He nui te rino i roto i tō tinana, engari kāore koe i te pai te āhua? He mate toto sideroblastic pea?

He maha ngā wā ka ngenge koe, ka poto hoki te manawa? He maha ngā wā ka rite koe ki te iti o te toto toto? He tohu pea ēnei o te anemia noa. Heoi, i ētahi wā he take uaua ake kei muri i tēnei. I tēnei rā ka kōrero tātou mō tētahi mate toto he onge noa iho, engari he mea nui kia mōhiotia. Ko te anemia sideroblastic tēnā, ko te ingoa rānei o ngā tākuta ko (Sideroblastic Anemia - SA).

Nā, he aha te mate toto iti sideroblastic?

He kupu ngāwari noa iho, he āhuatanga onge tēnei e pā ana ki te hanga toto whero o ō tātou tinana, arā, ngā toto whero i roto i ō tātou toto. Mēnā kei a koe tēnei āhuatanga, he iti noa iho ō toto whero, ko te tikanga he mate toto kore toto tōu. Engari i te wā anō, he mea miharo, he nui hoki te rino kei a koe. He aha tēnei e tupu ai? Nā te mea kāore tō tinana e whakamahi ana i te rino e hiahiatia ana hei hanga toto whero tika.

Ko wai te mea tino pāngia e tēnei āhuatanga?

E rua ngā huarahi e puta ai tēnei āhuatanga e kiia nei ko te (Sideroblastic Anemia). Ko tētahi ko te congenital sideroblastic anemia, CSA rānei . Arā, ka whānau mai ētahi pēpi me tēnei mate. Ko tētahi ko te acquired sideroblastic anemia . Koinei te momo tino noa. Ka puta pea i ētahi atu mate e pā ana ki te toto, te whakamahinga o ētahi rongoā, te nui rawa rānei o te pānga ki ētahi kohuke.

Whakaarohia, ko ngā pēpi me ngā tamariki nohinohi e whānau mai ana me tēnei mate ka pāngia e ngā raruraru hauora e morearea ana ki te ora nā te nui rawa o te rino i roto i ō rātou tinana, e mōhiotia ana ko te "rahi rawa o te rino". Mēnā ka pāngia ngā pakeke e tēnei mate, ka pāngia rātou e ngā mate pēnei i te mate manawa me te mate ate cirrhosis.

He rongo pai tēnei! Ahakoa kāore e taea e ngā tākuta te whakaora katoa i te (Sideroblastic Anemia) whānau, kei reira ngā rongoā hei whakahaere i ngā tohu me te ārai i ngā raruraru nui. Heoi, ka taea te whakaora i ētahi momo (Sideroblastic Anemia) e puta ake ana i muri mai i te ao.

Ko tēnei mate, koinei te momo e kitea ana i te whānautanga, ka pā ki ngā pēpi, ki ngā tamariki nohinohi, tae atu ki ngā pakeke taitamariki. I ētahi wā he tino ngawari ngā tohu o te CSA. Nō reira, ahakoa i whānau mai koe me tēnei mate, tera pea ētahi tāngata kāore he raruraru hauora nui e pāngia ana e rātou tae noa ki te pakeketanga.

Ko te momo o muri mai, e kiia nei ko te "Acquired CSA," ka puta pinepine i roto i te hunga he mate toto e kiia nei ko te "myelodysplastic syndrome." Ka taea hoki te puta mai i te pānga ki ngā kohuke pēnei i te mata me te konutea, te whakamahinga o ētahi rongoā, tetahi mea rānei e pā ana ki te kaha o te tinana ki te whakamahi i te parahi.

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He aha te pānga o tēnei āhuatanga ki tōku tinana?

Ko te hunga e pāngia ana e te anemia sideroblastic ka whakaatu i ngā tohu o te anemia. Arā, ka tino ngenge rātou, kāore he take.Te ngenge, te uaua ki te manawa, me ētahi atu. Ehara i te mea koinā anake, ka pāngia rātou e te "anemia macrocytic" (ngā toto whero he nui ake i te mea noa) me te "anemia microcytic" (ngā toto whero he iti iho i te mea noa). Ka taea hoki e ēnei momo anemia te tohu i ētahi atu momo anemia.

He aha ngā take o te anemia sideroblastic?

E ai ki tā tātou i kōrero ai i mua, ka kitea pea tēnei i te whānautanga mai, ka puta rānei i muri mai nā tētahi atu mate hauora, te pānga ki ētahi konganuku, kohuke, rongoā rānei.

Hei mārama ki ngā pūtake o te anemia sideroblastic whānau (congenital SA), he mea āwhina kia mōhio ki te mahi a ō tātou pūtau toto whero.

