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Kāore koe i te tino mōhio mō ngā ira tangata o tō pēpi? Me kōrero tāua mō tēnei mate onge (Ambiguous Genitalia)

Kāore koe i te tino mōhio mō ngā ira tangata o tō pēpi? Me kōrero tāua mō tēnei mate onge (Ambiguous Genitalia)
Kāore e taea te whakapuaki i te harikoa o te whaea, o te pāpā rānei ina titiro ana ki tētahi pēpi hou. Heoi, he tino onge te wā ka pāngia ētahi mātua e tētahi raruraru nui. Arā, kāore e taea e rātou te whakatau mārama mēnā he kōtiro, he tama rānei te pēpi mā te titiro ki ngā ira tangata o te pēpi hou. E mōhio ana tātou he mea tino tairongo, he mea whakapouri hoki tēnei. Kāore koe i te mokemoke. I tēnei rā, kei te kōrero tātou mō ngā mea tino nui me mōhio koe i tēnei wā.

He aha te Ambiguous Genitalia?

He māmā noa iho, he āhuatanga tēnei e kitea ana i te whānautanga mai. I tēnei wā, he uaua ki te tautuhi i ngā ira tāne, ira wahine rānei o te tamaiti. I ētahi wā, kāore pea ngā okana e whanake tika, he āhuatanga tāne, he āhuatanga wahine rānei.
Ko te mea nui, ehara tēnei i te mate. He rerekētanga tēnei i roto i te whanaketanga ā-ira tangata. I roto i ngā kupu hauora, ka kiia tēnei ko "Ngā Rerekētanga o te Whanaketanga Ā-ira Tangata" ( DSD ).
He maha ngā wā, kāore te āhua o waho o te tamaiti e ōrite ki tōna ira tangata o roto (te kōpū, ngā ovaries, ngā rae rānei) me tōna ira ira. Ehara tēnei i te mate tino noa. E pāngia ana te 1 i roto i te 1,000 ki te 4,500 pēpi.

He aha ngā tohu ka kitea i roto i tēnei āhuatanga?

Ko te āhuatanga matua ko te āhua o ngā ira tangata o waho kāore e rite ki te ure, ki te tara rānei. Engari ka rerekē pea tēnei i ia tamaiti, i ia tamaiti. Kei te take i pā ki te whanaketanga ā-ira tangata. Kia tirohia me pēhea te kitea o tēnei āhuatanga i roto i ngā kōtiro me ngā tama i runga i te ira.
Ngā āhuatanga ka kitea mēnā he wahine ira te tamaiti (XX) Ngā āhuatanga ka kitea mēnā he tāne ira tāne te tamaiti (XY)
Ka nui ake te ure iti i te mea noa, ā, ka rite tōna āhua ki tētahi ure iti. Tērā pea he tino iti te ure (tērā pea he rite ki te ure iti te āhua), kāore rānei e tupu.
Kua piri ngā labia tetahi ki tetahi, he rite te āhua ki te kiriuhi.Kei te pūtake o te ure te pūaha o te ure, kaua ki te pito. (Ka kiia tēnei ko Hypospadias)
Te tūnga rerekē o te whakatuwheratanga o te urethra. He iti te kiriuhi ure, he tuwhera, ā, he rite tōna āhua ki te labia.
He wāhi kei roto i te labia ka taea te pohehe he ngā rae. Kāore anō ngā rae kia heke ki roto i te kiriuhi.
Hei tāpiritanga, ka kitea pea ngā kore taurite o ngā homoni, te whakaroa, te wawe rānei o te pakeketanga, me ētahi atu āhuatanga i muri mai.

Me pēhea te tautuhi i tēnei mate? (Tautuhinga)

He maha ngā wā ka tātaritangahia te mate e te tīma hauora i te whānautanga. I ētahi wā, ka taea e ngā matawai i te wā e hapu ana te hoatu he tohu, engari kāore e whakaūtia kia whānau rā anō te pēpi. Ka pātai tuatahi tō tākuta me te tīma hauora mō te hītori hauora o tō whānau. Kātahi ka hiahiatia ētahi whakamātautau hei whakatau i te ira tūturu o te pēpi me te take tuturu o te mate.
  • Ngā whakamātautau toto : Tirohia ngā ira-chromosome (XX, XY rānei) o te pēpi me ngā taumata homoni .
  • Ngā whakamātautau whakaahua : Mā ngā whakamātautau pēnei i te ultrasound , te X-ray , te MRI rānei ka tirohia ngā whekau o roto i te tinana o te pēpi, pēnei i te kōpū , ngā ovaries, ngā testicles rānei.
  • Ngā whakamātautau motuhake: I ētahi wā, ka tangohia he wahi iti o te kiko mai i ngā ira tangata hei tirotiro (`Biopsy`) ka whakamahia rānei he kāmera iti hei tirotiro i roto i te tinana (`Laparoscopy`).

