, i roto i tētahi whenua pērā i te Hononga o Amerika, tata ki te 5,000 noa iho ngā kēhi hou e pūrongohia ana i ia tau. Heoi, nā te mea kāore i te tino tautuhia i ētahi wā, tera pea ka nui ake te maha. Nō reira, he mea tino nui kia mōhio ki ngā tohu.
He aha te pānga o te CTEPH ki tō hauora?
Ina piki te pēhanga i roto i ō pūkahukahu, inā koa i roto i te take o te CTEPH, ka nui te pēhanga o te taha matau o tō ngākau . Whakaarohia, me kaha ake te mahi a tō ngākau ki te pupuhi toto ki ō pūkahukahu. Ko te mea ka tupu, ka mau ētahi o ngā toto kāore i te nui te hāora ki roto i tō ngākau, ā, ka roa te wā ka tae atu ki ō pūkahukahu. Ka taea e tēnei te whakaiti i te taumata hāora o tō tinana. He mate kino rawa tēnei, kāore?
He aha i puta ai tēnei (CTEPH)? He aha ngā take?
Ko te take matua mō tēnei, kāore e memeha tika ngā toto toto e puta mai ana i roto i ngā oko toto iti o ngā pukahukahu. Ina tupu tēnei , ka puta he kiko rite ki te koha ki te wāhi i puta ai ngā koha. Ka whaiti ngā oko toto nā tēnei koha, pērā i te paipa wai e purua ana. I te piki haere o tēnei whaiti, ka piki ake hoki te pēhanga.
He aha ngā āhuatanga mōrearea e pā ana ki te whanaketanga o te CTEPH?
Tērā ētahi āhuatanga mōrearea ka whai wāhi ki te whanaketanga o te (CTEPH). Me titiro tātou ki ēnei āhuatanga:
- He momo toto anō ō rātou ehara i te momo O.
- He mate pāwera kei roto i ngā wheua (Osteomyelitis).
- Ētahi momo mate pukupuku.
- Hei tauira, ko ngā mate puku mau tonu, ko ngā āhuatanga pēnei i te (Inflammatory Bowel Disease).
- He wahine. (He nui ake te tūponotanga o ngā wāhine ki te pāngia e tēnei mate i ngā tāne.)
- Te mate o te kiko o te ngākau nā te taputapu whakateretere.
- Kei a koe, kei tētahi rānei o tō whānau he hītori o ngā mate toto totoka, pērā i te Antiphospholipid Syndrome.
- I tangohia te whēkau i mua (Splenectomy).
- Te tango i te rongoā whakakapinga homoni tairoi.
Ehara i te mea ka pāngia te katoa e ēnei mea katoa, engari kua tautuhia hei āhuatanga mōrearea.
He aha ngā tohu o te (CTEPH)?
Tērā pea ka pāngia te tangata whai CTEPH e ngā tohu pēnei i:
- Te mamae o te uma, te kikī rānei .
- Te mare toto (he mea onge tēnei).
- Te tae kikorangi o ngā pito o ngā maihao me ngā matimati (Cyanosis).
- Te pōuriuri .
- Te ngoikore o te ngākau.
- Te tino ngenge (‘Te ngenge nui’) .
- Mēnā kei te pā te uma, ka kiia tēnei ko te "Patpitations o te Manawa".
- Te uaua ki te manawa , inā koa i te wā e mahi ana i tetahi mea, e hikoi ana rānei.
- Te pupuhi o ngā waewae, nā te nui o te wai i roto i te tinana (edema).
Kaua e whakaaro kei a koe te CTEPH nā te mea kotahi, e rua rānei o ēnei tohu kei a koe. Engari, ki te mau tonu ēnei tohu, he pai ake te toro atu ki te tākuta.
Me pēhea te tātaritanga o tēnei mate (CTEPH)?
Ina kite koe i tētahi tākuta, ka whakahaerehia pea e ia ētahi whakamātautau tuatahi hei tirotiro mō te CTEPH, pēnei i:
- He whakamātautau e tirotiro ana i te hauhautanga me te rere o te toto ki ngā pukahukahu ((Matawai hauhautanga-whakaputa toto pukahukahu - matawai V/Q)).
- Ko te "Pulmonary Angiogram" he whakamātautau e tirotiro ana mō ngā toto totoka, ngā toto whāiti rānei i roto i ngā oko toto o ngā pukahukahu.
- Ngā Whakamātautau Mahi a te Pūkahukahu.
- He rite te Transthoracic Echocardiogram (TTE) ki te matawai ultrasound o te ngākau.
Whai muri i ēnei whakamātautau tuatahi, me whai atu pea ētahi atu whakamātautau hei whakaū i te mate CTEPH me te whakatau i tōna kaha. Kei roto pea i ēnei:
- Ko te Tātaritanga o te Ngākau Matau he whakamātautau e ine ana i te pēhanga mā te whakauru i tētahi ngongo iti ki te taha matau o te ngākau.
- Tirohia ngā uaua i roto i ngā pukahukahu mā te whakamahi i ngā tikanga whakaahua matatau pērā i te CT Pulmonary Angiography (CTPA) te Digital Subtraction Angiography rānei.