He kupu whakataki poto ki ngā toto whero

Ko ngā toto whero te momo pūtau tino kitea i roto i ō tātou toto. He mea nui ngā toto whero hauora, kua pakari, hei kawe i te hāora ki ngā kiko o tō tātou tinana. Mā te āwhina o te pūmua e kiia nei ko te hemoglobin ka taea tēnei e ngā toto whero. Ko te hemoglobin te mea e hoatu ana te tae whero ki ngā toto whero.

Me hiahia ngā pūtau toto whero ki te rino hei hanga i te hemoglobin. I te nuinga o te wā, ka puta mai ngā pūtau take i roto i te hinu wheua. Ka whanake ēnei pūtau take hei pūtau toto whero kāore anō kia pakari, e kiia nei ko ngā erythrocytes. Kei roto i ēnei pūtau kāore anō kia pakari te nui o te hemoglobin me te rino e tika ana hei hanga i ngā pūtau toto whero hauora, pakari.

Engari, ki te mea he anemia sideroblastic tōu, kāore e taea e tō tinana te whakamahi i tēnei rino. E rua ngā raruraru ka puta mai i tēnei. Ki te kore he rino, kāore ō toto toto whero e hanga i te hemoglobin e ranea ana hei kawe i te hāora puta noa i tō tinana. I tētahi atu taha, ka kohia te rino kāore i whakamahia i roto i tō hinu wheua. Ka puta mai i tēnei he momo pūtau rerekē e kiia nei ko te sideroblast mowhiti . Ko te sideroblast he toto toto whero kāore anō kia pakari, he mowhiti rino kei te taha o tōna karihi. Ka taea e ngā tākuta te kite i ēnei mowhiti ina tirohia e rātou ngā pūtau take i roto i te hinu wheua i raro i te karuārai. Ko te ingoa o te anemia sideroblastic i ahu mai i ēnei mowhiti rino. E tohu ana ēnei mowhiti rino kei te rongoa ngā pūtau i te rino, kaua ki te whakamahi. Ka kiia tēnei kohi rino he nui rawa te rino . Ko tēnei nui rawa te rino te take o te maha o ngā raruraru hauora nui ka puta mai i te anemia sideroblastic.

He aha ngā momo o te Anemia Sideroblastic Congenital (CSA)?

E toru ngā momo o te SA whānau. Ka puta ēnei i ngā whakarerekētanga ira i roto i ētahi ira e pā ana ki te mahi a ngā toto toto whero. Me titiro tātou ki ēnei:

• Te anemia sideroblastic hono-X:Koinei te momo mate toto whānau tino noa. Ka puta mai i te whakarerekētanga ira i roto i te ira e hanga ana i tētahi whākōkī motuhake e kiia nei ko te "ALAS2", ka puta he ngoikore o te hemoglobin. Ko te hunga whai mate pēnei he kiri mā, he iti iho i te tikanga o ngā toto whero (microcytic). He nui rawa hoki te rino i roto i ō rātou tinana.
• Te mate anemia sideroblastic autosomal recessive (ARCSA): Koinei te tuarua o ngā momo tino kitea. Ka pāngia ngā pēpi me ngā tamariki nohinohi e te ARCSA. He mate kino tēnei ka taea te whakararu i te ora i ētahi wā. Ka puta ina nui rawa te nui o te rino i roto i te toto.
• Whaea: Tata ki te 20% o ngā tūroro CSA katoa ka taka ki tēnei kāwai. Nā te mea kua whakarerekētia te ira MT-ATP6, ka pā ki te mahi a ō mitochondria. (Ko ngā mitochondria ngā whekau i roto i ō tātou pūtau. Ko rātou te kawenga mō te pūtake pūngao matua o ngā pūtau. Ka hurihia e ngā mitochondria te pūngao mai i te kai ki tētahi āhua ka taea e ngā pūtau te whakamahi.)

He aha ngā momo mate toto sideroblastic kua riro mai ka puta i muri mai i te oranga?

E rua ngā momo anemia sideroblastic ka puta i muri mai i te ao - tuatahi me te tuarua. Ko te SA Tuatahi e pā ana ki te SA e pā ana ki te mate e kiia nei ko te myelodysplastic syndrome. Ko te SA Tuarua e pā ana ki te SA ka puta i muri i te pānga nui ki ētahi konganuku, matū, me ngā rongoā. Ko ngā mea ka puta ai te anemia sideroblastic tuarua ko:

