He mate toto iti, engari he nui rawa te rino i roto i te tinana? Me kōrero tātou mō te mate toto iti sideroblastic

Ina rongo te nuinga o te tangata i te kupu 'anemia ' , ka whakaaro tonu rātou ki te korenga o te rino . Koia te take e ngenge tonu ai rātou, e ngoikore ana, e pōuri ana, ā, i ētahi wā kāore e taea te moe. Engari i mōhio koe i ētahi wā o te anemia, ko te ritenga kē te mea e tupu ana? Engari ko te korenga o te rino, ka 'piki' te rino i roto i ngā pūtau toto . Kāore ianei tēnei i te ahua rerekē? I tēnei rā kei te kōrero tātou mō tētahi āhuatanga motuhake o te anemia, engari kāore i te tino noa, e kiia nei ko te sideroblastic anemia.

He aha te tikanga o te Sideroblastic Anemia?

Hei mārama ki tēnei, me titiro tuatahi tātou ki ō tātou toto. Kei roto i ngā toto whero o roto i ō tātou toto he pūmua e kiia nei ko te hemoglobin . Ko tana mahi matua he hopu i te hāora e uru ana ki ngā pukahukahu ina manawa tātou, ā, ka kawe i taua hāora puta noa i te tinana. Nō reira, he mea nui tēnei hāora mō ia pūtau o roto i ō tātou tinana kia ora ai.

Nā, hei hanga i tēnei hemoglobin, me tino hiahia te tinana ki te kohuke 'rino'. I te nuinga o te wā, ka puta te anemia ina kore te tinana i te rino. Nō reira, kāore e taea e ia te hanga hemoglobin.

Whakaarohia he kīhini kei a ia te raihi, te wai, me te tote hei tunu raihi, engari kua pakaru te oumu raihi. Kātahi ka kore e taea te tunu raihi. Koia te āhua. I roto i tēnei mate, he nui te rino, he mea e hiahiatia ana hei hanga i te hemoglobin. Engari ko te wheketere e whakamahi ana i taua rino hei hanga i te hemoglobin, arā, ō tātou toto whero, kāore e mahi tika. Nō reira ka tīmata te kohikohi o te rino kāore i whakamahia ki roto i ēnei toto whero hapa. Ka karangatia ēnei pūtau rerekē kua kohikohi i te rino pēnei ko '(Sideroblasts)'.

He aha ngā tohu o tēnei mate?

He tino rite ngā tohu o tēnei mate ki ētahi atu mate toto iti, nō reira ka taea te whakapoauau i ētahi wā. Nā te puhoi o te whanaketanga o te mate, kāore pea koe e mōhio kei a koe. Koinei ngā tohu matua ka kitea e koe.

He aha ngā momo matua o te Anemia Sideroblastic?

Ka taea te wehewehe i tēnei mate ki ngā momo matua e rua.

1. Te mate toto iti o te taha raro

He mate tino onge tēnei, he mate ira. Arā, ka tukuna ki te tamaiti mā roto i ngā ira mai i tētahi o ngā mātua. Ko te momo tino noa o tēnei ko te X-linked Sideroblastic Anemia . Ka puta tēnei i te whakarerekētanga ira i roto i te ira e pā ana ki te hanga hemoglobin. Nō reira, ka ngana te tinana ki te mimiti i te rino mai i te kai hei whakakapi i te korenga o te hemoglobin. I ngā take kino, ka kino pea ngā whekau pēnei i te ate . Ko tēnei momo whānautanga ka kitea i mua i te 30 tau te pakeke.

