Kei te ngenge tonu koe? Kei te tino matewai koe? Me mimi pinepine rānei koe? Mena he toto toto tiketike tōu, me āwangawanga koe mō tēnei. Tērā pea ehara tēnei i te mea ngāwari pēnei i tā tātou e whakaaro nei. I tēnei rā ka kōrero tātou mō tētahi āhuatanga e kiia nei ko te Primary Aldosteronism , e mōhiotia ana hoki ko te Conn's Syndrome e ētahi.
He aha te Aldosteronism Tuatahi?
Ki te kī ngāwari, ko te aldosteronism tuatahi he āhuatanga e puta mai ana i te nui rawa o te homoni e whakaputaina ana e ō repe adrenal e kiia nei ko te aldosterone . Whakaarohia pēnei: ko ngā repe adrenal he repe iti e rua, he rite ki ngā taupoki iti i runga i ō whatukuhu. Engari ko ngā homoni e whakaputaina ana e rātou te whakahaere i ngā mahi nui o tō tinana.
He homoni steroid te Aldosterone . Ko tana mahi matua he whakahaere i te nui o te konutai (te tote e kainga ana e tātou) me te pāhare pāporo i roto i ō tātou toto. Ka āwhina hoki ia ki te whakahaere i te nui o te wai i roto i te tinana, te nui o te toto, me te toto toto.
Whakaarohia, he aha te mea ka puta mēnā ka nui rawa te homoni aldosterone? Koinei te wā ka tīmata ai ngā raruraru. Ko te toto toto tiketike (hypertension) me te pāhare pākawa iti o te toto (hypokalemia) ngā tohu matua e rua o te aldosteronism tuatahi. Ki te kore tēnei āhuatanga e rongoatia tika, ka puta pea ngā raruraru nui pērā i te mate ngakau me te ngoikore o te whatukuhu . Heoi, ki te kitea wawetia, ā, ka rongoatia tika, ka taea te whakahaere pai i tēnei āhuatanga.
He pēhea te noa o tēnei āhuatanga?
I mua, i kiia te aldosteronism tuatahi he mate onge. Engari kua rerekē te āhua i nāianei. Ka kitea i waenga i te 5% me te 10% o ngā pakeke he toto toto tiketike. He paku noa ake te kitea i roto i ngā wāhine. I te nuinga o te wā, ka kitea tēnei mate i te hunga kei roto i ō rātou tau 30 me te 40.
He aha ngā tohu o te Aldosteronism Tuatahi?
He maha ngā wā, he toto toto tiketike, he toto pāhare pāporo iti hoki te hunga whai mate pēnei. Ka piki ake te mōrearea o te mate ngakau me te whiu mēnā kāore e whakahaeretia te toto toto tiketike. Ka taea hoki e ngā taumata pāhare pāporo iti te whakararu i te ngakau o te tangata (arrhythmias) .
Hei tāpiri atu ki ēnei, ka kitea pea ētahi atu tohu:
- Te ngenge tonu (Te ngenge): Ahakoa te moe pai, tera pea ka ngenge tonu koe.
- Te matewai nui:Ahakoa te nui o te wai e inumia ana e au, e ahua ana kāore anō kia ranea.
- Te mimi pinepine: Me haere ki te wharepaku i ngā wā maha atu i mua.
- Mamae upoko: Tērā pea ka pāngia koe e te mamae upoko kino.
- Te mamae me te māuiui o ngā uaua: Tērā pea ka rongo koe i te mea kei te takahurihuri ētahi wahi uaua i roto i ō waewae me ō ringa.
- Ngoikoretanga o te uaua: Tērā pea ka ngoikore koe, ā, ka uaua ki te hiki i ngā taumaha.
- Te tirohanga pōuri: I ētahi wā ka pōuri te tirohanga.
Mena kei a koe tētahi, ētahi rānei o ēnei tohu, inā koa me te toto toto tiketike, he mea pai kia toro atu ki te tākuta mō ētahi tohutohu.
He aha ngā take o te Aldosteronism Tuatahi?
E ai ki tā mātou i kōrero ai i mua ake nei, ko te take o tēnei mate ko te nui rawa o te homoni aldosterone e whakaputaina ana e ngā repe adrenal. He maha ngā take e nui rawa ai te whakaputanga o tēnei homoni:
- Ngā pukupuku pai o tētahi, o ngā repe adrenal rānei e rua: Ehara ēnei i te matepukupuku, engari ka taea e rātou te whakanui ake i te hanga homoni.
- Ngā āhuatanga tuku iho: Hei tauira, ngā āhuatanga pēnei i te hyperplasia adrenal whānau .
- Matepukupuku repeure: He mate tino onge tēnei.
