Kua pāngia koe e te mamae o te upoko e mau tonu ana, te uaua ki te neke i ō kanohi, te ngaro ohorere rānei o te taurite i a koe e hikoi ana? Kua kite pea koe i ēnei tohu i roto i tāu tamaiti. Ahakoa he maha ngā wā ka warewarehia e tātou ēnei take, i ētahi wā ka taea e rātou te tohu i tētahi mate hauora nui. I tēnei rā, i Nirogi Lanka , kei te kōrero mātou mō tētahi pukupuku roro tino onge engari he mea nui kia mārama, e mōhiotia ana ko te Pineoblastoma .
He aha rawa te Pineoblastoma? He māmā noa iho…
I roto i ngā kupu māmā noa iho, he pukupuku kino (matepukupuku) te Pineoblastoma e ahu mai ana i te repe pineal o tō roro. He tino pukuriri tēnei momo pukupuku; ka tere te tipu, ā, ka horapa ki ngā kiko roro e karapoti ana me te wai e rere ana i tō roro, ka waiho hei āwangawanga hauora nui.
Taria, he aha te Pineal Gland?
Me tīmata tātou ki ngā kaupapa matua. He okana iti te repe pineal, he āhua kōne te āhua, he rite te rahi ki te nati paina, kei waenganui pū o tō roro. Ko tēnei repe te kawenga mō te whakaputa i tētahi homoni e kiia nei ko te melatonin . Kua rongo pea koe i te melatonin—he mea nui mō te whakahaere i tō manawataki circadian . Whakaarohia hei karaka ā-roto o tō tinana e āwhina ana i a koe kia mataara i te awatea, ā, e whakaoho ana i te moe i te pō.
He aha te momo pukupuku ko Pineoblastoma?
He pukupuku roro tere te tipu o te Pineoblastoma . He maha ngā wā ka whakarōpūtia e ngā tākuta hei pukupuku roro ā-roto o te angaanga taumata 4. Nā te mea he pukupuku kino , he kino ki te tinana, ā, ka horapa pea.
He pēhea te noa o te Pineoblastoma?
He tino onge te Pineoblastoma . E ai ki ngā pūrongo i te Hononga o Amerika, iti iho i te 0.2% o ngā pukupuku roro katoa ka kitea he pukupuku repe pineal. Ahakoa e kitea nuitia ana tēnei momo mate pukupuku i roto i ngā tamariki nohinohi, i ngā pakeke taitamariki rānei kei raro iho i te 20 tau te pakeke , he mea nui kia mahara ka taea te puta i ngā tau katoa.
He aha ngā tohu o te Pineoblastoma?
Kia tirohia ngā tohu ka puta mai i tēnei mate:
- Te ānini nui : Ehara ēnei i te ānini noa; he kaha tonu, he pumau tonu hoki.
- Ngenge tonu : He kare ā-roto o te ngenge nui rawa atu, ā, ka uaua haere ngā mahi o ia rā ( Ngenge ).
- Te uaua ki te nekeneke o ngā kanohi : Tērā pea ka uaua ki a koe te arotahi i ō kanohi, te titiro rānei ki ētahi huarahi.
- Ngā raruraru ki te taurite me te taunga o te tinana : Te āhua pōturi ina hikoi ana, te uaua rānei ki te hopu i ngā mea.
- Ngā huringa whanonga : Ka kitea ngā huringa o te wairua, pērā i te pikinga o te riri, te ohooho, te wehe ohorere rānei.
- Whakapairuaki me te ruaki .
He maha ngā wā ka puta mai ēnei tohu i te mate e kiia nei ko te hydrocephalus , te wāhi e nui haere ai te wai cerebrospinal, ka piki ake te pēhanga i roto i te roro. Ahakoa ka horapa te pukupuku mā roto i tēnei wai ki ētahi atu wāhanga o te Pūnaha Nervous Matua (CNS), he onge te horapa ki waho o te CNS.
Whakaarohia he tamaiti e amuamu ana mō te mamae o te upoko i ngā wā katoa, kāore e hiahia ki te tākaro, ā, he āhua pukuriri rawa. Tērā pea ka whakahēngia tēnei e ngā mātua he whanonga noa iho. Heoi, ki te mau tonu ngā tohu, he mea nui kia toro atu ki te tākuta tonu.
He aha te take o te Pineoblastoma?
Ko te tino take ko te tipu tere, kāore i te whakahaeretia o ngā pūtau motuhake i roto i te repe pineal e mōhiotia ana ko ngā pinealocytes . E ai ki ngā rangahau, nā ngā whakarerekētanga ira ka hē te mahi a ēnei pūtau, ka tipu rerekē hoki.
E rua ngā huarahi e puta ai ēnei huringa ira:
1. Tuku iho (ngā whakarerekētanga ira) : Tuku iho i ngā mātua ki te tamaiti i te wā e hapu ana.
2. Ngā whakarerekētanga ira tūpono : Ngā huringa tūpono ka puta i muri i te haputanga, ina kāore he hītori whānau o mua mō te mate.
