E mōhio ana koe ki ēnei mea mō te ventricle maui o tō ngākau? (Left Ventricular Non-Cimpaction - LVNC) Me kōrero tāua!

I tēnei rā ka kōrero tātou mō tētahi āhuatanga uaua, engari he tino nui pea, o te ngākau. Kāore pea koe i rongo i tēnei i mua. Ko te ingoa o tēnei āhuatanga ko te Left Ventricular Non-Cpaction (LVNC) e ai ki ngā tākuta. Ahakoa te ahua nui o te ingoa, kaua e manukanuka, kia māmā noa iho.

Nā, he aha te ngoikore o te ngākau kore-pūpū o te ventricle maui (LVNC)?

He whakarāpopototanga noa iho tēnei, he āhuatanga tēnei e puta ana ina kore e whanake tika te rūma o raro i te taha maui o tō tātou ngākau, te Ventricle Mauī . Whakaarohia, ko te tikanga he wahi kikokiko tino pakari, maeneene tēnei ventricle maui o tō tātou ngākau. Koinei te wāhanga matua e pupuhi ana i te toto ki tō tātou tinana katoa. Engari i roto i te tangata he `(LVNC)` tēnei, he rite te ventricle maui ki te hautai, he matotoru ake, ā, he rite ki te kupenga. He āhua pukepuke tōna, he rite ki te roto o te taro.

E kiia ana tēnei he mate ngākau whānau mai anō. Ko te tikanga, tera pea kei roto i tō ngākau tēnei mate mai anō i tō whānautanga. Ki te kore e rongoatia tika, ka taea e tēnei "(LVNC)" te arahi ki ngā raruraru ngākau nui, arā, te mate ngākau.

He aha te pānga o tēnei āhuatanga LVNC ki te mahi a te ngākau?

Titiro mai, he mahi tino nui tā te pūkahukahu maui o tō tātou ngākau. Koinei te mea e pupuhi ana i te toto whai hāora mai i ngā pukahukahu ki te tinana katoa. Pērā i te motuka wai. Heoi, ina puta tēnei āhuatanga `(LVNC)`, kāore e taea e te pūkahukahu maui, he rite ki te hautai, te kōpiri, te whakangāwari rānei. Arā, he uaua ki te whakakī me te pana i te toto ki mua, ki te whakangāwari anō rānei kia whakakīia ki te toto. Nō reira, ko te mutunga iho , kāore e tika te mahi pupuhi toto ki te tinana katoa . Koinei te take ka tīmata te puta o ngā raruraru maha.

E pēhea te onge o te ingoa o tēnei āhuatanga ko te LVNC?

He mate onge tēnei. E ai ki ngā tohunga hauora, tekau mā rua noa iho ngā tāngata i roto i te miriona e kitea ana tēnei mate i ia tau. Heoi, tera pea he nui ake te tokomaha tuturu . Ko te take, kāore ētahi tāngata e whakaatu i ngā tohumate. Kātahi ka kore rātou e haere ki te tākuta, ā, nō reira, kāore rātou e whiwhi tātaritanga.

He aha ngā tohu o te LVNC?

Koinei te mea tino nui. Tērā pea ētahi tāngata kāore e whakaatu i ngā tohu . Heoi, ka pāngia ētahi e ngā raruraru ngākau tino kino. Hei tauira, ka pāngia pea e te mate ngākau ohorere. Tata ki te rua hautoru o te hunga whai LVNC kei te mōrearea ki te pāngia e te ngoikore o te ngākau .

Āe, kia tirohia tātou he aha ngā momo tohu ka puta mai i te tangata whai `(LVNC)`:

Ngā tohu e kitea whānuitia ana :

• Ka taea te hanga i ngā toto totoka . He tino morearea ēnei, nā te mea ki te haere ēnei totoka ki te roro, ki ngā pukahukahu rānei, ka waiho hei raruraru nui.
• Tērā pea ka uaua ki te manawa i a koe e takoto ana i te moenga.
• Te hemo o te tinana .
• Te tere o te manawa - Ka rite tēnei ki te patu a te pahu i roto i te uma, ki te tere rānei te manawa.
• Te kore e taea te whakakori tinana, te poto o te manawa ahakoa he iti noa te whakapau kaha (Dyspnea) .
• Te auau o te ngakau kāore i te tika (Arrhythmia) .
• Te pupuhi o ngā waewae (Lymphedema) - inā koa ki ngā pona waewae.
• Te poto o te manawa / Te mate manawa - Te āhua nei kua pau te manawa ahakoa he iti noa te kaha.

He aha i puta ai tēnei āhuatanga LVNC? He aha ngā take?