• Waipiro: Ko te mate whakamahi waipiro te tino take o te anemia sideroblastic ka puta i muri mai.
• Te paihana konganuku taumaha: Kei roto i tēnei te paihana mata me te paihana āheniki.
• Te korenga o te huaora B: Ka āwhina te huaora B ki te hanga i tētahi wāhanga e kiia nei ko te heme, ka hurihia hei hemoglobin. Ko te heme te mea ka āwhina ki te kawe i te hāora.
• Te korenga o te parahi: Ka āwhina te parahi ki te hanga i tētahi whākōkī hei tiaki i te rino nui.
• Te nui rawa o te konutea: Ka pāngia te whakamahinga o te rino me te mimiti o te parahi e te tinana te nui o te konutea. Ka taea tēnei e ētahi tāngata te tango i ngā tāpiringa konutea.
• Ngā Rongoā: Ka taea e ētahi paturopi, chemotherapy, homoni, me ngā rongoā whakaiti parahi te whakaputa i te anemia sideroblastic tuarua. Ka rongoāhia e ngā tākuta tēnei momo SA mā te whakamātautau i ngā rongoā e tangohia ana e koe, me te tango i ngā rongoā e whakaarohia ana koia te take o te SA.

He aha ngā tohu o te anemia sideroblastic?

Pērā i ngā momo anemia maha, ko ngā tohu o te anemia sideroblastic ko:

• Ngenge nui:Ko te tikanga tēnei ka tino ngenge koe, ā, kāore e taea e koe te mahi i ngā mahi o ia rā.
• Te ngoikore o te manawa: He ahua ngoikore tēnei, he uaua rānei ki te manawa.
• Te tere o te manawa: He kare tēnei e tere rawa ana te pā o te manawa, he rerekē rānei te āhua.
• Te mamae o te upoko.

Tērā pea ka pāngia te hunga whai mate toto sideroblastic hono-X e ētahi atu tohu nā te korenga o te hemoglobin me te pikinga o ngā taumata rino i roto i te tinana. Ko ēnei tohu ko:

• Ate nui: He maha ngā mahi nui a tō ate i roto i te tinana.
• Te whēkau nui: He okana rite te rahi o tō whēkau ki te ringa, kei te puku o runga. Tērā pea kāore koe e kite kua nui ake tō whēkau i te mea noa, tērā pea ka pāngia koe e te mamae puhoi i tō puku o runga.
• Kiri parahi: Ki te nui rawa te rino e rongoatia ana e tō tinana, ka huri pea tō kiri ki te parauri parahi.
• Te mate huka kore e taea te whakahaere.

Me pēhea te tautuhi a ngā tākuta i te anemia sideroblastic?

Nā te mea ka kitea pea te anemia sideroblastic i te whānautanga, ka puta rānei i muri mai, ka whakamātautau tuatahi tō tākuta i a koe hei whakaū, hei whakakore rānei i te anemia sideroblastic kua whiwhi. Mēnā ka whakatau rātou ehara i te anemia sideroblastic kua whiwhi, ka mahi anō rātou i ētahi atu whakamātautau hei kimi i te momo anemia sideroblastic whānau kei a koe. Anei ētahi o ngā whakamātautau ka mahia pea e rātou:

• Te tatau toto katoa (CBC): Ka whakaatuhia e ngā hua CBC te rahi me te āhua o ngā pūtau i roto i tō toto, te maha o ngā pūtau toto hou e hangaia ana e tō tinana, ā, i roto i te take o te SA, e hia ngā pūtau toto whero kua pakari, kua kore rānei e pakari.
• Te whakamātautau toto ā-taha: He tikanga tēnei e whakamahia ana e ngā tākuta hei tirotiro i ngā pūtau toto. Ahakoa he mīhini te whakamahi i ētahi whakamātautau toto hei tātari i a rātou, i tēnei wā, ka tātarihia e ngā tākuta ngā pūtau toto i raro i te karuārai.
• Ngā rangahau rino: E whakaatu ana tēnei whakamātautau i ō taumata rino.
• Te tango i te hinu wheua: He tikanga tēnei hei tango tauira mai i te wāhanga wai o tō hinu wheua.
• Kohikohi wheua wheua: I roto i tēnei whakamātautau, ka tangohia e ngā tākuta he tauira iti o tō wheua wheua ka tirotirohia ngā pūtau wheua wheua.
• Whakamātautau ira:Mā te whakamātautau ira ka āwhina i te whakaū, te whakakore rānei i ngā āhuatanga ira motuhake. Ka āwhina hoki i a koe ki te mārama ki te tūponotanga o te tuku i te āhuatanga ki ō tamariki.

Me pēhea te rongoā a ngā tākuta i te anemia sideroblastic?