He aha te take o tēnei?

Ka puta tēnei āhuatanga ina he ārai i te whanaketanga o ngā ira tangata i ngā wāhanga tōmua o te whanaketanga o te pēpi i roto i te kōpū. He maha ngā take matua:
  • Ngā raruraru homoni:Kāore te kukune tāne ira (XY) e whiwhi ana i te nui o ngā homoni tāne hei whakawhanake i ngā ira tāne, kāore rānei te kukune wahine ira (XX) e pāngia ana e ngā homoni tāne.
  • Ngā huringa ira: Ngā whakarerekētanga ira i roto i ētahi ira e pā ana ki te whanaketanga ā-ira tangata ('ngā ira kua whakarerekētia').
  • Ngā rerekētanga o te ira tangata: He rerekētanga kei roto i ngā ira tangata o te pēpi, pērā i te ngaronga, te pikinga rānei o te ira tangata.

Ngā āhuatanga mōrearea

Tērā pea he pānga anō tō hītori whānau. Mena kua pāngia tētahi o tō whānau e ēnei āhuatanga e whai ake nei, tera pea ka paku teitei ake tō mōrearea:
  • Ngā matenga o ngā pēpi kāore i te mōhiotia te take.
  • Tērā pea ka pāngia ngā wāhine o te whānau e te uauatanga ki te whānau tamariki, te mutu o te paheketanga, te tupu nui rawa rānei o te huruhuru i te mata.
  • He rerekē ngā wāhanga o te tinana o tētahi atu o te whānau.
  • Ngā āhuatanga rerekē i te wā o te pakeketanga.
  • Ngā mate tuku iho e pā ana ki ngā repe adrenal, pērā i te Congenital Adrenal Hyperplasia (CAH) .
Mena kei te whakaaro koe kia whānau he tamaiti, ā, he hītori whānau tōu mō tēnei mate, he mea tino nui kia kite koe i tētahi tohunga me te kōrero mōna.

Me pēhea te maimoatanga, ā, he aha te mahi i muri mai?

Nā te mea he take uaua, he take tairongo hoki tēnei, kāore ngā whakatau e mahia ana e te tākuta kotahi anake. Mā tētahi rōpū tohunga koe me tāu tamaiti e āwhina. Ko te tikanga, kei roto i tēnei rōpū:
  • Te Tākuta Whānau Hou: He tākuta e tohunga ana ki ngā pēpi whānau hou.
  • Endocrinologist: He tākuta e tohunga ana ki ngā homoni.
  • Tohunga ira: He tohunga ki ngā ira me ngā chromosomes.
  • Tohunga Urologist: He tohunga ki ngā pūnaha mimi me te pūnaha whakaputa uri.
  • Taote pokanga: He tākuta e mahi ana i te pokanga mēnā e tika ana.
  • Kaimātai Hinengaro: He tohunga e tautoko ana i a koe me tāu tamaiti.
Mā tēnei tīma koe e āwhina ki te whakatau i te ira tangata tino tika mō tāu tamaiti i runga i ngā hua o te whakamātautau. Tērā pea ka uru atu ki te maimoatanga te rongoā whakakapinga homoni , te pokanga hanga anō rānei. Tērā pea ka mahia ngā pokanga e tika ana mō te hauora, pērā i te whakatika i te whakatuwheratanga o te ara mimi, i te wā pēpi tonu. Heoi, ka taea te whakaroa i ngā pokanga whakapaipai kia tae rā anō te tamaiti ki te pakeke ka mārama, ā, ka taea e ngā mātua me te tīma hauora te whakatau tahi mēnā ka whakaroahia te tukanga i runga i ō rātou hiahia.