I te nuinga o te wā, ko tēnei mate `(LVNC)` ka puta mai i tētahi huringa ira (whakarerekētanga ira) e puta ana i mua i tō whānautanga. He mea tino uaua tēnei. Ka taea e tēnei huringa ira te puta noa, arā, kāore he take, ka taea rānei te tuku iho i ō mātua. Arā, he mea e ahu mai ana i roto i ngā whānau. Whakaarohia, he nui te maha o ngā whānau e pāngia ana e tēnei momo mate ngākau.

Waihoki, he iti noa iho te ōrau o ngā wāhine ka pāngia e te LVNC mō te wā tuatahi i te wā e hapu ana, kāore he take e kitea ana. E whakaaro ana ngā tākuta he taumahatanga tāpiri pea tēnei ki te uaua o te ngākau i te wā e hapu ana. Mō ētahi wāhine, ka memeha haere ēnei tohu i muri i te whānautanga. Engari mō ētahi atu, ka pāngia pea rātou e te LVNC mō te wā roa.

Me pēhea te tautuhi a ngā tākuta i tēnei mate LVNC?

Ka whakahaerehia e te tākuta ētahi whakamātautau hei whakatau tika mēnā kei a koe tēnei mate "(LVNC)". Me titiro tātou ki ēnei:

• Echocardiogram: Ka tirohia te pai o te pupuhi toto o tō ngākau, te pai o te mahi a ngā takirere, me te mea he raruraru kei roto i ngā takirere. He rite ki te matawai ultrasound o te ngākau. Koinei te wāhi tuatahi ka kitea ai te āhua hautai o te ventricle maui.
• He whakamātautau hiko-ā-ringa (ECG): Mā tēnei ka ine i te ngohe hiko o tō ngākau. Ka taea e ia te kite i ngā raruraru o te manawataki o tō ngākau.
• Ngā whakamātautau whakaahua motuhake: Kei roto i ēnei ko ngā matawai CT o te ngākau me te whakaahua aukume (MRI). Ka taea e ēnei te whakaatu i te hanganga o te ngākau, pērā i te hanganga o te ngākau me te matotoru o ōna pakitara. I roto i te LVNC, ka kitea mārama te āhua rite ki te hautai i runga i ēnei matawai.
• Angiogram coronary: Ka whakamātautauhia te rere o te toto i roto i ngā uaua coronary e tuku toto ana ki te ngākau, me te whakamātautau mēnā he aukati. I ētahi wā ka hiahiatia pea tēnei whakamātautau hei whakakore i ētahi atu mate ngākau.

He aha ngā maimoatanga mō tēnei mate LVNC?

He rerekē te maimoatanga mō te LVNC i runga i ō tohu. Kāore e rite te maimoatanga mō te katoa. Hei tauira, ki te pāngia koe e te ngoikore o te ngākau, ka tohua pea e tō tākuta ngā rongoā pēnei i:

• Ngā aukati whākōkī huri-angiotensin (ngā aukati ACE): Hei tauira, benazepril (Lotensin®) lisinopril rānei (Prinivil®, Zestril®) sacubitril-valsartan (Entresto®) rānei (ngā aukati angiotensin-neprilysin). Ka mahi ēnei mā te whakangāwari me te whakatuwhera i ō uaua toto (ngā uaua me ngā uaua toto) kia māmā ake ai te rere o te toto mā roto i a rātou. Ka whakaitihia te taumahatanga ki te ngākau.
• Ngā ārai-beta: Hei tauira, ko te metoprolol (Lopressor®, Toprol XL®) te atenolol rānei (Tenormin®). Ka ārai ēnei i ētahi homoni (hei tauira, te adrenaline), ka whakaheke i te toto totoka me te whakahaere i te tere o te manawa.
• Digoxin (Digoxin®, Lanoxin®): Ka whakahaere tēnei i te tere o tō manawa, ka whakanui ake i te kaha pupuhi o tō manawa, ā, ka whakapai ake i te rere o te toto.
• Ngā rongoā whakaheke toto, ngā "pire wai" rānei: Mā te tinana e whakaputa te tote me te wai nui mā te mimi ka whakaiti i te pupuhi me te taumaha o te ngākau.

I ētahi wā, mēnā he tūponotanga o te hopukanga ohorere o te ngakau, ka tūtohu pea te tākuta kia whakatōkia he taputapu e kiia nei ko te Implantable Cardioverter Defibrillator (ICD) ki raro i te kiri o te ngakau. He taputapu iti tēnei e whakahaerehia ana e te pākahiko. Ka kitea he tere, he morearea te manawa i roto i te ngakau, ā, ka tukuna he ru hiko ki te ngakau hei whakahoki mai i te manawa noa. I ngā take tino kino, ki te kore e angitu ētahi atu maimoatanga, tera pea ka hiahiatia he whakawhitinga ngakau .

Ka taea te whakaora katoa i tēnei mate LVNC? Ka taea te whakakore?

