Kua rongo tātou katoa mai anō i te tamarikitanga mō te pai o te rino mō te tinana, ā, ki te kore he rino, ka pāngia tātou e ngā mate. He kōrero tonu tā tātou mō te "korenga o te rino", arā, te anemia. Engari kua whakaaro kē koe he raru nui te nui rawa o te rino i roto i te tinana? Ae, he pono. Ko tēnei mate e kiia nei e tātou ko te "hemochromatosis" ko te "rahinga nui o te rino" rānei i roto i te rongoā. I tēnei rā kei te kōrero tātou mō tēnei mate kāore i te mōhiotia e te tini o te tangata, engari me mōhio te katoa.
He aha tonu te Hemochromatosis?
Ki te kī ngāwari, koinei te wā e mimiti ai te tinana i te rino nui atu i te mea e hiahiatia ana. I te nuinga o te wā, he tino pai ō tātou tinana ki te tango i te nui o te rino e hiahiatia ana, me te whakakore i te toenga. Engari i roto i te tangata e pāngia ana e te hemochromatosis, he hapa kei roto i tēnei pūnaha whakahaere.
Nō reira, nā te mea kāore he huarahi hei tango i tēnei rino tāpiri mai i te tinana, ka tīmata te tinana ki te penapena i roto i ngā whekau rerekē. Pērā i tā tātou penapena i ngā taonga kāore e hiahiatia ana i te kokonga o tō tātou whare. I roto i te wā, ka kohia tēnei rino ki roto i ngā whekau nui pērā i te ngākau, te ate, me te repeure, ka kino ai aua whekau. Ki te kore e rongoatia, ka mate pea tēnei. Engari ko te mea pai rawa atu ko tēnei mate ka taea te rongoā me te whakahaere .
He aha ngā tohu o tēnei mate? Me pēhea te tautuhi i tōna mate?
Ko te raruraru nui o tēnei ko te roa o te wā ka puta mai ngā tohu. Ahakoa he whānau tonu tēnei mate, he maha ngā tau ka roa te wā ka kohia e te tinana ngā taumata kino o te rino. Nō reira, he tokomaha te hunga ka tīmata ki te pāngia e ngā tohu i muri i te 40, 50 rānei o te tau. I ētahi wā ka warewarehia ēnei tohu, me te whakaaro he āhuatanga noa ēnei e puta ana i te koroheketanga.
Kia tirohia ngā tohu matua o tēnei mate i te ripanga i raro nei.
| Tohu | He whakamārama māmā |
|---|---|
| Ngenge mau tonu | Te ngenge tonu me te ngenge, kāore he take. |
| Mamae hononga | Mamae, inā koa i ngā hononga o ngā maihao tohu me ngā maihao waenga. Ka kiia hoki tēnei ko te "ringa rino". |
| Te rerekētanga o te kiri | Ka huri te kiri hei hina, hei parahi rānei. Tērā pea te āhua kua wera i te rā. |
| Mamae o te puku o runga | Te mamae i te wāhi kei reira te ate, arā, i te taha matau o runga o te puku. |
| Ngā hapa o te ngakau | Tērā pea ka kitea ngā panoni o te tere o te manawa me te mamae o te uma (arrhythmias). |
| Te hekenga o te hiahia moepuku | Ka pāngia pea ngā tāne me ngā wāhine e te ngoikore o te hiahia moepuku, te ngoikore rānei o te ure. |
| Te ngaronga taumaha me te kore take | Te whakaiti taumaha me te kore kai, te korikori tinana rānei. |
He aha tēnei e tupu nei? He aha ngā take?
E rua ngā momo matua o ngā take o te hemochromatosis.
1. Ngā take tuku iho (Hemochromatosis tuku iho)
Koinei te momo tino noa. He māmā noa iho, he mate ira tēnei ka riro mai i ō mātua . He ira kei roto i tō tātou tinana e whakahaere ana i te rino. Ko te ingoa o tēnei ira ko te `(ira HFE)`. Mēnā he whakarerekētanga (whakarerekētanga) kei roto i tēnei ira, kāore e taea e te tinana te whakahaere i te rino.