He rerekē ngā maimoatanga a ngā tākuta mō te anemia sideroblastic whānau me te anemia sideroblastic i whiwhi. He rerekē ēnei maimoatanga i runga i tō āhua, nō reira ka matapakihia e tō tākuta te maimoatanga pai rawa atu māu. Hei tauira, ka hoatu pea he huaora B6 me ngā rongoā whakaiti rino ki tētahi tangata he X-linked SA (CSA). Mena he paihana mata te take o te SA, ka rongoatia e tō tākuta te paihana mata. He pai ake te kōrero ki tō tākuta mō tēnei.

Me pēhea taku ārai i tēnei?

He maha ngā wā ka puta te mate anemia sideroblastic i te whakarerekētanga ira. Ahakoa kāore e taea te ārai i tēnei momo mate anemia sideroblastic whānau, ka taea te rongoā. Mena kei a koe te (CSA) hono-X, ā, he ngawari ō tohu, mena rānei kei tētahi o tō whānau (ngā mātua, ngā tuākana, teina rānei, ngā tamariki rānei) he (CSA), he mea pai kia pātai atu ki tō tākuta mō ngā whakamātautau ira.

Heoi anō, kei reira ētahi mea ka taea e koe te mahi hei ārai i te whanaketanga o ētahi momo CSA kua riro mai i muri mai. Kei roto i ēnei mahi:

• Te karo i te paihana mata, te paihana ā-tīni rānei.
• Mena kei te tango koe i ngā tāpiringa konutea mō ngā mea pēnei i te makariri noa, pātai atu ki tō tākuta mō te horopeta tika.
• Whakaitihia tō inu waipiro. Ka taea e te waipiro te arahi ki te mate toto sideroblastic. Ngāna kia whakaitihia te nui o te waipiro e inuhia ana e koe i ia rā. Ki te hiahia āwhina koe, pātai atu ki tō tākuta kia tūtohu mai i ngā kaupapa e tika ana.

He aha taku e tumanako atu ai mō tēnei āhuatanga?

Ko tō matapae ka whakawhirinaki ki te momo anemia sideroblastic kei a koe. Hei tauira, ki te mea he anemia sideroblastic whānau-hononga X tōu, ka rongoā pea tō tākuta i tō mate ki te huaora B6 me ngā rongoā whakaheke rino. Mena kua pāngia koe e te anemia sideroblastic, i puta mai i te paihana mata, ka rongoā pea tō tākuta i te paihana mata.

Me pēhea taku tiaki i ahau anō?

He maha ngā tāngata e pāngia ana e te anemia sideroblastic me aroturukitia tonutia ō rātou taumata rino kia kore ai e nui rawa te rino. Mena kua pāngia koe e te anemia sideroblastic i mua, pātai atu ki tō tākuta he aha tāu e taea ai te mahi hei ārai i te SA hou.

He mate toto onge te anemia sideroblastic. E mōhio ana ētahi tāngata he aha rātou i pāngia ai e te anemia sideroblastic, engari kāore pea ētahi atu. Mēnā he anemia sideroblastic tōu, me pātai atu pea koe ki tō tākuta i ēnei pātai:

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* He aha te momo (SA) kei a au?

* He aha i whiwhi ai ahau i te (SA)?

* He aha ngā kōwhiringa maimoatanga mōku?

* He aha ngā pānga taha o te maimoatanga?

* He aha ngā mea ka taea e au te tumanako i muri i te maimoatanga?

* Ka taea e au te tuku i te (SA) ki aku tamariki?

Nā, he aha ngā mea tino nui hei maumahara mā tātou i tēnei pūrākau?

He mate toto onge engari he mate toto kino pea te anemia sideroblastic. Ko te SA ka puta mai i tētahi mea e whakararuraru ana i te kaha o te tinana ki te whakaputa i ngā toto toto whero hauora. He nui rawa te rino i roto i ngā toto o te hunga whai SA. I te nuinga o te wā, he ngāwari te rongoā i tēnei taumahatanga rino. Heoi, i roto i ngā pēpi me ngā tamariki nohinohi i whānau mai me te SA, ka taea e te taumahatanga rino te whakararu i te ora.

Whakaarohia, mēnā i whānau mai tāu tamaiti me te mate toto sideroblastic, ka tīmata tonu ā rātou tākuta ki te rongoā i te mate. Ka tino whakamataku, ka taumaha hoki te whānautanga o tētahi pēpi, o tētahi tamaiti rānei e tino mate ana. E mārama ana ō tākuta ki tēnei, ā, ka mahi i ngā mea katoa hei āwhina i a koe me tāu tamaiti i te wā e rongoatia ana, me muri hoki i te rongoā. Nō reira, mēnā kei a koe, kei tētahi rānei o tō whānau ēnei tohu, he mea nui kia kite tonu i tētahi tākuta mō ētahi tohutohu.

Rino , anemia, sideroblasts, hinu wheua, hemoglobin, ira, mate toto