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He aha te Central Pontine Myelinolysis? Kia mārama tātou.

MBBS

Medically reviewed by MBBS — Updated on Jul 15, 2026 · 10 min read

He aha te Central Pontine Myelinolysis? Kia mārama tātou.
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Mena kei te mate tetahi, ā, kei te hōhipera ia me te iti o te wai me te tote o te tinana, ka hoatu e ngā tākuta he tote tote ki a ia hei whakakapi i te ngoikore. He mea noa tēnā. Engari i mōhio koe i ētahi wā, ki te piki tere, ohorere hoki te iti o te konutai o te tinana, ka taea te kino i te roro? Koinei te mea e kiia nei e tātou he mate onge engari he kino e kiia nei ko te Central Pontine Myelinolysis. Ahakoa he ahua uaua te ingoa, me kōrero noa iho.

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He kīanga māmā noa iho, he aha te momo āhuatanga o tēnei?

He mate tēnei e pā ana ki te pūnaha io. Ka haere ngā tohu hiko e hiahiatia ana e te tinana mā roto i ngā pūtau io (ngā neuron) i roto i tō tātou roro. He hipoki tiaki kei te taha o ēnei pūtau io. Ka kiia e mātou ko te pūkahu myelin . He rite ki te pūkahu kirihou e karapoti ana i te waea hiko . Mā tēnei pūkahu myelin ka taea e ngā tohu hiko te haere tere me te kore he arai.

Ka puta te Central Pontine Myelinolysis (CPM) ina pakaru ngā pūkahu myelin i tētahi wāhi motuhake o te roro, arā, ko ngā pons . Ka pā pea tēnei kino ki te mahi a ngā wāhanga rerekē o te tinana.

I ētahi wā, i roto i te 10% pea o ngā take, ka pā tēnei kino ki ngā pons anake, engari ki ētahi atu wāhanga o te roro. Nō reira, e mōhiotia whānuitia ana tēnei āhuatanga e tētahi atu ingoa whānui. Ko te Osmotic Demyelination Syndrome (ODS) tēnā.

Ehara tēnei āhuatanga i te mea noa, engari kua kitea ko te 2.5% o ngā tūroro e whakaurua ana ki ngā wāhanga tiaki nui (ICU) kei te mōrearea ki te whakawhanake i te ODS.

He aha te take o tēnei āhuatanga?

Ko te take matua mō tēnei, ina tino iti te taumata konutai o te tinana (arā, ko te tote kei roto i te tote e kainga ana e tātou), ka piki ohorere, ka tere tonu hoki . Ka tino piki ake tēnei mōrearea ina neke atu i te rua ngā rā e iti ana te taumata konutai o te tinana, ā, kei te tukuna he maimoatanga.

Ko te mea nui, ehara tēnei i te mea e kainga ana, e inuhia ana rānei e tātou. He mea tēnei ka tupu pea i roto i te hōhipera, ina tukuna te konutai mā roto i te uaua , arā, mā te tote, hei maimoatanga hauora.

Whakaarohia pēnei. He maha ngā rā e ruaki ana te tangata, e pāngia ana rānei e te mate korere. Kātahi ka ngaro te wai anake, tae atu ki ngā tote pērā i te konutai i roto i tōna tinana. Ina tae mai rātou ki te hōhipera, he tino iti te taumata o te konutai. Ināianei kei te hoatu e ngā tākuta he tote ki a rātou hei ngana ki te whakahoki i te taumata o te konutai ki te noho noa. Heoi, ki te kore rātou e mōhio ki ngā āhuatanga mōrearea kē atu o te tūroro, tera pea ka taea e rātou te whakanui ake i te taumata o te konutai kia tere ake.

Ina tupu tēnā, ka turuturu ohorere te wai i roto i ngā pūtau roro i waho o ngā pūtau. Ka mimiti ngā pūtau pērā i te karepe maroke. Nā tēnei huringa ohorere ka pakaru ngā pūkahu myelin i kōrerotia e tātou.

Ko wai kei te mōrearea nui ake?

Ehara i te mea ka pāngia te katoa e tēnei mate ina tere rawa te pikinga o ō rātou taumata konutai , engari he nui ake te mōrearea o ētahi tāngata.

Rōpū mōrearea Whakaahuatanga
Ngā tāngata e whakamahi ana i te waipiro He mea noa te kore kai me te kore taurite o te tote i roto i te hunga e inu waipiro ana mō te wā roa.
Ngā tūroro whakawhitinga ate He tino teitei tēnei mōrearea mō te hunga kua oti te pokanga whakawhitinga ate.
Hyperemesis i te wā e hapu ana Ka taea e te Hyperemesis Gravidarum, he āhua o te ruaki tonu i te wā e hapū ana, te whakaheke nui i ngā taumata tote o te tinana.
Ngā mate roa Mā tētahi atu āhuatanga hauora roa e ngoikore ai te tinana, e hua ai rānei te kore kai pai ka nui ake te mōrearea.

He aha ngā tohu o tēnei mate?

Ko te tikanga ka tīmata ngā tohu i roto i ngā rā e rua, e toru rānei i muri i te whakatikatika i ngā taumata konutai o te tinana. Tērā ētahi tohu ka puta wawe mai, me ētahi tohu ka puta i muri i ngā wiki.