Āe, kāo. Kāore he rongoā mō te LVNC i tēnei wā . Arā, kāore e taea te whakakore. Kaua e manukanuka. Ka taea e te maimoatanga te whakapai ake i tō kounga o te oranga me te whakaiti i ngā raruraru ka puta mai i te mate ngakau . Ā, e ai ki taku kōrero i mua, i ngā wā tino kino, me whakawhiti ngakau.

Me pēhea tātou e karo ai i tēnei āhuatanga LVNC?

Kāore he huarahi hei ārai i te LVNC. Nā te mea he maha ngā wā ka puta mai i ngā āhuatanga ira. Heoi, ki te mea kei a koe te whakarerekētanga ira e puta ai te mate, ki te whakaaro rānei koe kei a koe (hei tauira, ki te mea kei roto i tō whānau te mate), he tino āwhina te whakamātautau ira.Mā te kaitohutohu ira koe e whakamārama ki a koe me tō whānau i ngā hua o tō whakamātautau. Mā rātou koe e āwhina ki te mārama ki te tikanga o te LVNC me te mōrearea o te tuku atu ki ō tamariki.

He aha atu anō ngā āhuatanga hauora e pā ana ki tēnei āhuatanga LVNC?

Āe. I ētahi wā, ka kitea anō hoki tēnei āhuatanga e kiia nei ko te `(LVNC)` hei wāhanga o ētahi atu āhuatanga ira (ngā mate). He uaua ake ēnei, engari ka whakaarohia hoki ēnei āhuatanga e ngā tākuta ina tātaritangahia ana te `(LVNC)`. Anei ētahi tauira:

• Te mate a Barth
• Te mate Noonan
• Te mate Roifman
• Te mate Toriello Carey

He aha te heke mai o te tangata whai LVNC? He aha te roanga o te oranga?

Ka rerekē pea te tirohanga mō te tangata whai LVNC. He rerekē i ia tangata, i ia tangata. Mēnā he pai te maimoatanga, ka taea te whakahaere i ngā tohu , ā, he rite tonu te roa o te oranga o ētahi tāngata.

He mate pea te LVNC, engari kāore i te pēnei tonu . Ko te nuinga o te hunga whai LVNC kāore e mate i te mate. Ko te mea nui ko te toro atu ki tētahi tohunga ngakau i ia wā, me te whakamātautau . Ka taea e ia te āwhina i a koe ki te whakahaere i tō hauora ngakau me te whakaiti i te tūponotanga o ngā raruraru.

Mena kei a au, kei taku tamaiti rānei te LVNC, he aha ngā pātai me pātai atu e au ki te tākuta?

Mena kei a koe, kei tāu tamaiti rānei (LVNC), he mea pai rānei kia pātai atu koe ki tō tākuta i ēnei pātai:

• He aha te tino take o te mate LVNC o taku/taku tamaiti? (arā, he ira tuku iho, he mea kē atu rānei)
• E taunaki ana koe i te whakamātautau ira mō te LVNC? Mena koinā, he mea nui rānei mō ētahi atu mema o te whānau?
• He aha ngā whakamātautau e hiahiatia ana e au/e taku tamaiti hei tautuhi i te LVNC? He aha ngā mea ka taea e au te tumanako mai i ēnei?
• He aha ngā kōwhiringa maimoatanga mō te LVNC? Ko tēhea maimoatanga te mea pai mōku/māku tamaiti? He pānga taha kei ēnei maimoatanga?
• Ki te pāngia taku tamaiti, taku tamaiti rānei e te mate manawa ohorere, he aha ngā tohu? Me aha tonu ahau?

Mā ēnei pātai koe e āwhina ki te kōrero ki tō tākuta mō ēnei mea, kia pai ake ai hoki tō māramatanga ki tō āhua.

Nā, he aha ngā mea tino nui hei maumahara mā tātou i tēnei pūrākau?

Ko te ngākau kore mahi o te ventricle maui (LVNC) he mate ngākau onge, he maha ngā wā ka whānau mai. Koinei te wā kāore te ventricle maui o te ngākau e whanake tika. Engari ehara i te mea he wahi uaua maeneene, kaha, ka matotoru, ka rite ki te hautai. Nā tēnei ka kore te ngākau e pupuhi tika i te toto.

Mena kei a koe te `(LVNC)`,Ko te mea nui ko te toro atu ki tētahi tākuta ngakau i ia wā, me te whai i ā rātou tohutohu. Ahakoa kāore he rongoā mō tēnei, mā te maimoatanga e hoatu ana e tō tākuta ka taea e koe te whakaiti i tō tupono ki ngā raruraru me te whakapai ake i tō kounga o te oranga. He mea nui kia kaua e mataku, engari me whiwhi i te maimoatanga tika . Kia mahara, kāore koe i te mokemoke, ā, kei reira ngā tākuta hei āwhina i a koe.

` Mate ngakau, ventricle maui, LVNC, ngā tohu o te mate ngakau, te ngoikore o te ngakau, ngā mate ira, te maimoatanga o te mate ngakau