Whakaarohia, kia puta ai tēnei mate, me whiwhi koe i ngā tārua e rua o tēnei ira hapa mai i tō whaea me tō pāpā. Mēnā kotahi noa te tārua i riro mai i a koe mai i ngā mea e rua, he kaikawe noa koe, ā, kāore koe e pāngia e te mate. Nō reira, ahakoa kei ō mātua tēnei ira, kāore pea rātou e pāngia e te mate. Ko ngā whakarerekētanga ira tino noa ko `(C282Y)` me `(H63D)`.
Hei tāpiritanga, he momo onge kei te kīia ko te "Juvenile Hemochromatosis" e puta mai ana i te wā taitamariki, arā, i waenga i te 15-30 tau. Nā ngā whakarerekētanga ira i roto i ngā ira `(HJV)` me `(HAMP)` rānei. I roto i tēnei, ka tere rawa te kohikohinga o te rino.
2. I puta mai i ētahi atu mate, i ētahi atu maimoatanga rānei (Hemochromatosis Tuarua)
Ka puta tēnei ina piki ake ngā taumata rino i roto i te tinana nā tētahi atu mate hauora, nā tētahi atu maimoatanga hauora rānei.
- Te Whakawhiti Toto Auau: Me whakawhiti toto tonu ngā tūroro e pāngia ana e te anemia pēnei i te thalassemia. Ka puta pea tēnei āhuatanga i te mea ka kohia te rino i roto i te toto i roto i te tinana.
- Mate Ate Mau tonu: Ki te tino pakaru te ate, kāore e taea e ia te tukatuka tika i te rino.
- Te inu nui rawa i te waipiro: Ehara i te mea ka kino noa te ate i te waipiro, engari ka whakanui ake hoki i te mimiti o te rino e te tinana.
He aha ngā raruraru o te nui rawa o te rino?
E ai ki tā mātou i kōrero ai i mua ake nei, he paitini te rino ki te tinana mēnā ka nui atu i te nui e hiahiatia ana. Nā te mea kāore he huarahi hei tango i tēnei rino taikaha, ka rongoatia e te tinana ki roto i ngā kiko. Ehara i te mea iti te kino ka pā mai i tēnei.
Ahakoa he mea nui te rino mō ō tātou tinana, ki te nui rawa, ka rite ki te paitini. Nō reira, he mea tino nui kia mōhio ki tēnei.
Ko te ate, te ngākau, me te repe taiaki ngā tino pānga. Mēnā kāore e rongoatia, ka puta pea ēnei raruraru nui:
- Te ngoikore o te ate mau tonu: Ko te mate ate ka puta mai i te kohikohinga rino i roto i te ate, ka mutu ka arahi atu ki te ngoikore katoa o te ate.
- Te ngoikore o te ngakau: Ka ngoikore te ngakau nā te mea ka pupū te rino i roto i te uaua o te ngakau, ā, ka kore e taea e ia te pupuhi i te toto ki te tinana.
- Mate huka: Ka pakaru ngā pūtau e whakaputa ana i te insulin i ngā putunga rino i roto i te repe taiaki, ā, ka hua ake pea tēnei mate huka (Momo 3c).
Hei tāpiri, ka pāngia hoki te mahi a te repe tairoi, te repe pituitary, te adrenals, me te pūnaha whakaputa uri.
Me pēhea te kitenga a te tākuta i tēnei?
Mena kei a koe tētahi o ngā tohu o runga ake nei, ki te mea rānei kei roto i tō whānau tēnei mate, he mea nui kia toro atu koe ki tō tākuta. Ka pātai tuatahi te tākuta i ētahi pātai ki a koe.
- Kua pāngia ō mātua, tō whānau rānei e te mate ate, e te nui rawa rānei o te rino?
- Kei te tango koe i ngā tāpiringa rino, i te huaora C rānei (e whakanui ake ana i te mimiti o te rino)?
- E hia te nui o te waipiro e inuhia ana e koe?