Ngā tohu CPM
Ngā tohu tōmua (i roto i ngā rā 2-3)
  • Te ngoikore o ngā uaua o ngā peka
  • Te uaua ki te kōrero (te koretake o te reo)
  • Te uaua ki te horomi
  • Ngā wiri me te pararutiki (paralsy)
  • Ka taea e ia te arahi ki te huringa o te hinengaro, tae atu ki te koma.
  • I ētahi wā onge, ka taea te mate.
Ngā tohu ka puta ake i muri mai (i muri i ētahi wiki, i ētahi marama rānei)
  • Te pararutiki o ngā ringa, o ngā waewae rānei
  • Te pakari o te tinana me ngā hononga
  • He uaua ki te taurite o te tinana me te whakataurite i ngā nekehanga
  • Te hekenga o te kare ā-roto o te pā me te wera i roto i te tinana
  • Ngā ngoikoretanga o te mahi hinengaro

Kaua e wehi. Ahakoa i whakaarohia i te tuatahi he teitei te reiti mate, i whakatauhia tēnā mā te tātaritanga tūpāpaku. E ai ki ngā raraunga hou, 94% o te hunga e pāngia ana e te mate ka ora . Waihoki, i waenga i te 25% me te 40% o rātou ka ora katoa . Heoi, i waenga i te 25% me te 30% ka waiho pea me ētahi hauātanga tuturu.

Me pēhea te kitenga a ngā tākuta i tēnei?

Ko te huarahi pai ki te tautuhi i tēnei mate ko te whakamahi i te matawai MRI (Magnetic Resonance Imaging) . Ka tirohia e tō tākuta ngā whakaahua MRI o tō roro, ka tirohia mēnā he huringa motuhake e tohu ana i te kino o ngā pūkahu myelin.

I ētahi wā, kāore tēnei kino e kitea tonutia i te MRI, nō reira ka tono pea tō tākuta kia mahia anō he MRI i roto i te wiki, e rua rānei.

Ka rite te CPM ki ētahi atu mate i runga i ngā whakaahua MRI. Nō reira, ka tino tupato ngā tākuta kei pohehe tēnei mate ki ēnei mate e whai ake nei.

  • Te Mate Pukupuku Maha
  • Te mumura o te roro (te mate pūnaha ārai mate, te mate pukupuku rānei)
  • Te vasculitis o te pūnaha io matua
  • Ētahi momo mate pukupuku

Ki te kore e taea e te MRI anake te whakaatu mārama i te kino, ka whakahaerehia e te tākuta he whakamātautau neurological hohonu ake. Tērā pea kei roto i tēnei ko ngā whakamātautau e ine ana i ngā tohu hiko i roto i te roro, pērā i te EEG (electroencephalography).

Me pēhea te rongoā? Ko te ārai te mea pai rawa atu!

Ko te tikanga, ko te maimoatanga matua mō te Central Pontine Myelinolysis ko te aukati i te puta mai o te mate .

He mea tino nui kia mōhio tō tīma hauora mō ngā āhuatanga mōrearea kei a koe (hei tauira, mēnā kei te inu waipiro koe, mēnā he mate hauora anō ōu) kia taea ai e rātou te whakapiki i ō taumata konutai me te haumaru, me te āta haere.

Ki te pāngia koe e tēnei mate, ka whakawhirinaki te maimoatanga ki ngā tohu e pā ana ki a koe. I roto i te nuinga o ngā wā, ka hiahiatia he marama o te whakaora tinana me ētahi atu maimoatanga whakaora.

Mena ka puta he tohu rite ki te mate a Parkinson, pērā i te wiri, ka tohua pea e tō tākuta he rongoā dopaminergic .

I a koe e noho ana i te hōhipera, he mea nui anō hoki te ārai i ngā raruraru tuarua o te maimoatanga. Ka aroturuki tonu te tīma hauora i ngā mea pēnei i:

  • Te whakawhirinaki ki te mīhini manawa
  • Ngā mate urutā mimi
  • Pūkahukahu
  • Te toto totoka i roto i te uaua (Te toto totoka o te uaua hohonu)
  • Te ngoikore o te uaua

Kei te haere tonu ngā whakamātautau haumanu mō tēnei mate, ā, ka tūtohu pea tō tākuta i tētahi.

Karere Tangohia ki te Kāinga

  • Ko te Central Pontine Myelinolysis (CPM) he mate kino e puta mai ana i te pakaru o ngā pukupuku myelin i roto i te roro nā te pikinga ohorere me te tere o te iti o te konutai (tote) i roto i te tinana.
  • Ko te rongoā pai rawa atu mō tēnei ko te ārai . I mua i te whiwhinga i tētahi rongoā, kōrerotia tō hītori hauora katoa ki tō tākuta, inā koa mō te whakamahinga waipiro, mō ētahi atu mate rānei.
  • Ki te puta tēnei āhuatanga, he nui te tūponotanga ka ora, engari ka roa pea te wā e ora katoa ai, tae atu ki te whakaora tinana.
  • Ki te pāngia koe, tētahi atu rānei e mōhiotia ana e koe, e te tangata rānei, e ēnei tohu, inā koa i muri i te whai i te rongoā whakakapinga konutai i te hōhipera, me whakamōhio tonu atu ki te tākuta.
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Ko wai kei te mōrearea nui ake?

Ehara i te mea ka pāngia te katoa e tēnei mate ina tere rawa te pikinga o ō rātou taumata konutai , engari he nui ake te mōrearea o ētahi tāngata.

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