2. Momo tīmatanga ā muri ake (Acquired Sideroblastic Anemia)

Koinei te momo tino noa. Ko te mea pai rawa atu, he maha ngā wā ka taea te whakaora . Ahakoa kāore ngā tākuta e mōhio ki te tino take i ētahi wā, he maha ngā āhuatanga matua e whai wāhi ana ki tēnei mate:

• Ngā rongoā motuhake: Tērā pea ko ētahi rongoā e hoatu ana mō te mate kohi.
• Te inu nui i te waipiro: Ko te inu nui i te waipiro i roto i te wā roa he tino take mōrearea.
• Ngā matū paitini : Te pānga roa ki ētahi matū paitini, pērā i te mata.
• Ētahi atu mate: Ka taea hoki tēnei āhuatanga te puta mai i ētahi atu mate pēnei i ngā mate ārai mate, ngā pukupuku, ngā mate pāwera rānei.

Hei tāpiritanga, ka taea e ngā momo e rua te whakawhanake i tētahi atu āhuatanga e kiia nei ko te hemochromatosis , e hua ai te nui o te rino i roto i te tinana.

Me pēhea te tautuhi tika i tēnei mate?

Nā te mea he rite ngā tohu ki ētahi atu mate anemia, he uaua pea te tautuhi i te mate. Nō reira he mea nui kia whakarongo ki tō tinana. Mena kei a koe tētahi, ētahi rānei o ngā tohu kua whakarārangihia i runga ake nei, tirohia tō tākuta.

Ka pātai mārire te tākuta ki a koe mō ō tohumate, ka tirotirohia koe, kātahi ka whakahau i ētahi whakamātautau hei whakaū mēnā kei a koe tēnei mate.

• Ngā Whakamātautau Toto: He mea nui te tatau toto katoa me ngā rangahau rino.
• Te Whakamātautau Toto Āpiti: I konei, ka tirohia he tauira toto i raro i te karuārai hei tirotiro mēnā he pūtau kohi rino rerekē (Sideroblasts) i kōrerohia e tātou i mua ake nei.
• Kohikohi i te Huka Wheua: I ētahi wā, me tango he tauira iti o te hinu wheua, ā, me whakamātautau hei whakaū i te mate.
• Ētahi atu whakamātautau: Mena e tika ana, ka tūtohu pea te tākuta i tētahi matawai MRI, i tētahi whakamātautau ira rānei.

Me pēhea te rongoā?

Ko ngā kōwhiringa maimoatanga e whakawhirinaki ana ki te momo whānautanga, ki te momo whiwhi rānei.

• Te Maimoatanga i te Take: Mena kei a koe te momo kua whiwhihia, ko te taahiraa tuatahi ko te tango i te take. Hei tauira, mena he rongoā te take o te mate, ka mutu taua rongoā e tō tākuta ka tohua he rongoā anō. Mena he tangata inu nui koe, me mutu rawa te inu waipiro.
• Huaora B6: Kua whakaatuhia e ngā rangahau he āwhina pea te huaora B6, te pyridoxine rānei, ki te rongoā i ngā momo mate e rua. Tērā pea ka tohua tēnei huaora e tō tākuta hei tāpiringa.
• Te tango i te rino nui: Tērā ētahi rongoā ka taea te hoatu hei tango i te rino nui mai i te tinana. Ka hoatu te Deferoxamine hei werohanga i raro i te kiri, ā, ka hoatu te Deferasirox hei pire. Heoi, ka pā pea ēnei rongoā ki ngā whatukuhu, nō reira me whakamahi i raro i te tirotiro tata a te tākuta.
• Te Whakawhitinga Toto: Ki te kore tō tinana e aro ki te maimoatanga huaora B6, ka tūtohu pea tō tākuta kia whakawhitia he toto. Heoi, he ngoikoretanga tēnei. Ki te haere tonu ngā whakawhiti toto, ka piki ake ngā taumata rino o tō tinana, ka piki ake te tūponotanga o te kino o te ate.
• Te Whakatō Huango Wheua: Koinei te rongoā whakamutunga. Ka whakaarohia tēnei i roto i ngā take tino kino kāore anō kia puta he rongoā i tētahi atu maimoatanga.