Te heke mai o te tamaiti

He mea maori te pātai i a koe pēnei i te, "Ka taea e taku tamaiti te whānau tamariki ā muri ake nei?" me te "Ka puta he take mō tōna tuakiri ira tangata?"
  • Te whānau tamariki:I runga i te pūtake o te mate, ka taea pea e ētahi tāngata te whānau tamariki ā muri ake nei. Hei tauira, ko ngā kōtiro he Congenital Adrenal Hyperplasia ka taea pea te hapu i muri i te maimoatanga homoni.
  • Tuakiri Ira Tangata: Kāore ngā ira tangata anake e whakatau i te tuakiri ira tangata o te tangata. He pānga anō hoki tā te mahi roro me ngā āhuatanga pāpori. Nō reira, he mea nui kia kōrerohia tēnei ki tētahi tīma hauora mātau, kia whakatau ai i tētahi mea hei whakarato i te oranga pai rawa atu mō te tamaiti.
Ko te mea nui ko te tiaki i te hauora hinengaro o tāu tamaiti i a ia e tipu ake ana. Kei reira tonu ngā tākuta me ngā kaiwhakatakoto whakaaro mātau hei tautoko i a koe me tāu tamaiti i tēnei haerenga.

Karere Tangohia ki te Kāinga

  • He mate onge te Ambiguous Genitalia, ehara i te he o ngā mātua te take.
  • Kia kitea rā anō tēnei mate, he mea nui kia rapu āwhina i tētahi tīma hauora motuhake. Kaua e whakatau ko koe anake.
  • He whakatau uaua rawa te hoatu i tētahi tuakiri ira tangata ki tētahi tamaiti. Me whai whakaaro ki ngā pūrongo hauora me ngā tohutohu katoa.
  • He mea nui ake i te maimoatanga te tautoko kare ā-roto me te aroha e hoatu ana ki te tamaiti me te whānau katoa.
  • Kōrerotia marietia ki tō tākuta mō ngā pātai, ngā wehi, ngā ruarua rānei kei a koe.
Ngā Ira Tangata Korekore, DSD, Ira Tangata o te Pēpi, Ngā Homoni, Ngā Ira Tangata, Ngā Mate Ira, Te Whakarahi Adrenal Whanau
⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Kāore koe i te tino mōhio mō ngā ira tangata o tō pēpi? Me kōrero tāua mō tēnei mate onge (Ambiguous Genitalia)

Kāore koe i te tino mōhio mō ngā ira tangata o tō pēpi? Me kōrero tāua mō tēnei mate onge (Ambiguous Genitalia)

Kāore e taea te whakapuaki i te harikoa o te whaea, o te pāpā rānei ina titiro ana ki tētahi pēpi hou. Heoi, he tino onge te wā ka pāngia ētahi mātua e tētahi raruraru nui. Arā, kāore e taea e rātou te whakatau mārama mēnā he kōtiro, he tama rānei te pēpi mā te titiro ki ngā ira tangata o te pēpi hou. E mōhio ana tātou he mea tino tairongo, he mea whakapouri hoki tēnei. Kāore koe i te mokemoke. I tēnei rā, kei te kōrero tātou mō ngā mea tino nui me mōhio koe i tēnei wā.

He aha te Ambiguous Genitalia?

He māmā noa iho, he āhuatanga tēnei e kitea ana i te whānautanga mai. I tēnei wā, he uaua ki te tautuhi i ngā ira tāne, ira wahine rānei o te tamaiti. I ētahi wā, kāore pea ngā okana e whanake tika, he āhuatanga tāne, he āhuatanga wahine rānei.
Ko te mea nui, ehara tēnei i te mate. He rerekētanga tēnei i roto i te whanaketanga ā-ira tangata. I roto i ngā kupu hauora, ka kiia tēnei ko "Ngā Rerekētanga o te Whanaketanga Ā-ira Tangata" ( DSD ).
He maha ngā wā, kāore te āhua o waho o te tamaiti e ōrite ki tōna ira tangata o roto (te kōpū, ngā ovaries, ngā rae rānei) me tōna ira ira. Ehara tēnei i te mate tino noa. E pāngia ana te 1 i roto i te 1,000 ki te 4,500 pēpi.

He aha ngā tohu ka kitea i roto i tēnei āhuatanga?