Ko wai kei te mōrearea nui ake ki te Pineoblastoma?
He nui ake te tūponotanga o ētahi tāngata ki te whakawhanake i te Pineoblastoma :
- Mena kei a koe te Retinoblastoma , he mate pukupuku o te retina o te kanohi, he nui ake tō mōrearea ki te pāngia.
- He nui ake te mōrearea o te hunga whai whakarerekētanga ira i roto i ngā ira RB1 , DICER1 rānei ki te pāngia e tēnei mate pukupuku . Ka taea e ēnei whakarerekētanga ira te tuku iho, te puta noa rānei i te wā.
Mena kei te whakaaro koe ki te whānau, ā, kei te āwangawanga koe mō ēnei āhuatanga mōrearea, he mea tika kia kōrero koe ki tētahi kaiwhakarato hauora mō ngā whakamātautau ira .
Me pēhea te tautuhi i te Pineoblastoma?
Mā te huinga o ngā aromatawai haumanu me ngā whakamātautau tātaritanga ka tātarihia e ngā tākuta te Pineoblastoma :
- Whakamātautau tinana : Ka arotakehia e tō tākuta ō tohu, tō hītori whānau, ā, ka whakahaerehia hoki ngā whakamātautau io, tae atu ki te tirotiro i te taunga o ō kanohi.
- Ngā tātaritanga matatau :
- Ngā matawai Whakaahua Āhua Aukume o te Roro ( MRI ).
- Ngā matawai Tomography Rorohiko (CT).
- I ētahi wā, ka whakamahia he matawai Positron Emission Tomography (PET).
- He koiora , ka tangohia he tauira kiko iti hei tātaritanga hei whakaū i te momo pukupuku.
- Ngā whakamātautau toto me/ranei te whakamātautau i te wai cerebrospinal mō ngā tohu pukupuku motuhake.
Ka taea te rongoā i te Pineoblastoma?
He āwangawanga noa tēnei. Ki te pono, kāore anō kia kitea he rongoā whānui mō te Pineoblastoma i tēnei wā. Heoi, kaua e ngaro te tumanako; he maha ngā huarahi maimoatanga kei reira. Mena kāore anō kia horapa te pukupuku, ko te tango pokanga te taahiraa tuatahi.
Nā te mea he momo mate pukupuku kaha te Pineoblastoma , he uaua ki te rongoā. Ka puta pea ngā raruraru, ā, ka pāngia te āhua o te mate mō te wā roa. Hei tāpiri, tera pea ka hoki anō te mate pukupuku i muri i te rongoā.
He aha ngā maimoatanga mō te Pineoblastoma?
Ko ngā maimoatanga mō te Pineoblastoma ka uru pea ki ēnei e whai ake nei:
- Pokanga : He maha ngā wā ka mahia te pokanga hei tango i tētahi wāhanga, i te katoa rānei o te pukupuku. Ka whakamāramahia e tō taote pokanga te tikanga me ōna mōrearea.
- Pokanga mō te Hydrocephalus : Hei whakaiti i te kohikohinga wai (wai cerebrospinal) huri noa i te roro, ka taea te whakanoho i tētahi shunt—he ngongo iti—hei tango i te wai nui me te whakamama i te pēhanga.
- Whakaora Irahiko : He maimoatanga whai muri noa iho tēnei i muri i te pokanga. Ka taea e te whakaora irahiko te āwhina i te whakaiti i te kiko pukupuku e toe ana, te whakangaro rānei i ngā pūtau matepukupuku.
- Te rongoā matū : Mā te whakamahi tahi me te pokanga me te irahiko, ka taea e te rongoā matū te whakaiti i te pukupuku i mua i te pokanga, te whakakore rānei i ngā pūtau matepukupuku e toe ana i muri mai.
- Te Whakaora Matepukupuku Horomanga-Teitei me te Whakatō Pūtau Taketake Autologous : I roto i tēnei tikanga, ka kohia ō ake pūtau take i mua i te whiwhinga i te rongoā matepukupuku nui. Kātahi ka whakahokia ēnei pūtau ki roto i tō tinana hei āwhina i tō pūnaha kia ora ake i muri i te maimoatanga.
I te whanaketanga o ngā rangahau hauora, tera pea ka whai wāhi koe ki ngā whakamātautau haumanu. Tērā pea ka uru atu ki ēnei ko te whakamātautau i ngā maimoatanga hou kua arotahihia, ngā rongoā ārai mate rānei.
Ko wai kei roto i tō rōpū tiaki?
Mena kua tāpaetia koe he Pineoblastoma, ko ētahi o ngā rōpū tiaki i Nirogi Lanka ko:
- He Tohunga Pūnaha
- He Tākuta Matepukupuku
- He Tākuta Matepukupuku Irahiko
- He Taote Pokanga Niho
He pānga taha kei roto i ēnei maimoatanga?