Kātahi ka whakahaerehia he whakamātautau tinana, ā, ki te tika, ka whakahaerehia ngā whakamātautau e whai ake nei.
| Whakamātautau | He aha tāu e kite nei i roto i tēnei? |
|---|---|
| Ngā whakamātautau toto | Ka inehia ngā mea pēnei i te nui o te rino i roto i te toto, te nui o te rino e rongoa ana (Serum Ferritin), me te Transferrin Saturation. |
| Whakamātautau ira | Hei whakaū mēnā he āhuatanga ira tēnei, ka whakamātauria te ira HFE mō ngā whakarerekētanga ira. |
| Te koiora ate | I ētahi wā, ka tangohia he wahi kiko iti mai i te ate mā te whakamahi i tētahi ngira iti, ā, ka tirohia i raro i te karuārai hei aromatawai i te nui o te rino kua whakatakotoria ki roto i te ate me te nui o te kino ki te ate. |
| Matawai MRI | Ka taea te whakamahi i te matawai MRI hei tikanga kore mamae hei ine i te nui o te rino kua whakatakotoria ki roto i ngā whekau pēnei i te ate. |
He aha ngā maimoatanga pai rawa atu?
Ko te whāinga matua o te rongoā i te hemochromatosis he whakaiti i te nui o te rino i roto i te tinana, me te pupuri i tōna taumata ki te taumata noa. Mā tēnei ka ārai i ngā kino atu ki ngā whekau.
| Tikanga Maimoatanga | He aha te mea ka tupu ki tēnei? |
|---|---|
| Te Whakaora i te Phlebotomy | Koinei te maimoatanga tino nui, tino whai hua hoki. Pērā i te tuku toto, ka tangohia e te ngira he iti noa te toto mai i tō tinana. Nā te mea ko te nuinga o te rino i roto i ō tātou tinana kei roto i ngā toto whero, ina tangohia te toto, ka tangohia hoki te rino. Me mahi pea tēnei i te tuatahi kotahi i te wiki. Kia mau tonu ō taumata rino, me mahi pea tēnei i ia torutoru marama. |
| Te Whakaora Chelation Rino | Ka tukuna tēnei maimoatanga ki te hunga kāore e taea te tango toto mō tētahi take (hei tauira, te mate ngākau, te anemia). Ko te tikanga he hoatu rongoā (he pire, he werohanga rānei) e herea ana ki te rino i roto i te tinana, ā, ka puta i roto i te mimi, i te paru rānei. |
| Ngā huringa o te kai | Tērā pea ka kī atu tō tākuta kia whakawhāitihia te kai i ngā kai nui te rino (pērā i te mīti whero, ngā pīni) me ngā kai nui te huaora C, ka nui ake te mimiti o te rino. Tērā pea ka kī atu ia kia mutu rawa te tango i ngā pire huaora kei roto te rino, me te karo hoki i te inu waipiro. |
Kei te pēhea te oranga me tēnei āhuatanga?
Tērā pea he whakamataku tēnei ki a koe. Engari ko te pono, ki te kitea wawetia, ā, ka rongoatia tika, he tino ngāwari te whakahaere i te hemochromatosis . Ka taea e koe te noho ora noa, hauora hoki. I ētahi wā, ka taea te whakakore i ētahi o ngā kino o te okana ina tīmata te maimoatanga.
Ko te raruraru, ki te kore koe e rongoatia mō te wā roa rawa, tērā pea kāore e taea te whakaora i te kino o ō whekau. Koia te mea nui kia toro atu koe ki te tākuta tonu mēnā he āwangawanga āu.
Karere Tangohia ki te Kāinga
- Ehara te hemochromatosis i te korenga o te rino i roto i te tinana, engari he nui rawa atu .
- Ko te nuinga o te wā ka puta mai tēnei i ngā āhuatanga ira, engari ka taea hoki e ētahi atu mate hauora te puta.
- I te mea ka puta mai ngā tohu i muri i te wā roa, kaua e warewarehia ngā mea pēnei i te ngenge tonu me te mamae o ngā hononga.
- Ki te kore e rongoatia, ka pā he kino nui ki ngā whekau nui pēnei i te ate, te ngākau, me te pancreas.
- Kāore he mea hei wehi. Mēnā ka kitea wawetia, ka taea te whakahaere katoa mā te whakamahi i ngā maimoatanga māmā noa iho, ā, ka taea e koe te noho ora.
- Mena he ruarua āu mō tēnei, tēnā kōrero ki tō tākuta whānau.
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