- He matawai MRI.
- He "Whakamātautau Taumahatanga Whakakorikori Tinana" e tirotiro ana i te mahi a te ngākau i te wā e whakakorikori tinana ana.
Mā ēnei whakamātautau ka taea e ngā tākuta te whakatau tika mēnā kei a koe te CTEPH me tōna taumata.
He aha ngā maimoatanga mō te (CTEPH)?
Ko te maimoatanga mō te CTEPH he pokanga, he tikanga rite rānei. E rua ngā kōwhiringa matua:
1. Te tango i te uaua o te pūkahukahu : He pokanga tuwhera tēnei. I roto i tēnei tikanga, ka tangohia ngā toto toto tawhito me ngā kiko whara e piri ana ki roto i ngā uaua o ngā pūkahukahu mā te pokanga. Ka mahia tēnei hei ngana ki te whakahoki mai i te rere o te toto ki ngā pūkahukahu.
2. (Angioplasty Pūwero Pūkahukahu)'I roto i tēnei, ka tāpirihia he poihau iti ki te pito o te ngongo roa (catheter), ka tukuna ki roto i te oko toto whaiti i roto i ngā pukahukahu. Ka pupuhihia te poihau hei pana i te kiko whara ki tahaki, ka whānui ake anō te oko toto.
Ko te whiriwhiri i tētahi o ēnei tikanga e rua e ahu mai ana i ngā āhuatanga maha, pērā i te āhua o te tūroro me te wāhi o te toto totoka.
He kōwhiringa maimoatanga anō kei reira?
Ae, kāore pea ētahi tāngata e taea te mahi i tēnei pokanga. Mō ēnei tāngata, mō te hunga rānei e pēhia tonutia ana ō rātou pukahukahu i muri i te pokanga, ka taea te hoatu he pire e kiia nei ko (Riociguat) . He rongoā tēnei e hoatu ana mō te toto toto tiketike o te pūkahukahu. Ka āwhina tēnei ki te whakamamae i ngā tohu.
Ka taea te ārai i te CTEPH?
He raruraru te CTEPH o ētahi atu mate hauora. Ko ētahi mea kāore e taea e tātou te whakahaere. Engari ko te mea nui rawa atu ka taea e koe ko te tiaki pai i ō pukahukahu . Arā, he mea tino nui te whakamutu i te kai hikareti mēnā kei te kai hikareti koe, me te karo i te tupeka.
He aha te tirohanga mō ngā tūroro e pāngia ana e te CTEPH?
Koinei ngā rongo pai rawa atu! Ka taea e te Pulmonary Endarterectomy me te Pulmonary Balloon Angioplasty te whakaora katoa i te CTEPH . He maha ngā tāngata e whiwhi ana i ēnei maimoatanga ka kite i ngā hua tino pai.
Heoi, ahakoa ēnei hua pai, tera pea ētahi tūroro e pāngia e te mamae hinengaro, te manukanuka, me te pouri. Tērā pea he pono tēnei mō te hunga kāore e tika ana kia whiwhi i ngā maimoatanga whakaora kua whakahuatia ake nei. Mēnā kei te pāngia koe e tētahi o ēnei mamae hinengaro, kōrero ki tō tākuta. Ka taea e rātou te whakarongo ki ō āwangawanga, me te taunaki i ngā maimoatanga hei āwhina i a koe kia pai ake te ahua.
He aha ngā mea nui hei mōhio māu ina noho tahi ana koe me te (CTEPH)?
- Tērā pea me tango e koe ngā rongoā whakaiti toto mō te toenga o tō oranga .
- Mena kei te tango koe i tētahi rongoā pēnei i te Warfarin, me whakawhāiti pea koe i ētahi kai (pēnei i te pīni soya me te broccoli, he nui te huaora K). Pātai atu ki tō tākuta mō tēnei.
- Mā te whakakori tinana māmā , pērā i te hikoi, ka taea e te tini o te tangata te whakahoki mai i te kaha me te noho hauora. Tērā pea ka tūtohu tō tākuta i tētahi kaupapa whakakori tinana e tirotirohia ana (te whakaora i ngā pūkahukahu).
Hei whakamutunga, kia mahara ki tēnei.
Ko te Chromboembolic Pulmonary Hypertension (CTEPH) he mate onge e piki ake ai te toto toto i roto i ngā oko toto o ngā pukahukahu, engari he mate ka taea te rongoā mēnā ka kitea wawe, ā, ka rongoatia tika . Mēnā kei a koe tētahi o ēnei tohu, kaua e mangere ki te rapu tohutohu hauora. Kia maumahara, mā te maimoatanga tika, ka taea e te nuinga o te tangata te ora pai. Nō reira kaua e mataku. Me whai i ngā tohutohu a tō tākuta, ā, ka taea e koe te ora wawe!
CTEPH, Te Toto Nui o te Pūkahukahu, Ngā Totoka Toto, Te Uauatanga o te Manawa, Te Mate Manawa, Te Pukupuku Pūkahukahu, Te Toto Nui o te Pūkahukahu
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