Ae, ka pāngia pea koe e ētahi maimoatanga, inā koa ko te irahiko. Tērā pea ka pāngia tō mahi endocrine e ēnei:
- Te tipu
- Ngā taumata pūngao
- Te momonatanga
I mua i te tīmatanga o te maimoatanga, me kōrero taipitopito ki tō tākuta mō ngā pānga taha pea . Ka aroturukihia koe i ia wā, ka mahi i ngā mahi e tika ana hei whakahaere i ngā raruraru ka puta.
Ka taea e koe te ora i te Pineoblastoma?
Ae, he maha ngā tūroro e ora tonu ana i te Pineoblastoma. Ko te reiti oranga mō te Pineoblastoma i roto i ngā tau e rima kei waenga i te 60% ki te 69.5% . Ahakoa he rerekē te oranga o tēnei mate, he maimoatanga whai hua kei reira hei āwhina i a koe kia ora pai, kia roa ake ai hoki tō oranga.
He aha te matapae mō te Pineoblastoma?
Whai muri i tō tātaritanga, ka matapakihia e tō tākuta tō matapae. Ahakoa kāore he "rongoa" kotahi, he maha ngā kōwhiringa maimoatanga e wātea ana. Ko te putanga o te tūroro ka whakatauhia e ngā āhuatanga pēnei i te hauora whānui, te urupare a tō tinana ki te maimoatanga, me te tere o te tipu o te pukupuku .
Whai muri i tō tātaritanga mate, ka whai wā tirotiro auau koe kia taea ai e tō tīma hauora te aroturuki mō ngā pānga taha me te whakarato i te tautoko e tika ana.
Ka taea te ārai i te Pineoblastoma?
Engari, kāore anō kia kitea he huarahi hei ārai i te Pineoblastoma i tēnei wā .
Āhea koe me toro atu ki te tākuta?
Mena ka pāngia koe, tāu tamaiti rānei e ngā tohu o te Pineoblastoma, pēnei i:
- Ngā mamae o te upoko e mau tonu ana
- Ngā huringa whanonga
- He uaua ki te nekehanga kanohi
Me toro atu ki te tākuta i tēnei wā tonu.
Mena kei te rongoatia koe i tēnei wā, ā, ka pāngia koe e ngā pānga taha hou, whakamōhio atu ki tō rōpū tiaki. Mena kei te āwangawanga koe mō te tipu, te whanaketanga rānei o tāu tamaiti i te wā e rongoatia ana, kōrerohia ēnei kitenga ki tō tākuta tamariki, ki tō tākuta mate pukupuku rānei.
He aha ngā pātai me pātai atu e au ki taku tākuta?
Ina tūtaki koe ki tō tākuta, he mea āwhina te pātai atu:
- He aha te maimoatanga e taunaki ana koe?
- Kua horapa te mate pukupuku?
- Me pokanga ahau?
- He aha ngā pānga taha ka pā mai pea i tēnei maimoatanga?
- He aha taku matapae?
Ka taea e te rongonga i te kupu "matepukupuku" te tino taumaha, te whakamataku hoki. He mea noa te ohorere, te manukanuka rānei mō te heke mai. Kaua e noho mokemoke. Kei konei tō tīma hauora i Nirogi Lanka hei āwhina i a koe ki te whakatere i tēnei tātaritanga me te whiriwhiri i te mahere maimoatanga e tika ana mōu. Whakawhirinaki ki ō hoa me tō whānau mō te tautoko. Kei te haere tonu te rangahau mō ngā maimoatanga hou mō te Pineoblastoma ki te tuku tumanako.
Karere Tangohia ki te Kāinga
- He pukupuku onge, tere te tipu te Pineoblastoma e whanake ana i roto i te repe pineal o te roro.
- Ka puta pea ngā tohu pēnei i te ānini o te upoko, ngā raruraru tirohanga, te ngaronga o te taurite, me ngā huringa whanonga, he maha ngā wā ka puta mai i te hydrocephalus (te pupūnga wai i roto i te roro).
- He take ira te nuinga o te wā; he nui ake te mōrearea o te hunga whai Retinoblastoma, RB1/DICER1 rānei.
- Ko te tātaritanga he MRI, he CT scan, me he biopsies.
- Ahakoa ngā wero, e wātea ana ngā maimoatanga whai hua pēnei i te pokanga, te radiation, me te chemotherapy.
- Ki te kite koe i ngā tohu, rapua tonutia he tohutohu hauora . Kaua e mangere ki te pātai.
- Kia kaha, kia tumanako tonu; kāore koe i te mokemoke i tēnei haerenga.
Ko te tumanako ka whai hua ēnei mōhiohio. Mena he āwangawanga āu mō tō hauora, whakaritea he wā hui ki tētahi tohunga hauora.