He rite tonu tēnei ki te aldosteronism tuarua?
Kāo. Ko te aldosteronism tuatahi ko te pikinga o te aldosterone nā te raruraru o ngā repe adrenal. Engari i ētahi wā, ka puta he nui rawa o te homoni aldosterone i tētahi atu mate. Ka kiia tēnei mate e ngā tākuta ko te aldosteronism tuarua . Ko ētahi o ngā mate ka puta ai tēnei ko:
- Mate ate
- Te whakatōtōtanga o te uaua whatukuhu: He whaiti tēnei o ngā uaua e kawe ana i te toto ki ngā whatukuhu.
- Te ngoikore o te ngākau
- Ētahi momo mate pukupuku whatukuhu
- Te haputanga
Ko wai kei te nui ake te mōrearea ki te whakawhanake i te Aldosteronism Tuatahi?
Ka taea e te tangata katoa te pāngia e tēnei mate. Heoi, he nui ake te mōrearea o ētahi tāngata ki te pāngia e tēnei mate. Ko ētahi o ēnei ko:
- Ngā tāngata he iti te pāhare pāporo i roto i te toto.
- Ngā tāngata i pāngia e te toto toto tiketike i mua i te 30 tau te pakeke.
- Ko te hunga e tango ana i ngā rongoā e toru, neke atu rānei, hei whakahaere i te toto toto tiketike.
- Ngā tāngata whai pukupuku repe adrenal.
He aha ngā raruraru ka puta mai i tēnei āhuatanga?
Ki te kore koe e rongoā i te aldosteronism tuatahi, ka piki ake tō toto toto ki ngā taumata morearea. Ka taea hoki e ia te whakararu i te taurite o ngā electrolytes o tō tinana (ngā kohuke e āwhina ana ki te pupuri i te taurite wai i roto i te tinana).
Ka whakanui ake te kore taurite o ngā electrolyte me te toto toto tiketike mō te wā roa i te mōrearea o ngā raruraru nui. Hei tauira:
- Te whakaeke ngakau , te ngoikore rānei o te ngakau
- Te manawa pāpaku koretake
- Te ngoikore o te whatukuhu
- Whiu
- Pararutiki rangitahi
He mea nui: Ahakoa te āhua kino o ēnei raruraru, he maha o ēnei ka taea te ārai mēnā ka kitea wawe te mate, ā, ka rongoatia tika. Nō reira, he mea tino nui kia rapu tohutohu hauora tonu mēnā ka puta ngā tohu.
Me pēhea te tautuhi i te Aldosteronism Tuatahi?
Ko te nuinga o ngā whakamātautau toto ka whakamahia e ngā tākuta hei tātaritanga i tēnei mate. E rapu ana ēnei whakamātautau i:
- Ko ngā taumata o ngā homoni pēnei i te aldosterone me te renin i roto i tō toto.
- Ngā taumata irahiko, tae atu ki te konutai me te pāhare pāporo.
Tērā pea e hiahiatia ana ētahi whakamātautau toto hei whakatau tika i te mate. Ka pā pea ētahi rongoā mō te toto toto tiketike ki ngā hua o ngā whakamātautau toto. Nō reira, ka taea e tō tākuta te whakarerekē i tō rongoā kia tika ai ngā whakamātautau.
He aha atu ngā whakamātautau ka mahia e koe?
Tērā pea ka tūtohu tō tākuta i ētahi atu whakamātautau hei tirotiro i ngā pukupuku adrenal, pēnei i:
- Matawai CT (Tomography Rorohiko - ngā matawai CT): Ka whakamahia e tēnei he hihi-X hei tango pikitia o roto o te tinana.
- Matawai MRI (Whakaahua Āhua Aukume - MRI): Ka whakamahia ngā ngaru reo irirangi me te papa aukume kaha hei tirotiro i te roto o te tinana.
Ka taea e ēnei whakamātautau te kite mārama i te rahi, te āhua, me te aroaro o ngā āhuatanga hē o ngā repe adrenal.
He aha ngā maimoatanga pai rawa atu mō te Aldosteronism Tuatahi?
Ko ngā rongoā me/ranei ko te pokanga te tikanga e whakamahia ana hei rongoā mō tēnei mate.
Rongoā
Mena ka nui rawa te aldosterone e whakaputaina ana e ngā repe adrenal e rua, ka tohua e ngā tākuta he rongoā pēnei i te Spironolactone (Aldactone®) me te Eplerenone (Inspra®) rānei. Ka mahi ēnei rongoā mā te aukati i te mahi a te homoni aldosterone.