Ko te āhuatanga matua ko te āhua o ngā ira tangata o waho kāore e rite ki te ure, ki te tara rānei. Engari ka rerekē pea tēnei i ia tamaiti, i ia tamaiti. Kei te take i pā ki te whanaketanga ā-ira tangata. Kia tirohia me pēhea te kitea o tēnei āhuatanga i roto i ngā kōtiro me ngā tama i runga i te ira.
Ngā āhuatanga ka kitea mēnā he wahine ira te tamaiti (XX) Ngā āhuatanga ka kitea mēnā he tāne ira tāne te tamaiti (XY)
Ka nui ake te ure iti i te mea noa, ā, ka rite tōna āhua ki tētahi ure iti. Tērā pea he tino iti te ure (tērā pea he rite ki te ure iti te āhua), kāore rānei e tupu.
Kua piri ngā labia tetahi ki tetahi, he rite te āhua ki te kiriuhi.Kei te pūtake o te ure te pūaha o te ure, kaua ki te pito. (Ka kiia tēnei ko Hypospadias)
Te tūnga rerekē o te whakatuwheratanga o te urethra. He iti te kiriuhi ure, he tuwhera, ā, he rite tōna āhua ki te labia.
He wāhi kei roto i te labia ka taea te pohehe he ngā rae. Kāore anō ngā rae kia heke ki roto i te kiriuhi.
Hei tāpiritanga, ka kitea pea ngā kore taurite o ngā homoni, te whakaroa, te wawe rānei o te pakeketanga, me ētahi atu āhuatanga i muri mai.

Me pēhea te tautuhi i tēnei mate? (Tautuhinga)

He maha ngā wā ka tātaritangahia te mate e te tīma hauora i te whānautanga. I ētahi wā, ka taea e ngā matawai i te wā e hapu ana te hoatu he tohu, engari kāore e whakaūtia kia whānau rā anō te pēpi. Ka pātai tuatahi tō tākuta me te tīma hauora mō te hītori hauora o tō whānau. Kātahi ka hiahiatia ētahi whakamātautau hei whakatau i te ira tūturu o te pēpi me te take tuturu o te mate.
  • Ngā whakamātautau toto : Tirohia ngā ira-chromosome (XX, XY rānei) o te pēpi me ngā taumata homoni .
  • Ngā whakamātautau whakaahua : Mā ngā whakamātautau pēnei i te ultrasound , te X-ray , te MRI rānei ka tirohia ngā whekau o roto i te tinana o te pēpi, pēnei i te kōpū , ngā ovaries, ngā testicles rānei.
  • Ngā whakamātautau motuhake: I ētahi wā, ka tangohia he wahi iti o te kiko mai i ngā ira tangata hei tirotiro (`Biopsy`) ka whakamahia rānei he kāmera iti hei tirotiro i roto i te tinana (`Laparoscopy`).

He aha te take o tēnei?

Ka puta tēnei āhuatanga ina he ārai i te whanaketanga o ngā ira tangata i ngā wāhanga tōmua o te whanaketanga o te pēpi i roto i te kōpū. He maha ngā take matua:
  • Ngā raruraru homoni:Kāore te kukune tāne ira (XY) e whiwhi ana i te nui o ngā homoni tāne hei whakawhanake i ngā ira tāne, kāore rānei te kukune wahine ira (XX) e pāngia ana e ngā homoni tāne.
  • Ngā huringa ira: Ngā whakarerekētanga ira i roto i ētahi ira e pā ana ki te whanaketanga ā-ira tangata ('ngā ira kua whakarerekētia').
  • Ngā rerekētanga o te ira tangata: He rerekētanga kei roto i ngā ira tangata o te pēpi, pērā i te ngaronga, te pikinga rānei o te ira tangata.

Ngā āhuatanga mōrearea

Tērā pea he pānga anō tō hītori whānau. Mena kua pāngia tētahi o tō whānau e ēnei āhuatanga e whai ake nei, tera pea ka paku teitei ake tō mōrearea:
  • Ngā matenga o ngā pēpi kāore i te mōhiotia te take.
  • Tērā pea ka pāngia ngā wāhine o te whānau e te uauatanga ki te whānau tamariki, te mutu o te paheketanga, te tupu nui rawa rānei o te huruhuru i te mata.
  • He rerekē ngā wāhanga o te tinana o tētahi atu o te whānau.
  • Ngā āhuatanga rerekē i te wā o te pakeketanga.
  • Ngā mate tuku iho e pā ana ki ngā repe adrenal, pērā i te Congenital Adrenal Hyperplasia (CAH) .
Mena kei te whakaaro koe kia whānau he tamaiti, ā, he hītori whānau tōu mō tēnei mate, he mea tino nui kia kite koe i tētahi tohunga me te kōrero mōna.

Me pēhea te maimoatanga, ā, he aha te mahi i muri mai?

Nā te mea he take uaua, he take tairongo hoki tēnei, kāore ngā whakatau e mahia ana e te tākuta kotahi anake. Mā tētahi rōpū tohunga koe me tāu tamaiti e āwhina. Ko te tikanga, kei roto i tēnei rōpū:
  • Te Tākuta Whānau Hou: He tākuta e tohunga ana ki ngā pēpi whānau hou.
  • Endocrinologist: He tākuta e tohunga ana ki ngā homoni.
  • Tohunga ira: He tohunga ki ngā ira me ngā chromosomes.
  • Tohunga Urologist: He tohunga ki ngā pūnaha mimi me te pūnaha whakaputa uri.
  • Taote pokanga: He tākuta e mahi ana i te pokanga mēnā e tika ana.
  • Kaimātai Hinengaro: He tohunga e tautoko ana i a koe me tāu tamaiti.
Mā tēnei tīma koe e āwhina ki te whakatau i te ira tangata tino tika mō tāu tamaiti i runga i ngā hua o te whakamātautau. Tērā pea ka uru atu ki te maimoatanga te rongoā whakakapinga homoni , te pokanga hanga anō rānei. Tērā pea ka mahia ngā pokanga e tika ana mō te hauora, pērā i te whakatika i te whakatuwheratanga o te ara mimi, i te wā pēpi tonu. Heoi, ka taea te whakaroa i ngā pokanga whakapaipai kia tae rā anō te tamaiti ki te pakeke ka mārama, ā, ka taea e ngā mātua me te tīma hauora te whakatau tahi mēnā ka whakaroahia te tukanga i runga i ō rātou hiahia.

Te heke mai o te tamaiti

He mea maori te pātai i a koe pēnei i te, "Ka taea e taku tamaiti te whānau tamariki ā muri ake nei?" me te "Ka puta he take mō tōna tuakiri ira tangata?"
  • Te whānau tamariki:I runga i te pūtake o te mate, ka taea pea e ētahi tāngata te whānau tamariki ā muri ake nei. Hei tauira, ko ngā kōtiro he Congenital Adrenal Hyperplasia ka taea pea te hapu i muri i te maimoatanga homoni.
  • Tuakiri Ira Tangata: Kāore ngā ira tangata anake e whakatau i te tuakiri ira tangata o te tangata. He pānga anō hoki tā te mahi roro me ngā āhuatanga pāpori. Nō reira, he mea nui kia kōrerohia tēnei ki tētahi tīma hauora mātau, kia whakatau ai i tētahi mea hei whakarato i te oranga pai rawa atu mō te tamaiti.
Ko te mea nui ko te tiaki i te hauora hinengaro o tāu tamaiti i a ia e tipu ake ana. Kei reira tonu ngā tākuta me ngā kaiwhakatakoto whakaaro mātau hei tautoko i a koe me tāu tamaiti i tēnei haerenga.

Karere Tangohia ki te Kāinga

  • He mate onge te Ambiguous Genitalia, ehara i te he o ngā mātua te take.
  • Kia kitea rā anō tēnei mate, he mea nui kia rapu āwhina i tētahi tīma hauora motuhake. Kaua e whakatau ko koe anake.
  • He whakatau uaua rawa te hoatu i tētahi tuakiri ira tangata ki tētahi tamaiti. Me whai whakaaro ki ngā pūrongo hauora me ngā tohutohu katoa.
  • He mea nui ake i te maimoatanga te tautoko kare ā-roto me te aroha e hoatu ana ki te tamaiti me te whānau katoa.
  • Kōrerotia marietia ki tō tākuta mō ngā pātai, ngā wehi, ngā ruarua rānei kei a koe.
Ngā Ira Tangata Korekore, DSD, Ira Tangata o te Pēpi, Ngā Homoni, Ngā Ira Tangata, Ngā Mate Ira, Te Whakarahi Adrenal Whanau
⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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