Pokanga
Mena kotahi anake o ngā repe adrenal e whakaputa ana i te nui rawa o te aldosterone, ka taea te mahi pokanga hei tango i taua repe (adrenalectomy) . I roto i ēnei āhuatanga, ka tūtohu pea ngā tākuta kia pokangahia.
I muri i te pokanga, me tango pea koe i te rongoā kia hoki rā anō tō toto ki te āhua noa. Mā tō tākuta e whakamārama ngā mea hei tumanakohia i runga i tō āhua.
Ka taea te ārai i tēnei āhuatanga?
Engari, kāore he huarahi i tēnei wā hei ārai katoa i tēnei mate. Heoi, mā te tirotiro i tō toto toto i ia wā ka āwhina i te tautuhi wawe i ngā raruraru.
He aha taku e taea ai hei whakaiti i te mōrearea?
Mā te whakarerekē i ētahi momo noho ka āwhina pea ki te whakaiti i te tūponotanga o te whakawhanake i te aldosteronism tuatahi ki tētahi taumata:
- Whakanuia te korikori tinana: He mea tino nui te korikori tinana i ia rā.
- Te whakawhāiti i te inu waipiro.
- Te whakaiti i te tote (konutai) i roto i te kai.
- Te whakamutu i te momi hikareti.
Ka āwhina hoki ēnei mea ki te whakahaere i te toto toto tiketike, nō reira he tino painga mō tō hauora whānui.
He aha ngā pānga roa o te Aldosteronism Tuatahi?
Ko te toto toto tiketike, he āhuatanga nui o tēnei mate, ka whakapiki ake i te mōrearea o te whiu, te ngoikore o te ngākau, te mate tākihi, me ētahi atu mate. Heoi, mā te maimoatanga tika, ka taea e te hunga whai aldosteronism tuatahi te wheako i te whakaiti i ngā tohu me te kounga pai ake o te oranga. He maha ngā pānga kino mo te wā roa ka puta i roto i te hunga kāore e whiwhi maimoatanga.
He aha te tirohanga mō te tangata e pāngia ana e te Aldosteronism Tuatahi?
Ki te tika te maimoatanga, he tino pai te tirohanga mō te tangata e pāngia ana e te aldosteronism tuatahi. Koia te mea nui kia toro atu ki te tākuta i te wā tonu e puta ai ngā tohu. Ki te kore e rongoatia, ka puta pea ngā raruraru morearea pēnei i te whiu, te mate ngakau, me te ngoikore o te whatukuhu.
Āhea ahau me toro atu ki te tākuta?
Ki te mea kei te ngenge tonu koe, kei te tino matewai koe, kei te hiahia rānei koe ki te mimi pinepine, me toro atu ki te tākuta tonu. Ka whakahaerehia e rātou ngā whakamātautau e tika ana hei whakatau i te mate.
Waihoki, ki te mea he toto toto tiketike tonu tōu, kua tāpaetia rānei he iti ō taumata pāhare pāporo i roto i tō toto, pātai atu ki tō tākuta mēnā me whakamātau koe mō te Aldosteronism Tuatahi, mō ētahi atu mate rānei e pā ana.
He aha ngā pātai me pātai atu e au ki taku tākuta?
Mena kua tāpaetia koe kei te mate koe i te Aldosteronism Tuatahi, me pātai atu pea koe ki tō tākuta i ēnei pātai:
- He aha te take i pēnei ai te āhua mōku?
- He aha atu ngā whakamātautau me mahi e au?
- He pukupuku repe tākihi tōku?
- He mate hauora anō kei ahau e pāngia ai aku tohumate?
- He aha te momo maimoatanga e taunaki ana koe?
- Me ine ahau i tōku toto toto ki te kāinga?
Hei whakamutunga, he karere hei kawe ki te kāinga
He tokomaha te hunga e tango ana i ngā rongoā mō te toto toto tiketike. Heoi, ki te mea ka ngenge tonu koe, ka matewai, ka mimi pinepine rānei i te nuinga o te wā, ehara pea i te toto toto tiketike anake. Ki te mea kua mōhio koe ki ēnei tohu, me toro atu ki te tākuta tonu. Ka whakahaerehia e rātou he whakamātautau hei rapu mēnā he raruraru anō. Ka taea e te aldosteronism tuatahi te whakaputa i ngā tohu maha e whakarihariha ana. Heoi, mā te maimoatanga tika, ka taea te whakaora i tēnei mate. Nō reira kaua e mataku, ā, whai i ngā tohutohu a tō tākuta. Kia tere tō ora!
` te aldosteronism tuatahi, te mate a Conn, te toto toto tiketike, te aldosterone, ngā repe adrenal, te pāhare pāporo iti, ngā tohu, te maimoatanga











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